Volume 13

Journal of Cystic Fibrosis

Volume 13

1

Reduced fat oxidation rates during submaximal exercise in boys with cystic fibrosis

Nguyen, Thanh, Obeid, Joyce, Baker, Jeff M., Takken, Tim, Pedder, Linda, Parise, Gianni, Timmons, Brian W.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 372 KB

english, 2014

2

Inflammatory and immunological biomarkers are not related to survival in adults with Cystic Fibrosis

Moffitt, K.L., Martin, S.L., Jones, A.M., Webb, A.K., Cardwell, C., Tunney, M.M., Elborn, J.S.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 222 KB

english, 2014

3

Investigating the role of matrix components in protection of Burkholderia cepacia complex biofilms against tobramycin

Messiaen, Anne-Sophie, Nelis, Hans, Coenye, Tom

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 361 KB

english, 2014

4

HRCT and MRI of the lung in children with cystic fibrosis: Comparison of different scoring systems

Sileo, Chiara, Corvol, Harriet, Boelle, Pierre-Yves, Blondiaux, Eléonore, Clement, Annick, Ducou Le Pointe, Hubert

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 1.02 MB

english, 2014

5

Interval exercise training in cystic fibrosis — Effects on exercise capacity in severely affected adults

Gruber, Wolfgang, Orenstein, David M., Braumann, Klaus M., Beneke, Ralph

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 156 KB

english, 2014

6

Clinical presentation of mild cystic fibrosis in a Serbian patient homozygous for the CFTR mutation c.1393-1G>A

Nikolic, Aleksandra, Radlovic, Nedeljko, Dinic, Jelena, Milosevic, Katarina, Radojkovic, Dragica

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 311 KB

english, 2014

7

Pulmonary exacerbations in CF patients with early lung disease

Anstead, Michael, Saiman, Lisa, Mayer-Hamblett, Nicole, Lands, Larry C., Kloster, Margaret, Goss, Christopher H., Rose, Lynn, Burns, Jane L., Marshall, Bruce, Ratjen, Felix

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 308 KB

english, 2014

8

Annual Review Clinic improves care in children with cystic fibrosis

Chuang, Sandra, Doumit, Michael, McDonald, Rebecca, Hennessy, Erika, Katz, Tamarah, Jaffe, Adam

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 156 KB

english, 2014

9

Anti-BPIFA1/SPLUNC1: A new autoantibody prevalent in patients with endstage cystic fibrosis

Budding, K., van de Graaf, E.A., Hoefnagel, T., Hack, C.E., Otten, H.G.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 599 KB

english, 2014

10

Inhalation solutions — Which ones may be mixed? Physico-chemical compatibility of drug solutions in nebulizers — Update 2013

Kamin, Wolfgang, Erdnüss, Frank, Krämer, Irene

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 370 KB

english, 2014

11

Comparison of different IRT-PAP protocols to screen newborns for cystic fibrosis in three central European populations

Sommerburg, Olaf, Krulisova, Veronika, Hammermann, Jutta, Lindner, Martin, Stahl, Mirjam, Muckenthaler, Martina, Kohlmueller, Dirk, Happich, Margit, Kulozik, Andreas E., Votava, Felix, Balascakova, Mi

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 415 KB

english, 2014

12

Cost effectiveness of newborn screening for cystic fibrosis: A simulation study

Nshimyumukiza, L., Bois, A., Daigneault, P., Lands, L., Laberge, A.-M., Fournier, D., Duplantie, J., Giguère, Y., Gekas, J., Gagné, C., Rousseau, F., Reinharz, D.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 375 KB

english, 2014

13

Culture-based diagnostic microbiology in cystic fibrosis: Can we simplify the complexity?

Burns, Jane L., Rolain, Jean-Marc

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 256 KB

english, 2014

14

Nasal potential difference measurements in diagnosis of cystic fibrosis: An international survey

Naehrlich, Lutz, Ballmann, Manfred, Davies, Jane, Derichs, Nico, Gonska, Tanja, Hjelte, Lena, van Konigsbruggen-Rietschel, Silke, Leal, Teresinha, Melotti, Paola, Middleton, Peter, Tümmler, Burkhard,

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 249 KB

english, 2014

15

Sweat conductivity: An accurate diagnostic test for cystic fibrosis?

Mattar, Ana Claudia Veras, Leone, Claudio, Rodrigues, Joaquim Carlos, Adde, Fabíola Villac

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 220 KB

english, 2014

16

Serum antibodies to Pseudomonas aeruginosa in cystic fibrosis as a diagnostic tool: A systematic review

Mauch, Renan Marrichi, Levy, Carlos Emilio

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 219 KB

english, 2014

17

Prediction of acute pancreatitis risk based on PIP score in children with cystic fibrosis

Terlizzi, V., Tosco, A., Tomaiuolo, R., Sepe, A., Amato, N., Casale, A., Mercogliano, C., De Gregorio, F., Improta, F., Elce, A., Castaldo, G., Raia, V.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 283 KB

english, 2014

18

Pneumococcal polysaccharide vaccine responses are impaired in a subgroup of children with cystic fibrosis

Browning, Michael J., Lim, Michael T.C., Kenia, Priti, Whittle, Michelle, Doffinger, Rainer, Barcenas-Morales, Gabriela, Kumararatne, Dinakantha, Viskaduraki, Maria, O'Callaghan, Christopher, Gaillard

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 328 KB

english, 2014

19

Iron supplementation does not worsen respiratory health or alter the sputum microbiome in cystic fibrosis

Gifford, Alex H., Alexandru, Diana M., Li, Zhigang, Dorman, Dana B., Moulton, Lisa A., Price, Katherine E., Hampton, Thomas H., Sogin, Mitchell L., Zuckerman, Jonathan B., Parker, H. Worth, Stanton, B

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 531 KB

english, 2014

20

Effects of nutritional status and dietetic interventions on survival in Cystic Fibrosis patients before and after lung transplantation

Hollander, F.M., van Pierre, D.D., de Roos, N.M., van de Graaf, E.A., Iestra, J.A.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 623 KB

english, 2014

21

Bronchiectases at early chest computed tomography in children with cystic fibrosis are associated with increased risk of subsequent pulmonary exacerbations and chronic pseudomonas infection

Bortoluzzi, Carla-Federica, Volpi, Sonia, D'Orazio, Ciro, Tiddens, Harm A.W.M., Loeve, Martine, Tridello, Gloria, Assael, Baroukh M.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 294 KB

english, 2014

22

Effectiveness of inhaled tobramycin in eradicating Pseudomonas aeruginosa in children with cystic fibrosis

Stanojevic, Sanja, Waters, Valerie, Mathew, Joseph L., Taylor, Louise, Ratjen, Felix

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 330 KB

english, 2014

23

Impact of azithromycin treatment on macrophage gene expression in subjects with cystic fibrosis

Cory, Theodore J., Birket, Susan E., Murphy, Brian S., Hayes, Don, Anstead, Michael I., Kanga, Jamshed F., Kuhn, Robert J., Bush, Heather M., Feola, David J.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 732 KB

english, 2014

24

Active video games as an exercise tool for children with cystic fibrosis

O'Donovan, Cuisle, Greally, Peter, Canny, Gerard, McNally, Paul, Hussey, Juliette

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 257 KB

english, 2014

25

Combined effects of VX-770 and VX-809 on several functional abnormalities of F508del-CFTR channels

Kopeikin, Z., Yuksek, Z., Yang, H.-Y., Bompadre, S.G.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 715 KB

english, 2014

26

Corrigendum to: “Update on cystic fibrosis-related diabetes” [Journal of Cystic Fibrosis 12 (2013) 318-331]

Kelly, Andrea, Moran, Antoinette

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 68 KB

english, 2014

27

Hypersensitivity to antibiotics in patients with cystic fibrosis

Roehmel, Jobst Fridolin, Schwarz, Carsten, Mehl, Anne, Stock, Philippe, Staab, Doris

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 361 KB

english, 2014

28

An observational study of matrix metalloproteinase (MMP)-9 in cystic fibrosis

Devereux, Graham, Steele, Sandra, Jagelman, Timothy, Fielding, Shona, Muirhead, Robert, Brady, Jeff, Grierson, Christal, Brooker, Richard, Winter, John, Fardon, Tom, McCormick, Jonathan, Huang, Jeffre

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 298 KB

english, 2014

29

Regarding the article entitled “Hypersensitivity to antibiotics in patients with cystic fibrosis”

Matar, R., Le Bourgeois, M., Scheinmann, P., de Blic, J., Ponvert, C.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 87 KB

english, 2014

30

Respiratory physicians and clinic coordinators' attitudes to population-based cystic fibrosis carrier screening

Cunningham, Fiona, Lewis, Sharon, Curnow, Lisette, Glazner, Judith, Massie, John

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 314 KB

english, 2014

31

Safety of inhaled (Tobi®) and intravenous tobramycin in young children with cystic fibrosis

Hennig, Stefanie, McKay, Karen, Vidmar, Suzanna, O'Brien, Katie, Stacey, Sonya, Cheney, Joyce, Wainwright, Claire E.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 348 KB

english, 2014

32

Prescribing practices for intravenous aminoglycosides in UK Cystic Fibrosis clinics: A questionnaire survey

Smyth, Alan R., Campbell, Emma L.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 307 KB

english, 2014

33

BIIL 284 reduces neutrophil numbers but increases P. aeruginosa bacteremia and inflammation in mouse lungs

Döring, Gerd, Bragonzi, Alessandra, Paroni, Moira, Aktürk, Firdevs-Fatma, Cigana, Cristina, Schmidt, Annika, Gilpin, Deirdre, Heyder, Susanne, Born, Torsten, Smaczny, Christina, Kohlhäufl, Martin, Wag

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 866 KB

english, 2014

34

Complicated Clostridium difficile colitis in children with cystic fibrosis: Association with gastric acid suppression?

Com, G., Cetin, N., O'Brien, C.E.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 420 KB

english, 2014

35

The value of soluble transferrin receptor and hepcidin in the assessment of iron status in children with cystic fibrosis

Uijterschout, Lieke, Swinkels, Dorine W., Akkermans, Marjolijn D., Zandstra, Thomas, Nuijsink, Marianne, Hendriks, Daniëlle, Hudig, Cisca, Tjalsma, Harrold, Vos, Rimke, van Goudoever, Johannes B., Bru

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 367 KB

english, 2014

36

Elevated metal concentrations in the CF airway correlate with cellular injury and disease severity

Smith, Daniel J., Anderson, Gregory J., Bell, Scott C., Reid, David W.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 263 KB

english, 2014

37

Sweat chloride as a biomarker of CFTR activity: Proof of concept and ivacaftor clinical trial data

Accurso, Frank J., Van Goor, Fredrick, Zha, Jiuhong, Stone, Anne J., Dong, Qunming, Ordonez, Claudia L., Rowe, Steven M., Clancy, John Paul, Konstan, Michael W., Hoch, Heather E., Heltshe, Sonya L., R

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 360 KB

english, 2014

38

Development of IgG antibodies to Exophiala dermatitidis is associated with inflammatory responses in patients with cystic fibrosis

Kondori, Nahid, Lindblad, Anders, Welinder-Olsson, Christina, Wennerås, Christine, Gilljam, Marita

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 755 KB

english, 2014

39

Editorial Board

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 53 KB

english, 2014

40

Marked repression of CFTR mRNA in the transgenic Cftrtm1kth mouse model

Zhang, Shaoyan, Ranganath, Neel K., Skinner, Daniel, Bedwell, David M., Buckley-Lanier, Jessica A., Sorscher, Eric J., Woodworth, Bradford A.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 204 KB

english, 2014

41

Effect of a dietary intervention on growth and energy expenditure in children with cystic fibrosis

