Volume 12

Journal of Cystic Fibrosis

Volume 12

1

Pseudomonas aeruginosa serology and risk for re-isolation in the EPIC trial

Anstead, Michael, Heltshe, Sonya L., Khan, Umer, Barbieri, Joseph T., Langkamp, Markus, Döring, Gerd, Dharia, Shimoni, Gibson, Ronald L., Treggiari, Miriam M., Lymp, James, Rosenfeld, Margaret, Ramsey

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 444 KB

english, 2013

2

Iron accumulates in the lavage and explanted lungs of cystic fibrosis patients

Ghio, Andrew J., Roggli, Victor L., Soukup, Joleen M., Richards, Judy H., Randell, Scott H., Muhlebach, Marianne S.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 1.78 MB

english, 2013

3

Metagenomics and metatranscriptomics: Windows on CF-associated viral and microbial communities

Lim, Yan Wei, Schmieder, Robert, Haynes, Matthew, Willner, Dana, Furlan, Mike, Youle, Merry, Abbott, Katelynn, Edwards, Robert, Evangelista, Jose, Conrad, Douglas, Rohwer, Forest

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 2.08 MB

english, 2013

4

Safety and early treatment effects of the CXCR2 antagonist SB-656933 in patients with cystic fibrosis

Moss, Richard B., Mistry, Sunil J., Konstan, Michael W., Pilewski, Joseph M., Kerem, Eitan, Tal-Singer, Ruth, Lazaar, Aili L.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 734 KB

english, 2013

5

Developing a measure of eating attitudes and behaviours in cystic fibrosis

Katy Randlesome, Mandy Bryon, Michael Evangeli

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 245 KB

english, 2013

6

Recurrent Clostridium difficile colitis in cystic fibrosis: An emerging problem

Katarine Egressy, Michaelene Jansen, Keith C. Meyer

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 352 KB

english, 2013

7

Impact of antibiotic treatment for pulmonary exacerbations on bacterial diversity in cystic fibrosis

T.W.V. Daniels, G.B. Rogers, F.A. Stressmann, C.J. van der Gast, K.D. Bruce, G.R. Jones, G.J. Connett, J.P. Legg, M.P. Carroll

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 306 KB

english, 2013

8

A retrospective analysis of the impact of azithromycin maintenance therapy on adults attending a UK cystic fibrosis clinic

J.E. Fleet, K. Guha, S. Piper, W. Banya, D. Bilton, M.E. Hodson

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 220 KB

english, 2013

9

Comparison of two treatment regimens for eradication of Pseudomonas aeruginosa infection in children with cystic fibrosis

M. Proesmans, F. Vermeulen, L. Boulanger, J. Verhaegen, K. De Boeck

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 383 KB

english, 2013

10

Oxidative stress in stable cystic fibrosis patients: Do we need higher antioxidant plasma levels?

Antonela Lezo, Fiorella Biasi, Paola Massarenti, Roberto Calabrese, Giuseppe Poli, Bruna Santini, Elisabetta Bignamini

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 630 KB

english, 2013

11

Miglustat effects on the basal nasal potential differences in cystic fibrosis

Bradlee A. Jenkins, L. Lee Glenn

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 73 KB

english, 2013

12

Miglustat effects on the basal nasal potential differences in cystic fibrosis

Anissa Leonard, Patrick Lebecque, Jasper Dingemanse, Teresinha Leal

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 75 KB

english, 2013

13

A cohort study of the Copenhagen CF Centre eradication strategy against Staphylococcus aureus in patients with CF

Christina Schjellerup Dalbøge, Tacjana Pressler, Niels Høiby, Kim Gjerum Nielsen, Helle Krogh Johansen

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 199 KB

english, 2013

14

Inhaled amiloride and tobramycin solutions fail to eradicate Burkholderia dolosa in patients with cystic fibrosis

Ahmet Z. Uluer, David A. Waltz, Leslie A. Kalish, Summer Adams, Craig Gerard, Dawn A. Ericson

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 196 KB

english, 2013

15

P. aeruginosa LPS stimulates calcium signaling and chloride secretion via CFTR in human bronchial epithelial cells

J.M. Buyck, V. Verriere, R. Benmahdi, G. Higgins, B. Guery, R. Matran, B.J. Harvey, K. Faure, V. Urbach

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 624 KB

english, 2013

16

Misdiagnosis of cystic fibrosis — Experience from Germany

Lutz Naehrlich, Azadeh Bagheri-Behrouzi

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 7.32 MB

english, 2013

17

Mycobacterium avium and Mycobacterium abscessus complex target distinct cystic fibrosis patient subpopulations

Emilie Catherinot, Anne-Laure Roux, Marie-Anne Vibet, Gil Bellis, Sophie Ravilly, Lydie Lemonnier, Evelyne Le Roux, Claire Bernède-Bauduin, Muriel Le Bourgeois, Jean-Louis Herrmann, Didier Guillemot,

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 238 KB

english, 2013

18

Secretory IgA as a diagnostic tool for Pseudomonas aeruginosa respiratory colonization

Kasper Aanaes, Helle Krogh Johansen, Steen Seier Poulsen, Tacjana Pressler, Christian Buchwald, Niels Høiby

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 732 KB

english, 2013

19

Corrigendum to “CT of the paranasal sinuses is not a valid indicator for sinus surgery in CF patients” [J Cyst Fibros 11(2012)93–99]

Jacob Rasmussen, Kasper Aanæs, Rikke Norling, Kim G. Nielsen, Helle Krogh Johansen, Christian von Buchwald

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 71 KB

english, 2013

20

Eosinophilic esophagitis in cystic fibrosis: A case series and review of the literature

Jennifer L. Goralski, Daniel M. Lercher, Stephanie D. Davis, Evan S. Dellon

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 133 KB

english, 2013

21

Answer to the letter to the editor “Quantitative bone ultrasound in pediatric patients with cystic fibrosis”

Jean De Schepper

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 65 KB

english, 2013

22

Quantitative bone ultrasound in pediatric patients with cystic fibrosis

Juan D. Pedrera-Zamorano, Jesus M. Lavado-Garcia, Jose M. Moran

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 73 KB

english, 2013

23

Identification and distribution of Achromobacter species in cystic fibrosis

Spilker, Theodore, Vandamme, Peter, LiPuma, John J.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 213 KB

english, 2013

24

Epidemiology and resistance of Achromobacter xylosoxidans from cystic fibrosis patients in Dijon, Burgundy: First French data

Amoureux, Lucie, Bador, Julien, Siebor, Eliane, Taillefumier, Nathalie, Fanton, Annlyse, Neuwirth, Catherine

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 143 KB

english, 2013

25

Distribution of CFTR mutations in the Czech population: Positive impact of integrated clinical and laboratory expertise, detection of novel/de novo alleles and relevance for related/derived populations

Křenková, Petra, Piskáčková, Tereza, Holubová, Andrea, Balaščaková, Miroslava, Krulišová, Veronika, Čamajová, Jana, Turnovec, Marek, Libik, Malgorzata, Norambuena, Patricia, Štambergová, Alexandra, Dv

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 857 KB

english, 2013

26

Dietary essential amino acids are highly anabolic in pediatric patients with cystic fibrosis

Engelen, Mariëlle P.K.J., Com, Gulnur, Wolfe, Robert R., Deutz, Nicolaas E.P.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 554 KB

english, 2013

27

ARFI and transient elastography for characterization of cystic fibrosis related liver disease: First longitudinal follow-up data in adult patients

Karlas, Thomas, Neuschulz, Marie, Oltmanns, Annett, Wirtz, Hubert, Keim, Volker, Wiegand, Johannes

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 184 KB

english, 2013

28

Cystic fibrosis, gastroduodenal inflammation, duodenal ulcer, and H. pylori infection: The “cystic fibrosis paradox” revisited

Ramos, Ana Flávia Passos, de Fuccio, Marcelo Bicalho, Moretzsohn, Luciana Dias, Barbosa, Alfredo José Afonso, Passos, Maria do Carmo Friche, Carvalho, Rhaissa Said, Coelho, Luiz Gonzaga Vaz

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 502 KB

english, 2013

29

Xbox Kinect™ represents high intensity exercise for adults with cystic fibrosis

Holmes, Hayley, Wood, Jamie, Jenkins, Sue, Winship, Peta, Lunt, Dianne, Bostock, Susan, Hill, Kylie

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 178 KB

english, 2013

30

Factors influencing the acquisition of Stenotrophomonas maltophilia infection in cystic fibrosis patients

Stanojevic, Sanja, Ratjen, Felix, Stephens, Derek, Lu, Annie, Yau, Yvonne, Tullis, Elizabeth, Waters, Valerie

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 671 KB

english, 2013

31

A review of renal disease in cystic fibrosis

Nazareth, Dilip, Walshaw, Martin

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 324 KB

english, 2013

32

Molecular detection of an atypical, highly resistant, clonal Pseudomonas aeruginosa isolate in cystic fibrosis patients

Keating, Deirdre, Crowe, Mary J., Kennedy, Barry, Salmon, Abigail, Britton, David, Gallagher, Charles G., McKone, Edward F., Schaffer, Kirsten

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 485 KB

english, 2013

33

Consequences of partial duplications of the human CFTR gene on cf diagnosis: Mutations or ectopic variations

El-Seedy, Ayman, Pasquet, Marie-Claude, Bienvenu, Thiery, Bieth, Eric, Audrezet, Marie-Pierre, Kitzis, Alain, Ladeveze, Véronique

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 362 KB

english, 2013

34

Cascade testing in families of carriers identified through newborn screening in Western Brittany (France)

Duguépéroux, Ingrid, Audrézet, Marie-Pierre, Parent, Philippe, Audebert-Bellanger, Séverine, Roussey, Michel, Férec, Claude, Scotet, Virginie

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 228 KB

english, 2013

35

Treatment response of airway clearance assessed by single-breath washout in children with cystic fibrosis

Abbas, Chiara, Singer, Florian, Yammine, Sophie, Casaulta, Carmen, Latzin, Philipp

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 861 KB

english, 2013

36

Adherence to nebulised therapies in adolescents with cystic fibrosis is best on week-days during school term-time

Ball, Rosemary, Southern, Kevin W., McCormack, Pamela, Duff, Alistair J.A., Brownlee, Keith G., McNamara, Paul S.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 314 KB

english, 2013

37

Treatment complexity in cystic fibrosis: Trends over time and associations with site-specific outcomes

Sawicki, Gregory S., Ren, Clement L., Konstan, Michael W., Millar, Stefanie J., Pasta, David J., Quittner, Alexandra L.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 310 KB

english, 2013

38

Changing thresholds and incidence of antibiotic treatment of cystic fibrosis pulmonary exacerbations, 1995–2005

VanDevanter, Donald R., Elkin, Eric P., Pasta, David J., Morgan, Wayne J., Konstan, Michael W.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 312 KB

english, 2013

39

Cytokines in nasal lavages and plasma and their correlation with clinical parameters in cystic fibrosis

Paats, Marthe S., Bergen, Ingrid M., Bakker, Marleen, Hoek, Rogier A.S., Nietzman-Lammering, Karin J., Hoogsteden, Henk C., Hendriks, Rudi W., van der Eerden, Menno M.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 538 KB

english, 2013

40

Dysbiosis of bifidobacteria and Clostridium cluster XIVa in the cystic fibrosis fecal microbiota

Duytschaever, Gwen, Huys, Geert, Bekaert, Maarten, Boulanger, Linda, De Boeck, Kris, Vandamme, Peter

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 584 KB

english, 2013

41

CFTR-mutation specific applications of CFTR-directed monoclonal antibodies

van Meegen, M.A., Terheggen, S.W.J., Koymans, K.J., Vijftigschild, L.A.W., Dekkers, J.F., van der Ent, C.K., Beekman, J.M.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 1.76 MB

english, 2013

42

Characterization of a recurrent 3.8kb deletion involving exons 17a and 17b within the CFTR gene

Tang, Sha, Moonnumakal, Siby P., Stevens, Blair, Douglas, Ganka, Mason, Sally, Schmitt, Eric S., Eng, Christine M., Katz, Marcia, Fang, Ping

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 926 KB

english, 2013

43

Pro-inflammatory effect of cystic fibrosis sputum microparticles in the murine lung

Porro, Chiara, Di Gioia, Sante, Trotta, Teresa, Lepore, Silvia, Panaro, Maria Antonietta, Battaglino, Anna, Ratclif, Luigi, Castellani, Stefano, Bufo, Pantaleo, Martinez, Maria Carmen, Conese, Massimo

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 1.20 MB

english, 2013

44

Cirrhosis and other liver disease in cystic fibrosis

Flass, Thomas, Narkewicz, Michael R.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 326 KB

english, 2013

45

25 Analysis of CFTR gene mutations in Portuguese patients with idiopathic bronchiectasis

Grangeia, A., Amorim, A., Moura, C. Pinto, Fernandes, S., Barros, A., Carvalho, F.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 67 KB

english, 2013

46

26 Cystic fibrosis transmembrane conductance regulator (CFTR) gene sequence variation in Portuguese infertile males

Pacheco, P., Loureiro, P., Silva, C.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 61 KB

english, 2013

47

Pain in CF: Review of the literature

Havermans, Trudy, Colpaert, Kristine, De Boeck, Kris, Dupont, Lieven, Abbott, Janice

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 157 KB

english, 2013

48

332 Pulmonary status does not predict school attendance in children with CF

Kansra, S., Bhatt, J., Smyth, A.R., Overend, J., Bertenshaw, C.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 57 KB

english, 2013

49

Impaired CFTR function in mild cystic fibrosis associated with the S977F/T5TG12complex allele in trans with F508del mutation

Sorio, Claudio, Angiari, Chiara, Johansson, Jan, Verzè, Genny, Ettorre, Michele, Buffelli, Mario, Castellani, Carlo, Assael, Baroukh Maurice, Melotti, Paola

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 366 KB

english, 2013

50

170 Pseudomonas aeruginosa quorum sensing (QS) impact on host defences: QS-inhibitors and treatment of lung infections in cystic fibrosis (CF)

Genevois, A., Chusseau, A. Furiga, Belkhelfa, H., Lajoie, B., Haddioui, L., Roques, C.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 67 KB

english, 2013

51

Newborn screening for cystic fibrosis in Switzerland — Consequences after analysis of a 4 months pilot study

Torresani, Toni, Fingerhut, Ralph, Rueegg, Corina S., Gallati, Sabina, Kuehni, Claudia E., Baumgartner, Matthias R., Barben, Juerg

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 388 KB

english, 2013

52

2 New insights in CF molecular diagnostics applying the next generation sequencing technologies

Ramos, M.D., Trujillano, D., Sotillo, F., Armengol, L., Estivill, X., Casals, T.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 64 KB

english, 2013

53

Molecular detection of CF lung pathogens: Current status and future potential

Pattison, Sally H., Rogers, Geraint B., Crockard, Martin, Elborn, J. Stuart, Tunney, Michael M.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 285 KB

english, 2013

54

Comparison of real time diagnostic chemistries to detect Pseudomonas aeruginosa in respiratory samples from cystic fibrosis patients

Fothergill, J.L., Ledson, M.J., Walshaw, M.J., McNamara, P.S., Southern, K.W., Winstanley, C.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 324 KB

english, 2013

55

Non-invasive measurement of liver and pancreas fibrosis in patients with cystic fibrosis

Friedrich-Rust, Mireen, Schlueter, Nina, Smaczny, Christina, Eickmeier, Olaf, Rosewich, Martin, Feifel, Kirstin, Herrmann, Eva, Poynard, Thierry, Gleiber, Wolfgang, Lais, Christoph, Zielen, Stefan, Wa

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 511 KB

english, 2013

56

Eradication therapy for Pseudomonas aeruginosa colonization episodes in cystic fibrosis patients not chronically colonized by P. aeruginosa

Schelstraete, Petra, Haerynck, Filomeen, Van daele, Sabine, Deseyne, Sarah, De Baets, Frans

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 156 KB

english, 2013

57

WS1.1 Evolutionary pathways in two dominant clinical Pseudomonas aeruginosa clones

Johansen, H.K., Markussen, T., Damkir, S., Marvig, R.L., Pressler, T., Høiby, N., Jelsbak, L., Molin, S.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 65 KB

english, 2013

58

131 Surveillance of Pseudomonas aeruginosa infections at the Prague CF centre

Kalferstova, L., Dedeckova, K., Antuskova, M., Nemec, A., Dřevínek, P.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 65 KB

english, 2013

59

133 Usefulness of real-time PCR in diagnosing initial Pseudomonas aeruginosa infection in cystic fibrosis patients

Bassani, L., Colombrita, D., Gazzola, L., Timpano, S., Caruso, A., Padoan, R.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 65 KB

english, 2013

60

134 Serology and clinical parameters for diagnosis of Pseudomonas aeruginosa infection in children with cystic fibrosis

Castanhinha, S., Pereira, L., Aguiar, S., Ramirez, M., Rodrigues, T., Cristino, J. Melo, Barreto, C.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 66 KB

english, 2013

61

Cystic fibrosis CFBE41o‐ cells contain TLR1 SNP I602S and fail to respond to Mycobacterium abscessus

Kempaiah, Prakasha, Davidson, Lisa B., Perkins, Douglas J., Byrd, Thomas F.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 651 KB

english, 2013

62

Nutritional status is associated with health-related quality of life in children with cystic fibrosis aged 9–19years

Shoff, Suzanne M., Tluczek, Audrey, Laxova, Anita, Farrell, Philip M., Lai, HuiChuan J.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 419 KB

english, 2013

63

Effect of allergy and inflammation on eicosanoid gene expression in CFTR deficiency

Bickford, Justin S., Mueller, Christian, Newsom, Kimberly J., Barilovits, Sarah J., Beachy, Dawn E., Herlihy, John D., Keeler, Benjamin, Flotte, Terence R., Nick, Harry S.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 471 KB

english, 2013

64

WS7.4 Lumacaftor, an investigational CFTR corrector, in combination with ivacaftor, a CFTR potentiator, in CF patients with the F508del-CFTR mutation: Phase 2 interim analysis

Boyle, M., Bell, S.C., Konstan, M., Colley, S. Mc, Flume, P., Kang, L., Wu, Y., Waltz, D., Patel, N.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 72 KB

english, 2013

65

Inhaled aztreonam lysine vs. inhaled tobramycin in cystic fibrosis: A comparative efficacy trial

Assael, Baroukh M., Pressler, Tacjana, Bilton, Diana, Fayon, Michael, Fischer, Rainald, Chiron, Raphael, LaRosa, Mario, Knoop, Christiane, McElvaney, Noel, Lewis, Sandra A., Bresnik, Mark, Montgomery,

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 844 KB

english, 2013

66

Change in the Executive Editorial Team at JCF

Bell, Scott, Hartl, Dominik, Heijerman, Harry

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 67 KB

english, 2013

67

WS5.1 A high degree of variation in virulence of clonal Burkholderia cenocepacia ST32 isolates from cystic fibrosis patients in zebra fish embryos

Dedeckova, K., Vergunst, A., Dřevínek, P.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 70 KB

english, 2013

68

WS4.3 Rescue of F508del-CFTR without the regulatory insertion (ΔRI) and regulatory extension (ΔRE) in combination with genetic revertants and small molecules

Uliyakina, I., da Paula, A.C., Sousa, M., Felicio, V., Afonso, S., Awatade, N.T., Ramalho, A.S., Amaral, M.D.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 63 KB

english, 2013

69

Rapid emergence of a ceftazidime-resistant Burkholderia multivorans strain in a Cystic Fibrosis patient

Stokell, Joshua R., Gharaibeh, Raad Z., Steck, Todd R.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 306 KB

english, 2013

70

Prognostic relevance of dynamic hyperinflation during cardiopulmonary exercise testing in adult patients with cystic fibrosis

Stevens, D., Stephenson, A., Faughnan, M.E., Leek, E., Tullis, E.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 375 KB

english, 2013

71

WS4.6 MicroRNA-30s negatively regulate planar cell polarity genes in human cystic fibrosis bronchial epithelial cells

Delbart, W., Dhooghe, B., Wallemacq, P., Lebecque, P., Leal, T., Noël, S.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 55 KB

english, 2013

72

Nasal polyposis in lung transplant recipients with cystic fibrosis

Vital, Domenic, Holzmann, David, Boehler, Annette, Hofer, Markus

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 167 KB

english, 2013

73

WS11.2 Change pathways: The power of engaging in partnerships to change and enhance care for adults with cystic fibrosis

Player, R., Greville, H.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 65 KB

english, 2013

74

135 The use of rep-PCR (Diversilab, bioMerieux) in combination with multiplex PCR (targeting virulence genes) reveals the transmission of Pseudomonas aeruginosa isolates among cystic fibrosis patients in a hospital background

