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Fibulin-4 E57K Knock-in Mice Recapitulate Cutaneous, Vascular and Skeletal Defects of Recessive Cutis Laxa 1B with both Elastic Fiber and Collagen Fibril Abnormalities
Igoucheva, Olga, Alexeev, Vitali, Halabi, Carmen M., Adams, Sheila M., Stoilov, Ivan, Sasaki, Takako, Arita, Machiko, Donahue, Adele, Mecham, Robert P., Birk, David E., Chu, Mon-LiVolume:
290
Language:
english
Journal:
Journal of Biological Chemistry
DOI:
10.1074/jbc.M115.640425
Date:
August, 2015
File:
PDF, 10.20 MB
english, 2015