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DLHex-DGJ, a novel derivative of 1-deoxygalactonojirimycin with pharmacological chaperone activity in human GM1-gangliosidosis fibroblasts
Katrin Fantur, Doris Hofer, Georg Schitter, Andreas J. Steiner, Bettina M. Pabst, Tanja M. Wrodnigg, Arnold E. Stütz, Eduard PaschkeVolume:
100
Year:
2010
Language:
english
DOI:
10.1016/j.ymgme.2010.03.019
File:
PDF, 400 KB
english, 2010