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Miglustat (NB-DNJ) works as a chaperone for mutated acid β-glucosidase in cells transfected with several Gaucher disease mutations
Pilar Alfonso, Sandra Pampín, Jorge Estrada, José Carlos Rodríguez-Rey, Pilar Giraldo, Javier Sancho, Miguel PocovíVolume:
35
Year:
2005
Language:
english
Pages:
277
DOI:
10.1016/j.bcmd.2005.05.007
File:
PDF, 285 KB
english, 2005