Reduced expression of ATP7B affected by Wilson disease–causing mutations is rescued by pharmacological folding chaperones 4-phenylbutyrate and curcumin
Peter V. E. van den Berghe, Janneke M. Stapelbroek, Elmar Krieger, Prim de Bie, Stan F. J. van de Graaf, Reinoud E. A. de Groot, Ellen van Beurden, Ellen Spijker, Roderick H. J. Houwen, Ruud Berger, LVolume:
50
Year:
2009
Language:
english
Pages:
13
DOI:
10.1002/hep.23209
File:
PDF, 1.86 MB
english, 2009