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4-PBA ameliorates cellular homeostasis in fibroblasts from osteogenesis imperfecta patients by enhancing autophagy and stimulating protein secretion
Roberta, Besio, Giusy, Iula, Nadia, Garibaldi, Lina, Cipolla, Simone, Sabbioneda, Marco, Biggiogera, Marini Joan, C., Antonio, Rossi, Antonella, ForlinoLanguage:
english
Journal:
Biochimica et Biophysica Acta (BBA) - Molecular Basis of Disease
DOI:
10.1016/j.bbadis.2018.02.002
Date:
February, 2018
File:
PDF, 14.72 MB
english, 2018