Groleau, Veronique, Schall, Joan I., Dougherty, Kelly A., Latham, Norma E., Maqbool, Asim, Mascarenhas, Maria R., Stallings, Virginia A.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 194 KB

english, 2014

42

Neonatal screening for cystic fibrosis: Comparing the performances of IRT/DNA and IRT/PAP

Sarles, Jacques, Giorgi, Roch, Berthézène, Patrice, Munck, Anne, Cheillan, David, Dagorn, Jean-Charles, Roussey, Michel

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 276 KB

english, 2014

43

Comparison of two tobramycin nebuliser solutions: Pharmacokinetic, efficacy and safety profiles of T100 and TNS

Sands, Dorota, Sapiejka, Ewa, Gąszczyk, Grzegorz, Mazurek, Henryk

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 565 KB

english, 2014

44

Susceptibility to varicella zoster of children with cystic fibrosis

Polychronakis, T., Davies, G., Balfour-Lynn, I.M.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 139 KB

english, 2014

45

The relative frequency of CFTR mutation classes in European patients with cystic fibrosis

De Boeck, K., Zolin, A., Cuppens, H., Olesen, H.V., Viviani, L.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 1008 KB

english, 2014

46

Depression and anxiety in adolescents and adults with cystic fibrosis in the UK: A cross-sectional study

Duff, Alistair J.A., Abbott, Janice, Cowperthwaite, Carolyn, Sumner, Clare, Hurley, Margaret A., Quittner, Alexandra

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 460 KB

english, 2014

47

Commentary for JCF review “Drug induced complications; can we do more?” J Cyst Fibros 2013 Dec;12(6):547–58

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 71 KB

english, 2014

48

Reassessment of the importance of mucins in determining sputum properties in cystic fibrosis

Horsley, Alex, Rousseau, Karine, Ridley, Caroline, Flight, William, Jones, Andrew, Waigh, Thomas A., Thornton, David J.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 478 KB

english, 2014

49

Early assessment of glucose abnormalities during continuous glucose monitoring associated with lung function impairment in cystic fibrosis patients

Leclercq, A., Gauthier, B., Rosner, V., Weiss, L., Moreau, F., Constantinescu, A.A., Kessler, R., Kessler, L.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 397 KB

english, 2014

50

Evaluating the predictive ability of sweat chloride

Heltshe, Sonya L., Rowe, Steven M., Mayer- Hamblett, Nicole

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 80 KB

english, 2014

51

The role of respiratory viruses in adult patients with cystic fibrosis receiving intravenous antibiotics for a pulmonary exacerbation

Etherington, C., Naseer, R., Conway, S.P., Whitaker, P., Denton, M., Peckham, D.G.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 208 KB

english, 2014

52

Impact of Scedosporium apiospermum complex seroprevalence in patients with cystic fibrosis

Parize, Perrine, Billaud, Sandrine, Bienvenu, Anne L., Bourdy, Stéphanie, le Pogam, Marie A., Reix, Philippe, Picot, Stéphane, Robert, Raymond, Lortholary, Olivier, Bouchara, Jean-Philippe, Durieu, Is

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 339 KB

english, 2014

53

Sinonasal manifestations of cystic fibrosis: A correlation between genotype and phenotype?

Berkhout, M.C., van Rooden, C.J., Rijntjes, E., Fokkens, W.J., el Bouazzaoui, L.H., Heijerman, H.G.M.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 451 KB

english, 2014

54

The impact of switching to the new global lung function initiative equations on spirometry results in the UK CF Registry

Stanojevic, Sanja, Stocks, Janet, Bountziouka, Vassiliki, Aurora, Paul, Kirkby, Jane, Bourke, Stephen, Carr, Siobhán B., Gunn, Elaine, Prasad, Ammani, Rosenfeld, Margaret, Bilton, Diana

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 1.21 MB

english, 2014

55

Editorial Board

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 56 KB

english, 2014

56

Inhaled aztreonam for chronic Burkholderia infection in cystic fibrosis: A placebo-controlled trial

Tullis, D. Elizabeth, Burns, Jane L., Retsch-Bogart, George Z., Bresnik, Mark, Henig, Noreen R., Lewis, Sandra A., LiPuma, John J.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 517 KB

english, 2014

57

Spiritual coping predicts 5-year health outcomes in adolescents with cystic fibrosis

Reynolds, Nina, Mrug, Sylvie, Britton, LaCrecia, Guion, Kimberly, Wolfe, Kelly, Gutierrez, Hector

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 241 KB

english, 2014

58

Effect of ivacaftor on CFTR forms with missense mutations associated with defects in protein processing or function

Van Goor, Fredrick, Yu, Haihui, Burton, Bill, Hoffman, Beth J.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 404 KB

english, 2014

59

Levels of moderate–vigorous physical activity are low in Spanish children with cystic fibrosis: A comparison with healthy controls

Aznar, Susana, Gallardo, Cristian, Fiuza-Luces, Carmen, Santana-Sosa, Elena, López-Mojares, Luis M., Santalla, Alfredo, Rodríguez-Romo, Gabriel, Pérez, Margarita, Garatachea, Nuria, Lucia, Alejandro

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 322 KB

english, 2014

60

Nebulized voriconazole in infections with Scedosporium apiospermum — Case report and review of the literature

Holle, J., Leichsenring, M., Meissner, P.E.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 397 KB

english, 2014

61

Hemoglobin≤12.9g/dl predicts risk of antibiotic treatment in cystic fibrosis

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 163 KB

english, 2014

62

The screening and diagnosis of cystic fibrosis-related diabetes in the United Kingdom

Wickens-Mitchell, Kate L., Gilchrist, Francis J., McKenna, D., Raffeeq, P., Lenney, Warren

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 164 KB

english, 2014

63

Validation of a multi-sensor armband during free-living activity in adults with cystic fibrosis

Cox, Narelle S., Alison, Jennifer A., Button, Brenda M., Wilson, John W., Morton, Judith M., Dowman, Leona M., Holland, Anne E.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 233 KB

english, 2014

64

Neutrophil elastase-mediated increase in airway temperature during inflammation

Schmidt, Annika, Belaaouaj, Azzaq, Bissinger, Rosi, Koller, Garrit, Malleret, Laurette, D'Orazio, Ciro, Facchinelli, Martino, Schulte-Hubbert, Bernhard, Molinaro, Antonio, Holst, Otto, Hammermann, Jut

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 639 KB

english, 2014

65

Impact of pulmonary hypertension on survival in patients with cystic fibrosis undergoing lung transplantation: An analysis of the UNOS registry

Hayes, Don, Higgins, Robert S., Kirkby, Stephen, McCoy, Karen S., Wehr, Allison M., Lehman, Amy M., Whitson, Bryan A.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 340 KB

english, 2014

66

Reply to Professor Taylor

Peckham, Daniel, Whitaker, Paul

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 64 KB

english, 2014

67

Inhaled versus nebulised tobramycin: A real world comparison in adult cystic fibrosis (CF)

Harrison, M.J., McCarthy, M., Fleming, C., Hickey, C., Shortt, C., Eustace, J.A., Murphy, D.M., Plant, B.J.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 510 KB

english, 2014

68

Bordetella bronchiseptica in a pediatric Cystic Fibrosis center

Brady, Cynthia, Ackerman, Patricia, Johnson, Mahrya, McNamara, John

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 186 KB

english, 2014

69

Induced sputum compared to bronchoalveolar lavage in young, non-expectorating cystic fibrosis children

Blau, Hannah, Linnane, Barry, Carzino, Rosemary, Tannenbaum, Esta-Lee, Skoric, Billy, Robinson, Philip J., Robertson, Colin, Ranganathan, Sarath C.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 146 KB

english, 2014

70

Neonates with cystic fibrosis have a reduced nasal liquid pH; A small pilot study

Abou Alaiwa, Mahmoud H., Beer, Alison M., Pezzulo, Alejandro A., Launspach, Janice L., Horan, Rebecca A., Stoltz, David A., Starner, Timothy D., Welsh, Michael J., Zabner, Joseph

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 192 KB

english, 2014

71

Feasibility of parental collected nasal swabs for virus detection in young children with cystic fibrosis

Gangell, C.L., Shackleton, C., Poreddy, S., Kappers, J., Gaydon, J.E., Sloots, T.P., Stick, S.M., Ranganathan, S.C., Sly, P.D.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 248 KB

english, 2014

72

Rate of improvement of CF life expectancy exceeds that of general population—Observational death registration study

Hurley, Matthew N., McKeever, Tricia M., Prayle, Andrew P., Fogarty, Andrew W., Smyth, Alan R.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 692 KB

english, 2014

73

Is there evidence for correct diagnosis in cystic fibrosis registries?

Thomas, Muriel, Lemonnier, Lydie, Gulmans, Vincent, Naehrlich, Lutz, Vermeulen, François, Cuppens, Harry, Castellani, Carlo, Norek, Aleksandra, De Boeck, Kris

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 193 KB

english, 2014

74

Answer to “Letter to the Editor” concerning the article “Hypersensitivity to antibiotics in patients with cystic fibrosis” by Roehmel et al.

Roehmel, Jobst Fridolin, Staab, Doris

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 126 KB

english, 2014

75

Efficacy and tolerability of a new nasal spray formulation containing hyaluronate and tobramycin in cystic fibrosis patients with bacterial rhinosinusitis

Di Cicco, Maurizio, Alicandro, Gianfranco, Claut, Laura, Cariani, Lisa, Luca, Nicola, Defilippi, Gloria, Costantini, Diana, Colombo, Carla

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 178 KB

english, 2014

76

Development and evaluation of an educational website for adults with cystic fibrosis

Anand, Anju, Tullis, Elizabeth, Stephenson, Anne, Abhyankar, Preyanka

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 318 KB

english, 2014

77

Airway hyperresponsiveness in FVB/N delta F508 cystic fibrosis transmembrane conductance regulator mice

Bazett, Mark, Haston, Christina K.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 1.50 MB

english, 2014

78

Skin contamination leading to falsely elevated fingerprick tobramycin levels in a patient taking dry powder inhaled tobramycin

Barry, Peter J., Jones, Andrew M.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 92 KB

english, 2014

79

Evaluation of specific immune response in early P. aeruginosa infection in cystic fibrosis patients

Dolce, Daniela, Cariani, Lisa, Campana, Silvia, Ravenni, Novella, Mergni, Gianfranco, Biffi, Arianna, Colombo, Carla, Gagliardini, Rolando, Cirilli, Natalia, Manso, Ester, Padoan, Rita, Soncini, Elena

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 84 KB

english, 2014

80

Cystic fibrosis carrier screening attitudes and multiple hypothesis testing

Jenkins, Bradlee A., Glenn, L. Lee

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 75 KB

english, 2014

81

Cystic fibrosis and pregnancy in the modern era: A case control study

Ahluwalia, Monica, Hoag, Jeffrey B., Hadeh, Anas, Ferrin, Marianne, Hadjiliadis, Denis

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 226 KB

english, 2014

82

Relationship between sweat chloride, sodium, and age in clinically obtained samples

Traeger, Nadav, Shi, Qiuhu, Dozor, Allen J.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 275 KB

english, 2014

83

Improvement of digestive health and reduction in proteobacterial populations in the gut microbiota of cystic fibrosis patients using a Lactobacillus reuteri probiotic preparation: A double blind prospective study

del Campo, Rosa, Garriga, María, Pérez-Aragón, Ana, Guallarte, Pilar, Lamas, Adelaida, Máiz, Luis, Bayón, Carmen, Roy, Garbiñe, Cantón, Rafael, Zamora, Javier, Baquero, Fernando, Suárez, Lucrecia

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 526 KB

english, 2014

84

A randomized double blind, placebo controlled phase 2 trial of BIIL 284 BS (an LTB4 receptor antagonist) for the treatment of lung disease in children and adults with cystic fibrosis