Dingemans, J., Craggs, M., Bilocq, F., Willekens, J., Eyns, H., Crabbé, A., De Vos, D., Pirnay, J.-P., Malfroot, A., Cornelis, P.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 65 KB

english, 2013

75

Effect of supervised training on FEV1 in cystic fibrosis: A randomised controlled trial

Kriemler, Susi, Kieser, Stephanie, Junge, Sibylle, Ballmann, Manfred, Hebestreit, Alexandra, Schindler, Christian, Stüssi, Christoph, Hebestreit, Helge

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 445 KB

english, 2013

76

The effect of intravenous antibiotics on anaemia in cystic fibrosis

Kathiresan, Bhuvaneswari, Waine, David, Derry, David

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 77 KB

english, 2013

77

WS16.4 Treatment algorithm for vitamin D deficiency – A review a year on

Pandya, S., Ochota, A., Walshaw, M.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 65 KB

english, 2013

78

WS18.2 Impact of pregnancy in women with cystic fibrosis (CF) – A retrospective single centre study

Tierney, A.C., Robinson, C., Swan, I., Nyulasi, I., Wilson, J.W.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 65 KB

english, 2013

79

299 The impact of transition on patient adherence to nebuliser therapy

Park, J., McCormack, P., Lloyd, E.A., Pitman, A., Southern, K.W., Walshaw, M., McNamara, P.S.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 62 KB

english, 2013

80

119 Contamination of CF sputum with Streptococcus constellatus

Worlitzsch, D., Jaschinski, A.L., Stotz, M., Borneff-Lipp, M.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 70 KB

english, 2013

81

214 Individual efficacy of Cough Technique versus Forced Expiration Technique in cystic fibrosis

Gursli, S., Sandvik, L., Skrede, B., Stuge, B.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 62 KB

english, 2013

82

WS20.4 The rs1078761 polymorphism is associated with reduced SPLUNC1 expression and increased pulmonary disease severity in cystic fibrosis patients

Saferali, A., Bérubé, J.-C., Paré, P.D., Bossé, Y., Sandford, A.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 68 KB

english, 2013

83

WS16.8 Validation of bioelectrical impedance for routine monitoring of nutritional status in cystic fibrosis patients

Dusser, P., Elie, C., Nguyen, H.A., Sermet-Gaudelus, I.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 62 KB

english, 2013

84

310 Detecting health changes in Omani children with cystic fibrosis (CF), using a novel nurse-led questionnaire

Norrish, C., Fass, U., Shivalingam, G., Salmani, M. Al, Norrish, M., Kallesh, H., Clark, F., Heming, T., Khusaiby, S. Al

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 60 KB

english, 2013

85

15 Update of CFTR mutation frequencies in cystic fibrosis patients in Uruguay

Rey, M.A., Esperon, P., Guecaimburu, M.R., Vital, M., Rutz, G., Caballero, G., Parallada, G., Sereno, V., Pinchack, C.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 70 KB

english, 2013

86

6 The difficulty of the diagnosis of cystic fibrosis when a new mutation is present

Cardoso, J., Ferraz, C., Carvalho, F., Grangeia, A., Vaz, L.G.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 64 KB

english, 2013

87

63 The use of high resolution computerized tomography of the chest in evaluating the effect of ataluren in nonsense mutation cystic fibrosis (nmCF) lung disease

Ajayi, T., Konstan, M., Accurso, F.J., De Boeck, K., Kerem, E., Rowe, S., Sermet-Gaudelus, I., Wilschanski, M., Brody, A., Miller, N., Elfring, G., Spiegel, R., Peltz, S., Barth, J.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 68 KB

english, 2013

88

Single high-dose oral vitamin D3 (stoss) therapy — A solution to vitamin D deficiency in children with cystic fibrosis?

Shepherd, Darren, Belessis, Yvonne, Katz, Tamarah, Morton, John, Field, Penny, Jaffe, Adam

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 248 KB

english, 2013

89

Accurate assessment of systemic iron status in cystic fibrosis will avoid the hazards of inappropriate iron supplementation

Smith, D.J., Anderson, G.J., Lamont, I.L., Masel, P., Bell, S.C., Reid, D.W.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 77 KB

english, 2013

90

360 Clinical evolution of cystic fibrosis in 20 years: Experience at a referral center

Marson, F.A., Bertuzzo, C.S., Ribeiro, A.F., Ribeiro, J.D.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 64 KB

english, 2013

91

90 Inhalation of colistimethate dry powder (Colobreathe) results in negligible systemic exposure

Riethmueller, J., Goldman, M., Turay, P.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 67 KB

english, 2013

92

202 Pulmonary tomosynthesis in adults with cystic fibrosis: Our preliminary experience

Nespoli, P., Parlatano, D., Cortese, G., Messore, B., Bena, C., Chiesa, M., Veltri, A.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 63 KB

english, 2013

93

Reply to ‘Methicillin-resistant Staphylococcus Aureus’

Vanderhelst, E., De Meirleir, L., Verbanck, S., Piérard, D., Vincken, W., Malfroot, A.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 69 KB

english, 2013

94

85 Investigation into the antibiotic resistome of the Streptococcus genus from adult cystic fibrosis patients

Thornton, C.S., Grinwis, M.E., Sibley, C.D., Rabin, H.R., Surette, M.G.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 66 KB

english, 2013

95

WS9.4 Non invasive ventilation as airway clearance technique compared to PEP in adult patients with cystic fibrosis

Hortal, M.C. Rodriguez, Hjelte, L.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 65 KB

english, 2013

96

WS11.1 Characterising extreme survival in cystic fibrosis: A case series of over-50 year olds

Constantinou, P., Bilton, D., Simmonds, N.J.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 65 KB

english, 2013

97

125 Investigation of cystic fibrosis airway microbiome in patients showing a severe decline in lung function and not responding to conventional antimicrobial therapy

Bevivino, A., Fiscarelli, E., Mengoni, A., Taccetti, G., Manno, G., Paganin, P., Tuccio, V., Chiancianesi, M., Dolce, D., Morelli, P.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 64 KB

english, 2013

98

WS16.1 Treatment of early diagnosed CFRD with oral drugs versus insulin: An open prospective randomized study

Ballmann, M., Hubert, D., Assael, B.M., Mosnier-Pudar, H., Smaczny, C., Kessler, L., Fink, K., Ocampo, M., Holl, R.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 65 KB

english, 2013

99

Extensive diversification is a common feature of Pseudomonas aeruginosa populations during respiratory infections in cystic fibrosis

Ashish, Abdul, Paterson, Steve, Mowat, Eilidh, Fothergill, Joanne L., Walshaw, Martin J., Winstanley, Craig

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 172 KB

english, 2013

100

164 Neutrophil elastase-mediated increase in airway temperature during inflammation

Döring, G., Schmidt, A., Bissinger, R., Koller, G., Malleret, L., D'Orazio, C., Assael, B.M., Facchinelli, M., Piacentini, G., Schulte-Hubbert, B., Hammermann, J., Schniedejans, M., Häußler, S., Meyer

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 67 KB

english, 2013

101

WS10.2 Complete sequencing of 2,000 cystic fibrosis and CFTR-related disease high risk alleles

Brock, J., Tobi, S., Schwarz, M.J.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 61 KB

english, 2013

102

260 Insulin release responses to a mixed meal and standard oral glucose tolerance test in CF

Nazareth, D., Mohan, K., Browning, P., Walshaw, M.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 62 KB

english, 2013

103

361 Clinical, genetic, microbiological and functional characteristics of patients with cystic fibrosis in the Moscow region

Nikonova, V., Krasovskiy, S., Kapranov, N., Amelina, E., Kashirskaya, N., Kondrateva, E., Sherman, V.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 64 KB

english, 2013

104

283 Evaluation of a novel behavioural intervention programme (BIP) to modify mealtime behaviour for young children with cystic fibrosis

Coates, A.J., Harte, C., Urquhart, D.S.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 62 KB

english, 2013

105

WS7.3 VX-661, an investigational CFTR corrector, in combination with ivacaftor, a CFTR potentiator, in patients with CF and homozygous for the F508Del-CFTR mutation: Interim analysis

Donaldson, S., Pilewski, J., Griese, M., Dong, Q., Lee, P.-S.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 72 KB

english, 2013

106

WS21.8 Exchange proteins directly activated by cyclic AMP: Novel CFTR interactors?

Fernandes, J., Amaral, M.D., Farinha, C.M.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 67 KB

english, 2013

107

264 Determinants of bone loss in cystic fibrosis

Gensburger, D., Chapurlat, R., Nové-Josserand, R., Rabilloud, M., Durieu, I.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 65 KB

english, 2013

108

305 Red cell parameters to monitor vitamin B12 status in children with cystic fibrosis

Khosravi, S.L., Burrows, E., McNamara, P.S., Southern, K.W.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 58 KB

english, 2013

109

147 Description of Burkholderia contaminans isolates recovered from sputum of cystic fibrosis (CF) patients with different courses of infection

de Volder, A. Lopez, Ibarra, L., Pioli, V., Teves, S., Vazquez, M., Degrossi, J., Galanternik, L.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 65 KB

english, 2013

110

Reduced physical activity associated with work and transport in adults with cystic fibrosis

Rasekaba, Tshepo M., Button, Brenda M., Wilson, John W., Holland, Anne E.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 161 KB

english, 2013

111

257 Challenges in CFRD: The advantages of continuous glucose monitoring (CGM)

Dyce, P., Sumner, C., Malone, V., Nazareth, D., Walshaw, M.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 62 KB

english, 2013

112

WS11.3 Improving communication between adults with cystic fibrosis and their CF physician

Hubert, D., Lacarrière, C., Panzo, R., Toulorge, C., Clavel, F., David, V.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 65 KB

english, 2013

113

184 Determinants of nontuberculous mycobacteria eradication in cystic fibrosis

Coupet, L., Prevotat, A., Dominique, S., Rault, G., Chiron, R., Sermet, I., Domblides, P., Murris, M., Bui, S., Grenet, D., Langlois, C., Wallaert, B.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 65 KB

english, 2013

114

WS9.5 Saline at lower tonicity in cystic fibrosis (SALTI-CF) trial – A randomised, controlled trial comparing 0.9% v 3% v 6% nebulised saline

Dwyer, T., Elkins, M., Dentice, R., Forbes, S., Mcarthur, M., Cooper, P., Jaffe, A., Middleton, P., Wark, P., Bye, P.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 60 KB

english, 2013

115

93 Aztreonam lysine for inhalation as a treatment for Burkholderia cepacia complex in CF

Willekens, J., De Wachter, E., De Schutter, I., Vanderhelst, E., De Meirleir, L., Malfroot, A.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 68 KB

english, 2013

116

Phenotypic expression of the 3120+1G>A mutation in non-Caucasian children with cystic fibrosis in South Africa

Masekela, R., Zampoli, M., Westwood, A.T., White, D.A., Green, R.J., Olorunju, S., Kwofie-Mensah, M.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 114 KB

english, 2013

117

318 Prevalence and impact of anxiety and depression symptoms in adolescents and adults with cystic fibrosis in Spain

Solé, A., Cebrián, M., Olveira, G., Quittner, A.L.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 63 KB

english, 2013

118

WS21.6 A novel 5′ alternative CFTR mRNA isoform may be a cause of CFTR dysfunction in a patient with nasal polyposis

Hinzpeter, A., de Becdelièvre, A., Bieth, E., Gameiro, C., Brémont, F., Martin, N., Costes, B., Costa, C., Aissat, A., Goossens, M., Fanen, P., Girodon, E.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 67 KB

english, 2013

119

191 Resistance and reactance measured by impulse oscillometry: Structural functional correlation in adult cystic fibrosis

Hurt, K., Nair, A., Sheard, S., Hansell, D., Hodson, M., Usmani, O., Bilton, D.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 59 KB

english, 2013

120

190 Ventilation inhomogeneity in patients with cystic fibrosis aged 10–18 years

Pradal, U., Borruso, A., Menin, L., Fedrigo, E., Assael, B.M.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 58 KB

english, 2013

121

WS16.3 Vitamin D supplementation in patients with cystic fibrosis: A pilot randomized controlled trial

Pincikova, T., Flodström-Tullberg, M., Hjelte, L.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 65 KB

english, 2013

122

24 ENaC-related disorder as a new CF-like clinical entity

Norek, A., Scheinert, S., Kusmierek, E., Chrzescijanska, E., Nowakowska, A., Sapiejka, E., Swierczynska, B., Sands, D., Derichs, N.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 68 KB

english, 2013

123

71 Pharmacokinetics of nasal administered tobramycin in patients with cystic fibrosis

Berkhout, M.C., van Velzen, A.J., Touw, D.J., Bouazzaoui, L.H. el, Rijntjes, E., Heijerman, H.G.M.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 72 KB

english, 2013

124

WS17.6 Phase 3 trial of inhaled levofloxacin (Aeroquin™, MP-376, APT-1026) vs. tobramycin inhalation solution (TIS) in intensively treated CF patients over 6 months

Elborn, J.S., Geller, D., Conrad, D., Aaron, S., Smyth, A.R., Fischer, R., Kerem, E., Bell, S.C., Loutit, J., Flume, P.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 65 KB

english, 2013

125

WS12.3 Prognostic value of the 6 minute walk test in adults with cystic fibrosis

Burgel, P.-R., Chapron, J., Hubert, D., Kanaan, R., Honoré, I., Paillasseur, J.-L., Aubourg, F., Dinh-Xuan, A.-T., Dusser, D., Fajac, I., Martin, C.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 61 KB

english, 2013

126

189 Nocturnal pulse oximetry in paediatric cystic fibrosis patients. Is FEV1 a good predictor?

Silva, A.M., Constant, C., Salgueiro, M., Descalço, A., Pereira, L., Bandeira, T., Ferreira, R.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 67 KB

english, 2013

127

WS21.3 Clinical variability in patients with cystic fibrosis and D1152H mutation

Terlizzi, V., Ingino, R., Elce, A., Tosco, A., Improta, F., Cirilli, N., Gagliardini, R., Salvatore, D., Carnovale, V., D'Agostino, M.A., Sepe, A., Amato, N., De Gregorio, F., Casale, A., Raia, V., Ca

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 66 KB

english, 2013

128

161 E3 ubiquitin ligases: A potential role in regulating the inflammatory phenotype of cystic fibrosis?

Canato, S., Telhada, M., Amaral, M.D., Clarke, L.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 66 KB

english, 2013

129

WS11.4 Education and employment: A qualitative exploration of the beliefs, aspirations and experiences of young people with CF

Claxton, M., Latchford, G., Duff, A., Peckham, D.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 65 KB

english, 2013

130

WS4.1 New molecular models of CFTR based on ABC transporter structures

Hoffmann, B., Lehn, P., Mornon, J.-P., Callebaut, I.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 62 KB

english, 2013

131

353 Clinical trial drop out(s): Experience of a CF clinical research center

Passiu, M., Meneghelli, I., Cipolli, M., Assael, B.M.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 57 KB

english, 2013

132

WS1.6 Successful treatment of Mycobacterium abscessus infection in cystic fibrosis patients using a novel regimen

Jones, A.L., Perrin, F., Hurt, K., Cowman, S., Alshafi, K., Gyi, K., Loebinger, M.R., Simmonds, N.J., Bilton, D.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 60 KB

english, 2013

133

WS13.5 Structural correlation of multiple breath washout indices derived from alveolar slope analysis in adult cystic fibrosis

Hurt, K., Hansell, D., Nair, A., Sheard, S., Hodson, M., Kalsi, H., Bilton, D., Usmani, O.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 58 KB

english, 2013

134

105 Adaptation of Pseudomonas aeruginosa in the CF host: Link between laboratory findings and the clinic?

Willekens, J., Dingemans, J., Eyns, H., Crabbé, A., Cornelis, P., Malfroot, A.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 69 KB

english, 2013

135

WS9.3 Bronchial hyperreactivity related to 4 commonly used inhalation drugs in cystic fibrosis

Eyns, H., Willekens, J., Vaes, P., Malfroot, A.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 65 KB

english, 2013

136

238 Faecal calprotectin is increased in CF patients with pancreatic insufficiency

Fjellsson, A., Karlge-Nilsson, E., Andersson, B.A., Lindblad, A., Gilljam, M.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 64 KB

english, 2013

137

Timing of inhaled tobramycin affects assessment of intravenous tobramycin pharmacokinetic monitoring

Stenbit, Antine E., Bullington, Wendy M., Heh, Julie L., Flume, Patrick A.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 203 KB

english, 2013

138

153 Direct detection and identification of controversial pathogens in CF – Pandoraea apista and Inquilinus limosus

Melter, O., Tkadlec, J., Šulcová, R., Skalická, V., Kučerová, T., Dřevínek, P.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 66 KB

english, 2013

139

WS18.5 When women with CF become mothers: A qualitative study on psychosocial impact and adjustment

Cammidge, S., Latchford, G., Duff, A., Etherington, C.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 51 KB

english, 2013

140

Achromobacter species in cystic fibrosis: Cross-infection caused by indirect patient-to-patient contact

Hansen, C.R., Pressler, T., Ridderberg, W., Johansen, H.K., Skov, M.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 507 KB

english, 2013

141

WS18.3 Pregnancy outcomes in cystic fibrosis: A 10-year experience from a UK centre

Renton, M., Priestley, L., Bennett, L., Mackillop, L., Chapman, S.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 65 KB

english, 2013

142

61 Tiotropium Respimat in cystic fibrosis: Efficacy and safety results of phase III randomized placebo-controlled trial

Ratjen, F., Koker, P., Geller, D., Langellier-Cocteaux, B., Maulf, F. Le, Kattenbeck, S., Moroni-Zentgraf, P., Elborn, J.S.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 68 KB

english, 2013

143

138 Sampling and processing for Pseudomonas aeruginosa identification across ECFS-CTN sites: Standardisation of clinical practice is important for patient selection for research studies

Denton, M., Kent, L., Sermet, I., Taccetti, G.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 64 KB

english, 2013

144

WS6.4 Benchmarking in Germany: An expanding systematic quality improvement project

Niemann, N., Stern, M.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 58 KB

english, 2013

145

269 Nutritional assessment and dietary intake in children and teenagers with cystic fibrosis

Asseiceira, I., Mexia, S., Pinheiro, J., Pereira, L., Barreto, C.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 64 KB

english, 2013

146

WS12.2 The impact of switching to the new global lung function initiative equations on spirometry results in the UK CF registry

Aurora, P., Stanojevic, S., Stocks, J., Kirkby, J., Bountziouka, V., Bourke, S., Carr, S.B., Gunn, E., Prasad, A., Bilton, D.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 61 KB

english, 2013

147

230 Barriers to exercise participation in adult CF patients

Haynes, F., Dewar, J.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 58 KB

english, 2013

148

311 Do quality of life responses signal severe loss of lung function?

Schusser, S., Smrekar, U., Mitmansgruber, H., Beck, T., Hohenberger, C., Eder, J., Niedermayr, K., Ellemunter, H.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 59 KB

english, 2013

149

WS2.5 The development, implementation and evaluation of a therapeutic group for non-affected siblings of children and young people with cystic fibrosis attending a regional paediatric CF centre

Anderson, C., Dixon, C., McKail, R., Burrows, E., Watling, R.M., McCormack, P., Pitman, A., Southern, K.W.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 51 KB

english, 2013

150

55 Reliability of intestinal current measurement as CFTR biomarker and responsiveness to oral ivacaftor treatment

Scheinert, S., Pinders-Kessel, L., Klosinski, M., Derichs, N.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 73 KB

english, 2013

151

WS19.4 A randomised controlled trial of the effect of hypertonic saline (HS) inhalation on exacerbation resolution, hospital length of stay and time to relapse in adults with cystic fibrosis

Dentice, R., Elkins, M., Middleton, P., Bishop, J., Wark, P., Dorahy, D., Harmer, C., Bye, P.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 63 KB

english, 2013

152

211 What physiotherapy is being carried out for infants with cystic fibrosis (CF) in the UK since the introduction of newborn screening? Results from a national physiotherapy survey conducted by the Cystic Fibrosis Trust

Ferguson, K.V., Old, K.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 58 KB

english, 2013

153

113 Unveiling the Burkholderia cenocepacia J2315 RNA chaperone Hfq2 interactome

Sousa, S.A., Soares-Castro, P., Feliciano, J.R., Ramos, C.G., Santos, P.M., Leitão, J.H.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 65 KB

english, 2013

154

174 Quantification of major urinary metabolite of PGE2 in cystic fibrosis (CF) patients: Correlation with parameters of disease severity

Gartner, S., Jabr, S., Roca-Ferrer, J., Milne, G., Moreno, A., Picado, C.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 62 KB

english, 2013

155

WS3.5 Clostridium difficile in adult cystic fibrosis (CF): Prevalence, ribotyping and toxigenic capability. A prospective study

