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Pharmacological inhibition of carnitine palmitoyltransferase 1 restores mitochondrial oxidative phosphorylation in human trifunctional protein deficient fibroblasts
Lefort, Bruno, Gouache, Elodie, Acquaviva, Cécile, Tardieu, Marine, Benoist, Jean François, Dumas, Jean-François, Servais, Stéphane, Chevalier, Stéphan, Vianey-Saban, Christine, Labarthe, FrançoisVolume:
1863
Language:
english
Journal:
Biochimica et Biophysica Acta (BBA) - Molecular Basis of Disease
DOI:
10.1016/j.bbadis.2017.04.005
Date:
June, 2017
File:
PDF, 1004 KB
english, 2017