Konstan, M.W., Döring, G., Heltshe, S.L., Lands, L.C., Hilliard, K.A., Koker, P., Bhattacharya, S., Staab, A., Hamilton, A.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 392 KB

english, 2014

85

Pharmacokinetic variability of clarithromycin and differences in CYP3A4 activity in patients with cystic fibrosis

Dalbøge, C.S., Nielsen, X.C., Dalhoff, K., Alffenaar, J.W., Duno, M., Buchard, A., Uges, D.R.A., Jensen, A.G., Jürgens, G., Pressler, T., Johansen, H.K., Høiby, N.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 254 KB

english, 2014

86

Predictors for future cystic fibrosis-related diabetes by oral glucose tolerance test

Schmid, Kerstin, Fink, Katharina, Holl, Reinhard W., Hebestreit, Helge, Ballmann, Manfred

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 156 KB

english, 2014

87

Long-term follow-up of cystic fibrosis newborn screening: Psychosocial functioning of adolescents and young adults

Tluczek, Audrey, Laxova, Anita, Grieve, Adam, Heun, Anne, Brown, Roger L., Rock, Michael J., Gershan, William M., Farrell, Philip M.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 255 KB

english, 2014

88

The development and deployment of integrated electronic care records in a regional adult and paediatric cystic fibrosis unit

Peckham, D., Etherington, C., White, H., Mehta, A., Shaw, N., Morton, A., Pollard, K., Lee, T., Brownlee, K., Taylor, J., Whitaker, P., Conway, S.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 217 KB

english, 2014

89

Antibacterial properties of the CFTR potentiator ivacaftor

Reznikov, Leah R., Abou Alaiwa, Mahmoud H., Dohrn, Cassie L., Gansemer, Nick D., Diekema, Daniel J., Stoltz, David A., Welsh, Michael J.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 512 KB

english, 2014

90

Daily serum creatinine monitoring promotes earlier detection of acute kidney injury in children and adolescents with cystic fibrosis

Downes, Kevin J., Rao, Marepalli B., Kahill, Laurie, Nguyen, Hovi, Clancy, John P., Goldstein, Stuart L.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 288 KB

english, 2014

91

Stigma and optimism in adolescents and young adults with cystic fibrosis

Oliver, Kendea N., Free, Matthew L., Bok, Cody, McCoy, Karen S., Lemanek, Kathleen L., Emery, Charles F.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 276 KB

english, 2014

92

Agreement of bioelectric impedance analysis and dual-energy X-ray absorptiometry for body composition evaluation in adults with cystic fibrosis

Ziai, S., Coriati, A., Chabot, K., Mailhot, M., Richter, M.V., Rabasa-Lhoret, R.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 325 KB

english, 2014

93

Lung clearance index: Evidence for use in clinical trials in cystic fibrosis

Kent, L., Reix, P., Innes, J.A., Zielen, S., Le Bourgeois, M., Braggion, C., Lever, S., Arets, H.G.M., Brownlee, K., Bradley, J.M., Bayfield, K., O'Neill, K., Savi, D., Bilton, D., Lindblad, A., Davie

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 334 KB

english, 2014

94

Sinonasal inhalation of dornase alfa administered by vibrating aerosol to cystic fibrosis patients: A double-blind placebo-controlled cross-over trial

Mainz, Jochen G., Schien, Claudia, Schiller, Isabella, Schädlich, Katja, Koitschev, Assen, Koitschev, Christiane, Riethmüller, Joachim, Graepler-Mainka, Uta, Wiedemann, Bärbel, Beck, James F.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 788 KB

english, 2014

95

Acknowledgement to Reviewers 2013

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 125 KB

english, 2014

96

Contamination of hypertonic saline solutions in use by cystic fibrosis patients in Israel

Peled, Orit, Kalamaro, Vardit, Kerem, Eitan, Shoseyov, David, Blau, Hannah, Efrati, Ori, Block, Colin

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 393 KB

english, 2014

97

At last, Burkholderia spp. is one of the inclusion criteria — A negative (but published) randomised controlled trial

Balfour-Lynn, I.M.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 122 KB

english, 2014

98

Genotype-specific alterations in vascular smooth muscle cell function in cystic fibrosis piglets

Guo, Jinny J., Stoltz, David A., Zhu, Vivian, Volk, Kenneth A., Segar, Jeffrey L., McCray, Paul B., Roghair, Robert D.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 1.09 MB

english, 2014

99

Impact of different breathing protocols on multiple-breath washout outcomes in children

Yammine, Sophie, Singer, Florian, Gustafsson, Per, Latzin, Philipp

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 504 KB

english, 2014

100

Editorial Board

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 56 KB

english, 2014

101

An exploratory study of microbial diversity in sinus infections of cystic fibrosis patients by molecular methods

Rudkjøbing, Vibeke Børsholt, Aanaes, Kasper, Wolff, Tine Yding, von Buchwald, Christian, Johansen, Helle Krogh, Thomsen, Trine Rolighed

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 266 KB

english, 2014

102

Paranasal sinus pathogens in children with cystic fibrosis: Do they relate to lower respiratory tract pathogens and is eradication successful?

Wilson, P., Lambert, C., Carr, S.B., Pao, C.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 196 KB

english, 2014

103

Simultaneous liver–pancreas transplantation for cystic fibrosis-related liver disease: A multicenter experience

Bandsma, R.H.J., Bozic, M.A., Fridell, J.A., Crull, M.H., Molleston, J., Avitzur, Y., Mozer-Glassberg, Y., Gonzalez-Peralta, R.P., Hodik, M., Fecteau, A., de Angelis, M., Durie, P., Ng, V.L.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 257 KB

english, 2014

104

9 CFTR rearrangements in Serbian patients with classical cystic fibrosis

Rankov, A. Divac, Deretić, J., Petrić, M., Ljujic, M., Nikolic, A., Radojkovic, D.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 64 KB

english, 2014

105

Electronic care records — Can they fulfil their promise?

Wainwright, Claire E., Tullis, Elizabeth

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 100 KB

english, 2014

106

7 Genetic prevention of cystic fibrosis as a part of the national strategy for rare diseases in University Hospital Brno, Czech Republic (genetic counselling – DNA analysis – newborn screening – education)

Gaillyová, R., Valášková, I., Nečasová, J., Spěšná, R., Vinohradská, H., Holčíková, A., Homolá, L., Pokojová, E., Dostál, O.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 64 KB

english, 2014

107

WS3.4 Lack of correlation between sputum Pseudomonas aeruginosa density and FEV1 changes among CF patients treated with inhaled antibiotics

Vandevanter, D.R., Flume, P.A., Cohen, F., Fleming, R., Elborn, J.S.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 67 KB

english, 2014

108

12 Associated conditions in cystic fibrosis: findings at diagnosis and changes in time, impact on clinical outcomes and quality of life

Dracea, L.-L., Tamas, L.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 58 KB

english, 2014

109

WS23.2 Characterization of the CFTR mutation c.3700A>G informs strategies for future medical intervention

Molinski, S.V., Gonska, T., Huan, L.J., Baskin, B., Janahi, I.A., Ray, P.N., Bear, C.E.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 61 KB

english, 2014

110

WS12.3 Detachment of mucus requires a specific proteolytic cleavage in the MUC2 mucin explaining why the cystic fibrosis mucus is attached to the epithelium

Schütte, A., Ermund, A., Becker-Pauly, C., Johansson, M.E.V., Rodríguez-Pineiro, A.M., Bäckhed, F., Müller, S., Lottaz, D., Bond, J.S., Hansson, G.C.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 64 KB

english, 2014

111

44 An alginate oligomer (OligoG) developed as a dry powder for inhalation in cystic fibrosis demonstrates an excellent safety profile, similar to a nebulised solution used in a phase 2a trial

Myrset, A.H., Phillips, L., Moore, S.A., Dessen, A.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 58 KB

english, 2014

112

WS1.1 The effect of ivacaftor, a CFTR potentiator, in patients with cystic fibrosis and a non-G551D-CFTR gating mutation, the KONNECTION study

De Boeck, K., Munck, A., Walker, S., Faro, A., Hiatt, P., Chan, J., Gilmartin, G.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 70 KB

english, 2014

113

WS19.4 Pro-inflammatory response of THP-1 monocytic cells to lipopolysaccharide from Prevotella sp. isolated from CF patients

Matier, T., Glasgow, A., Hanuszkiewicz, A., Valvano, M., Silipo, A., Molinaro, A., Taggart, C., Weldon, S., Elborn, J.S., Tunney, M.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 69 KB

english, 2014

114

WS2.1 Liposomal clarithromycin effect on bacterial adhesion to epithelia of cystic fibrosis patients

Omri, A., Halwani, M.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 65 KB

english, 2014

115

WS8.2 Pulmonary arterial hypertension in adult CF lung transplantation candidates

Fila, L., Grandcourtova, A., Valentova Bartakova, L.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 60 KB

english, 2014

116

WS10.1 Can home drug audit prevent oversupply and indicate adherence?

Whitton, C., Waine, D., Goodwin, M., Donohue, K., Weston, D., Stone, C., Derry, D.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 57 KB

english, 2014

117

WS16.2 Highly multiplexed molecular detection of CF lung infections

Pattison, S.H., Snape, C., O'Neill, J., Crockard, M., Tunney, M., Elborn, J.S.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 63 KB

english, 2014

118

WS11.1 Development of a comprehensive workflow for the analysis of CFTR gene using next generation sequencing technology

Valášková, I., Necasova, J., Selingerova, R.M., Spesna, R., Holčíková, A., Homola, L., Pokojová, E., Gaillyová, R.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 59 KB

english, 2014

119

WS3.3 MRI-based pulmonary blood flow and lung function in CF patients – flow changes with pulmonary decline

Clancy, J.P., Amin, R., Szczesniak, R., Mcphail, G., Fleck, R.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 67 KB

english, 2014

120

WS2.7 Use of the Galleria mellonella in vivo model to determine the virulence of bacteria colonising the CF airways

Spence, C., Henderson, J., McLean, D., McCaughey, G., Johnston, E., McIlreavey, L., McGrath, S.J., Elborn, J.S., Tunney, M.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 66 KB

english, 2014

121

42 Tobramycin powder for inhalation is effective in advanced stage CF lung disease: the EAGER trial

Chiron, R., Geller, D.E., Angyalosi, G., Debonnett, L., Yadao, A., Bader, G., Konstan, M.W.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 60 KB

english, 2014

122

37 Clinical outcomes of real world Kalydeco (CORK) study

Ronan, N.J., O'Callaghan, G., Harrison, M.J., Shortt, C., McCarthy, M., Hickey, C., Fleming, C., Cronin, K., Jennings, R., O'Donovan, D., Shanahan, P., Chroinin, M. Ni, Murphy, D.M., Mullane, D., Plan

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 59 KB

english, 2014

123

WS7.1 Pre-clinical evaluation of novel antibiotic POL7001 against Pseudomonas aeruginosa in lung infection models

Bragonzi, A., Bernardini, F., Facchini, M., Alcalà-Franco, B., Cigana, C., De Fino, I., Riva, C., Rossi, A., Obrecht, D.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 64 KB

english, 2014

124

WS16.5 Selective ion-flow mass spectrometry (SIFT-MS) analysis of exhaled breath as a non-invasive determinant of Pseudomonas aeruginosa infection in CF patients

Pabary, R., Huang, J., Kumar, S., Alton, E.W., Bush, A., Hanna, G.B., Davies, J.C.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 64 KB

english, 2014

125

CFTR functional measurements in human models for diagnosis, prognosis and personalized therapy

Beekman, Jeffrey M., Sermet-Gaudelus, Isabelle, de Boeck, Kris, Gonska, Tanja, Derichs, Nico, Mall, Marcus A., Mehta, Anil, Martin, Ulrich, Drumm, Mitch, Amaral, Margarida D.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 252 KB

english, 2014

126

WS3.2 The effect of ivacaftor treatment on lung ventilation defects, as measured by hyperpolarized helium-3 MRI, on patients with cystic fibrosis and a G551D-CFTR mutation

