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Rescue of mutant α-galactosidase A in the endoplasmic reticulum by 1-deoxygalactonojirimycin leads to trafficking to lysosomes
Ryoji Hamanaka, Tetsuji Shinohara, Shinji Yano, Miki Nakamura, Aiko Yasuda, Shigeo Yokoyama, Jian-Qiang Fan, Kunito Kawasaki, Makoto Watanabe, Satoshi IshiiVolume:
1782
Year:
2008
Language:
english
Pages:
414
DOI:
10.1016/j.bbadis.2008.03.001
File:
PDF, 825 KB
english, 2008