Harrison, M.J., Burke, D., Fleming, C., Mccarthy, M., Shortt, C., O'Callaghan, G., Murphy, D.M., Shanahan, F., Hill, C., Ross, P., Stanton, C., Eustace, J.A., Rea, M.C., Plant, B.J.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 64 KB

english, 2013

156

11 A new multiplex PCR method for the quantification of aberrant transcripts from nasal epithelial cells of patients

Raynal, C., Guittard, C., Bergougnoux, A., Aufray, M., Taulan, M., Chiron, R., Bareil, C., Claustres, M., des Georges, M.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 61 KB

english, 2013

157

285 Comprehensive management of senso-motor disorders of orality in paediatric CF patients

Costanzo, A., Badet, N., Clouzeau, H., Senez, C., Fayon, M., Bui, S.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 65 KB

english, 2013

158

Editorial Board

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 56 KB

english, 2013

159

Nutritional intervention in patients with Cystic Fibrosis: A systematic review

Woestenenk, J.W., Castelijns, S.J.A.M., van der Ent, C.K., Houwen, R.H.J.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 184 KB

english, 2013

160

WS5.4 Increased production of IL-17A in circulating Th17 and dysfunctional Tregs in adults with cystic fibrosis-related diabetes

Ziai, S., Rabasa-Lhoret, R., Gauthier, M.-S., Mailhot, M., Coderre, L., Berthiaume, Y., Richter, M.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 70 KB

english, 2013

161

WS5.3 GSNOR inhibitors as potential, novel anti-inflammatory therapy in cystic fibrosis

Shoemaker, S., Troha, J., Gabriel, S., Scoggin, C., Blonder, J., Mutka, S., Donaldson, S.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 70 KB

english, 2013

162

Editorial Board

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 64 KB

english, 2013

163

Calculation of the capnographic index based on expiratory molar mass–volume-curves — A suitable tool to screen for cystic fibrosis lung disease

Fuchs, Susanne I., Junge, Sibylle, Ellemunter, Helmut, Ballmann, Manfred, Gappa, Monika

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 430 KB

english, 2013

164

WS3.4 Clostridium difficile, but not Giardia lamblia, is a frequent finding in the stool of CF-patients

Bagheri-Behrouzi, A., Zimmermann, A., Naehrlich, L.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 70 KB

english, 2013

165

Erratum to “Secretory IgA as a diagnostic tool for Pseudomonas aeruginosa respiratory colonization” [J Cyst Fibros 12 (1) (2013) 81–7]

Aanaes, Kasper, Johansen, Helle Krogh, Poulsen, Steen Seier, Pressler, Tacjana, Buchwald, Christian, Høiby, Niels

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 76 KB

english, 2013

166

Editorial Board

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 66 KB

english, 2013

167

WS14.4 Effects of individualised aerobic exercise training in adults with cystic fibrosis: A 4 year controlled trial

Petrovic, M., Kaluza, I., Pohl, W.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 62 KB

english, 2013

168

32 Uptake of genetic counseling and analysis of DNA testing outcomes following newborn screening for cystic fibrosis: Experience of the Prague centre

Holubová, A., Krulišová, V., Piskáčková, T., Balaščaková, M., Skalická, V., Votava, F., Macek, M.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 62 KB

english, 2013

169

WS10.1 The performance of the UK national newborn screening (NBS) programme for CF – Results from a UK regional paediatric network

Harrington, J., Southern, K.W., Burrows, E., Barton, P.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 61 KB

english, 2013

170

182 Chronic Pseudomonas aeruginosa infection and respiratory muscle impairment in cystic fibrosis

Dassios, T.G., Katelari, A., Doudounakis, S., Dimitriou, G.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 65 KB

english, 2013

171

WS2.4 Use of non-prescribed medicines, supplements and therapies by children with cystic fibrosis, other chronic illnesses and children with an acute injury – A comparative mixed-methods study

Hurley, M., Ho, J., Gates, J., Gaunt, A., Smyth, A.R.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 59 KB

english, 2013

172

106 Pseudomonas aeruginosa quorum-sensing molecule inhibits junctional integrity and cell-to-cell communication in human airway epithelial cells

Losa, D., Köhler, T., Bacchetta, M., Van Delden, C., Chanson, M.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 69 KB

english, 2013

173

149 Epidemiology and clinical impact of Burkholderia cepacia complex: A single-centre analysis

Willekens, J., Eyns, H., De Wachter, E., De Schutter, I., De Bel, A., Echahidi, F., Malfroot, A.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 65 KB

english, 2013

174

WS13.6 Evidence of short-term acinar response following intravenous antibiotics therapy in adults with cystic fibrosis

Vanderhelst, E., Schuermans, D., Malfroot, A., Vincken, W., Verbanck, S.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 58 KB

english, 2013

175

243 Transient elastography and abdominal ultra-sound investigation of adult CF patients monitored at the Copenhagen CF centre

Katzenstein, T.L., Andersen, E.S., Pressler, T., Jensen, F.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 64 KB

english, 2013

176

Update on cystic fibrosis-related diabetes

Kelly, Andrea, Moran, Antoinette

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 743 KB

english, 2013

177

221 Does the use of a telehealth system, (I-neb Insight Online) improve nebuliser adherence and reduce treatment times in children with cystic fibrosis?

Thornton, C., Moss, N.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 58 KB

english, 2013

178

WS16.2 Glucose handling in CF – Implications for the diagnosis and screening of CFRD

Nazareth, D., Dyce, P., Mohan, K., Walshaw, M.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 65 KB

english, 2013

179

232 Preliminary findings of a study comparing Incremental Step Test (IST) performance and physical activity levels in children with CF

Holden, H.J., Douglas, E., Bolton, M., Smyth, A.R.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 58 KB

english, 2013

180

289 Vitamin D deficiency in patients attending the Tuscan regional cystic fibrosis centre

Galici, V., Repetto, T., Neri, A., Braggion, C., de Martino, M., Taccetti, G.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 65 KB

english, 2013

181

WS22.1 Basophil activation is a reliable biomarker of allergic bronchopulmonary aspergillosis (ABPA) in CF: Interim results of a longitudinal cohort study

Moss, R.B., Waters, J., Dunn, C., Davies, Z., Everson, C., Tirouvanziam, R., Tameresis, J., Herzenberg, L.A., Gernez, Y.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 65 KB

english, 2013

182

154 A single centre experience of non-tuberculous mycobacteria in children with cystic fibrosis

O'Reilly, R., Prasad, A., Suri, R.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 65 KB

english, 2013

183

116 Effect of Staphylococcus aureus supernatant on airway epithelium functionality in infants with cystic fibrosis

Bessaci-Kabouya, K., Gaultier, B., Zahm, J.-M., Coraux, C., Mauran, P., Weiss, L., Dalphin, M.-L., Derelle, J., Tatopoulos, A., Huet, F., Perez-Martin, S., Birembaut, P., Abely, M.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 70 KB

english, 2013

184

WS18.1 Evolution of pregnancies in the French CF Registry: 1992–2011

Lemonnier, L., Cazes, M.-H., Bellis, G., Sponga, M., Durieu, I.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 65 KB

english, 2013

185

192 Volumetric capnography is correlated with spirometry in cystic fibrosis patients

Oliveira, P.M.N., Ribeiro, M.A.G.O., Almeida-Junior, A.A., Ribeiro, J.D.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 58 KB

english, 2013

186

304 Premature vascular ageing in children with cystic fibrosis (CF)

Jain, K., Prayle, A., Symmonds, M., Hull, J.H., Bolton, C.E., Smyth, A.R.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 58 KB

english, 2013

187

WS20.2 Over-expression of miR-494 and miR-145 correlates with CFTR and SMAD3 down-regulation in cystic fibrosis patients

Megiorni, F., Cialfi, S., Cimino, G., De Biase, R.V., Savi, D., Dominici, C., Quattrucci, S., Pizzuti, A.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 68 KB

english, 2013

188

9 Detection of a novel complex allele c.[869+11C>T;3909C>G] in CFTR gene

Farhat, R., Puissesseau, G., Pasquet, M.-C., Adolphe, C., Mégarbané, A., Kitzis, A., Ladevèze, V.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 61 KB

english, 2013

189

346 A qualitative study to explore factors that impact adherence to aerosol therapy in young people with CF: Patient and parent perspectives

O'Toole, D., Latchford, G., Duff, A., Ball, R., McCormack, P., McNamara, P.S., Southern, K.W., Brownlee, K.G.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 59 KB

english, 2013

190

120 Duplication in CHIT1 gene and the risk for Aspergillus lung disease in CF patients

Livnat, G., Bar-Yoseph, R., Mory, A., Dagan, E., Elias, N., Gershoni, R., Bentur, L.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 66 KB

english, 2013

191

53 Lung function, weight, and sweat chloride responses in patients with cystic fibrosis and the G551D-CFTR mutation treated with ivacaftor: A secondary analysis

Plant, B.J., Konstan, M., Aherns, R., Rodriguez, S., Munck, A., Elborn, J.S., Johnson, C.M.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 73 KB

english, 2013

192

216 Periodic application of continuous positive airway pressure (pCPAP) as airway clearance technique during advanced lung disease in cystic fibrosis: Another clue?

Gambazza, S., Zuffo, S., Innocenti, D., Pasotto, R., Mariotti, E., Masolini, M., Braggion, C.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 62 KB

english, 2013

193

1 Targeted next generation sequencing (NGS) of the CFTR locus: Comparison of three technical approaches

Guéguen, P., Audrézet, M.-P., Despres, A., Le Maréchal, C., Férec, C.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 64 KB

english, 2013

194

52 Evaluation of marker proteins for quantitation of CFTR

van Barneveld, A., Stolpe, C., Schulz, A., Dittrich, A.-M., Müller, C., Tümmler, B.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 56 KB

english, 2013

195

Screening for depression in a single CF centre

Latchford, Gary, Duff, Alistair J.A.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 95 KB

english, 2013

196

Antibiotic susceptibility testing in early and chronic respiratory infections with Pseudomonas aeruginosa

Foweraker, Juliet E., Govan, John R.W.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 76 KB

english, 2013

197

WS22.5 Effect of the Burkholderia cenocepacia exoproteome on CFTR protein expression in human cystic fibrosis lung epithelial cell models

Canato, S., Telhada, M., Amaral, M.D., Clarke, L.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 63 KB

english, 2013

198

WS13.4 Chest HRCT (cCT) score predicts later Pseudomonas infection in young children with cystic fibrosis

Bortoluzzi, C., Volpi, S., D'Orazio, C., Amenta, G., Loeve, M., Tiddens, H.A.W.M., Assael, B.M.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 65 KB

english, 2013

199

WS18.4 Does the presence of diabetes affect lung function outcomes in a pregnant individual with cystic fibrosis?

Williams, E., Wilson, J.W., Finlayson, F., Wesselingh, K., Button, B.M.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 65 KB

english, 2013

200

Hypertriglyceridemia is associated with insulin levels in adult cystic fibrosis patients

Ishimo, Marie-Claire, Belson, Linda, Ziai, Sophie, Levy, Emile, Berthiaume, Yves, Coderre, Lise, Rabasa-Lhoret, Rémi

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 247 KB

english, 2013

201

WS5.5 Impact of antibiotic treatment on concentration of pro-inflammatory cytokines in nasal lavages of CF patients

Hentschel, J., Jäger, M., Beiersdorf, N., Doht, F., Michl, R., Markert, U.R., Böer, K., Keller, P., Pletz, M.W., Mainz, J.G.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 64 KB

english, 2013

202

WS10.3 What can next-generation sequencing do for CF?

Varilh, J., Bonini, J., Thèze, C., Altiéri, J.-P., Claustres, M., Raynal, C., des Georges, M., Taulan-Cadars, M.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 61 KB

english, 2013

203

12 Using a mRNA-based approach to detect rare CFTR mutations

Felicio, V., Amaral, M.D., Ramalho, A.S.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 61 KB

english, 2013

204

334 What is it like to be an adolescent with cystic fibrosis? Reversing the roles of patient and health-professional

van der Vegte, K., Bremer-Ophorst, I., Bethlehem, S. Aufenacker-van, Segers, L., Arets, B., van Geelen, S.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 58 KB

english, 2013

205

273 Low fat free mass index is a risk factor for hospitalization in adult patients with cystic fibrosis

Bisogno, A., Alicandro, G., Bianchi, M.L., Colombo, C.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 61 KB

english, 2013

206

123 A shotgun metaproteomics approach to study the faecal microbiome of patients with cystic fibrosis reveals a reduction of butyrate-producing bacteria

Debyser, G., Mesuere, B., Clement, L., Duytschaever, G., Van Hecke, P., Dawyndt, P., De Boeck, K., Vandamme, P., Devreese, B.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 63 KB

english, 2013

207

224 Adherence to the administration of aerosolized promixin with the I-neb adaptive aerosol delivery (AAD) system, lung function and administration times in patients with cystic fibrosis (CF)

Donà, M., Alatri, F., Brivio, A., Mamprin, G., Barbisan, M., Varchetta, M., De Sanctis, S., Gambazza, S., Karapanagiotis, S., Ros, M.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 59 KB

english, 2013

208

356 Phenotype characteristics of homozygous F508del mutation in Northern Portugal: Experience of two pediatric centers

Barbosa, T.F., Ferreira, I., Corujeira, S., Ferraz, C., Vaz, L.G., Senra, V., Rocha, H.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 62 KB

english, 2013

209

31 Comparative study for the evaluation of a new technology for cystic fibrosis screening

Rongioletti, M.C.A., Papa, F., Vaccarella, C., Majolini, M.B., Centrone, C., Minuti, B., Luciano, A., Mazzucchi, V., Belli, M., Giotti, I., Giuliani, C., Torricelli, F., Liumbruno, G.M.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 63 KB

english, 2013

210

Bacterial sinusitis can be a focus for initial lung colonisation and chronic lung infection in patients with cystic fibrosis

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 1.02 MB

english, 2013

211

30 Sixteen years of newborn screening for cystic fibrosis using the IRT/IRT strategy in Buenos Aires Province, Argentina

Borrajo, G., Gomez, F., Punzi, M., D'Alessandro, V., Diez, G., Vodanovich, C.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 62 KB

english, 2013

212

WS22.3 Role of macrophage proteases in the killing of intracellular bacteria

Cifani, N., Reeves, E.P., McElvaney, N.G., Pompili, B., Del Porto, P., Ascenzioni, F.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 65 KB

english, 2013

213

282 Evaluation of nutrition education in a group of children with moderate to severe cystic fibrosis (CF)

Owen, E., Bryon, M., Prasad, A., Suri, R.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 62 KB

english, 2013

214

280 Impact of n-3 fatty acids supplementation on inflammatory markers in cystic fibrosis patients

Cunha, A.L.P., Vasconcelos, Z., Costa, R.S.S., Cabello, G.M.K., Carmo, M.G.T., Chaves, C.R.M.M.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 65 KB

english, 2013

215

WS21.5 Evolution of CFTR exon 10 and duplications in primates

Farhat, R., Puissesseau, G., Pasquet, M.-C., Kitzis, A., Ladèveze, V.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 67 KB

english, 2013

216

110 Quantitative exoproteomic analysis to better understand the mechanisms underlying Burkholderia cenocepacia persistence and virulence in CF lung infections

Maldonado, R.F., dos Santos, S.S., Sá-Correia, I.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 65 KB

english, 2013

217

Reproducibility of maximal cardiopulmonary exercise testing for young cystic fibrosis patients

Saynor, Zoe L., Barker, Alan R., Oades, Patrick J., Williams, Craig A.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 268 KB

english, 2013

218

Lung transplantation in cystic fibrosis normalizes essential fatty acid profiles

Witters, Peter, Dupont, Lieven, Vermeulen, François, Proesmans, Marijke, Cassiman, David, Wallemacq, Pierre, De Boeck, Kris

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 305 KB

english, 2013

219

320 Predictors of depression and anxiety in Belgian patients with CF: A cross-sectional study

Lambrecht, P., Vandenoetelaere, A., Matossian, A., Jansegers, S.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 63 KB

english, 2013

220

Baby bottle steam sterilizers disinfect home nebulizers inoculated with bacterial respiratory pathogens

Towle, Dana, Callan, Deborah A., Farrel, Patricia A., Egan, Marie E., Murray, Thomas S.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 279 KB

english, 2013

221

57 Ivacaftor in French patients with cystic fibrosis and a G551D mutation in the real world setting

Hubert, D., David, V., Rault, G., Dominique, S., Mély, L., Munck, A.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 73 KB

english, 2013

222

WS1.4 Significant bacterial infection missed using cough swabs compared to bronchoalveolar lavage in 1-year old newborn screened CF infants

Thia, L.P., Rand, S., Hill, L., Prasad, S.A., Bush, A., Balfour-Lynn, I.M., Pao, C., Ruiz, G., Stocks, J., Wallis, C., Suri, R.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 65 KB

english, 2013

223

WS8.1 The role of second-generation sequencing in describing the fungal microbiota in the adult cystic fibrosis (CF) airway and its correlation with clinical phenotype

Harrison, M.J., Twomey, K.B., McCarthy, Y., O'Connell, O.J., Alston, M., Febrer, M., Murphy, D.M., Eustace, J.A., Plant, B.J.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 65 KB

english, 2013

224

324 First experiences with a patient education program for children with cystic fibrosis and their parents

Staab, D., Lehmann, C., Stephan, V., Biedermann, T., Behl, E.S., Menrath, I.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 58 KB

english, 2013

225

ZnT8 antibodies in patients with cystic fibrosis: An expression of secondary beta-cell damage?

Bizzarri, Carla, Giannone, Germana, Benevento, Danila, Montemitro, Enza, Alghisi, Federico, Cappa, Marco, Lucidi, Vincenzina

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 101 KB

english, 2013

226

72 Inspiratory flow characteristics of the T-326 dry powder inhaler (DPI) in CF patients

Geller, D., Ament, B., Heuerding, S., Maykut, R., Pavkov, R.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 71 KB

english, 2013

227

WS15.3 Human amniotic mesenchymal stem cells modify the function and cytokine production of F508del airway epithelial cells upon coculture

Carbone, A., Castellani, S., Paracchini, V., Favia, M., Diana, A., Seia, M., Di Gioia, S., Casavola, V., Colombo, C., Conese, M.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 67 KB

english, 2013

228

39 Evaluation of the Nanoduct sweat test method after newborn screening for cystic fibrosis

Langen, A.M. Vernooij-van, Dompeling, E., Arets, H.G.M., Tiddens, H.A.W.M., Yntema, J.B., Dankert-Roelse, J.E.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 62 KB

english, 2013

229

343 A survey to assess patients' perceptions of CF psychosocial and nursing care during the process of lung transplantation

Prosser, A., O'Leary, C., Mcculloch, A.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 57 KB

english, 2013

230

What is the clinical significance of filamentous fungi positive sputum cultures in patients with cystic fibrosis?