Altes, T., Johnson, M., Higgins, M., Fidler, M., Botfield, M., Mugler III, J.P., Tustison, N., Froh, D.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 68 KB

english, 2014

127

WS5.4 Can registry data be used to examine cystic fibrosis (CF) health service utilisation? Perspectives of the Irish CF Registry

Jackson, A., Suthoff, E., Fletcher, G., Kelleher, C., Harrington, M., Zhou, S., McKone, E.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 57 KB

english, 2014

128

6 CFTR dele2,3 (21 kb) mutation in cystic fibrosis patients in Latvia

Taurina, G., Piekuse, L., Kempa, I., Krumina, Z., Micule, I., Svabe, V., Krumina, A.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 64 KB

english, 2014

129

WS6.3 Subtle defects in glucose metabolism prior to development of diabetes in patients with cystic fibrosis

Marko, L., Hershkop, K., Eshel, N., Eliashar Iron, H., Cohen, M., Kerem, E., Weiss, R.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 60 KB

english, 2014

130

WS10.5 Social support, self-esteem and treatment barriers in adolescents with CF: the LINFA study

Neri, L., Lucidi, V., Catastini, P., Colombo, C.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 56 KB

english, 2014

131

25 Cystic fibrosis (CF) prevalence derived from CF newborn screening (CFNBS) in the Czech Republic: comparison of previous epidemiological and current CFNBS-based disease prevalence data

Krulišová, V., Holubová, A., Piskáčková, T., Balaščaková, M., Skalická, V., Gaillyová, R., Valášková, I., Vinohradská, H., Votava, F., Macek, M.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 62 KB

english, 2014

132

WS21.4 Use of genome sequencing to study population diversification and transmission of a Pseudomonas aeruginosa epidemic strain

Winstanley, C., Williams, D., Fothergill, J.L., Evans, B., Haldenby, S., Loman, N., Hilliam, Y., Walshaw, M., Brockhurst, M.A., Paterson, S.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 62 KB

english, 2014

133

WS13.1 Patients with mutations that permit 3% or more of wild-type CFTR function are associated with higher FEV1

Sosnay, P.R., Raraigh, K.S., Vangoor, F., Yu, H., Penland, C.M., Corey, M., Lewis, M.H., Castellani, C., Rommens, J., Cutting, G.R.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 66 KB

english, 2014

134

WS9.5 The role of daily physical activity on exercise performance in adults with cystic fibrosis

Savi, D., Di Paolo, M., Simmonds, N.J., Perelli, T., Varchetta, M., Bertasi, S., Cimino, G., Troiani, P., D'Alù, V., Quadrucci, S., Cucchiara, S., Palange, P.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 56 KB

english, 2014

135

WS20.1 Are pre-school lung clearance index (LCI) measurements a predictor for later structural lung disease?

Gerbrands, K., Lindblad, A., Hop, W., Tiddens, H.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 65 KB

english, 2014

136

European Cystic Fibrosis Society Standards of Care: Best Practice guidelines

Smyth, Alan R., Bell, Scott C., Bojcin, Snezana, Bryon, Mandy, Duff, Alistair, Flume, Patrick, Kashirskaya, Nataliya, Munck, Anne, Ratjen, Felix, Schwarzenberg, Sarah Jane, Sermet-Gaudelus, Isabelle,

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 302 KB

english, 2014

137

62 A rapid biofilm antimicrobial susceptibility assay under 24 hours for cystic fibrosis patients with Pseudomonas aeruginosa lung infection

Hengzhuang, W., Cao, B., Moser, C., Skjåstad, R., Høiby, N.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 70 KB

english, 2014

138

WS11.3 Change of algorithm in the CF centers influences the amount of equivocal CF diagnoses in the newborn screening program in Switzerland

Rueegg, C.S., Spalinger, J., Hafen, G.M., Moeller, A., Gallati, S., Kuehni, C.E., Torresani, T., Baumgartner, M., Fingerhut, R., Barben, J.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 60 KB

english, 2014

139

European cystic fibrosis society standards of care: A road map to improve CF outcome

Kerem, Eitan, Webb, A. Kevin

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 110 KB

english, 2014

140

WS3.5 Inhaled 7% hypertonic saline treatment in preschool children with cystic fibrosis

Palacio, S., Giugno, H., Díaz Casaux, A., Lucero, B., Smith, S., Giorgetti, M., Bonina, Á., Castaños, C.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 56 KB

english, 2014

141

WS1.4 A rAAV2/5 based gene therapy model for cystic fibrosis airway disease

Carlon, M., Vidović, D., Van den Haute, C., Bijvelds, M., Baekelandt, V., de Jonge, H., Gijsbers, R., Debyser, Z.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 70 KB

english, 2014

142

WS11.2 Age related cut-off levels for immunoreactive trypsin (IRT) in healthy newborns in the first two months of life

Torresani, T., Rueegg, C.S., Baumgartner, M., Fingerhut, R., Barben, J.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 59 KB

english, 2014

143

28 Developing a specialist nurse run adult sweat test clinic

Peres, A., Madge, S., Talbot, S., Dack, K., Holder, E., Bilton, D., Simmonds, N.J.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 64 KB

english, 2014

144

WS17.4 Expression of ENaC subunits in Fischer Rat Thyroid cells as an investigation tool of the interaction between CFTR and ENaC and evaluation of ENaC inhibitors

Castellani, S., Carbone, A., Di Gioia, S., Cannito, S., Ascenzioni, F., Lucarelli, M., Conese, M.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 63 KB

english, 2014

145

WS8.3 Extracorporeal life support as a bridge to lung transplantation: outcome in cystic fibrosis recipients

Inci, I., Bürgi, U., Benden, C., Huber, L.C., Kestenholz, P., Weder, W.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 61 KB

english, 2014

146

52 Burkholderia cenocepacia shows increased attachment to cystic fibrosis lung epithelial cells over time of colonisation

Cullen, L., Schaffer, K., Callaghan, M., McClean, S.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 63 KB

english, 2014

147

43 Experience with fosfomycin: clinical outcomes at an adult UK CF centre

Wilson, P.I., Ohri, C.M., Range, S.P., Pandya, T.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 59 KB

english, 2014

148

A new method of sweat testing: the CF Quantum®sweat test

Rock, Michael J., Makholm, Linda, Eickhoff, Jens

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 1.42 MB

english, 2014

149

16 Influence of newborn screening on the age of diagnosis in cystic fibrosis patients

Zybert, K., Mielus, M., Mierzejewska, E., Ottarzewski, M., Sands, D.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 62 KB

english, 2014

150

59 Population structure and antimicrobial susceptibility of Pseudomonas aeruginosa from a national survey involving 24 cystic fibrosis units in Spain

Caballero, J.D.D., del Campo, R., Cobo, M., Chinchón, G., López-Causapé, C., Antonio, O., Tato, M., Cantón, R.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 63 KB

english, 2014

151

19 Newborn screening for cystic fibrosis – Polish experience with CFTR sequencing strategy

Sobczynska-Tomaszewska, A., Czerska, K., Ołtarzewski, M., Wertheim-Tysarowska, K., Bal, J.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 63 KB

english, 2014

152

WS9.6 The All Wales Adult Cystic Fibrosis Centre (AWACFC) Virtual Instruction of Exercise With Technology to Enhance Care – VIEWTEC Programme

Howard, S., Speight, L., Mills-Bennett, R., Lau, D., Ketchell, R.I., Duckers, J.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 56 KB

english, 2014

153

WS15.4 Cystic fibrosis bronchial epithelial cells have impaired ability to activate vitamin D

Pincikova, T., Flodström-Tullberg, M., Hjelte, L.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 56 KB

english, 2014

154

WS7.4 Inhaled aztreonam lysine (Cayston) therapy significantly improves lung function, weight, hospitalisations and excerbation rates prospectively – an Irish and UK real world experience

Plant, B.J., Downey, D., Eustace, J.A., Gunaratnam, C., Haworth, C., Jones, A., McKone, E., Peckham, D., Ketchell, I., Bilton, D.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 65 KB

english, 2014

155

41 Pharmacokinetics of nasally administered tobramycin, colistin sulphomethate sodium and a combination of tobramycin and colistin sulphomethate sodium

van Velzen, A.J., Berkhout, M.C., Touw, D.J., de Kok, B.M., Heijerman, H.G.M.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 60 KB

english, 2014

156

Adherence to clinical care guidelines for cystic fibrosis-related diabetes in 659 German/Austrian patients

Scheuing, Nicole, Berger, Gabriele, Bergis, Dominik, Gohlke, Bettina, Konrad, Katja, Laubner, Katharina, Lilienthal, Eggert, Moser, Christine, Schütz-Fuhrmann, Ingrid, Thon, Angelika, Holl, Reinhard W

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 511 KB

english, 2014

157

WS6.4 A placebo-controlled trial of insulin therapy with or without adjuvant metformin in patients with cystic fibrosis-related diabetes (CFRD)

van der Meer, R., Heijerman, H.G.M.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 60 KB

english, 2014

158

WS20.5 A high colony count of anaerobic bacteria is related to lung clearance index in cystic fibrosis

O'Neill, K., Johnston, E., McGrath, S.J., McIlreavey, L., Bradley, J.M., Rowan, S., Reid, A., Bradbury, I., Tunney, M., Elborn, J.S.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 54 KB

english, 2014

159

WS14.1 Day-time variability and short term effect of chest physiotherapy on multiple breath nitrogen washout in children with cystic fibrosis

Voldby, C., Green, K., Kongstad, T., Philipsen, L., Buchvald, F.F., Skov, M., Pressler, T., Gustafsson, P., Nielsen, K.G.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 63 KB

english, 2014

160

WS8.4 Extracorporeal life support in cystic fibrosis; a single centre experience

Keating, D., Finlayson, F., Williams, E., Edgeworth, D., Kotsimbos, T., Wilson, J.W.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 61 KB

english, 2014

161

WS8.5 Outcome of lung transplantation for cystic fibrosis in Sweden

Gilliam, M., Nyström, U.M., Dellgren, G., Skog, I., Hansson, L.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 56 KB

english, 2014

162

WS1.5 Restoration of the CFTR function by antisense oligonucleotide splicing modulation

Irony-Tur Sinai, M., Wilton, S., Kerem, B.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 58 KB

english, 2014

163

WS21.2 Sequence–function analysis of clinical LasR variants of Pseudomonas aeruginosa

Wolter, D.J., Pope, C.E., Dandekar, A.A., Hoffman, L.R.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 62 KB

english, 2014

164

WS15.1 Hyperosmolar saline causes detachment of cystic fibrosis mucus

Ermund, A., Meiss, L., Hansson, G.C.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 62 KB

english, 2014

165

WS13.6 Structural alterations in the end-stage cystic fibrosis lung: comparing histopathology to microCT

Lammertyn, E., Bosch, B., Boon, M., Verleden, S., Goeminne, P., Vanaudenaerde, B., Verbeken, E., Verschakelen, J., Van Raemdonck, D., Verleden, G., Hogg, J., De Boeck, K., Dupont, L.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 58 KB

english, 2014

166

WS23.5 Clinical importance of homozygous R117C (c.349C>T) CFTR mutation

de Monestrol, I.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 61 KB

english, 2014

167

11 Disease related CFTR variants found in the Norwegian screening program

Gaup, H.J., Lundman, E., Bjørnæs, A.M., Storrøsten, O.-T., Rootwelt, T., Pettersen, R.D.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 64 KB

english, 2014

168

WS16.3 Rethinking Pseudomonas aeruginosa (PA) lung infection: using molecular microbiology rather than culture and antibodies

Johansen, H.K., Madsen, L.M., Marvig, R.L., Pressler, T., Molin, S.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 63 KB

english, 2014

169

WS9.1 Can lung function predict exercise capacity in patients with CF?

