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Cellular stress due to impairment of collagen prolyl hydroxylation complex is rescued by the chaperone 4-phenylbutyrate
Besio, Roberta, Garibaldi, Nadia, Leoni, Laura, Cipolla, Lina, Sabbioneda, Simone, Biggiogera, Marco, Mottes, Monica, Aglan, Mona, Otaify, Ghada A., Temtamy, Samia A., Rossi, Antonio, Forlino, AntonelVolume:
12
Language:
english
Journal:
Disease Models & Mechanisms
DOI:
10.1242/dmm.038521
Date:
June, 2019
File:
PDF, 7.41 MB
english, 2019