Liu, Jane C., Modha, Deborah E., Gaillard, Erol A.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 160 KB

english, 2013

231

274 Do childhood eating habits in cystic fibrosis influence future behaviour and outcomes?

Kent, W., Wight, A., Sarkar, R., Dunne, J., Ledson, M., Walshaw, M.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 62 KB

english, 2013

232

56 Effect of withdrawal of ivacaftor therapy on CFTR channel activity and lung function in patients with cystic fibrosis

Accurso, F.J., Ratjen, F., Altes, T., Lubarsky, B., Dong, Q., Kang, L., Davies, J.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 73 KB

english, 2013

233

13 Genotype, disease severity, and healthcare resource use by patients with CF in the UK National Health Service

Wyatt, H., Ingram, A., Wasiak, R., Lambrelli, D., Davies, J., Bilton, D., Becker, C., Harrow, B.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 70 KB

english, 2013

234

268 Renal function impairment in cystic fibrosis

Freitas, F.J., Lopes, C.C., Azevedo, P., Barreto, C.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 65 KB

english, 2013

235

297 Comparison of two models of medical care for adult patients with cystic fibrosis (CF) in Uruguay

Parallada, G., Alemán, A., Rutz, M.G., Castro, M., Cosentino, D., Rey, A., Ramirez, P., Rios, M., Facal, M.N.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 58 KB

english, 2013

236

196 Airway surface liquid concentrations of aztreonam lysine for inhalation in children with cystic fibrosis: A modelling study

Bos, A.C., Vos, W.G., de Backer, J.W., van Holsbeke, C., Janssens, H.M., Tiddens, H.A.W.M.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 65 KB

english, 2013

237

58 Pulmonary exacerbations in CF patients with the G551D-CFTR mutation treated with ivacaftor

Flume, P., Wainwright, C., Tullis, E., Rodriguez, S., Davies, J., Wagener, J.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 73 KB

english, 2013

238

78 Pharmacokinetic variability of clarithromycin and ciprofloxacin in patients with cystic fibrosis (CF)

Dalbøge, C.S., Nielsen, X.C., Dalhoff, K., Alffenaar, J.-W., Duno, M., Buchard, A., Uges, D.R.A., Jensen, A.G., Jürgens, G., Pressler, T., Høiby, N., Johansen, H.K.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 69 KB

english, 2013

239

220 Control of sinonasal symptoms improves quality of life

Haynes, F., Dewar, J.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 66 KB

english, 2013

240

62 Oral reduced L-glutathione improves weight and calprotectin in pediatric cystic fibrosis patients

Visca, A., Hilton, S.C., Hudson, V.M., Bishop, C.T.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 68 KB

english, 2013

241

171 Anti-Pseudomonas aeruginosa IgY antibodies promote specific bacterial aggregation and internalization in polymorphonuclear neutrophils

Thomsen, K., Christophersen, L., Bjarnsholt, T., Jensen, P.Ø., Moser, C., Høiby, N.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 67 KB

english, 2013

242

89 Evaluation of a twice daily tobramycin regimen in adult cystic fibrosis patients

McCabe, D., Rodgers, H.C.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 67 KB

english, 2013

243

Dynamic vascular changes following intravenous antibiotics in patients with cystic fibrosis

Hull, James H., Garrod, Rachel, Ho, Timothy B., Knight, Ronald K., Cockcroft, John R., Shale, Dennis J., Bolton, Charlotte E.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 184 KB

english, 2013

244

266 Cystic fibrosis related osteopenia: What is the etiology?

Gokdemir, Y., Erdem, E., Haliloglu, B., Turan, S., Ersu, R., Karakoc, F., Karadag, B.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 65 KB

english, 2013

245

WS15.5 Effect of treatment with oligosaccharide nanomedicine OligoG on the rheology of cystic fibrosis sputum

Pritchard, M.F., Powell, L., Hill, K., Hawkins, K., Curtis, D., Doull, I., Onsøyen, E., Rye, P., Thomas, D.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 55 KB

english, 2013

246

150 Staphylococcus aureus small-colony variants are independently associated with worse lung disease in children with cystic fibrosis

Wolter, D., Emerson, J.C., McNamara, S., Buccat, A.M., Qin, X., Cochrane, E., Houston, L.S., Rogers, G.B., Marsh, P., Prehar, K., Pope, C.E., Blackledge, M., Déziel, E., Bruce, K.D., Ramsey, B.W., Gib

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 66 KB

english, 2013

247

137 Hydrogen cyanide concentrations in the breath of adult cystic fibrosis patients with and without Pseudomonas aeruginosa infection

Gilchrist, F.J., Bright-Thomas, R.J., Jones, A.M., Smith, D., Spanel, P., Webb, A.K., Lenney, W.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 64 KB

english, 2013

248

347 Team insights into adherence barriers: Learning from diabetes self-management exercise

Milne, A., Attfield, R., Thornton, S., Jones, S., Wildman, M.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 58 KB

english, 2013

249

WS19.1 Mediastinal lymphadenopathy: A prognostic tool in adult patients with cystic fibrosis

Morlacchi, L., Rosti, V., Mantero, M., D'Adda, A., Zanardelli, M., Pizzamiglio, G.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 63 KB

english, 2013

250

Importance of bacteriology in upper airways of patients with Cystic Fibrosis

Berkhout, M.C., Rijntjes, E., el Bouazzaoui, L.H., Fokkens, W.J., Brimicombe, R.W., Heijerman, H.G.M.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 136 KB

english, 2013

251

48 Reserpine inhibits the cystic fibrosis transmembrane conductance regulator (CFTR) chloride channel in Caco-2 monolayers

Awatade, N.T., Winpenny, J.P.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 65 KB

english, 2013

252

Development and validation of a cystic fibrosis genetic knowledge questionnaire within the general population of the United States

Baker, Hannah M., Brown, Roger L., Tluczek, Audrey

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 386 KB

english, 2013

253

255 Screening glucose disorders in cystic fibrosis: Continuous subcutaneous glucose monitoring compared to oral glucose tolerance test

Santalha, M., Barbosa, T.F., Amaral, B., Borges, T., Ribeiro, L., Silva, A.P., Cardoso, C., Oliveira, M.J., Cardoso, H., Senra, V., Herculano, R.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 67 KB

english, 2013

254

WS15.1 Development of a human model of airway epithelial cells invalidated for CFTR

Bellec, J., Losa, D., Bacchetta, M., Nguyen, T.H., Chanson, M.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 67 KB

english, 2013

255

67 Clinical outcomes and patient satisfaction following initiation of the TOBI Podhaler in CF adults

Brown, C.J., Nash, E.F., Cameron, S., Rashid, R., Whitehouse, J.L.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 62 KB

english, 2013

256

139 Evidence of Pseudomonas aeruginosa super-shedding from individual patients leading to airborne dissemination in a UK CF centre

Jauri, K., Holden, S., Cruz, S., Clayton, A.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 65 KB

english, 2013

257

54 UK and Ireland review of ivacaftor in severe CF: Impact on hospitalisations and antibiotic use

Barry, P.J., Plant, B.J., Simmonds, N.J., Bicknell, S., Shafi, N.T., Bell, N.J., Daniels, T., Felton, I., Gunaratnam, C., McKone, E.F., Jones, A.M., Horsley, A.R.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 73 KB

english, 2013

258

97 Antarctic bacteria as producers of antibiotic volatile compounds inhibiting cystic fibrosis pathogens

Maida, I., Papaleo, M.C., Perrin, E., Fondi, M., Orlandini, V., Emiliani, G., Romoli, R., Bartolucci, G., Tutino, M.L., Parrilli, G., De Pascale, D., Michaud, L., Lo Giudice, A., Fani, R.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 65 KB

english, 2013

259

315 Quality of life assessment in cystic fibrosis – Use of the Rasch latent trait model

Wanyama, S.S., Sevens, C., Malfroot, A., Knoop, C., Depoorter, A.M.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 61 KB

english, 2013

260

309 The use of a volumetric infusion device for intravenous antibiotic desensitisation in cystic fibrosis

Butler, M., Thompson, K., Watson, D., Kuitert, L.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 59 KB

english, 2013

261

178 Does nasal and bronchial nitric oxide in CF correlate to pathogen colonization in both airway levels?

Michl, R., Hentschel, J., Fischer, C., Beck, J.F., Mainz, J.G.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 68 KB

english, 2013

262

69 A randomised comparison of VANTOBRA and TOBI in cystic fibrosis patients with chronic Pseudomonas aeruginosa infection for pharmacokinetic and therapeutic equivalence

Sands, D., Sapiejka, E., Mazurek, H., Gaszczyk, G.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 72 KB

english, 2013

263

262 Glucose tolerance in cystic fibrosis patients: The DIAMUCO study

Bourdy, S., Touzet, S., Nové-Josserand, R., Reix, P., Pin, I., Quetant, S., Martin, C., Drai, J., Durieu, I.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 65 KB

english, 2013

264

151 Outbreak of multidrug-resistant Serratia marcescens detections in a paediatric cystic fibrosis (CF) centre

Rodman, J., Praprotnik, M., Aldeco, M., Lepej, D., Ostir, M., Seme, K., Krivec, U.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 66 KB

english, 2013

265

199 Early predictors of bronchiectasis and trapped air severity in cystic fibrosis

Tepper, L.A., Caudri, D., Rosenfeld, M., Tiddens, H.A.W.M.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 62 KB

english, 2013

266

132 Anti-Pseudomonas aeruginosa IgG ELISA in a CF referral center in Brazil. Preliminary results

Mauch, R.M., Rossi, C.L., Ribeiro, J.D., Ribeiro, A.F., Levy, C.E.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 65 KB

english, 2013

267

Multilocus sequence typing of Scedosporium apiospermum and Pseudallescheria boydii isolates from cystic fibrosis patients

Bernhardt, A., Sedlacek, L., Wagner, S., Schwarz, C., Würstl, B., Tintelnot, K.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 423 KB

english, 2013

268

143 The social network in cystic fibrosis centre care and the risk of shared Pseudomonas aeruginosa strain infection

Kidd, T.J., Magalhães, R.J. Soares, Paynter, S., Bell, S.C.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 68 KB

english, 2013

269

316 Preliminary results of the Quality of Life Systemic Inventory for children in pediatric cystic fibrosis: A tool for clinical interventions?

Touchèque, M., Etienne, A.-M.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 61 KB

english, 2013

270

124 Ribosomal RNA intergenic spacer analysis (RISA) as a rapid and diagnostic means to profile microbial diversity in cystic fibrosis sputum

Flight, W.G., Marchesi, J.R., Norville, P., Dedeckova, K., Bull, M., Bright-Thomas, R.J., Mutton, K.J., Dřevínek, P., Jones, A.M., Mahenthiralingam, E.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 64 KB

english, 2013

271

WS9.1 Effectiveness of airway clearance techniques when patients choose their airway clearance technique

McIlwaine, M.P., Agnew, J.L., Alarie, N., Lands, L.C., Davidson, G.F., Ratjen, F.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 65 KB

english, 2013

272

WS19.5 Characterization of fungal colonization phenotypes in pediatric cystic fibrosis lung disease

Graepler-Mainka, U., Berenbrinker, S., Hector, A., Riethmueller, J., Stern, M., Hartl, D.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 62 KB

english, 2013

273

51 Effect of arginase inhibition on NO formation in cystic fibrosis sputum

Grasemann, H., Nasiri, J., Ratjen, F.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 56 KB

english, 2013

274

WS19.7 Assessment of habitual physical activity in adults with cystic fibrosis

Savi, D., Quattrucci, S., Troiani, P., Zullo, S., De Biase, R.V., Di Paolo, M., Internullo, M., Cucchiara, S., Palange, P.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 62 KB

english, 2013

275

WS14.2 Assessing components of fitness in cystic fibrosis: The practicality and value of using a battery of exercise tests in CF clinical practice

Morris, A.R., Greenwood, J., Ledson, M., Walshaw, M.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 62 KB

english, 2013

276

WS10.4 A new molecular strategy using CFTR2 data for improving IRT/DNA screening

Farrell, P., Baker, M., Atkins, A.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 61 KB

english, 2013

277

107 Bronchial infection with Burkholderia cepacia complex in cystic fibrosis. Experience at a Spanish regional cystic fibrosis centre

Vazquez, C., Martinez, N., Sojo, A., Gomez, A., Gomez, B., Cabero, M.J., Belmonte, E. Perez, Santiago, M., Rodriguez, A., Urra, E., Saez, J.A., Baranda, F.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 69 KB

english, 2013

278

WS12.5 Lung clearance index and exercise capacity among children with mild CF- and non-CF bronchiectasis

Hatziagorou, E., Avramidou, V., Kirvassilis, F., Kontouli, K., Georgopoulou, V., Tsanakas, J.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 61 KB

english, 2013

279

236 Agreement between real-time auscultation and computerised respiratory analyses

Marques, A., Oliveira, A., Jácome, C., Dinis, J., Pinho, C.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 62 KB

english, 2013

280

Elevated levels of miR-145 correlate with SMAD3 down-regulation in Cystic Fibrosis patients

Megiorni, Francesca, Cialfi, Samantha, Cimino, Giuseppe, De Biase, Riccardo Valerio, Dominici, Carlo, Quattrucci, Serena, Pizzuti, Antonio

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 325 KB

english, 2013

281

41 Nasal airway resistance in adult patients with cystic fibrosis

Berkhout, M.C., van der Meijden, G.M.W., Rijntjes, E., Bouazzaoui, L.H. el, Heijerman, H.G.M.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 62 KB

english, 2013

282

WS12.1 Evidence of diminished FEV1 in CF 6-year-olds followed in the European CF registry, 2007–2009

VanDevanter, D.R., Pasta, D.J.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 61 KB

english, 2013

283

WS4.4 Restoration of F508Δ-CFTR trafficking and function by liposome-mediated delivery of antibodies against cytokeratin 8

Chatin, B., Mével, M., Edelman, A., Pitard, B.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 62 KB

english, 2013

284

WS4.2 Exploration of the ATP binding site in CFTR-NBD1 for enhanced ligand binding

Fichman, M., Schmidt, A., Thomas, P.J., Senderowitz, H.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 62 KB

english, 2013

285

207 Non-invasive ventilation in cystic fibrosis

Almeida, S., Gil, J., Nunes, T., Barreto, C., Pereira, L.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 60 KB

english, 2013

286

279 Composition of fatty acids in erythrocytes and its correlation with the nutritional status, genotype, pancreatic and pulmonary function in cystic fibrosis patients

Cunha, A.L.P., Chaves, C.R.M.M., Lacerda, S.V., Noronha, A.R.N., Werner, M.L.F., Cabello, G.M.K., Carmo, M.G.T.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 66 KB

english, 2013

287

126 Changes in the microbiology of the pulmonary secretions in cystic fibrosis (CF) patients: Report on 4 different years during 25 years

Galanternik, L., Lubovich, S., Zaragoza, S., Rodríguez, V., Vazquez, M., Teper, A.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 63 KB

english, 2013

288

Sputum neutrophils in cystic fibrosis patients display a reduced respiratory burst

Houston, Neralee, Stewart, Niall, Smith, Daniel S., Bell, Scott C., Champion, Alan C., Reid, David W.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 637 KB

english, 2013

289

WS5.6 Regulatory T cells in cystic fibrosis patients infected with Pseudomonas aeruginosa

Hector, A., Schäfer, H., Pöschel, S., Bakele, M., Rieber, N., Carevic, M., Hogardt, M., Neri, D., Graepler-Mainka, U., Riethmueller, J., Stern, M., Hartl, D.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 64 KB

english, 2013

290

142 Cross infection of Pseudomonas aeruginosa (PA) among children under 24 months of age

Bassani, L., Colombrita, D., Panteghini, C., Pavoni, E., Caruso, A., Padoan, R., Bertasi, B., Timpano, S., Rodella, E., Zini, A.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 65 KB

english, 2013

291

185 Invasive pulmonary mycosis caused by Scedosporium and Pseudallescheria spp. in patients with CF. Diagnostic and treatment guidelines

Schwarz, C., Melichar, V., Staab, D., Runge, C., Heuer, E., Sahly, H., Martin, S., Holger, K., Schmidt-Grohé, S., Bouchara, P., Meißner, P., Skopnik, H., Tintelnot, K.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 66 KB

english, 2013

292

WS13.3 Lung clearance index: A tool to assess the response to intravenous treatment among children with cystic fibrosis

Hatziagorou, E., Avramidou, V., Kirvassilis, F., Tsanakas, J.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 64 KB

english, 2013

293

194 Clinical impact of inhaled mannitol in an adult cystic fibrosis population

Button, B.M., Finlayson, F., Borg, B., Ivulich, S., Wilson, J.W.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 65 KB

english, 2013

294

WS17.4 Anti-pseudomonal bacteriophage cocktail reduces inflammatory responses in the murine lung

Pabary, R., Singh, C., Morales, S., Bush, A., Alshafi, K., Bilton, D., Alton, E.W., Smithyman, A., Davies, J.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 71 KB

english, 2013

295

284 The development of guidelines for the use of megestrol acetate (Megace®) as an appetite stimulant in adults with cystic fibrosis

Al-Siaidi, J., Keele, A., Bateman, K.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 62 KB

english, 2013

296

37 Comparison of two sweat test systems (Macroduct versus Nanoduct) for the diagnosis of cystic fibrosis in the newborn screening program in Switzerland

Barben, J., Rüegg, C.S., Gallati, S., Kuehni, C.E., Baumgartner, M., Torresani, T., Schöni, M.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 60 KB

english, 2013

297

WS6.3 Airway clearance and physical activity – Results from a UK survey

Ferguson, K.V., Old, K.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 58 KB

english, 2013

298

60 Permanent correction of >80% of disease-causing mutations in human CF cells

Hollywood, J.A., Lee, C.M., Flynn, R., Scallan, M.F., Harrison, P.T.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 73 KB

english, 2013

299

117 Achromobacter xylosoxidans characteristics important for lung colonization of cystic fibrosis (CF) patients

Trancassini, M., Citerà, N., Tuccio, V., Magni, A., Iebba, V., De Biase, R.V., Schippa, S.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 70 KB

english, 2013

300

181 The use of a rationalised antibiotic susceptibility testing protocol for children with cystic fibrosis and chronic Pseudomonas aeruginosa infection

Hurley, M., Monk, K., Smyth, A.R.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 68 KB

english, 2013

301

102 Denitrification by cystic fibrosis pathogens

Kolpen, M., Bjarnsholt, T., Kühl, M., Hansen, C.R., Dalbøge, C.S., Høiby, N., Jensen, P.Ø.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 68 KB

english, 2013

302

141 An investigation into the clinical relevance and cross-infection risk of Pseudomonas aeruginosa cluster A in CF patients

Kenna, D., Martin, K., Mustafa, N., Baddal, B., Payne, Z., Perry, C., Denton, M., Turton, J.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 65 KB

english, 2013

303

330 The “Ready, Steady, Go” programme – Addressing the needs of those in transition

Ginnity, T.M. Mc, Maddison, J.C., Harris, A.L.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 57 KB

english, 2013

304

77 Microbiological monitoring of the respiratory tract in cystic fibrosis patients

Nikonova, V., Krasovskiy, S., Kondrateva, E., Kapranov, N.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 68 KB

english, 2013

305

20 Cystic fibrosis in Egypt: New mutational detection of the CFTR gene in patients from Alexandria, northern Egypt

El-Seedy, A., Pasquet, M.-C., Shafiek, H., El-Komy, M., Kitzis, A., Ladevèze, V.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 67 KB

english, 2013

306

80 Determination of patient screen failure and dropout rates for industry-sponsored CF inhaled antibiotic studies

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 67 KB

english, 2013

307

339 Segregation of patients with cystic fibrosis – Examining patient and parental knowledge and opinions

Alanoor, R.K., Pai, P., Shorten, H., Betteridge, A., Kavanagh, C.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 58 KB

english, 2013

308

325 Development and evaluation of an internet-based psychological intervention for parents of children with cystic fibrosis

Goldbeck, L., Knaevelsrud, C., Lehmann, C., Weiss, C., Fidika, A., Herle, M.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 58 KB

english, 2013

309

241 Evidence for a cystic fibrosis enteropathy

Adriaanse, M., van der Sande, L., Dompeling, E., Buurman, W., Vreugdenhil, A.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 64 KB

english, 2013

310

206 Clinical and paraclinical profile and risk of exacerbations in patients with cystic fibrosis attending a national reference center in Latin America

Rey, M.A., Rutz, G., Parallada, G., Rios, M., Castro, M., Consentino, D., Ramirez, P., Fontan, M.N.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 60 KB

english, 2013

311

Peripheral neuropathy in cystic fibrosis: A prevalence study

Chakrabarty, Biswaroop, Kabra, S.K., Gulati, Sheffali, Toteja, G.S., Lodha, Rakesh, Kabra, Madhulika, Pandey, R.M., Srivastava, Achal

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 349 KB

english, 2013

312

101 Microbial communities and interactions in chronic lung infection in cystic fibrosis patients

Fothergill, J., Martin, L., Ledson, M., Walshaw, M., Winstanley, C.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 68 KB

english, 2013

313

259 The diurnal variation in glucose handling in CF – Is a change in guidance needed?

Nazareth, D., Dyce, P., Malone, V., Walshaw, M.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 62 KB

english, 2013

314

Effect of VX-770 (Ivacaftor) and OAG on Ca2+ influx and CFTR activity in G551D and F508del-CFTR expressing cells

Vachel, Laura, Norez, Caroline, Becq, Frédéric, Vandebrouck, Clarisse

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 431 KB

english, 2013

315

166 Beneficial immunomodulatory effect of vardenafil in mouse CF macrophages

Vaz, P. Castanho, Dhooghe, B., Palmai, M., Lebecque, P., Noël, S., Leal, T.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 66 KB

english, 2013

316

WS17.2 ALX-109 potentiates the effect of inhaled antibiotics at killing Pseudomonas aeruginosa biofilms on human airway cells

Moreau-Marquis, S., Drexinger, J.D., Perez, V. Juarez, Stanton, B.A.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 71 KB

english, 2013

317

5 Large scale, high throughput, cystic fibrosis screening using a new kit for CFTR mutation detection

Centrone, C., Minuti, B., Falconi, S., Mariottini, A., Gozzini, A., Torricelli, F.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 64 KB

english, 2013

318

100 Comparison of airway microbiota composition in healthy children and children with CF

McGrath, S.J., McIlreavey, L., O'Neill, K., Johnston, E., Fulton, C.R., Elborn, J.S., Tunney, M., Gilpin, D.F.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 68 KB

english, 2013

319

179 Early eradication of Pseudomonas aeruginosa (PA) in cystic fibrosis patients (CF): Which is the better treatment?

Lubovich, S., Villagra, G., Fili, S., Zaragoza, S., Rodriguez, V., Galanternik, L., Ratto, P., Colom, A., Teper, A.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 68 KB

english, 2013

320

WS21.7 Identification and characterization of two novel mutations in conserved sequences tags (CSTs) of CFTR gene