Jensen, I.Ø., Petersen, M.K., Olesen, H.V., Schmidt, A.M.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 59 KB

english, 2014

170

46 Ex vivo efficacy of Lynovex®, a next generation tri-functional candidate cystic fibrosis therapy

Mercer, D., Charrier, C., Robertson, J., Kowalczuk, A., Devlin, E., Fraser-Pitt, D., Devereux, G., O'Neil, D.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 58 KB

english, 2014

171

WS9.3 Reduced physical activity participation is associated with increased need for hospitalisation in adults with cystic fibrosis

Cox, N.S., Alison, J.A., Button, B.M., Wilson, J.W., Morton, J.M., Holland, A.E.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 59 KB

english, 2014

172

WS12.4 Planar cell polarity protein network, which controls ciliogenesis and cilia function, is altered in human cystic fibrosis bronchial epithelial cells through response to endoplasmic reticulum stress

Noël, S., Delbart, W., Dhooghe, B., Leal, T.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 63 KB

english, 2014

173

WS6.5 Body mass index, carbohydrate intake and insulin dosage per carbohydrate unit in 131 female and 77 male patients with cystic fibrosis-related diabetes

Scheuing, N., Bauer, M., Karsten, C., Konrad, K., Meissner, T., Seufert, J., Schoenau, E., Schöfl, C., Thon, A., Woelfle, J., Holl, R.W.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 65 KB

english, 2014

174

WS6.2 Glucose tolerance in pediatric patients with cystic fibrosis

Zazzeron, L., Gambazza, S., Colombo, C.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 59 KB

english, 2014

175

WS1.2 Vardenafil promotes relocalization of F508del-CFTR in human and mouse airways

Dhooghe, B., Noël, S., Bouzin, C., Behets-Wydemans, G., Leal, T.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 70 KB

english, 2014

176

WS11.6 Interpretation of nasal potential difference (nPD) measurements in difficult cases of possible cystic fibrosis and the role of published equations

Pabary, R., Waller, M., Harman, K., Ya-Tung, I., Bilton, D., Simmonds, N.J., Alton, E.W., Davies, J.C.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 54 KB

english, 2014

177

51 The impact of coliforms isolated from cough swabs from infants under the age of one year with cystic fibrosis

Robson, E.A., Brownlee, K., Denton, M.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 60 KB

english, 2014

178

WS8.1 Lung transplant referrals and outcomes: experience of a regional adult CF centre 2008–2013

Etherington, C., Boland, A., Clifton, I., Whitaker, P., Peckham, D.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 61 KB

english, 2014

179

WS6.1 Longitudinal associations between FEV1 and HbA1c in a UK cohort of young people with cystic fibrosis

Williams, R.M., Rootsey, T., Ong, K.K., McShane, D., Shelby, L.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 60 KB

english, 2014

180

WS7.6 Incorporation of a third inhaled antipseudomonal antibiotic class into the management of patients at an adult CF care center

Vandevanter, D.R., Dasenbrook, E.C., Konstan, M.W.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 60 KB

english, 2014

181

56 Pseudomonas aeruginosa end-stage isolates: analysis of virulence traits and interaction with macrophages

Cifani, N., Pompili, B., Ferri, V., Fradiani, P., Di Domenico, E.G., Venuta, F., Anile, M., Del Porto, P., Ascenzioni, F.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 63 KB

english, 2014

182

63 Distribution of tobramycin and the impact on bacterial killing in a biofilm model

Cao, B., Christophersen, L., Thomsen, K., Sønderholm, M., Bjarnsholt, T., Jensen, P. Østrup, Høiby, N., Moser, C.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 70 KB

english, 2014

183

WS19.3 Virulence of serial Pseudomonas aeruginosa isolates grown under aerobic and anaerobic conditions using the Galleria mellonella infection model

Vallières, E., Sherrard, L., McLean, D., Downey, D.G., Tunney, M., Elborn, J.S.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 69 KB

english, 2014

184

27 Infants with an equivocal diagnosis at the Oslo CF centre following newborn screening for CF in Norway

Bakkeheim, E., Storrøsten, O.-T., Lundman, E., Gaup, H.J., Pettersen, R.D.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 62 KB

english, 2014

185

WS11.5 Newborn screening for cystic fibrosis in Norway

Lundman, E., Gaup, H.J., Bjørnæs, A.M., Storrøsten, O.-T., Rootwelt, T., Pettersen, R.D.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 54 KB

english, 2014

186

WS5.2 Travelling abroad with cystic fibrosis (CF): current practice and problems

Lenaghan, S., Blanch, L., Bourke, S., Doe, S., Caraher, M., Anderson, A.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 57 KB

english, 2014

187

WS17.1 Recruitment of CFTR to the enterocyte apical membrane is coordinated with internalization of the transmembrane mucin MUC17 and secretion of the MUC2 mucin from the goblet cells

Schneider, H., Berger, E., Pelaseyed, T., Hansson, G.C.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 63 KB

english, 2014

188

60 Evaluation of twice-a-year antibiotic susceptibility testing for Pseudomonas aeruginosa in adult patients with cystic fibrosis

Morand, P.C., Chapron, J., Loubinoux, J., Honoré, I., Poupet, H., Kanaan, R., Burgel, P.-R., Poyart, C., Dusser, D., Hubert, D.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 70 KB

english, 2014

189

Editorial Board

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 86 KB

english, 2014

190

WS10.4 Pharmacist intervention to influence beliefs about medication in an adult cystic fibrosis clinic

Wilson, P.I., Ohri, C.M., Range, S.P.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 57 KB

english, 2014

191

66 Association of urinary kidney injury molecule-1 with aminoglycoside exposure in children with cystic fibrosis

McWilliam, S.J., Antoine, D.J., Smyth, R.L., Pirmohamed, M.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 63 KB

english, 2014

192

23 Implementation of a diagnostic work up after newborn screening for CF in Oslo, Norway

Hunstad, E.J., Skraastad, B.J., Watle, S.S.V., Bakkeheim, E.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 59 KB

english, 2014

193

WS6.9 Cystic fibrosis related diabetes (CFRD): evidence for a role of miR-155, miR-370 and miR-708

Montanini, L., Gullì, M., Smerieri, A., Pisi, G., Bernasconi, S., Marminoli, N., Street, M.E.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 52 KB

english, 2014

194

WS10.3 Adherence with ivacaftor in cystic fibrosis patients with the G551D mutation

Fox, J., Jones, G.H., Sapina-Vivo, R., Phitidis, E., Ledson, M., Walshaw, M., Greenwood, J.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 57 KB

english, 2014

195

39 ‘Real world’ tolerability, ease of use, patient satisfaction and reported adherence in CF adults commencing Colobreathe®

Cameron, S., Choyce, J., Ahitan, B., Brown, C., Rashid, R., Whitehouse, J.L., Nash, E.F.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 59 KB

english, 2014

196

European Cystic Fibrosis Society Standards of Care: Quality Management in cystic fibrosis

Stern, Martin, Bertrand, Dominique Pougheon, Bignamini, Elisabetta, Corey, Mary, Dembski, Birgit, Goss, Christopher H., Pressler, Tanja, Rault, Gilles, Viviani, Laura, Elborn, J. Stuart, Castellani, C

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 313 KB

english, 2014

197

WS2.6 Novel murine model for persistence, migration and adaptation of Pseudomonas aeruginosa in the respiratory tract

Fothergill, J.L., Neill, D.R., Loman, N., Winstanley, C., Kadioglu, A.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 66 KB

english, 2014

198

WS14.3 UK use of bronchial challenge for new therapies

Lloyd, E.A., Greenwood, J., Walshaw, M.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 63 KB

english, 2014

199

Cytokine gene polymorphisms and severity of CF lung disease

de Vries, Leonieke, Griffiths, Amanda, Armstrong, David, Robinson, Philip J.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 339 KB

english, 2014

200

1 Alleles polymorphism of microsomal epoxide hydrolase gene (mEPHX) as modifier factor in cystic fibrosis

Rohovyk, N., Vishtak, N., Makuh, H., Bober, L., Lyha, O.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 68 KB

english, 2014

201

WS20.4 Is lung clearance index (LCI) affected by the severity of lung disease in CF?

Hatziagorou, E., Avramidou, V., Georgopoulou, V., Kirvasillis, F., Tsanakas, J.N.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 65 KB

english, 2014

202

WS16.6 MALDI-TOF as an alternative method for the identification and typing of Prevotella species from CF patients

McIlreavey, L., Graham, K., McLean, D., McGrath, S.J., Bull, M., Mahenthiralingam, E., Elborn, J.S., Tunney, M., Rolain, J.-M., Gilpin, D.F.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 64 KB

english, 2014

203

WS2.2 Identification of two novel immunogenic Burkholderia cepacia complex proteins involved in lung cell attachment

Dennehy, R., Mujica, C., Valvano, M., Callaghan, M., McClean, S.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 65 KB

english, 2014

204

4 Prevalence of ΔF508 mutation in patients with cystic fibrosis in a miscegenated population of the Brazilian Northeast

Souza, E.L., Pimentel, C.S.S., Sena, N.A., Bittencourt, P.H., Mota, L.R., Lima, R.L.F.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 68 KB

english, 2014

205

WS17.6 Colonic mucus formation relies on bicarbonate secretion via apical Cl−/HCO3−exchange

Gustafsson, J.K., Hansson, G.C.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 59 KB

english, 2014

206

49 Subgingival plaque in patients with cystic fibrosis: potential source for airway colonisation

McLean, D., Sherrard, L., Graham, K., McIlreavey, L., McGrath, S.J., Johnston, E., Irwin, C., Elborn, J.S., Tunney, M.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 60 KB

english, 2014

207

2 Genome sequence of the Danish epidemic strain of Achromobacter ruhlandii

Handberg, K.J., Andreasen, T., Wang, M., Ridderberg, W., Nørskov-Lauritsen, N.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 68 KB

english, 2014

208

Exocrine cell-derived microparticles in response to lipopolysaccharide promote endocrine dysfunction in cystic fibrosis

Constantinescu, Andrei Alexandru, Gleizes, Céline, Alhosin, Mahmoud, Yala, Elhassan, Zobairi, Fatiha, Leclercq, Alexandre, Stoian, Gheorghe, Mitrea, Ioan Liviu, Prévost, Gilles, Toti, Florence, Kessle

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 887 KB

english, 2014

209

WS20.3 Lung clearance index and Aspergillus colonization are clinical markers of chronic lung changes by spirometry controlled CT in children with cystic fibrosis

Kongstad, T., Green, K., Buchvald, F.F., Skov, M., Gustafsson, P., Pressler, T., Nielsen, K.G.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 65 KB

english, 2014

210

47 A novel point of care lipase (ALCT-460) increases fat hydrolysis and omega-3 fat absorption in pigs with exocrine pancreatic insufficiency (EPI)

Martin, C.R., Grujic, D., Goncharova, K., Kirko, S., Pierzynowski, S.G., Szwiec, K., Freedman, S.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 58 KB

english, 2014

211

31 Feasibility of 1H-NMR spectroscopy to detect occurrence of Pseudomonas aeruginosa in saliva of cystic fibrosis patients

Rivas, R., Cerantola, S., Barbier, G., Revert, K., Gouriou, S., Rault, G., Boisramé-Gastrin, S.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 64 KB

english, 2014

212

WS14.4 Analysis of expiratory flow rates used in autogenic drainage. Are they sufficiently high to mobilize secretions?

