Straight-Chain Acyl-CoA Oxidase Knockout Mouse Accumulates Extremely Long Chain Fatty Acids from α-Linolenic Acid: Evidence for Runaway Carousel-Type Enzyme Kinetics in Peroxisomal β-Oxidation Diseases
Juan P. Infante, Carolyn L. Tschanz, Natacha Shaw, Anthony L. Michaud, Peter Lawrence, J.Thomas BrennaVolume:
75
Year:
2002
Language:
english
Pages:
120
DOI:
10.1006/mgme.2001.3279
File:
PDF, 129 KB
english, 2002