Tomaiuolo, R., Scorza, M., Elce, A., Giordano, S., Castaldo, G.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 67 KB

english, 2013

321

WS5.2 Toll-like receptor 9 deficiency protects mice against Pseudomonas aeruginosa pulmonary infection

Ben Mohamed, F., Medina, M., Zhang, Y., Maschalidi, S., Chignard, M., Manoury, B., Touqui, L.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 70 KB

english, 2013

322

163 A role for the WFDC protein, WAP2, in the regulation of inflammatory response in the lung

Glasgow, A., Weldon, S., Scott, A., McLean, D., Camper, N., Lundy, F., McNally, P., Elborn, J.S., Taggart, C.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 66 KB

english, 2013

323

348 From rescue to prevention: Collaborative social marketing project developing posters to promote adherence for nebulised therapy in adults with cystic fibrosis

Jones, S., Babiker, N., Field, E., Royle, J., Wildman, M.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 58 KB

english, 2013

324

Inhaled nitric oxide decreases the bacterial load in a rat model of Pseudomonas aeruginosa pneumonia

Miller, Christopher C., Hergott, Christopher A., Rohan, Marta, Arsenault-Mehta, Kyle, Döring, Gerd, Mehta, Sanjay

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 283 KB

english, 2013

325

Author Index

Journal:

Journal of Cystic Fibrosis

Year:

2013

File:

PDF, 149 KB

2013

326

WS21.9 Screening for novel F508del-CFTR correctors identified by pharmacophore modelling through automated microscopy and NBD1 folding assays

Dahimène, S., Romão, A., Botelho, H.M., Palma, M., Correia, A.R., Farinha, C.M., King-Underwood, J., Williams, J., Hirst, S., Gomes, C.M., Amaral, M.D.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 55 KB

english, 2013

327

22 Misdiagnosis of cystic fibrosis in adulthood

Baran, E., Granero, N., Hendriksen, B., Butti, F., D'Ascenzo, V., Ibarra, S., Pistorio, V., Volta, L., García, G.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 68 KB

english, 2013

328

329 Preparing parents for the transition from paediatric to adult cystic fibrosis (CF) care

Oxley, H., Woodhead, S., Biesty, J., Fauset-Jones, J., Trenchard, S., Jones, A.M.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 57 KB

english, 2013

329

81 A UK survey of anti-staphylococcal antibiotic prophylaxis (ASAP) for cystic fibrosis patients

Waterhouse, B.R., Stewart, B.J., Southern, K.W.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 69 KB

english, 2013

330

167 Molecular mechanisms of enhanced expression of interleukin 8 (CXCL8) in cystic fibrosis (CF) airway epithelial (AE) cells

Poghosyan, A., Clifford, R.L., Coward, W., Pang, L., Knox, A.J.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 66 KB

english, 2013

331

292 Vitamin blood levels after introducing multivitamin supplementation with AquADEKs® in cystic fibrosis children

Moen, I.E., Storroesten, O.-T., Bakkeheim, E.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 65 KB

english, 2013

332

WS14.3 Chronic inflammation and infection affect exercise training response in adolescents with cystic fibrosis

Arets, H.G.M., van de Weert-van Leeuwen, P.B., Hulzebos, H.J., Werkman, M.S., Michel, S., Vijftigschild, L.A.W., van Meegen, M.A., van der Ent, C.K., Beekman, J.M.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 62 KB

english, 2013

333

169 Comparison of inflammatory response from CF bronchial epithelial cells following stimulation with aerobic and anaerobic Pseudomonas aeruginosa

Mawhinney, A., Moffitt, K.L., Tunney, M., Elborn, J.S.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 66 KB

english, 2013

334

162 Serum amyloid A as a useful serum marker of lung inflammation in cystic fibrosis

Cresta, F., Naselli, A., Favilli, F., Casciaro, R., De Alessandri, A., Pistorio, A., Minicucci, L.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 66 KB

english, 2013

335

WS19.9 A prospective multicenter study to dissect Staphylococcus aureus-colonization from infection in cystic fibrosis patients

Junge, S., Wiedemann, B., Tümmler, B., Dübbers, A., Küster, P., Nofer, J., Ellemunter, H., Mainz, J.G., Heuer, E., Sextro, W., Körner-Rettberg, C., Ballmann, M., Mellies, U., Hammermann, J., Teschler,

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 66 KB

english, 2013

336

WS8.6 Interaction of microorganisms modulating the cystic fibrosis clinical severity

Marson, F.A., Bertuzzo, C.S., Levy, C.E., Ribeiro, A.F., Ribeiro, J.D.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 54 KB

english, 2013

337

Methicillin-resistant Staphylococcus aureus

Turner, Evie, Brownlee, Keith G., Denton, Miles

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 72 KB

english, 2013

338

140 Population structure of Pseudomonas aeruginosa and the prevalence of epidemic clones in patients with cystic fibrosis over four years

van Mansfeld, R., de Vrankrijker, L., Brimicombe, R., Heijerman, H.G.M., van Berkhout, F. Teding, van der Ent, C.K., Wolfs, T., Bonten, M., Willems, R.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 65 KB

english, 2013

339

Association between Staphylococcus aureus alone or combined with Pseudomonas aeruginosa and the clinical condition of patients with cystic fibrosis

Hubert, Dominique, Réglier-Poupet, Hélène, Sermet-Gaudelus, Isabelle, Ferroni, Agnès, Le Bourgeois, Muriel, Burgel, Pierre-Régis, Serreau, Raphaël, Dusser, Daniel, Poyart, Claire, Coste, Joël

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 210 KB

english, 2013

340

27 Diagnosing cystic fibrosis: Neonatal screening versus clinical diagnosis. A national registration

Gerzon, R., Dankert-Roelse, J.E., Langen, A.M. Vernooij-van

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 61 KB

english, 2013

341

Mitochondrial OXPHOS function is unaffected by chronic azithromycin treatment

Negari, Shelly Ben-Harush, Aouizerat, Tzemach, Tenenbaum, Ariel, Cohen-Cymberknoh, Malena, Shoseyov, David, Kerem, Eitan, Saada, Ann

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 342 KB

english, 2013

342

270 Body mass index percentiles in children with cystic fibrosis

Creedon, M., Owen, E., Prasad, A., Suri, R.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 64 KB

english, 2013

343

293 A serum vitamin D >75 nmol/l is achievable in children with cystic fibrosis (CF)

Jones, K.D., McShane, D., Iles, R., Ross-Russell, R., Saward, C.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 61 KB

english, 2013

344

210 What airway clearance is being carried out by the cystic fibrosis (CF) population in the UK? Results from a UK national survey conducted by the Cystic Fibrosis Trust

Ferguson, K.V., Old, K.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 58 KB

english, 2013

345

256 The diagnostic utility of continuous glucose monitoring (CGM) in cystic fibrosis related diabetes (CFRD)

Dyce, P., Malone, V., Nazareth, D., Walshaw, M.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 66 KB

english, 2013

346

98 Searching for new antimicrobial targets in Burkholderia genus: In silico analysis of the RND superfamily

Perrin, E., Fondi, M., Papaleo, M.C., Maida, I., Emiliani, G., Buroni, S., Pasca, M.R., Riccardi, G., Fani, R.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 65 KB

english, 2013

347

122 The impact of human rhinovirus infection on the cystic fibrosis lung microbiome

Flight, W.G., Marchesi, J.R., Norville, P., Mutton, K.J., Webb, A.K., Bright-Thomas, R.J., Jones, A.M., Mahenthiralingam, E.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 66 KB

english, 2013

348

16 The −765G>C and 8473T>C polymorphism in COX2 gene and 57460C>T polymorphism in IFRD1 gene as modifiers of cystic fibrosis severity

Marceliino, A.R., Marson, F.A., Bertuzzo, C.S., Ribeiro, J.D.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 70 KB

english, 2013

349

290 Relationship between serum 25-hydroxyvitamin D (25(OH)D) level and parathyroid hormone (PTH) level in adults with cystic fibrosis

Robb, L., Richardson, M., Peters, A., Mullan, C. Mc, Robertson, J., Intosh, L. Mc, Greening, A., Rodgers, H.C.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 66 KB

english, 2013

350

144 A multiple-locus variable-number tandem repeat analysis (MLVA) typing scheme developed for genetic fingerprinting of Burkholderia cenocepacia and applied to nation-wide epidemiological analysis

Segonds, C., Thouverez, M., Pourcel, C.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 68 KB

english, 2013

351

50 Modification of the salivary secretion assay in F508del mice – Salivary chloride quantification and its correlation to the human sweat test

Droebner, K., Mao, Q., Sandner, P.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 65 KB

english, 2013

352

WS7.1 Multi-target corrective effect of vardenafil on F508del-CFTR function and localization

Dhooghe, B., Noël, S., Bouzin, C., Lebecque, P., Wallemacq, P., Leal, T.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 71 KB

english, 2013

353

272 Caloric intake in children and adolescents with cystic fibrosis

Woestenenk, J.W., Castelijns, S.J., van der Ent, C.K., Houwen, R.H.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 64 KB

english, 2013

354

341 Patients' preferences of medical information

Strandner, K., Gilljam, M.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 57 KB

english, 2013

355

WS4.5 LMTK2 regulates CFTR endocytosis by phosphorylation at CFTR Ser-737

Luz, S., Cihil, K., Thibodeau, P.H., Brautigan, D.L., Amaral, M.D., Farinha, C.M., Swiatecka-Urban, A.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 55 KB

english, 2013

356

WS10.5 Impact of CFTR mutations affecting mRNA processing and looking for therapeutic compounds

Ramalho, A.S., Felicio, V., Amaral, M.D.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 57 KB

english, 2013

357

247 Diagnoses of cystic fibrosis liver disease in an adult cystic fibrosis centre

Addy, C., Bateman, K., Bell, N.J.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 58 KB

english, 2013

358

Poor growth in an infant with cystic fibrosis due to an antenatal perforation and incomplete bowel obstruction

Brookes, Isobel, Desai, Maya, Duthie, Gillian, Lander, Anthony

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 184 KB

english, 2013

359

209 Physical activity and attitudes towards exercise in the cystic fibrosis (CF) population – Results from a UK national survey conducted by the Cystic Fibrosis Trust

Ferguson, K.V., Old, K.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 58 KB

english, 2013

360

281 Home parenteral nutrition (HPN) in malnourished cystic fibrosis (CF) patients: A safe and effective nutritional therapy

Lezo, A., Santini, B., Sabet, D., Bignamini, E.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 62 KB

english, 2013

361

271 Implications of transitioning from CDC to WHO growth charts on growth evaluation in young children with cystic fibrosis in the US

Zhang, Z., Shoff, S.M., Lai, H.J.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 64 KB

english, 2013

362

335 Comparing the clinical characteristics of adolescents with CF at transition over the past 10 years

Sheehan, D., Colombage, R., Prasad, A., Suri, R.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 58 KB

english, 2013

363

28 Performance of a novel newborn screening strategy in the Dutch routine heel prick program

Dankert-Roelse, J.E., Elvers, B., Lanting, C.I.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 61 KB

english, 2013

364

8 The in cis effect of c.2562T>G and c.2657+5G>A CFTR splice variants

Igreja, S., Casals, T., Amaral, M.D., Ramalho, A.S.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 64 KB

english, 2013

365

70 Use of an electronic monitoring system to generate objective information on patients' adherence to taking treatments of a novel inhaled tobramycin solution (VANTOBRA)

Sands, D., Sapiejka, E., Mazurek, H., Gaszczyk, G.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 72 KB

english, 2013

366

342 Therapeutic patient education and quality improvement program: What synergy?

David, V., Rault, G., Pougheon-Bertrand, D., Dorenlot, E.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 57 KB

english, 2013

367

36 Clinical outcomes of cystic fibrosis patients during their first year of life after neonatal screening implementation

Gomez, C.C.S., Servidoni, M.F., Souza, J.F., Ribeiro, M.A.G.O., Toro, A.A.D.C., Vinagre, A.M., Goto, M., Nogueira, R.J.N., Levy, C.E., Hessel, G., Ribeiro, J.D., Ribeiro, A.F.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 60 KB

english, 2013

368

336 Neuropsychological functioning in children with cystic fibrosis: First results of a prospective comparative study

Kok, T.B., Kingma, A., Merkus, P.F.J.M., Post, W.J., Kamps, W.A., Tucha, O., De Bont, E.S.J.M., Vrijlandt, E.J.L.E.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 58 KB

english, 2013

369

WS11.5 The effect of social deprivation, disease severity, and time in hospital on employment chances in the UK cystic fibrosis population: A longitudinal study

Taylor-Robinson, D., Smyth, R., Diggle, P., Whitehead, M.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 54 KB

english, 2013

370

249 Liver disease in children with cystic fibrosis – The contribution of ultrasound evaluation

Pinto, M. Valente, Castanhinha, S., Pereira, L., Lopes, A.I., Barreto, C.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 63 KB

english, 2013

371

45 Exhaled nitric oxide is associated with Pseudomonas aeruginosa infection and peripheral airway obstruction in cystic fibrosis

Genkova, N., Todorova, M., Marinov, B., Mandadzhieva, S., Bosheva, M., Kostianev, S.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 68 KB

english, 2013

372

130 Chronic infection with Pseudomonas aeruginosa in cystic fibrosis – A risk factor for nasal polyposis after lung transplantation

Vital, D., Holzmann, D., Boehler, A., Hofer, M.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 67 KB

english, 2013

373

Self-efficacy: Empowering parents of children with cystic fibrosis

McDonald, Catherine M., Haberman, Diane, Brown, Natalie

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 121 KB

english, 2013

374

242 Evaluation of the size and contraction of the gallbladder by ultrasound in cystic fibrosis patients with and without pancreatic insufficiency

Yamada, R.M., Ribeiro, A.F., Ribeiro, J.D., Marson, F.A., Servidoni, M.F., Nogueira, R.J.N., Toro, A.A.D.C., Levy, C.E., Hessel, G.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 64 KB

english, 2013

375

152 Prevotella spp. isolated from patients with cystic fibrosis: Transient or persistent colonisers?

Gilpin, D.F., Graham, K.A., Sherrard, L., McGrath, S.J., McIlreavey, L., Johnston, E., Bull, M., Mahenthiralingam, E., Elborn, J.S., Tunney, M.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 66 KB

english, 2013

376

222 Real life timing and cleaning of inhalation therapy

Parrott, H., Agent, P., Bilton, D.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 58 KB

english, 2013

377

228 The ultimate Olympic challenge: Getting CF patients involved in and motivated by exercise

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 61 KB

english, 2013

378

WS9.2 Patient- and physiotherapist-reported adherence to airway clearance therapy, inhalational therapy and exercise in cystic fibrosis

Button, B.M., Kotowicz, E., Holland, A.E., Burge, A., Ivulich, S., Ellis, M., Wilson, J.W.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 65 KB

english, 2013

379

64 Tiotropium in cystic fibrosis: Pooled analysis of phase II and III randomized, controlled trials

Geller, D., Koker, P., Elborn, J.S., Le Maulf, F., Kattenbeck, S., Moroni-Zentgraf, P., Ratjen, F.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 68 KB

english, 2013

380

Acknowledgment to reviewers 2012

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 125 KB

english, 2013

381

Novel diagnostic PCR assay for Burkholderia cenocepacia epidemic strain ST32 and its utility in monitoring infection in cystic fibrosis patients

Dedeckova, Klara, Kalferstova, Lucie, Strnad, Hynek, Vavrova, Jolana, Drevinek, Pavel

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 347 KB

english, 2013

382

WS12.6 Comparison of two methods to identify bronchiectasis on chest computed tomography scans in two cohorts of young patients with cystic fibrosis

Kuo, W., Rosenow, T., Bos, A.C., Stick, S.M., Tiddens, H.A.W.M.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 61 KB

english, 2013

383

148 Direct detection, clonal analysis, and characterization of wild type and small colony variant strains of Staphylococcus aureus from the sputa of CF patients of the Prague CF centre

Tkadlec, J., Bukáčková, E., Fila, L., Bartošová, J., Dřevínek, P., Melter, O.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 65 KB

english, 2013

384

95 Ceftazidime continuous IV infusion in patients with cystic fibrosis and pyridine production

Bourget, P., Amin, A., Dupont, C., Abely, M., Desmazes-Dufeu, N., Dubus, J.-C., Jaouani, B.-L., Nové-Josserand, R., Pages, J., Panzo, R., Hubert, D.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 68 KB

english, 2013

385

109 The Burkholderia cepacia small colony variants (SCV) are a more pathogenic bacterial form that may facilitate persistent respiratory infections in CF patients

Pinto-de-Oliveira, A., Coutinho, C.P., Ramos, C.G., Sousa, S.A., de Carvalho, C.C.C.R., Leitão, J.H., Sá-Correia, I.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 65 KB

english, 2013

386

WS6.1 A cross-sectional evaluation of factors influencing adherence in children with cystic fibrosis

Goodfellow, N.A., Reid, A., Shields, M.D., Hawwa, A.F., McElnay, J.C.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 58 KB

english, 2013

387

244 The effect of lubiprostone on human duodenal biopsy samples

Taylor, C.J., Przeworek, J., Robson, L.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 64 KB

english, 2013

388

WS21.1 Cystic fibrosis incidence in Portugal

Pacheco, P., Silva, C., Loureiro, P.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 65 KB

english, 2013

389

127 Characterization of bacteria isolated from the respiratory tract of pediatric cystic fibrosis patients followed in a CF specialized center

Romão, P., Jotta, R., Sousa, R., Pereira, L., Barreto, C.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 67 KB

english, 2013

390

219 Use of the ‘lung flute’ for sputum induction in children with cystic fibrosis: A pilot study

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 66 KB

english, 2013

391

WS20.1 Role of transcription factors and microRNAs in CFTR gene expression

Bonini, J., Varilh, J., Viart, V., Claustres, M., Taulan-Cadars, M.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 67 KB

english, 2013

392

WS2.1 “Feeling my way”: Information needs for parents whose child has been diagnosed with CF following newborn screening

Jessup, M., Shields, L., Grogan, S., Branch-Smith, C.A., Douglas, T.A.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 59 KB

english, 2013

393

WS2.3 Parents' roles and involvement in young adults' clinic appointments

Beresford, B., Stuttard, L.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 58 KB

english, 2013

394

Drug induced complications; can we do more?