McIlwaine, M.P., Chilvers, M., Lee Son, N., Richmond, M.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 63 KB

english, 2014

213

WS20.6 The use of LCI as an effective tool for monitoring clinical response to ivacaftor therapy in CF patients with at least one G551D-allele

Jenkins, L.E., Reid, A., Downey, D.G., Elborn, J.S., Rendall, J.C.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 54 KB

english, 2014

214

5 Phenotypic characteristics of p.E92K mutation in adults with cystic fibrosis (CF) in Russia

Usacheva, M., Krasovskiy, S., Stepanova, A., Polyakov, A., Amelina, E.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 64 KB

english, 2014

215

WS21.1 The genetic basis of Pseudomonas aeruginosa pathoadaptation to the airways of cystic fibrosis patients

Marvig, R.L., Madsen, L.M., Pressler, T., Molin, S., Johansen, H.K.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 62 KB

english, 2014

216

WS19.6 Inverse protease–antiprotease relation in upper and lower airway secretions of cystic fibrosis patients

Hentschel, J., Fischer, N., Markert, U.R., Sonnemann, J., Böer, K., Pfister, W., Hipler, U.-C., Mainz, J.G.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 59 KB

english, 2014

217

WS16.1 Development of a competitive ELISA for the detection of the Burkholderia cenocepacia siderophore, ornibactin

Whelan, N., Callaghan, M., Doyle, S.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 63 KB

english, 2014

218

WS13.4 Small-airway disease in cystic fibrosis studied with multidetector CT and microCT

Bosch, B., Boon, M., Verleden, S., Goeminne, P., Lammertyn, E., Vanaudenaerde, B., Van Raemdonck, D., Verbeken, E., Verleden, G., Hogg, J., Verschakelen, J., Dupont, L., De Boeck, K.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 66 KB

english, 2014

219

64 The prevalence of cochlear and vestibular dysfunction in patients with cystic fibrosis

Przeracki, P., MacLean, K., Harris, V., Seabrook, J., Webber, A., Lewis, D., Husein, M., Price, A.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 63 KB

english, 2014

220

18 The first date with patients detected by newborn screening – what do we see?

Hammermann, J., Ulbrich, K., Schulte-Hubbert, B.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 62 KB

english, 2014

221

WS5.6 Cost-effectiveness of performing positive expiratory pressure versus high frequency chest wall oscillation

McIlwaine, M.P., Richmond, M., Agnew, J.L., Alarie, N., Lands, L., Chilvers, M., Ratjen, F.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 56 KB

english, 2014

222

WS13.2 Change in FEV1% predicted in one year in patients with nonsense mutations and patients homozygous for F508del

De Boeck, K., Viviani, L., Zolin, A.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 66 KB

english, 2014

223

14 Updated survey of newborn screening for cystic fibrosis

Pybus, S., Barben, J., Castellani, C., Dankert-Roelse, J., Gartner, S., Kashirskaya, N., Linnane, B., Mayell, S., Munck, A., Sands, D., Sommerburg, O., Winters, V., Southern, K.W.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 59 KB

english, 2014

224

WS17.5 A new tool for CF diagnosis: short circuit current measurements in human nasal epithelial cells collected by nasal brushing

Pruliere-Escabasse, V., Fajac, I.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 59 KB

english, 2014

225

21 Outcomes of children referred after positive cystic fibrosis (CF) newborn screening, who have a normal sweat test

Grime, C., Edmondson, C.L., Balfour-Lynn, I.M.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 59 KB

english, 2014

226

WS2.3 Multifaceted iron acquisition mechanisms of Burkholderia cenocepacia

Whelan, N., Thomas, M., Doyle, S., Callaghan, M.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 65 KB

english, 2014

227

WS10.6 Objective predictors of self-report of adherence in adults with cystic fibrosis

Denman, S., White, H., Shaw, N., Driffil, A., Peckham, D.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 56 KB

english, 2014

228

WS23.4 Rare CF genotype with severe hepatic failure associated with medium chain acid deficiency (MCAD) in a neonate

Mornand, A., Petit, L.-M., Kern, I., Karam, O., Bottani, A., Barazzone-Argiroffo, C.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 61 KB

english, 2014

229

WS8.6 Bacterial flora in the airways after lung transplantation in patients with cystic fibrosis

Hansson, L., Lindberg, U., Inghammar, M., Skog, I.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 56 KB

english, 2014

230

WS21.3 In vitro non-mucoid to mucoid phenotypic switching in clinical isolates of Pseudomonas aeruginosa is induced by mannitol

Moore, J.E., Rendall, J.C., Downey, D.G.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 62 KB

english, 2014

231

WS19.5 An investigation of Burkholderia cenocepacia adaptation during chronic infection and its impact on host response modulation

McGuigan, L., Tyrrell, J., Sá Correia, I., McClean, S., Callaghan, M.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 58 KB

english, 2014

232

Recurrent pulmonary exacerbations are associated with low fat free mass and low bone mineral density in young adults with cystic fibrosis

Alicandro, Gianfranco, Bisogno, Arianna, Battezzati, Alberto, Bianchi, Maria Luisa, Corti, Fabiola, Colombo, Carla

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 264 KB

english, 2014

233

Prenatal diagnosis for CF using High Resolution Melting Analysis and simultaneous haplotype analysis through QF-PCR

Poulou, Myrto, Destouni, Aspasia, Kakourou, Georgia, Kanavakis, Emmanuel, Tzetis, Maria

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 264 KB

english, 2014

234

Spontaneous coronary artery dissection associated with coughing

Sivam, S., Yozghatlian, V., Dentice, R., McGrady, M., Moriarty, C., Di Michiel, J., Bye, P.T.P., Rees, D.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 596 KB

english, 2014

235

306 Bisphosphonate related atypical fracture in cystic fibrosis (CF) – a case study

Evans, L., Al-Azzani, W., Speight, L., Lea-Davies, M., Stone, M., Ketchell, R.I., Duckers, J., Lau, D.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 65 KB

english, 2014

236

News

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 113 KB

english, 2014

237

Nasal saline as a placebo in chronic rhinosinusitis

Karadag, Ahmet, Catal, Ferhat

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 106 KB

english, 2014

238

Predictive values of antibodies against Pseudomonas aeruginosa in patients with cystic fibrosis one year after early eradication treatment

Kappler, Matthias, Nagel, Felicitas, Feilcke, Maria, Heilig, Gabriele, Grimmelt, Ann-Christin, Pawlita, Ingo, Irnstetter, Armin, Hildebrandt, Jenna, Burmester, Helen, Kröner, Caroline, Griese, Matthia

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 780 KB

english, 2014

239

Early detection of infection with Pseudomonas aeruginosa in cystic fibrosis: The Holy Grail or an achievable goal?

Taccetti, Giovanni, Sly, Peter D.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 145 KB

english, 2014

240

Medical consensus, guidelines, and position papers: A policy for the ECFS

De Boeck, K., Castellani, C., Elborn, J.S.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 136 KB

english, 2014

241

A cocktail drug therapy for patients with cystic fibrosis?

Chen, Jeng-Haur

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 125 KB

english, 2014

242

Serology as a diagnostic tool for predicting initialPseudomonas aeruginosa acquisition in childrenwith cystic fibrosis

Daines, Cori, VanDeVanter, Donald, Khan, Umer, Emerson, Julia, Heltshe, Sonya, McNamara, Sharon, Anstead, Michael, Langkamp, Markus, Doring, Gerd, Ratjen, Felix, Ramsey, Bonnie, Gibson, Ronald L., Mor

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 384 KB

english, 2014

243

Response to Karadag

Mainz, Jochen G., Michl, Ruth, Arnold, Christin

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 125 KB

english, 2014

244

Physiological response during activity programs using Wii-based video games in patients with cystic fibrosis (CF)

del Corral, Tamara, Percegona, Janaína, Seborga, Melisa, Rabinovich, Roberto A., Vilaró, Jordi

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 359 KB

english, 2014

245

Efficacy and safety of ivacaftor in patients with cystic fibrosis and a non-G551D gating mutation

De Boeck, Kris, Munck, Anne, Walker, Seth, Faro, Albert, Hiatt, Peter, Gilmartin, Geoffrey, Higgins, Mark

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 413 KB

english, 2014

246

JCF — 2014 and beyond

Bell, Scott C., Heijerman, Harry, Hartl, Dominik

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 105 KB

english, 2014

247

Chronic ivacaftor treatment: Getting F508del-CFTR into more trouble?

Mall, Marcus A., Sheppard, David N.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 139 KB

english, 2014

248

News

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 172 KB

english, 2014

249

224 Improving CF inpatient admissions using a value stream mapping approach

Pitfield, C., Marote, A., Bryon, M., Prasad, A., Suri, R.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 60 KB

english, 2014

250

92 Molecular epidemiological surveillance of Pseudomonas aeruginosa at a Swedish CF centre over a > 10-year period (1999–2012)

Johansson, E.A., Lindblad, A., Gilljam, M., Welinder-Olsson, C.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 66 KB

english, 2014

251

303 Kwashiorkor – a clinical manifestation of cystic fibrosis

Mehl, A., Rolinck-Werninghaus, C., Staab, D.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 64 KB

english, 2014

252

212 Impact of enteral tube feeding on body fat and lean body mass

White, H., Morton, A., Peckham, D.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 60 KB

english, 2014

253

84 Respiratory microbiota in children with cystic fibrosis and healthy controls

Holmes, C.W., Rivett, D.W., Modha, D.E., Bruce, K.D., Gaillard, E.A.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 66 KB

english, 2014

254

78 Comparison of pierced versus broken capsules on delivered fine particle dose for the colistimethate dry powder inhaler

Ng, M., Kassamali, A., Scott, C.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 64 KB

english, 2014

255

75 Efficacy of inhaled antibiotics in CF patients with Pseudomonas aeruginosa (Pa) infection: a network meta-analysis (NMA)

Higashi, K., Janssen, K., Jansen, J., Angyalosi, G., Balp, M.-M., Calado, F., Debonnett, L., Sagkriotis, A., Döring, G., Elborn, J.S.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 69 KB

english, 2014

256

149 Changes in antimicrobial susceptibility in adult CF patients with chronic Pseudomonas aeruginosa infection treated with daily inhalation of tobramycin or colistin

Brouwer, J., Dezaire, D., Brimicombe, R.W., Bouazzaoui, L.H., Heijerman, H.G.M.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 63 KB

english, 2014

257

76 Aerosolized antibiotic therapy in cystic fibrosis with Pseudomonas aeruginosa airway infection in children

Sciuca, S., Eremciuc, R., Dimitrova, O., Cotoman, A.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 68 KB

english, 2014

258

152 Inhaled antibiotics and Candida albicans chronic colonization in cystic fibrosis

Noni, M., Katelari, A., Dimopoulos, G., Kaditis, A., Theochari, I., Lympari, I., Alexandrou, H., Doudounakis, S.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 63 KB

english, 2014

259

Editorial Board

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 53 KB

english, 2014

260

Editorial Board

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 99 KB

english, 2014

261

68 Fast and convenient metalloprotease activity assay based on flow cytometry and its application in cystic fibrosis

Bergamini, G., Sandri, A., Assael, B.M., Melotti, P., Sorio, C.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 63 KB

english, 2014

262

69 Rapid induction of high level azithromycin resistance in clinical CF isolates

McGettigan, C., Kenny, C., Sherrard, L., McCaughey, G., McGrath, S.J., McIlreavey, L., Elborn, J.S., Tunney, M.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 67 KB

english, 2014

263

70 Expression of RND-type efflux pumps as a mechanism of antibiotic resistance in clinical Prevotella isolates

Sherrard, L., Schaible, B., Gilpin, D.F., Elborn, J.S., Tunney, M.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 67 KB

english, 2014

264

71 Extended-spectrum β-lactamase (ESβL) production: a mechanism of resistance to ceftazidime in Prevotella species isolated from patients with CF

Sherrard, L., Matier, T., Gilpin, D.F., Muhlebach, M., Elborn, J.S., Schneiders, T., Tunney, M.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 67 KB

english, 2014

265

72 Inhalatory antibiotic therapy in cystic fibrosis and emergence of colistin resistant Gram-negative non-fermenting bacteria: a new problem in pulmonary infection treatment?

