Antiprion drugs 6-aminophenanthridine and guanabenz reduce PABPN1 toxicity and aggregation in oculopharyngeal muscular dystrophy
Nicolas Barbezier, Aymeric Chartier, Yannick Bidet, Anja Buttstedt, Cécile Voisset, Hervé Galons, Marc Blondel, Elisabeth Schwarz, Martine SimoneligVolume:
3
Year:
2011
Language:
english
Pages:
15
DOI:
10.1002/emmm.201000109
File:
PDF, 696 KB
english, 2011