Peckham, Daniel, Whitaker, Paul

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 1.27 MB

english, 2013

395

302 CF related low bone mineral density – Who has it and what are we doing about it?

Lea-Davies, M., Speight, L., Michael, T., Stone, M., Ketchell, R.I., Lau, D., Duckers, J.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 62 KB

english, 2013

396

208 A two and a half year review of bronchoscopy findings in paediatric patients with cystic fibrosis

Jawad, M., Clayton, S., Peach, J., Alexander, J., Lenney, W., Gilchrist, F.J.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 60 KB

english, 2013

397

WS7.6 UK and Ireland review of ivacaftor in severe CF: Impact on lung function and weight

Barry, P.J., Plant, B.J., Nair, A., Simmonds, N.J., Bicknell, S., Shafi, N.T., Bell, N.J., Daniels, T., Felton, I., Gunaratnam, C., McKone, E.F., Jones, A.M., Horsley, A.R.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 60 KB

english, 2013

398

Pooled analysis of two large randomised phase III inhaled mannitol studies in cystic fibrosis

Bilton, Diana, Bellon, Gabriel, Charlton, Brett, Cooper, Peter, De Boeck, Kris, Flume, Patrick A., Fox, Howard G., Gallagher, Charles G., Geller, David E., Haarman, Eric G., Hebestreit, Helge U., Kolb

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 682 KB

english, 2013

399

WS15.2 Derivation of normal and cystic fibrosis human induced pluripotent stem cells (iPSCs) from airway epithelium

Loi, R., Pinna, S., Weiss, D.J.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 67 KB

english, 2013

400

204 Clinical and functional determinants of exercise performance in adults with cystic fibrosis

Pastre, J., Prevotat, A., Tardif, C., Mammar, A., Perruchini, J.M., Wemeau-Stervinou, L., Perez, T., Duhamel, A., Wallaert, B.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 63 KB

english, 2013

401

118 Characterisation of lipopolysaccharide from Prevotella spp. isolated from CF patients

Matier, T., Tunney, M., Valvano, M., Muhlebach, M., Hatch, J., Wolfgang, M.C., Elborn, J.S.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 70 KB

english, 2013

402

WS14.5 Interval exercise training in cystic fibrosis – Effects on maximal and submaximal exercise capacity in severely affected adults

Gruber, W., Braumann, K.M., Beneke, R.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 59 KB

english, 2013

403

352 Embedding motivational interviewing training capacity in cystic fibrosis dietitians and physiotherapists

Rose, C., Attfield, R., Milne, A., Thornton, S., Jones, S., Royle, J., Wildman, M.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 58 KB

english, 2013

404

21 Genotype–phenotype correlation of CFTR p.Leu206Trp mutation in 22 paediatric and adult cystic fibrosis (CF) patients

Gartner, S., de Gracia, J., Alvarez, A., Casals, T., Rovira, S., Asensio, O., de Mir, I., Torrent, A., Bosque, M., Moreno, A.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 67 KB

english, 2013

405

74 Improved tolerability, adherence and reduced intravenous (IV) antibiotic usage in CF patients receiving inhaled versus nebulised antibiotic prophylaxis. A real world comparison of tobramycin inhaled powder (TIP) and tobramycin inhaled solution (TIS)

Harrison, M.J., Mccarthy, M., Fleming, C., Shortt, C., Hickey, C., Eustace, J.A., Murphy, D.M., Plant, B.J.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 62 KB

english, 2013

406

34 Children with a late diagnosis of CF despite a long-established newborn screening programme

Jaksic, M., Byrnes, C., Tate, J.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 60 KB

english, 2013

407

201 CT findings in cystic fibrosis diagnosed in adulthood

Nespoli, P., Parlatano, D., Cortese, G., Messore, B., Bena, C., Chiesa, M., Veltri, A.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 62 KB

english, 2013

408

WS19.3 The value of deep oropharyngeal suction specimens in identifying lower airway bacteria in young children with cystic fibrosis

Doumit, M., Belessis, Y., Stelzer-Braid, S., Rawlinson, W.D., Jaffe, A.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 63 KB

english, 2013

409

WS13.2 Lung clearance index (LCI) and airway infection in CF

O'Neill, K., Bradley, J.M., Johnston, E., Reid, A., McCaughan, J., Moore, J.E., Tunney, M., Elborn, J.S.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 65 KB

english, 2013

410

65 Miglustat therapy ameliorates bone mass and bone formation in F508del cystic fibrosis mice

Le Henaff, C., Häy, E., Velard, F., Marty, C., Marie, P., Jacquot, J.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 62 KB

english, 2013

411

84 Azithromycin resistance in Prevotella species isolated from CF patients

Sherrard, L., Graham, K.A., McGrath, S.J., McIlreavey, L., Hatch, J., Muhlebach, M., Gilpin, D.F., Elborn, J.S., Schneiders, T., Tunney, M.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 67 KB

english, 2013

412

183 Pseudomonas aeruginosa acquisition in CF patients in the context of otorhinolarynological surgery or dentist attendance – Case series and discussion of preventive concepts

Mainz, J.G., Michl, R., Gerber, A., Nader, A., Mueller, A., Beck, J.F.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 65 KB

english, 2013

413

180 Pseudomonas aeruginosa colonization of the respiratory tract in cystic fibrosis

Corujeira, S., Barbosa, T.F., Senra, V., Ferraz, C., Rocha, H., Vaz, L.G.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 68 KB

english, 2013

414

252 Survey of malignancies at Scandinavian CF centers

Krjukova, J., Hansson, L., Meyer, P., Gilljam, M., Lindblad, A., Eriksson-Hollsin, A., Vebert-Olesen, H., Pressler, T., Finstad, P. Leyell, Mared, L., Hjelte, L.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 63 KB

english, 2013

415

338 “Let's talk about it”, a mediation tool in couples, for adults living with cystic fibrosis

David, V., Ouksel, H., Badatcheff, A., Ravilly, S., Racineux, J.-L., Lasserre-Moutet, A., Chambouleyron, M.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 58 KB

english, 2013

416

340 Experiences of physical activity: A phenomenological study of individuals with cystic fibrosis

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 58 KB

english, 2013

417

WS3.1 Gastric aspiration into the CF lung – relationship with reflux symptoms and lung function

Crossfield, G.L., Krishnan, A., Lordan, J., Bourke, S., Anderson, A., Dettmar, P.W., Brownlee, I.A., Ward, C., Pearson, J.P.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 71 KB

english, 2013

418

326 Parent's satisfaction with an internet-based supportive intervention for parents of children with cystic fibrosis

Fidika, A., Herle, M., Knaevelsrud, C., Lehmann, C., Weiss, C., Goldbeck, L.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 58 KB

english, 2013

419

WS8.3 Cystic fibrosis transmembrane conductance regulator (CFTR) allelic variants relate to shifts in fecal microbiota of cystic fibrosis patients

Iebba, V., Santangelo, F., De Biase, R.V., Starnato, A., Bertasi, S., Savi, D., Lucarelli, M., Conte, M.P., Schippa, S., Quattrucci, S.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 65 KB

english, 2013

420

217 Randomized double-blind monocentric trial on tolerability, acceptability and efficacy of two formulations of inhaled 7% hypertonic saline with and without hyaluronic acid in reducing airways inflammation in patients with cystic fibrosis – Preliminary results

Brivio, A., Ceruti, C., Gambazza, S., Colombo, C.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 66 KB

english, 2013

421

349 The ceremonial order of the CF clinic: Time for a new model of partnership?

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 58 KB

english, 2013

422

P. aeruginosa in the paranasal sinuses and transplanted lungs have similar adaptive mutations as isolates from chronically infected CF lungs

Ciofu, Oana, Johansen, Helle Krogh, Aanaes, Kasper, Wassermann, Tina, Alhede, Morten, von Buchwald, Christian, Høiby, Niels

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 499 KB

english, 2013

423

WS6.2 The impact of transition to adult services on weight and BMI for patients with cystic fibrosis

Cousins, C.A., Haworth, C.S., Floto, R.A., Barker, H.C., Shafi, N.T., Johnson, C.M., Watson, H.M.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 58 KB

english, 2013

424

275 Eating habits and nutritional intervention in CF adolescents

Daldoss, M., Perobelli, S., Volpi, S., Cipolli, M., Assael, B.M.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 61 KB

english, 2013

425

88 Development of microspheres for pulmonary administration in cystic fibrosis lung disease

Gaspar, M., Couet, W., Olivier, J.-C., Pais, A., Sousa, J.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 66 KB

english, 2013

426

250 Portal hypertension in cystic fibrosis children – One center experience

Ciuca, I., Pop, L., Popa, Z., Tamas, L., Popa, I.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 63 KB

english, 2013

427

317 Depression, anxiety and quality of life in adolescents with cystic fibrosis

Harning, K., Brucefors, A. Bergsten, Hjelte, L.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 62 KB

english, 2013

428

323 Bringing bad news: The diagnosis of cystic fibrosis in childhood

Vertommen, A., Tack, J., Havermans, T., Proesmans, M.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 58 KB

english, 2013

429

Eradication of chronic methicillin-resistant Staphylococcus aureus infection in cystic fibrosis patients. An observational prospective cohort study of 11 patients

Vanderhelst, Eef, De Wachter, Elke, Willekens, Julie, Piérard, Denis, Vincken, Walter, Malfroot, Anne

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 238 KB

english, 2013

430

WS3.3 Molecular characterization of fecal microbiota and metabolic profiles association in cystic fibrosis patients

Iebba, V., Santangelo, F., Macone, A., De Biase, R.V., Gagliardi, A., Cimino, G., Troiani, P., D'Alù, V., Matarese, M., Conte, M.P., Quattrucci, S., Schippa, S.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 71 KB

english, 2013

431

Chronic Stenotrophomonas maltophilia infection and mortality or lung transplantation in cystic fibrosis patients

Waters, Valerie, Atenafu, Eshetu G., Lu, Annie, Yau, Yvonne, Tullis, Elizabeth, Ratjen, Felix

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 184 KB

english, 2013

432

114 Role of BceF BY-kinase in host–pathogen interaction, biofilm formation and survival to stress by the cystic fibrosis pathogen Burkholderia cepacia IST408: Transcriptomic and phenotypic approaches

Ferreira, A.S., Oliveira, V.H., Silva, I.N., Becker, J.D., McClean, S., Callaghan, M., Moreira, L.M.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 65 KB

english, 2013

433

WS11.6 Unmet needs in end of life care for the adult cystic fibrosis patient: A review of expectations, challenges, and current practice

Quinn, B.J., Wann, L.-C., Maniscalco, P., Cohen, R.I.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 54 KB

english, 2013

434

WS16.7 Growth, nutritional care and biological assessment in newborn screened CF infants

Munck, A., Languepin, J., Alberti, C., Gross, G., Costanzo, A., Priso, A.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 62 KB

english, 2013

435

298 Delivery of CF care through the patients' eyes: Repeated surveys of patients' experiences at Innsbruck CF centre

Ellemunter, H., Stahl, K., Busche, M., Eder, J., Smrekar, U., Steinkamp, G.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 58 KB

english, 2013

436

112 Unveiling the roles of small non-coding RNAs and RNA chaperones on the biology of opportunistic pathogens of the Burkholderia cepacia complex

Ramos, C.G., Grilo, A.M., da Costa, P.J., Feliciano, J.R., Leitão, J.H.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 65 KB

english, 2013

437

231 How active are CF children? Assessing physical activity levels at annual review

Holden, H.J., Douglas, E., Bolton, M., Smyth, A.R.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 58 KB

english, 2013

438

WS15.6 Development of nanomedicines for the treatment of pulmonary biofilm infections: Insights from advanced fluorescence microscopy studies

Forier, K., Messiaen, A.-S., Risseeuw, M., Van Calenbergh, S., Deschout, H., Raemdonck, K., Nelis, H., Danhier, F., Préat, V., De Baets, F., De Smedt, S., Demeester, J., Coenye, T., Braeckmans, K.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 55 KB

english, 2013

439

229 Using theory to design a physical activity behaviour change intervention: An evidence synthesis of barriers, enablers and pathways of change in CF

Kent, L., Bradley, J.M.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 58 KB

english, 2013

440

96 Incidence of nephrotoxicity associated with concomitant colistimethate and vancomycin use in cystic fibrosis patients

Adeola, M., Coralic, A., Hart, S., Barto, T.L., Katz, M.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 65 KB

english, 2013

441

82 Secondary prophylactic antibiotics against Staphylococcus aureus (Sa) during the winter months in children with cystic fibrosis

Ferret, V., Bui, S., Clouzeau, H., Debelleix, S., Christoflour, N., Valentin, F., Bouvier, C., Fayon, M.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 70 KB

english, 2013

442

296 The impact of transfer of care from local hospital to regional specialist cystic fibrosis unit

Storrar, W., Daniels, T.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 58 KB

english, 2013

443

WS17.1 Biofilm disruption and potentiating antimicrobial effects of a novel alginate oligomer on Pseudomonas aeruginosa in a murine lung infection model

Hengzhuang, W., Song, Z., Ciofu, O., Onsøyen, E., Rye, P., Høiby, N.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 71 KB

english, 2013

444

WS8.5 Airway bacterial community structure and correlation during health and disease

Einarsson, G.G., Tunney, M., Klem, E.R., Fodor, A.A., Wolfgang, M.C., Elborn, J.S.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 55 KB

english, 2013

445

246 High frequency of liver abnormalities in adult cystic fibrosis patients after lung transplantation

Staufer, K., Halilbasic, E., Niculescu, A., Harm, S., Rutter, K., Brichta, A., Jaksch, P., Muraközy, G., Hielle-Wittmann, E., Klepetko, W., Trauner, M., Kazemi-Shirazi, L.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 58 KB

english, 2013

446

38 Sweat testing using the CF Quantum® Sweat Test system

Rock, M., Makholm, L., Laguna, T., Boerner-Noren, B., Brown, I., Chatfield, B., Oldroyd, H., Farrell, P.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 62 KB

english, 2013

447

A randomized controlled trial of inhaled l-Arginine in patients with cystic fibrosis

Grasemann, H., Tullis, E., Ratjen, F.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 317 KB

english, 2013

448

33 High rate of false-positive results in cystic fibrosis newborn screening among a Spanish population of Maghribian origin

Mondejar-Lopez, P., Pastor-Vivero, M.D., Mula-Anton, A., Olmos-García, J.M., Fiot, E., Sanchez-Solis, M.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 62 KB

english, 2013

449

Progression of structural lung disease on CT scans in children with cystic fibrosis related diabetes

Widger, John, Ranganathan, Sarath, Robinson, Philip J.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 268 KB

english, 2013

450

351 A 12 month program using observed consultations and transcript scoring to increase motivational interviewing skills in an adult CF team

Attfield, R., Field, E., Thornton, S., Milne, A., Rose, C., Royle, J., Wildman, M.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 58 KB

english, 2013

451

235 Prevalence of urinary incontinence in women with cystic fibrosis

Lacarrière, C., Conquy, S., Courtin, E., Tourret, F., Grenet, D., Hubert, D.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 62 KB

english, 2013

452

Obituary for Professor Dr. Gerd Döring

Høiby, Niels, Elborn, Stuart, Heijerman, Harry, Dubois, Christine, Worlitzsch, Dieter

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 194 KB

english, 2013

453

92 Early treatment with inhaled antibiotics postpones recurrence of Achromobacter species in cystic fibrosis

Wang, M., Ridderberg, W., Hansen, C.R., Høiby, N., Jensen-Fangel, S., Olesen, H.V., Skov, M., Lemming, L.E., Pressler, T., Johansen, H.K., Nørskov-Lauritsen, N.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 68 KB

english, 2013

454

WS2.2 What do parents experience and how do they cope with the AREST CF early surveillance program for infants and children with cystic fibrosis?

Branch-Smith, C.A., Pooley, J., Shields, L., Stick, S.M., Douglas, T.A.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 59 KB

english, 2013

455

83 Investigation of RND efflux pumps in clinical Prevotella species isolated from CF patients

Schaible, B., Sherrard, L., Gilpin, D.F., Elborn, J.S., Tunney, M.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 69 KB

english, 2013

456

WS3.6 Probiotic intake improves the gastrointestinal health of cystic fibrosis patients

Garriga, M., de Blas, A., Burreros, M., Guallarte, P., Pérez-Aragón, A., Lamas, A., del Campo, R., Suárez, L.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 64 KB

english, 2013

457

306 Influenza and pneumococcal vaccinations in an adult centre – Who knows what's happening?

Speight, L., Lea-Davies, M., Ketchell, R.I., Lau, D., Duckers, J.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 58 KB

english, 2013

458

WS6.9 Urinary kidney injury molecule-1 is superior to creatinine and cystatin-C based formulas at predicting chronic kidney disease in patients with cystic fibrosis

Prayle, A.P., Jain, K., Knox, A.J., Watson, A.R., Smyth, A.R.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 51 KB

english, 2013

459

Evidence of diminished FEV1 and FVC in 6-year-olds followed in the European cystic fibrosis patient registry, 2007–2009

VanDevanter, Donald R., Pasta, David J.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 245 KB

english, 2013

460

337 Eating attitudes and behaviours in males and females with cystic fibrosis. The role of body image and coping styles

Melhuish, L.S., Pearce, A., Brignell, C.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 58 KB

english, 2013

461

Measures of body habitus are associated with lung function in adults with cystic fibrosis: A population-based study

Forrester, Doug L., Knox, Alan J., Smyth, Alan R., Fogarty, Andrew W.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 297 KB

english, 2013

462

158 Trichosporon mycotoxinivorans – Epidemiological and clinical aspects of an uncommon fungus identified in patients with cystic fibrosis

Tintelnot, K., Tegtmeyer, F.K., Albert, F., Runge, C., Seibold, M., Müller, C., Sahly, H., Haas, A., Schwarz, C., Klotz, M.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 65 KB

english, 2013

463

159 Frequency and pathogenicity of individual rhinovirus species during adult exacerbations

Whitaker, P., McIntyre, C., Shah, A., Hale, T., Etherington, C., Simmonds, P., Peckham, D.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 54 KB

english, 2013

464

198 Time and handling of the I-Neb in target inhalation mode (TIM) and tidal breathing mode (TBM) assessed in mild to severe CF patients

Haeussermann, S., Healy, J., Edelman, J.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 62 KB

english, 2013

465

4 Multiplex amplification of specific targets for resequencing using next generation sequencing technology, applied in molecular diagnostics of cystic fibrosis

Valášková, I., Spesna, R., Holčíková, A., Homola, L., Gaillyová, R.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 64 KB

english, 2013

466

115 Phenotypic variation of Burkholderia dolosa along 5.5 years of chronic colonization with decline of lung function of a cystic fibrosis patient

Moreira, A.S., Coutinho, C.P., Carvalho, C.C.C.R., Azevedo, P., Lito, L., Cristino, J. Melo, Sá-Correia, I.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 65 KB

english, 2013

467

234 Physical activity level in thirteen children with CF, at Stockholm CF-center

Hedborg, A., Salomonsson, S., Hjelte, L.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 62 KB

english, 2013

468

313 Health-related quality of life in Russia: Data on the CFQ-R in children with cystic fibrosis

Gorinova, Y., Quittner, A.L., Simonova, O.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 61 KB

english, 2013

469

10 The role of complex alleles in patients with cystic fibrosis and L997F

Cirilli, N., Terlizzi, V., Nardiello, P., Gagliardini, R., Tosco, A., Sepe, A., Quarta, B.M., Amato, N., Improta, F., Romano, R., De Gregorio, F., Casale, A., Carnovale, V., D'Agostino, M.A., Raia, V.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 61 KB

english, 2013

470

WS12.7 Pulmonary emphysema in cystic fibrosis detected by densitometry on chest multidetector computed tomography (MDCT)

Wielpütz, M., Weinheimer, O., Eichinger, M., Wiebel, M., Biederer, J., Kauczor, H.-U., Heußel, C.P., Mall, M.A., Puderbach, M.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 61 KB

english, 2013

471

333 Brazilian children's perceptions about the routine treatment in cystic fibrosis

Pizzignacco, T., Furtado, M.C., Lima, R.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 58 KB

english, 2013

472

331 Looking at young kids with cystic fibrosis as students

Costa, S., Guerreiro, D., Semedo, M.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 57 KB

english, 2013

473

312 Quality of life and related factors in patients with cystic fibrosis in Newfoundland and Labrador

Hawboldt, J., Davis, E., Mccarthy, R.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 59 KB

english, 2013

474

Subclinical deterioration of systolic right ventricular function parameters in adolescents with mild cystic fibrosis

Koestenberger, Martin, Ravekes, William

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 72 KB

english, 2013

475

WS6.7 Patient responses to the introduction of telemedicine and EHRs

Wilson, J.W., Clark, D., Finlayson, F., Williams, E., George, E., Braithwaite, M., Ambrose, H., Kotsimbos, T.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 59 KB

english, 2013

476

Soluble inflammation markers in nasal lavage from CF patients and healthy controls

Beiersdorf, Natalie, Schien, Matthias, Hentschel, Julia, Pfister, Wolfgang, Markert, Udo R., Mainz, Jochen G.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 302 KB

english, 2013

477

103 Bacterial diversity and dynamics during the early stages of Pseudomonas aeruginosa colonization in cystic fibrosis airways

Keravec, M., Mounier, J., Rosec, S., Gouriou, S., Le Berre, R., Rault, G., Barbier, G., Héry-Arnaud, G.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 69 KB

english, 2013

478

Employment in CF adults deserves much more attention

Ullrich, Gerald

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 71 KB

english, 2013

479

176 Prevalence of autoimmune antibodies in patients with cystic fibrosis after lung transplantation

Staufer, K., Halilbasic, E., Harm, S., Niculescu, A., Jaksch, P., Muraközy, G., Hielle-Wittmann, E., Lichtenberger, C., Vogelsang, H., Klepetko, W., Trauner, M., Kazemi-Shirazi, L.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 63 KB

english, 2013

480

173 Basophil activation test: A novel approach to the diagnosis of allergic bronchopulmonary aspergillosis in cystic fibrosis patients

Katelari, A., Tzanoudaki, M., Noni, M., Kanariou, M., Doudounakis, S.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 67 KB

english, 2013

481

261 Effect of different treatment regimens of CFRD on clinical status: A register study

Polat, S., Koerner-Rettberg, C., Heesen, I., Ballmann, M.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 65 KB

english, 2013

482

156 Chronic airway colonization by Aspergillus fumigatus (Af) in patients with cystic fibrosis (CF): Does it contribute to lung function decline?