Morelli, P., Delfino, E., Casciaro, R., Formiga, A., Pellettieri, A., Fenu, L.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 67 KB

english, 2014

266

73 Real world evidence on inhaled tobramycin use in CF patients: analysis of the RAMQ data (Canada)

Lachaine, J., Lapierre, M.-È., Beauchemin, C., Angyalosi, G., Balp, M.-M., Calado, F., Debonnett, L., Desforges, J., Sagkriotis, A.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 69 KB

english, 2014

267

74 An evaluation of treatment burden following initiation of TOBI® Podhaler® in patients with CF

Bilton, D., Nash, E.F., Peckham, D., Haworth, C.S., Carroll, M., Connett, G., Uden, R.M., Oswald, L., De Iorio, F., Oliver, G.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 69 KB

english, 2014

268

77 Long-term safety of tobramycin powder for inhalation in patients with cystic fibrosis: ETOILES study

Sommerwerck, U., Virella-Lowell, I., Angyalosi, G., Viegas, A.S., Iqbal, A., Wan, R., Debonnett, L.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 64 KB

english, 2014

269

79 Intravenous colistin and neurotoxicity: recommendations for optimal use in cystic fibrosis (CF) patients

Schelstraete, P., Claus, B., Snauwaert, S., Haerynck, F., Van Daele, S., De Baets, F.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 64 KB

english, 2014

270

80 Therapeutical drug monitoring of piperacillin/tazobactam, given as continuous infusion to patients with cystic fibrosis

Öbrink-Hansen, K., Hardlei, T.F., Jensen-Fangel, S., Brock, B., Thomsen, M.K., Petersen, E.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 64 KB

english, 2014

271

81 Susceptibility of Exophiala dermatitidis to antifungal agents

Kondori, N., Welinder-Olsson, C.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 66 KB

english, 2014

272

82 Effect of ivacaftor on CF clinical isolates of Pseudomonas aeruginosa, Staphylococcus aureus and Streptococcus sp. in comparison to antimicrobial peptides

Payne, J., McLean, D., McIlreavey, L., McGrath, S.J., Tunney, M., Weldon, S., Taggart, C., Elborn, J.S.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 66 KB

english, 2014

273

83 Bronchopulmonary infection/colonization in cystic fibrosis: results from a Spanish multicenter study

Caballero, J.D.D., Cobo, M., Chinchón, G., López-Causapé, C., Oliver, A., de la Pedrosa, E. Gómez, del Campo, R., Tato, M., Cantón, R.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 66 KB

english, 2014

274

85 What is bacterial colonisation of cystic fibrosis children toothbrushes?

Genevois, A., Roques, C., Segonds, C., Cavalié, L., Brémont, F., Maubisson, L., Mittaine, M.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 60 KB

english, 2014

275

86 Comparative study for the evaluation of a new technology for cystic fibrosis screening

Rongioletti, M.C.A., Papa, F., Vaccarella, C., Majolini, M.B., Centrone, C., Minuti, B., Luciano, A., Mazzucchi, V., Belli, M., Giotti, I., Giuliani, C., Torricelli, F., Liumbruno, G.M.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 60 KB

english, 2014

276

87 Metagenomic approach to bacterial identification in induced sputum from cystic fibrosis subjects

del Campo, R., de Valbuena, M. Ruiz, Máiz, L., Rosa, G., Barrio, M.I., Caballero, J.D.D., Cantón, R., Suárez, L., Lamas, A.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 60 KB

english, 2014

277

88 Use of MALDI-TOF-MS for identification of anaerobic bacteria in CF patients

Ravenni, N., Cocchi, P., Dolce, D., Mergni, G., Taccetti, G., Braggion, C., Campana, S.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 60 KB

english, 2014

278

89 Hypermutation in Burkholderia cepacia complex is highly prevalent in chronic respiratory infections of cystic fibrosis patients

Bosch, A., Martina, P., Feliziani, S., Juan, C., Bettiol, M., Gatti, B., Valeiras, B., Yantorno, O., Smania, A., Oliver, A.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 66 KB

english, 2014

279

90 Burkholderia contaminans in cystic fibrosis: genetic and phenotypic diversity among isolates from long-term infections

Bosch, A., Martina, P., Prieto, C., Valeiras, B., Bettiol, M., Montanaro, P., Yantorno, O.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 66 KB

english, 2014

280

91 Epidemiological study of CF patients with chronic Pseudomonas aeruginosa colonization in a reference center in Brazil

Caçador, N.C., Capizzani, C.P.C., Torres, L.A.G.M.M., Fernandes, M.I.M., Martinez, R., Tonani, L., Pereira, L.A., Darini, A.L.C.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 66 KB

english, 2014

281

93 Infection control in cystic fibrosis: assessment of Pseudomonas aeruginosa genotypes isolated from Italian children patients

Morelli, P., Bandettini, R., Casciaro, R., de Alessandri, A., Minicucci, L.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 64 KB

english, 2014

282

94 The effect of Pseudomonas aeruginosa infection on pulmonary function outcome in a cohort of patients with nonsense mutation cystic fibrosis

Kerem, E., Wilschanski, M., Sermet-Gaudelus, I., De Boeck, K., Accurso, F.J., Konstan, M.W., Rowe, S.M., Elfring, G.L., Spiegel, R., Peltz, S., Barth, J., Ajayi, T.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 65 KB

english, 2014

283

95 Susceptibility testing of isolates of Pseudomonas aeruginosa in patients with cystic fibrosis – Service evaluation

Baker, I., Addy, C., Bateman, K., Williams, O.M., Bell, N.J.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 64 KB

english, 2014

284

96 Staphylococcus aureus in Czech cystic fibrosis patients – prospective study

Tkadlec, J., Melter, O., Bukáčková, E., Fila, L., Pantůček, R., Indráková, A., Botka, T., Růičková, V.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 64 KB

english, 2014

285

97 Prevalence and spa genotype characterization of Staphylococcus aureus isolated from patients attending Gothenburg CF centre

Johansson, E.A., Oshalim, M., Lindblad, A., Ericson, P., Welinder-Olsson, C.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 66 KB

english, 2014

286

98 NTM: lessons from the UK CF registry

MacNeill, S.J., Vamvakas, G., Rosenthal, M.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 66 KB

english, 2014

287

99 Low prevalence of non-tuberculous mycobacteria (NTM) in a referral CF center in Brazil: methodological limitation or reality?

Aiello, T.B., Mauch, R.M., Salles, P.D., Bensi, E.P., Paschoal, I.A., Pereira, M.C., Toro, A.D., Ribeiro, A.F., Ribeiro, J.D., Levy, C.E.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 66 KB

english, 2014

288

100 Common clone of Mycobacterium abscessus identified among adults and children in a large UK CF Centre

Denton, M., Lee, T., Etherington, C., Peckham, D.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 66 KB

english, 2014

289

101 Non-tuberculous mycobacterial infection in a large paediatric cystic fibrosis centre: epidemiology and possible transmission event

Nair, L.R., Thomas, M.F., Brodlie, M., Robb, A., Perry, A., O'Brien, C.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 67 KB

english, 2014

290

102 Fungal colonization in the airways of Spanish cystic fibrosis patients: results from a multicenter study

Caballero, J.D.D., Cobo, M., Chinchón, G., del Campo, R., Cantón, R., de la Pedrosa, E. Gomez

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 67 KB

english, 2014

291

103 ‘A mushrooming problem or not’ – prevalence of fungal isolation at the All Wales Adult CF Centre (AWACFC)

Speight, L., Lau, D., Barnes, R., Ketchell, R.I., Duckers, J.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 67 KB

english, 2014

292

104 High prevalence of Aspergillus spp. in a reference CF center in Brazil: an agent that should not be neglected?

Aiello, T.B., Mauch, R.M., Salles, P.D., Paschoal, I.A., Pereira, M.C., Toro, A.D., Ribeiro, A.F., Ribeiro, J.D., Schreiber, A.Z., Levy, C.E.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 67 KB

english, 2014

293

105 Evaluation of fungal diagnostic stains and prolonged sputum culture in cystic fibrosis fungal disease

Felton, I.C., Benson, S., Alshafi, K., Nicholson, A.G., Simmonds, N.J., Bilton, D.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 61 KB

english, 2014

294

106 Epidemiological study of Achromobacter xylosoxidans in a reference center for CF treatment in Brazil

Capizzani, C.P.C., Caçador, N.C., Torres, L.A.G.M.M., Fernandes, M.I.M., Martinez, R., Tonani, L., Pereira, L.A., Darini, A.L.C.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 61 KB

english, 2014

295

107 Time trends in clinical indicators for cystic fibrosis (CF) patients at transition to adult care

Sandhu, H.K., Geake, J., Bell, S.C.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 61 KB

english, 2014

296

108 Reduced effect of intravenous antibiotic treatment on sinonasal compared to pulmonary inflammatory markers

Mainz, J.G., Hentschel, J., Fischer, N., Markert, U.R., Böer, K., Pfister, W., Doht, F.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 61 KB

english, 2014

297

109 Increased IL-8 production in human CFTR-deficient macrophages

Pompili, B., Cifani, N., Cimino, G., Ascenzioni, F., Del Porto, P.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 61 KB

english, 2014

298

110 Connectivity mapping: an advanced bioinformatics approach to predict A20-inducing small molecules to reduce inflammation

Barsden, R., Elborn, J.S., Schock, B.C., Ennis, M., Kelly, C., Zhang, S.-D.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 61 KB

english, 2014

299

111 Defective A20 signalling in cystic fibrosis: anti-inflammatory action of gibberellin

Reihill, J., Malcomson, B., Barsden, R., Elborn, J.S., Kelly, C., Ennis, M., Schock, B.C.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 61 KB

english, 2014

300

112 Anti-inflammatory action of gibberellin in cystic fibrosis epithelial cells is associated with reduction of kinase expression

Todd, A., Barsden, R., Kelly, C., Ennis, M., Schock, B.C.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 69 KB

english, 2014

301

113 Increased susceptibility to enterovirus infections in a model for cystic fibrosis is associated with an impaired innate and adaptive antiviral immune response

Svedin, E., Hühn, M.H., Utorova, R., Larsson, P., Lind, K., Pincikova, T., Scholte, B.J., Hjelte, L., Flodström-Tullberg, M.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 69 KB

english, 2014

302

114 Prevotella modulate the Pseudomonas aeruginosa mediated host response in cystic fibrosis bronchial epithelial cells

Bertelsen, A., Schneiders, T., Elborn, J.S.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 69 KB

english, 2014

303

115 Comparison of serum resistance in Prevotella isolates cultured from CF patients when stable and during pulmonary exacerbation

Mooney, D., Tunney, M., Graham, K., McGrath, S.J., McIlreavey, L., Johnson, E., Matier, T., Elborn, J.S.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 69 KB

english, 2014

304

116 Prevotella histicola drives transcription of an elevated host response compared to P. nigrescens in cystic fibrosis bronchial epithelial cells