Braggion, C., Pasotto, R., Mergni, G., Taccetti, G., Dolce, D., Cocchi, P., Campana, S.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 65 KB

english, 2013

483

WS17.5 Evaluation of antibiofilm activity of new homoserine lactones (HSL) analogs of Pseudomonas aeruginosa

Chusseau, A. Furiga, Lajoie, B., Hage, S. El, Baziard, G., Roques, C.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 65 KB

english, 2013

484

357 Is being Albanian a risk factor for cystic fibrosis?

Repetto, T., Galici, V., Mergni, G., Zavataro, L., Festini, F., Taccetti, G.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 62 KB

english, 2013

485

WS19.8 Use of palivizumab to prevent respiratory syncytial virus (RSV) infection in cystic fibrosis. A 10 year retrospective review pre and post introduction of palivizumab prophylaxis in Northern Ireland

Groves, H.E., Jenkins, L., Macfarlane, M., Reid, A., Shields, M.D.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 62 KB

english, 2013

486

136 Development of a sensor for detection of Pseudomonas aeruginosa lung infection in the breath of CF patients

Lauridsen, R.K.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 64 KB

english, 2013

487

121 Candida colonisation status in adults and children with cystic fibrosis

Lavelle, G.M., Greene, C.M., McElvaney, N.G.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 66 KB

english, 2013

488

218 Cystic fibrosis sputum induction trial (CF-SpIT). Tolerability data for induced sputum sampling in children with cystic fibrosis

Tame, J., Ronchetti, K., Doull, I., Forton, J.T.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 66 KB

english, 2013

489

Growth retardation and reduced growth hormone secretion in cystic fibrosis. Clinical observations from three CF centers

Ciro, D'Orazio, Padoan, Rita, Blau, Hannah, Marostica, Anna, Fuoti, Maurizio, Volpi, Sonia, Pilotta, Alba, Meyerovitch, Joseph, Sher, Daniel, Assael, Baroukh M.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 118 KB

english, 2013

490

276 Nutritional controversies in adult cystic fibrosis (CF) care – Results of a survey by European CF Nutrition Group

Smith, C., Shimmin, D., White, H.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 62 KB

english, 2013

491

99 Performance of MALDI-TOF mass spectrometry method for identification of bacteria commonly isolated from cystic fibrosis patients

Wahab, A. Abdul, Taj-Aldeen, S.J., Abu-Madi, M., Talaq, E.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 65 KB

english, 2013

492

328 Exploring parents' concerns about transition from paediatric to adult cystic fibrosis (CF) services

Oxley, H., Woodhead, S., Biesty, J., Fauset-Jones, J., Trenchard, S.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 58 KB

english, 2013

493

WS3.2 Higher levels of fecal calprotectin levels are associated with SIBO in cystic fibrosis after lung transplantation

Halilbasic, E., Staufer, K., Harm, S., Niculescu, A., Jaksch, P., Muraközy, G., Hielle-Wittmann, E., Klepetko, W., Vogelsang, H., Trauner, M., Kazemi-Shirazi, L.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 71 KB

english, 2013

494

359 Use of radiological tools in French cystic fibrosis centers: A national survey

Reix, P., Mazur, S., Delaup, V., Houdouin, V.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 64 KB

english, 2013

495

165 An immunomodulatory role for the serine protease inhibitor, eppin, in the lung

Glasgow, A., Scott, A., McCrudden, M., McLean, D., Lundy, F., Irwin, C., Timson, D., Tunney, M., Elborn, J.S., Weldon, S., Taggart, C.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 67 KB

english, 2013

496

WS6.5 Experience and satisfaction of patients and parents with CF services – A nationwide survey in Germany

Steinkamp, G., Schwarz, C., Stahl, K.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 59 KB

english, 2013

497

WS8.2 Effect of Staphylococcus aureus on the outcome of pulmonary Pseudomonas aeruginosa infection in a murine model

Monahan, A., Ryan, R., Elborn, J.S., Ingram, R.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 64 KB

english, 2013

498

Tobramycin is a suppressor of premature termination codons

Altamura, Nicola, Castaldo, Rosa, Finotti, Alessia, Breveglieri, Giulia, Salvatori, Francesca, Zuccato, Cristina, Gambari, Roberto, Panin, Giulia Chiara, Borgatti, Monica

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 442 KB

english, 2013

499

WS22.4 Biofilm formation by cystic fibrosis-relevant Burkholderia cepacia complex (Bcc) bacteria allows them to evade neutrophil anti-microbial activities

Murphy, M., Callaghan, M., Caraher, E.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 65 KB

english, 2013

500

WS21.2 Non-invasive prenatal diagnosis (NIPD) of cystic fibrosis by quantitative real time mutant enrichment with 3′-modified oligonucleotides (MEMO) PCR

Guissart, C., Debant, V., Bareil, C., Viart, V., des Georges, M., Claustres, M., Vincent, M.C.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 66 KB

english, 2013

501

175 The onset of CFRD does not impact the association of IL-6 with worse clinical status

Coriati, A., Ziai, S., Gauthier, M.-S., Berthiaume, Y., Rabasa-Lhoret, R.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 62 KB

english, 2013

502

Amoxicillin–clavulanic acid resistance in fecal Enterobacteriaceae from patients with cystic fibrosis and healthy siblings

Duytschaever, Gwen, Huys, Geert, Boulanger, Linda, De Boeck, Kris, Vandamme, Peter

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 210 KB

english, 2013

503

WS1.3 Respiratory microbiota dynamics in newborns with cystic fibrosis and healthy controls: A longitudinal study

Prevaes, S.M.P.J., de Winter-de Groot, K.M., Tramper-Stranders, G.A., Tiddens, H.A.W.M., van Westreenen, M., Janssens, H.M., Wyllie, A., van der Ent, C.K., Sanders, E.A.M., Bogaert, D.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 65 KB

english, 2013

504

Effects of ivacaftor on severely ill patients with cystic fibrosis carrying a G551D mutation

Hebestreit, Helge, Sauer-Heilborn, Annette, Fischer, Rainald, Käding, Manfred, Mainz, Jochen G.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 481 KB

english, 2013

505

226 Comparison between standard and empiric Spirotiger® setup in patients with cystic fibrosis (CF)

Ceruti, C., Brivio, A., Gambazza, S., Colombo, C.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 61 KB

english, 2013

506

322 Prenatal diagnosis of cystic fibrosis: Parental opinion, clinical course in the first year of life and influence of having a sibling with the disease

Sousa, R., Romão, P., Jotta, R., Pereira, L., Barreto, C.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 58 KB

english, 2013

507

59 A Cochrane review of CFTR potentiators in cystic fibrosis

Sinha, I.P., Schechter, M.S., Echevarria, C., Dwan, K., Southern, K.W.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 73 KB

english, 2013

508

68 Comparison of pharmacy prescription refill frequency in CF adults before and after switching from tobramycin inhalation solution (TIS) to TOBI Podhaler – ‘Real world’ evidence of improved adherence

Nash, E.F., Ahitan, B., Brown, C.J., Thakrar, K., Carrolan, V., Rashid, R., Whitehouse, J.L.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 63 KB

english, 2013

509

Maximal daily dose of pancreatic enzyme replacement therapy in infants with cystic fibrosis: A reconsideration

Borowitz, Drucy, Gelfond, Daniel, Maguiness, Karen, Heubi, James E., Ramsey, Bonnie

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 135 KB

english, 2013

510

Enteral tube feeding in adults with cystic fibrosis; patient choice and impact on long term outcomes

White, H., Morton, A.M., Conway, S.P., Peckham, D.G.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 328 KB

english, 2013

511

300 Outpatient oxygen prescription in All Wales Adult Cystic Fibrosis Centre: Getting closer to the truth

Thomas, S.S., Olaniyi, P., Speight, L., Ketchell, R.I., Lau, D., Duckers, J.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 62 KB

english, 2013

512

WS1.2 Three clinically distinct chronic pediatric airway infections share a common core microbiota

van der Gast, C.J., Cuthbertson, L., Pope, C.E., Marsh, R.L., Rogers, G.B., Smith-Vaughan, H.C., Redding, G.J., Bruce, K.D., Chang, A.B., Hoffman, L.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 65 KB

english, 2013

513

128 Pseudomonas aeruginosa infecting lung-transplanted cystic fibrosis patients: A longitudinal study

Cocchi, P., Taccetti, G., Ravenni, N., Bresci, S., Braggion, C., de Martino, M., Campana, S.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 67 KB

english, 2013

514

213 Positive expiratory pressure values in infants: A pilot study

Stewart, R., Anderson, P.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 61 KB

english, 2013

515

Left ventricular and aortic dysfunction in cystic fibrosis mice

Sellers, Zachary M., Kovacs, Attila, Weinheimer, Carla J., Best, Philip M.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 767 KB

english, 2013

516

WS1.5 First evidence of Mycobacterium abscessus biofilm in the lungs of chronically infected CF patients

Qvist, T., Eickhardt-Sørensen, S.R., Katzenstein, T.L., Pressler, T., Iversen, M., Andersen, C.B., Bjarnsholt, T., Høiby, N.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 60 KB

english, 2013

517

3 Evaluation of the Multiplicom CFTR MASTR V2 kit on a Roche 454 Junior NGS platform as a diagnostic tool for a comprehensive analysis of the CFTR gene

Pagin, A., Verneau, F., Devos, A., Altiéri, J.-P., Lalau, G., des Georges, M.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 64 KB

english, 2013

518

233 Kinect active video game in cystic fibrosis: Exercise or fun?

Salonini, E., Gambazza, S., Tridello, G., Sanguanini, M., Cazzarolli, C., Zanini, A., Meschi, A., Assael, B.M.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 62 KB

english, 2013

519

Expression of the inflammatory regulator A20 correlates with lung function in patients with cystic fibrosis

Kelly, Catriona, Williams, Mark T., Elborn, J. Stuart, Ennis, Madeleine, Schock, Bettina C.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 490 KB

english, 2013

520

355 The importance of the M470V polymorphism

Celik, T., Gunesacar, R., Balci, A., Unal, S., Aldic, G., Eskici, H., Atilgan, N., Elmaci, S., Tutanc, M., Can, D.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 62 KB

english, 2013

521

23 Diagnosis of cystic fibrosis in a patient carrying the cystic fibrosis transmembrane conductance regulator 186–8T/C allele

Caldrer, S., Sorio, C., Angiari, C., Johansson, J., Verzé, G., Ettorre, M., Buffelli, M., Assael, B.M., Melotti, P.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 68 KB

english, 2013

522

193 Influence of nebulized Obracin® versus Tobi® on ciliary beat frequency

Boon, M., Jorissen, M., Proesmans, M., Vermeulen, F., De Boeck, K.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 58 KB

english, 2013

523

WS10.6 Organ-specific CFTR dysfunction: Comparison of biomarkers for CF diagnosis and CFTR modulator effects

Pinders-Kessel, L., Scheinert, S., Klosinski, M., Staab, D., Derichs, N.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 57 KB

english, 2013

524

WS20.6 High throughput screening as a source for novel cystic fibrosis therapeutic targets

Botelho, H.M., Dahimène, S., Uliyakina, I., Neumann, B., Tischer, C., Pepperkok, R., Amaral, M.D.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 60 KB

english, 2013

525

19 Cystic fibrosis transmembrane regulator gene mutations (CFTR) in a tertiary care centre in Saudi Arabia

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 67 KB

english, 2013

526

WS22.6 The Pseudomonas aeruginosa pangenome: Impact of genomic diversity on bacterial pathogenicity and host response in airway infections

Dethlefsen, S., Munder, A., Bezuidt, O., Fischer, S., Hilker, R., Klockgether, J., Voigt, B., Wiölbeling, F., Hecker, M., Goesmann, A., Gulbins, E., Tümmler, B.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 64 KB

english, 2013

527

75 Modulation of Burkholderia cenocepacia virulence factors and biofilm formation by liposomal tobramycin-bismuth

Burns, K., Omri, A.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 61 KB

english, 2013

528

215 Comparison of acute effects of conventional high frequency chest oscillation (HFCWO) and hand held percussor (Electro-Flo 5000) for airway clearance in cystic fibrosis patients

Dunn, C., Davies, Z., Kim, L., Zirbes, J., Everson, C., Milla, C.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 62 KB

english, 2013

529

WS20.3 Transcriptomics of native nasal epithelium expressing F508del-CFTR and intersecting data from comparable studies

Clarke, L.A., Sousa, L., Amaral, M.D.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 67 KB

english, 2013

530

A pilot outreach physiotherapy and dietetic quality improvement initiative reduces IV antibiotic requirements in children with moderate–severe cystic fibrosis

Ledger, Sean J., Owen, Elizabeth, Prasad, S. Ammani, Goldman, Allan, Willams, Jane, Aurora, Paul

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 155 KB

english, 2013

531

146 Trombones – A potential source of recurrent Burkholderia cepacia complex infection?

Denton, M., Etherington, C., Peckham, D.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 68 KB

english, 2013

532

Molecular analysis of changes in Pseudomonas aeruginosa load during treatment of a pulmonary exacerbation in cystic fibrosis

Reid, D.W., Latham, R., Lamont, I.L., Camara, M., Roddam, L.F.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 638 KB

english, 2013

533

177 Strategies to improve influenza vaccination coverage in at-risk children: The experience of patients with cystic fibrosis

Giagnorio, M.G., Minicucci, V., Mariano, M., Romano, R., Napolitano, C., Manchisi, M., Macchiaroli, A., Vecchio, A. Lo, Raia, V., Giannattasio, A.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 63 KB

english, 2013

534

29 A review of the management of infants with an equivocal diagnosis of cystic fibrosis (CF) following newborn screening in a UK CF regional network

Burrows, E., Harrison, G.A., Mayell, S.J., Barton, P., Bennett, S., Morrison, D., Watling, R.M., Southern, K.W.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 61 KB

english, 2013

535

WS14.6 Physical activity, energy expenditure and quality of life in CF adults receiving intravenous antibiotics at home and in hospital

Khiroya, H., Pound, R., Qureshi, U., Turner, A., Edward, N.F.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 59 KB

english, 2013

536

240 Is gastric emptying delayed in children with cystic fibrosis?

Hauser, B., Malfroot, A., De Schutter, I., De Wachter, E., Devreker, T., Veereman, G., De Greef, E., Vandenplas, Y.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 64 KB

english, 2013

537

WS8.4 Temporal bacterial community dynamics of cystic fibrosis lung infections

Cuthbertson, L., Rogers, G.B., Walker, A.W., Oliver, A., Daniels, T., Carroll, M.P., Parkhill, J., Bruce, K.D., van der Gast, C.J.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 64 KB

english, 2013

538

294 Individualized vitamin A supplementation for patients with cystic fibrosis

Naehrlich, L., Simon, A., Brei, C., Krawinkel, M.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 61 KB

english, 2013

539

160 Is pet ownership a risk for bacterial or fungal infections in patients with CF?

Heger, N., Antweiler, E., Staab, D., Tintelnot, K., Schwarz, C.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 54 KB

english, 2013

540

301 An analysis of medical resource utilisation (MRU) associated with hospitalised pulmonary exacerbations (PulmEx) in the DPM-CF-301 and DPM-CF-302 registration trials of inhaled mannitol (Bronchitol®) in patients with cystic fibrosis (CF)

Toward, T.J., Van Engen, A., Bilton, D.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 62 KB

english, 2013

541

40 Longitudinal values of sweat chloride concentration among infants identified by cystic fibrosis (CF) newborn screening (NBS) in California

Zirbes, J., Hardy, K., Sudhakar, R., Salinas, D., Saeed, M., Kharrazi, M., Milla, C.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 62 KB

english, 2013

542

WS15.4 Purinergic signalling regulates pancreatic epithelial transport and pancreatic stellate cells

Novak, I., Wang, J., Hayashi, M., Kowal, J.M., Haanes, K.A.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 67 KB

english, 2013

543

Targeting bacterial integration host factor to disrupt biofilms associated with cystic fibrosis

Gustave, Jodi E., Jurcisek, Joseph A., McCoy, Karen S., Goodman, Steven D., Bakaletz, Lauren O.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 477 KB

english, 2013

544

287 Seasonal variation in vitamin D status in an adult CF clinic population

Barrett, J., Henderson, R., Whitehouse, J.L.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 65 KB

english, 2013

545

295 Use of allied health services in CF centres – Results from a nationwide survey in Germany

Steinkamp, G., Ullrich, G., Stahl, K.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 58 KB

english, 2013

546

248 Evaluation of the clinical picture, considering liver lesions in infants with cystic fibrosis diagnosed during newborn screening

Wiecek, S., Wos, H., Kordys-Darmolinska, B., Grzybowska-Chlebowczyk, U.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 58 KB

english, 2013

547

WS21.4 Clinical and morphological characteristics of sporadic genetically determined pancreatitis compared with idiopathic pancreatitis: Higher risk of pancreatic cancer in CFTR variants

Pepermans, X., Hamoir, C., Piessevaux, H., Jouret-Mourin, A., Weynand, B., Habyalimana, J.-B., Geubel, A., Gigot, J.-F., Deprez, P.H., Leal, T.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 66 KB

english, 2013

548

WS7.5 Interim results of the phase 3 open-label study of ataluren in nonsense mutation cystic fibrosis (nmCF)

Kerem, E., Wilschanski, M., Sermet-Gaudelus, I., De Boeck, K., Accurso, F.J., Konstan, M., Rowe, S., Miller, N., Elfring, G., Spiegel, R., Peltz, S., Barth, J., Ajayi, T.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 61 KB

english, 2013

549

Improved air trapping evaluation in chest computed tomography in children with cystic fibrosis using real-time spirometric monitoring and biofeedback

Kongstad, Thomas, Buchvald, Frederik F., Green, Kent, Lindblad, Anders, Robinson, Terry E., Nielsen, Kim G.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 818 KB

english, 2013

550

267 Bone turnover in patients with cystic fibrosis

Jakovska-Maretti, T., Meceska-Jovcevska, J., Fustik, S., Spirevska, L.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 65 KB

english, 2013

551

155 Isolation of fungi from nebuliser devices used by people with cystic fibrosis

Peckham, D., Wynne, S., Denton, M., Pollard, K., Barton, R.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 65 KB

english, 2013

552

WS14.1 Evaluation of physical activity using the habitual activity estimation scale (HAES) questionnaire in a multicenter study

Alarie, N., Agnew, J.L., McIlwaine, M.P., Ratjen, F., Davidson, G.F., Milner, R., Lands, L.C.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 62 KB

english, 2013

553

The effect of gastric juice on interleukin-8 production by cystic fibrosis primary bronchial epithelial cells

Pauwels, Ans, Verleden, Stijn, Farre, Ricard, Vanaudenaerde, Bart M., Van Raemdonck, Dirk, Verleden, Geert, Sifrim, Daniel, Dupont, Lieven J.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 279 KB

english, 2013

554

314 Mapping the Cystic Fibrosis Questionnaire-Revised (CFQ-R) to a preference based utility index

Acaster, S., Pinder, B., Osmond, J., Mukuria, C.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 61 KB

english, 2013

555

258 Has the age of diagnosis of cystic fibrosis related diabetes (CFRD) changed over the last 10 years?

Kent, W., Dyce, P., Sarkar, R., Wight, A., Ledson, M., Walshaw, M.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 62 KB

english, 2013

556

WS12.4 Determinants of 6 minute walking distance and desaturation during the 6 minute walk test in adults with cystic fibrosis

Burgel, P.-R., Chapron, J., Hubert, D., Kanaan, R., Honoré, I., Paillasseur, J.-L., Aubourg, F., Dinh-Xuan, A.-T., Dusser, D., Fajac, I., Martin, C.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 61 KB

english, 2013

557

18 Frequency of delta F508 mutation in Venezuelan patients with cystic fibrosis

Sánchez, K., Arcia, O., Matute, X., Mendiola, L., Chaustre, I., Villalon, M., Takiff, H.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 67 KB

english, 2013

558

157 Epidemiology of aspergillosis in CF and response to antifungal therapy

Lauren, L., Williams, K., Wynne, S., Johnstone, A., Woolston, A., Baxter, P., Denton, M., Peckham, D., Whitaker, P., Barton, R.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 65 KB

english, 2013

559

237 A new endoscopic short test for exocrine pancreatic function in cystic fibrosis

Engjom, T., Lrum, B.N., Erchinger, F., Tjora, E., Gilja, O.H., Dimcevski, G.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 64 KB

english, 2013

560

354 CFUnite.org – Bridging the gap between researchers and people with cystic fibrosis

Hurley, M., Boote, J.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 50 KB

english, 2013

561

35 Neonatal screening for cystic fibrosis – A new experience for genetic counseling

Gaillyová, R., Valášková, I., Vinohradská, H., Holčíková, A., Homola, L.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 60 KB

english, 2013

562

86 Real time genome sequencing to decipher the molecular mechanism of resistance of Chryseobacterium oranimense, anew multidrug resistant species isolated from a cystic fibrosis patient

Sharma, P., Diene, S., Gupta, S.K., Robert, C., Reynaud-Gaubert, M., Dubus, J.-C., Rolain, J.-M.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 67 KB

english, 2013

563

WS17.3 Allicin revisited: Antimicrobial activity against the Burkholderia cepacia complex and interaction with a peroxidase target

Doherty, C., Wallock, D., Doherty, L., Clarke, D., Govan, J., Campopiano, D.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 71 KB

english, 2013

564

278 Conventional and novel assessment tools for the evaluation of nutrition status of children with cystic fibrosis

Hatziagorou, E., Katseni, V., Karagiozoglou-Lampoudi, T., Lampoudis, D., Tsanakas, J.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 65 KB

english, 2013

565

128 Differences in lower airway infection rates between AREST CF study centres

Hart, E., Ranganathan, S.C.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 66 KB

english, 2013

566

172 Modulation of dendritic cell functions by clonal variants of Burkholderia cenocepacia isolated from a cystic fibrosis patient

Pereira, M.J., Coutinho, C.P., Lopes, A., Sá-Correia, I., Videira, P.A., Cabral, M.G.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 67 KB

english, 2013

567

308 Temporal bone pneumatization in adult patients with cystic fibrosis

Berkhout, M.C., van Rooden, C.J., Aalbers, R.C., Rijntjes, E., Bouazzaoui, L.H. el, Heijerman, H.G.M.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 54 KB

english, 2013

568

188 Association of lung function with adherence to inhaled antibiotic treatment in patients with cystic fibrosis (CF)

Solé, A., Gartner, S., Alvarez, A., Pastor, D., Baranda, F., Girón, R., Martinez, T., Prados, C., Máiz, L., Oliva, C., González, M.-I.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 67 KB

english, 2013

569

251 Fecal incontinence in adult CF patients: Prevalence

Dufeu, N., Vitton, V., Coltey, B., Gomez, C., Baumstark, K., Bouvier, M., Pfau, I., Grimaud, J.-C., Reynaud-Gaubert, M.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 63 KB

english, 2013

570

327 What parents want from parents' evenings

Gormley, H.B., Duff, A., Brownlee, K.G., Hearnshaw, C.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 58 KB

english, 2013

571

187 Spirometry in pediatric patients with cystic fibrosis. Are we adequately reporting?

Silva, A.M., Constant, C., Salgueiro, M., Descalço, A., Bandeira, T.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 67 KB

english, 2013

572

WS16.6 Newborn screening and early life weight recovery are associated with better adolescent growth in children with CF

Zhang, Z., Farrell, P., Lai, H.J.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 62 KB

english, 2013

573

225 Education for physiotherapeutic caregivers of patients with cystic fibrosis

Andrade, T., Guitton, B., Monteiro, E., Deolindo, V.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 61 KB

english, 2013

574

245 A 10-year retrospective study of cystic fibrosis patients with distal intestinal obstruction syndrome (DIOS)

FitzPatrick, M.E.B., Bilton, D., Perrin, F., Westaby, D., Simmonds, N.J.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 58 KB

english, 2013

575

79 Microarray analysis of the effect of fosfomycin and tobramycin against Pseudomonas aeruginosa from CF patients

McCaughey, G., Gilpin, D.F., Schneiders, T., Hoffman, L., McKevitt, M., Elborn, J.S., Tunney, M.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 69 KB

english, 2013

576

76 Which cystic fibrosis treatment features matter most to adult patients and parents of pediatric patients?

Mohamed, A.F., Johnson, F.R., Balp, M.-M., Calado, F.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 68 KB

english, 2013

577

362 The rebirth of the Brazilian CF Registry (REBRAFC)

Filho, L.V.R.F. Silva, Reis, F.J.C., Damaceno, N., Hira, A.Y.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 64 KB

english, 2013

578

263 Detection of autonomic neuropathy in adult cystic fibrosis patients – It is not all about hyperglycaemia!

Choudhury, M., Wong, S.F., Speight, L., Lee, J., Duckers, J., Ketchell, R.I.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 65 KB

english, 2013

579

73 Influence of treatment with sildenafil on lung function and exercise tolerance in cystic fibrosis adults

Fila, L., Grandcourtova, A., Vichova, M., Bartakova, L. Valentova

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 61 KB

english, 2013

580

17 Modulation of cystic fibrosis disease severity by macrophage migration inhibitory factor polymorphisms

Leal, T., Mafficini, A., Lebecque, P., Ortombina, M., Pintani, E., Pepermans, X., Sorio, C., Assael, B.M., Melotti, P.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 51 KB

english, 2013

581

319 Anxiety and depression symptoms in caregivers of children and adolescents with cystic fibrosis in Spain

Cebrián, M., Solé, A., Olveira, C., Quittner, A.L.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 63 KB

english, 2013

582

80 Long term effects of azithromycin maintenance treatment on lung function in pediatric cystic fibrosis patients chronically infected with Pseudomonas aeruginosa

Schoutens, A., Wilms, E., Stellato, R., van der Ent, C.K., Terheggen, S.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 70 KB

english, 2013

583

WS6.6 A prospective multi centre study to examine the impact of home intravenous antibiotic treatment (H-IVAT) on carer well being

Hope, H.F., Glasscoe, C., Dale, C., Hill, J., Nunn, T., Brownlee, K.G., Burrows, E., Southern, K.W.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 59 KB

english, 2013

584

288 Vitamin D levels among CF adults pending lung transplant

Mailhot, M., Berthiaume, Y., Jeanneret, A., Lavoie, A., Mircescu, H., Rabasa-Lhoret, R., Silviet-Carricart, M.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 65 KB

english, 2013

585

197 Influence of inhalation mode on aerosol lung deposition in patients with cystic fibrosis PART 1: Pharmacokinetic data as representative of lung deposition

van Velzen, A.J., Shahbabai, P., Uges, J.W.F., Touw, D.J., Heijerman, H.G.M.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 65 KB

english, 2013

586

253 The shape and relevance of the oral glucose tolerance test (OGTT) curve in CF

Nazareth, D., Mohan, K., Browning, P., Walshaw, M.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 66 KB

english, 2013

587

212 Rate of decline appears to be decreased in patients with higher self-reported adherence scores

Button, B.M., Kotowicz, E., Holland, A.E., Burge, A., Ellis, M., Ivulich, S., Wilson, J.W.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 58 KB

english, 2013

588

203 A longitudinal survey of physical performance and quality of life in adult CF patients

Hofer, M., Lienert, B. Fiechter, Hirt, A., Kurowski, T., Boehler, A.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 63 KB

english, 2013

589

227 The use of nasal high flow humidification with cystic fibrosis patients – A pilot

Lloyd, E.A., Park, J., Churchyard, K., Greenwood, J., Walshaw, M.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 62 KB

english, 2013

590

WS19.2 Sinus pathogens in children with cystic fibrosis: Do they relate to lower respiratory tract pathogens and is eradication successful?

Wilson, P., Lambert, C., Carr, S.B., Pao, C.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 63 KB

english, 2013

591

345 Systematic review of qualitative studies investigating barriers to adherence in patients with cystic fibrosis using framework analysis structured by a conceptual framework of behaviour change

Jones, S., Curley, R., Wildman, M.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 58 KB

english, 2013

592

14 Genetic characterization of the pediatric patients from southern and central Portugal and islands

Pereira, L., Cavaco, J., Felix, M., Gonçalves, J., Nunes, S., Freitas, C., Silva, T., Barreto, C.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 70 KB

english, 2013

593

94 The interaction of liposomal tobramycin-bismuth with lung cells: Fusion efficacy and toxicity studies

Tshimanga, F.N., Omri, A.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 68 KB

english, 2013

594

321 Anxiety and depression in transplant patients

Catastini, P., Desiati, C., Martellacci, A., de Masi, S., Braggion, C.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 58 KB

english, 2013

595

195 Efficacy of inhaled amiloride solution versus hypertonic saline, prospective open label single center study in children with cystic fibrosis

Homola, L., Holčiková, A., Mikolášek, P., Krbková, L.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 65 KB

english, 2013

596

WS20.5 Genetic interaction of NOS-1 and CFTR gene and its association with cystic fibrosis severity

Marson, F.A., Bertuzzo, C.S., Ribeiro, A.F., Ribeiro, J.D.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 60 KB

english, 2013

597

WS22.2 Pseudomonas aeruginosa-induced apoptosis in airway epithelial cells is mediated by gap junctional communication in a CFTR-dependent manner

Losa, D., Köhler, T., Bellec, J., Dudez, T., Crespin, S., Bacchetta, M., Nguyen, T.H., Van Delden, C., Chanson, M.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 65 KB

english, 2013

598

WS7.2 Ex vivo effect of CFTR modulators VX770, VX809 and PTC124 on CFTR-mediated chloride secretion in rectal biopsies from CF patients

Scheinert, S., Pinders-Kessel, L., Derichs, N.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 71 KB

english, 2013

599

254 The prognostic significance of hypoglycaemia on oral glucose tolerance tests in adults with cystic fibrosis (CF): A prospective clinical study

Harrison, M.J., Neff, K.J., Shortt, C., Fleming, C., Mccarthy, M., O'Riordan, S.M., Murphy, D.M., O'Halloran, D.J., Plant, B.J.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 66 KB

english, 2013

600

205 St George's Respiratory Questionnaire (SGRQ): A useful tool in adult CF patients

Hofer, M., Hirt, A., Lienert, B. Fiechter, Kurowski, T., Boehler, A.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 63 KB

english, 2013

601

200 Is sweat chloride predictive for severity of cystic fibrosis (CF) lung disease assessed by chest computed tomography (CT)?

Zitter, D., Caudri, D., Bronsveld, I., Tiddens, H.A.W.M.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 62 KB

english, 2013

602

7 It's a family affair – A diagnostic dilemma of cystic fibrosis within a family

Rose, I.M., Rewitzky, G., Kavanagh, C.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 64 KB

english, 2013

603

108 Adaptive mechanisms associated with increased virulence and persistence of Burkholderia cenocepacia during chronic lung infection: A quantitative proteomic analysis

Madeira, A., dos Santos, S.C., Santos, P.M., Coutinho, C.P., Tyrrell, J., McClean, S., Callaghan, M., Sá-Correia, I.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 65 KB

english, 2013

604

145 The prevalence and significance of methicillin resistant Staphylococcus aureus infection in patients with cystic fibrosis in a Macedonian CF center

Fustik, S., Jakovska, T., Lidija, S.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 68 KB

english, 2013

605

44 Nitrogen washout using an ultrasonic device for routine measurement of the LCI in patients with CF

Fuchs, S., Petri, E., Küster, P., Hülskamp, G., Gappa, M.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 68 KB

english, 2013

606

46 Functional properties of CFTR in human monocytes measured by patch clamp technique

Ettorre, M., Verzé, G., Caldrer, S., Johansson, J., Assael, B.M., Melotti, P., Buffelli, M., Sorio, C.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 65 KB

english, 2013

607

WS13.1 Lung clearance index predicts time to pulmonary exacerbation in children with CF

Vermeulen, F., Boon, M., Proesmans, M., Havermans, T., De Boeck, K.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 64 KB

english, 2013

608

43 Lung-MRI for monitoring cystic fibrosis (CF) patients with pulmonary exacerbation

De Leo, F., Tavano, V., Bertolo, S., Ros, M., Ciet, P., Morana, G.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 68 KB

english, 2013

609

WS16.5 Comparison of cystic fibrosis adolescents with normal and low bone mineral density

Mielus, M., Sands, D., Oralewska, B., Ołtarzewski, M., Walkowiak, J.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 62 KB

english, 2013

610

111 The Burkholderia cenocepacia J2315 small non-coding RNA MavA is required for fitness and virulence

Sousa, S.A., Feliciano, J.R., Ramos, C.G., Leitão, J.H.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 64 KB

english, 2013

611

91 Sequential inhalative tobramycin–colistin-combination stabilizes patients with chronic Pseudomonas aeruginosa colonization

Herrmann, G., Hellwig, D., Heuer, H.-E., Heyder, S., Köster, H., Kröger, K., Paul, K., Mellies, U., Schmitt, A., Wagenseil, D., Riethmueller, J.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 68 KB

english, 2013

612

66 Effects of a 3-year therapy with glargine among pediatric patients with cystic fibrosis and early glucose derangements

Fattorusso, V., Raia, V., Mozzillo, E., Natale, C., De Nitto, E., Amato, N., De Gregorio, F., Franzese, A., Casale, A.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 63 KB

english, 2013

613

265 Prevalence and treatment of reduced BMD in a cystic fibrosis cohort undergoing lung transplantation

Mohammadieh, A., Benden, C., Glanville, A.R.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 65 KB

english, 2013

614

Ventilatory pattern and energy expenditure are altered in cystic fibrosis mice

Darrah, Rebecca J., Bederman, Ilya R., Mitchell, Anna L., Hodges, Craig A., Campanaro, Cara K., Drumm, Mitchell L., Jacono, Frank J.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 514 KB

english, 2013

615

WS19.6 Changes in the weather and the respiratory health of adults with cystic fibrosis

Flight, W.G., Sarran, C., Mutton, K.J., Morris, J., Webb, A.K., Bright-Thomas, R.J., Jones, A.M.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 62 KB

english, 2013

616

303 Retinal screening in Wales – A real eye opener!

Roberts, R., Speight, L., Lee, J., Ketchell, R.I., Lau, D., Duckers, J.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 58 KB

english, 2013

617

358 CF registry mortality analysis to understand the effects of widespread genetic testing on the trend of median age at death: Is the increased life-expectancy related to increased prevalence of mild phenotypes?

Hoo, Z.H., Wildman, M., Teare, M.D.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 62 KB

english, 2013

618

186 Omalizumab in the treatment of ABPA in 32 patients with cystic fibrosis

Grard, S., Auzou, L.G., Nové-Josserand, R., Reix, P., Murris-Espin, M., Brémont, F., Mammar, B., Mély, L., Hubert, D., Burgel, P.-R., Durieu, I.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 67 KB

english, 2013

619

223 Nebulised meropenem: A review of one year outcome in an adult cystic fibrosis centre

Kendall, V., Parker-Stafford, J., Johnson, S., Jones, A.M., Brennan, A.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 58 KB

english, 2013

620

291 Vitamin D status in children with cystic fibrosis

Denis, M.-H., Caron, E., Lebel, D.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 65 KB

english, 2013

621

350 What strategies are used by young “expert patients” with cystic fibrosis and healthcare professionals to maintain and negotiate partnership?

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 57 KB

english, 2013

622

277 Nutritional status of Russian children with cystic fibrosis diagnosed before and after neonatal screening

Roslavtseva, E., Gorinova, Y., Simonova, O.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 65 KB

english, 2013

623

WS9.6 Cystic fibrosis-related postural and baropodometric changes: A comparison with healthy individuals

Donadio, M.V., Schindel, C.S., Hommerding, P.X., Melo, D.A., Batista, R.R., Marostica, P.J.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 59 KB

english, 2013

624

WS6.8 Intensive care unit outcomes in cystic fibrosis patients admitted with hemoptysis vs all other indications

Markewitz, B., Markewitz, D., Liou, T.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 59 KB

english, 2013

625

239 Parenchymal and functional ultrasonographic imaging of the pancreas in cystic fibrosis correlates with exocrine pancreatic function

Engjom, T., Lrum, B.N., Erchinger, F., Tjora, E., Dimcevski, G., Gilja, O.H.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 64 KB

english, 2013

626

104 Clinical profile of Pseudomonas aeruginosa clone C infection in CF children

Gopalakaje, S., O'Brien, C.J., Robb, A., Spencer, D.A.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 69 KB

english, 2013

627

49 Rectal forceps biopsy procedure in cystic fibrosis: Technical aspects and patients' perspective for clinical trials feasibility

Servidoni, M.F., Sousa, M., Vinagre, A.M., Cardoso, S., Ribeiro, M.A.G.O., Meirelles, L., Carvalho, R., Kunzelmann, K., Ribeiro, J.D., Ribeiro, A.F., Amaral, M.D.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 65 KB

english, 2013

628

307 Kidney transplantation after lung transplantation in cystic fibrosis patients

Cimino, G., Bertasi, S., Troiani, P., Rossi, P., D'Alù, V., Cucchiara, S.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 54 KB

english, 2013

629

Subtherapeutic itraconazole and voriconazole levels in children with cystic fibrosis

Bentley, S., Gupta, A., Balfour-Lynn, I.M.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 80 KB

english, 2013

630

286 Is there a place for CTX with cystic fibrosis?

Ochota, A., Pandya, S., Walshaw, M.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 65 KB

english, 2013

631

42 Comparison of 2 nasal potential difference measurement (NPD) methods (needle–abrasia): Is one more patient-friendly than the other?

De Wachter, E., De Schutter, I., Haentjens, P., Stinckens, S., Malfroot, A.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 68 KB

english, 2013

632

The use of ivacaftor in an adult with severe lung disease due to cystic fibrosis (ΔF508/G551D)

Polenakovik, Hari M., Sanville, Bradley

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 90 KB

english, 2013

633

The predictive potential of the sweat chloride test in cystic fibrosis patients with the G551D mutation

Seliger, Verena I., Rodman, David, Van Goor, Fredrick, Schmelz, Andreas, Mueller, Peter

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 456 KB

english, 2013

634

Early treatment with inhaled antibiotics postpones next occurrence of Achromobacter in cystic fibrosis

Wang, M., Ridderberg, W., Hansen, C.R., Høiby, N., Jensen-Fangel, S., Olesen, H.V., Skov, M., Lemming, L.E., Pressler, T., Johansen, H.K., Nørskov-Lauritsen, N.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 215 KB

english, 2013

635

Prevalence of Helicobacter pylori infection in patients with cystic fibrosis

Drzymała-Czyż, Sławomira, Kwiecień, Jarosław, Pogorzelski, Andrzej, Rachel, Marta, Banasiewicz, Tomasz, Pławski, Andrzej, Szczawińska-Popłonyk, Aleksandra, Herzig, Karl-Heinz, Walkowiak, Jarosław

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 128 KB

english, 2013

636

Itraconazole and inhaled fluticasone causing hypothalamic–pituitary–adrenal axis suppression in adults with cystic fibrosis

Gilchrist, Francis J., Cox, Katrina J., Rowe, Rachel, Horsley, Alex, Webb, A. Kevin, Jones, Andrew M., Bright-Thomas, Rowland J.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 105 KB

english, 2013

637

Positive parental attitudes to participating in research involving newborn screened infants with CF

Chudleigh, Jane, Hoo, Ah-Fong, Ahmed, Deeba, Prasad, Ammani, Sheehan, Denise, Francis, Jackie, Buckingham, Sarah, Cowlard, Jacqui, Thia, Lena, Nguyen, The Thanh Diem, Stocks, Janet

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 216 KB

english, 2013

638

Development of a quantitative immunofluorescence assay for detection of Stenotrophomonas maltophilia antibodies in patients with cystic fibrosis

Vidigal, P. Gonçalves, Schmidt, D., Stehling, F., Mellies, U., Steinmann, E., Buer, J., Rath, P.-M., Steinmann, J.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 240 KB

english, 2013

639

Exhaled molecular profiles in the assessment of cystic fibrosis and primary ciliary dyskinesia

Paff, T., van der Schee, M.P., Daniels, J.M.A., Pals, G., Postmus, P.E., Sterk, P.J., Haarman, E.G.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 368 KB

english, 2013

640

CFTR: Effect of ICL2 and ICL4 amino acids in close spatial proximity on the current properties of the channel

Billet, Arnaud, Mornon, Jean-Paul, Jollivet, Mathilde, Lehn, Pierre, Callebaut, Isabelle, Becq, Frédéric

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 2.11 MB

english, 2013

641

Modification of the salivary secretion assay in F508del mice — The murine equivalent of the human sweat test

Droebner, Karoline, Sandner, Peter

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 466 KB

english, 2013

642

Aztreonam for inhalation solution, challenges to drug approval and integration into CF care

Goss, Christopher H., Bell, Scott C.

Journal:

Journal of Cystic Fibrosis

Year:

2013

Language:

english

File:

PDF, 91 KB

english, 2013

To build up a library is to create a life. It’s never just a random collection of books.

— Carlos María Domínguez

Official channel

Z-Library Desktop Launcher

Tor version

Z-Library

Z-Library Since 2009 support@z-lib.do

EnglishРусскийEspañolItalianoελληνικάاللغة العربيةBahasa IndonesiaBahasa Malaysiaहिन्दीDeutschFrançaisPortuguêsУкраїнськаPolski中文繁體中文日本語Tiếng ViệtAzərbaycan DiliՀայոց լեզուภาษาไทยTürk Diliქართველიবাংলাپښتوతెలుగుاردو한국어SrpskiБългарски