Bertelsen, A., Schneiders, T., Elborn, J.S.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 66 KB

english, 2014

305

118 BPI-ANCA and Pseudomonas serology in Swedish CF patients – a comparison

Lindberg, U., Carlsson, M., Hellmark, T., Segelmark, M.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 66 KB

english, 2014

306

119 Diagnostic value of serum antibodies to Pseudomonas aeruginosa in patients with CF in a Brazilian referral center

Mauch, R.M., Rossi, C.L., da Silva, M.T.N., Ribeiro, A.F., Ribeiro, J.D., Levy, C.E.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 66 KB

english, 2014

307

120 Anti-Pseudomonas aeruginosa IgY antibodies promote bacterial clearance in a murine pneumonia model

Thomsen, K., Christophersen, L., Moser, C., Jensen, P.Ø., Bjarnsholt, T., Høiby, N.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 68 KB

english, 2014

308

121 Anti-Pseudomonas aeruginosa antibodies and microbiological outcome in not chronically infected patients

Dolce, D., Ravenni, N., Mergni, G., Braggion, C., Campana, S., Taccetti, G.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 68 KB

english, 2014

309

122 Modulation of cystic fibrosis gut inflammation – a pivotal role of the lung gut axis?

O'Callaghan, G., Ronan, N., Houston, A., Shanahan, F., Plant, B.J.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 68 KB

english, 2014

310

123 How frequent is Clostridium in our CF patients?

Pop, L., Ciuca, I., Popa, Z., Tamas, L., Guta, B. Almajan, Horhat, F., Popa, I.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 68 KB

english, 2014

311

124 The prevalence and financial impact of beta-lactam allergy in CF

Rowan, C., Denman, S., Etherington, C., Peckham, D., Whitaker, P.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 50 KB

english, 2014

312

125 Feasibility of carrying out spirometry in 3 and 4 year old children in a standard clinic setting

Cole, P., Hampton, F., Beeforth, D.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 60 KB

english, 2014

313

126 What factors determine lung function decline in Polish CF children?

Olszowiec-Chlebna, M., Koniarek-Maniecka, A., Ruszczyk-Bilecka, T., Stelmach, I.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 60 KB

english, 2014

314

127 Improving the multiple breath washout test: closed circuit washin with a novel bolus gas delivery system substantially reduces washin time and does not alter washout

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 60 KB

english, 2014

315

128 Multiple breath nitrogen washout in adults with cystic fibrosis: a comparison of two commercially available devices

Poncin, W., Aubriot, A.-S., Lebecque, P.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 60 KB

english, 2014

316

129 Shortened SF6 MBW is a repeatable and sensitive test in adults and children with CF

Hannon, D., Bradbury, I., Bradley, J.M., Reid, A., Bell, N.J., Elborn, J.S., O'Neill, K.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 62 KB

english, 2014

317

130 Enhanced photoacoustic gas analyser (Innocor) for multiple breath washout. Improvements to analyser response time maintains accuracy at fast ventilation rates, and produces a system that meets all washout technology performance targets

Horsley, A., Macleod, K., Gupta, R., Goddard, N., Bell, N.J.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 62 KB

english, 2014

318

131 Multiple breath nitrogen washout in healthy children and adults: a comparison of two commercially available devices

Poncin, W., Aubriot, A.-S., Lebecque, P.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 62 KB

english, 2014

319

132 Improving the feasibility of multiple-breath nitrogen washout in cystic fibrosis adults

Poncin, W., Aubriot, A.-S., Lebecque, P.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 61 KB

english, 2014

320

133 Slow and fast lung compartments in cystic fibrosis measured by nitrogen multiple-breath washout (N2 MBW)

Houltz, B., Gilljam, M., Lindblad, A., Robinson, P.D., Gustafsson, P.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 61 KB

english, 2014

321

134 Nutritional status, lung function and LCI among children with CF

Hatziagorou, E., Katseni, V., Kampouras, A., Avramidou, V., Lamboudis, D., Karagiozoglou-Lampoudi, T., Tsanakas, J.N.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 61 KB

english, 2014

322

135 MEF25 as parameter to evaluate effects of mannitol inhalation

Leichsenring, M., Meissner, P.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 61 KB

english, 2014

323

136 Nocturnal oximetry in children with cystic fibrosis (CF)

Stockley, E.L., Patel, N., Rosenthal, M., Tan, H.-L.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 61 KB

english, 2014

324

137 Sleep disturbances in CF children: looking for severity predictors

Silva, A.M., Salgueiro, M., Descalço, A., Pereira, L., Barreto, C., Ferreira, R.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 58 KB

english, 2014

325

138 Depiction of anatomic structures of relevance for scoring of cystic fibrosis changes by chest tomosynthesis and computed tomography

Asgeirsdottir, H., Johnsson, Å., Gilljam, M., Vikgren, J., Båth, M., Norrlund, R.R.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 58 KB

english, 2014

326

139 Respiratory motion suppression for three-dimensional, high isotropic spatial resolution, magnetic resonance imaging of the lung without contrast agent injection

Delacoste, J., Bonanno, G., Piccini, D., Chevre, P., Qanadli, S.D., Beigelman, C., Stuber, M., Sauty, A.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 58 KB

english, 2014

327

140 Is bronchoalveolar lavage necessary for monitoring and treating respiratory infections in children with cystic fibrosis?

Alden, B., Kavanagh, C., Larner, E.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 58 KB

english, 2014

328

141 Platelet aggregation capability in children with cystic fibrosis

Simonova, O., Gordeeva, O., Gorinova, Y., Botvinyeva, V.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 65 KB

english, 2014

329

142 Immunisation coverage in children with cystic fibrosis: a French multicenter survey

Masson, A., Launay, O., Delaisi, B., Remus, N., Lebourgeois, M., Chedevergne, F., Corvol, H., Bonnel, A.-S., Bassinet, L., Bailly, C., de Blic, J., Sermet-Gaudelus, I.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 65 KB

english, 2014

330

143 Seasonality of Pseudomonas aeruginosa isolation in patients with cystic fibrosis

Vilella, M., Larramona, H., Bosque, M., Costa, J., Espasa, M., Valdesoiro, L., Asensio, O., Domingo, X., Guijarro, E.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 65 KB

english, 2014

331

144 The impact of Pseudomonas aeruginosa colonization in CF

Nascimento, R., Lopes, C., Freitas, F., Azevedo, P., Bárbara, C.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 65 KB

english, 2014

332

145 The efficacy of the inhalatory treatment with tobramycin in controlling Pseudomonas aeruginosa lung infection in patients with cystic fibrosis

Sciuca, S., Eremciuc, R.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 66 KB

english, 2014

333

146 Pseudomonas serology can guide aggressive Pseudomonas eradication programmes

Pao, C.S., Fisher, D.L., Carr, S.B.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 66 KB

english, 2014

334

147 Causes of failure to eradicate Pseudomonas aeruginosa in patients with CF

Cohen-Cymberknoh, M., Gilead, N., Shoseyov, D., Breuer, O., Blau, H., Muzzafi, H., Gur, M., Rivlin, J., Picard, E., Armoni, S., Aviram, M., Bentur, L., Kerem, E.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 67 KB

english, 2014

335

148 Use of whole-genome sequencing to identify transmission of Pseudomonas aeruginosa between cystic fibrosis patients

Loman, N., Manzoor, S., Quick, J., Fothergill, J.L., Gossain, S., Kenna, D., Turton, J., Walshaw, M., Whitehouse, J.L., Pallen, M., Winstanley, C., Hawkey, P., Nash, E.F.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 67 KB

english, 2014

336

150 The impact of viral symptoms on rhinovirus positive pulmonary exacerbations in patients with CF

Mcweeney, L., Shah, A., Etherington, C., Whitaker, P., Peckham, D.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 63 KB

english, 2014

337

151 Rare and resistant germs in the examination of sputum and throat swab in patients with cystic fibrosis. Results of the German working group “Rare germs” of the benchmarking project

Schwarz, C., Melichar, V., Stern, M., Niemann, N.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 63 KB

english, 2014

338

153 Fungal colonisation of the airway in children with cystic fibrosis

Wilkinson, S., Wardlaw, A.W., Fairs, A., Pashley, C.H., Gaillard, E.A.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 69 KB

english, 2014

339

154 Scedosporium apiospermum isolation in cystic fibrosis patients

Noni, M., Katelari, A., Dimopoulos, G., Alexandrou, H., Kaditis, A., Doudounakis, S.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 69 KB

english, 2014

340

155 Aspergillus pulmonary infections in children with cystic fibrosis (CF): prevalences in three Scandinavian CF centres

Skov, M., Hollsing, A., Lindblad, A.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 69 KB

english, 2014

341

156 ABPA syndrome (ABPAs) in CF: FEV1 decline, infectious exacerbations and BMI before and after the year of diagnosis (index year), a case control study

De Baets, F., Wanyama, S., De Keyzer, L., Haerynck, F., Schelstraete, P., Thomas, M., Van Daele, S.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 69 KB

english, 2014

342

157 Long-term impact of fungi on pediatric cystic fibrosis lung disease

Hector, A., Berenbrinker, S., Kirn, T., Graepler-Mainka, U., Riethmueller, J., Kappler, M., Griese, M., Hartl, D.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 65 KB

english, 2014

343

158 Prevalence of Pneumocystis jirovecii in a cross section of patients attending a large UK adult cystic fibrosis centre

Green, H., Bright-Thomas, R., Barry, P., Horsley, A., Mutton, K., Jones, A.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 65 KB

english, 2014

344

159 Genotyping of Achromobacter xylosoxidans in a cystic fibrosis (CF) centre

Van Daele, S., Schelstraete, P., De Baets, F., Vanderkerken, M., Raman, A., Carton, A., Mahieu, L., Pyl, F., Van Simaey, L., Vaneechoutte, M.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 65 KB

english, 2014

345

160 Molecular profiling demonstrates clustering of Mycobacterium abscessus isolates in CF patients from a single centre

Green, H., Bright-Thomas, R., Barry, P., Horsley, A., Isalska, B., Woodford, N., Kenna, D., Jones, A.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 65 KB

english, 2014

346

161 The first results of antimicrobial susceptibility of isolates from adult patients with cystic fibrosis from the Province of Vojvodina, Serbia

Skrbic, D., Trudic, A., Povazan, D., Kurucin, T., Djuric, M.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 58 KB

english, 2014

347

162 Bronchial artery embolization (BAE) in adults with cystic fibrosis: a single-centre case series

Marquette, M., Shaida, N., Cousins, C., Winterbottom, A., Johnson, C., Shafi, N., Haworth, C., Barker, H.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 58 KB

english, 2014

348

163 TIVAD infection and TIVAD related cardiac problems in transplanted CF patients

Colpaert, K., Ruelens, C., Vos, R., Yserbyt, J., Verleden, G., Dupont, L.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 58 KB

english, 2014

349

164 Incidence, management and outcomes following spontaneous pneumothorax in adult patients with CF attending a Regional Centre

Etherington, C., Coleman, H., Whitaker, P., Clifton, I., Peckham, D.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 58 KB

english, 2014

350

165 Management of pneumothoraces in cystic fibrosis (CF): a novel approach using an ambulatory suction device (Thopaz™ system, Medela Ltd)

Addy, C., Bateman, K., Bell, N.J.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 58 KB

english, 2014

351

166 The prevalence and aetiology of pleural effusions and empyema in patients attending a regional adult CF centre

Sawant, A.P., Etherington, C., Whitaker, P., Denton, M., Fitch, G., Peckham, D.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 58 KB

english, 2014

352

167 Epidemiology and risk factors for CF arthropathy

Röhmel, J., Kallinich, T., Staab, D., Schwarz, C.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 58 KB

english, 2014

353

168 Cystic fibrosis: an ageing condition

Phitidis, M.E., Murthy, M., Hunt, N., Jones, G.H., Fox, J., Ledson, M., Greenwood, J., Walshaw, M.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 58 KB

english, 2014

354

169 A new tool to improve inhalation

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 62 KB

english, 2014

355

170 The King's experience of Bronchitol®. One UK centre's results of Bronchitol® initiation

Scott, E., Reilly, C., Elston, C., Perrin, F., Lee, K.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 63 KB

english, 2014

356

171 The patients’ view of nebulised drugs: knowledge, adherence, and difficulties

Miles, K., Lenaghan, S., Blanch, L., Doe, S., Bourke, S., Caraher, M., Anderson, A.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 63 KB

english, 2014

357

172 Implementation of non-medical prescribing (NMP) within the clinical CF setting

Henry, A.C., Forster, E., Bell, N.J., Bateman, K.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 63 KB

english, 2014

358

173 Cystic fibrosis patients’ performance on Modified Shuttle Walk Test

Karapanagiotis, S., Gambazza, S., Brivio, A., Colombo, C.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 57 KB

english, 2014

359

174 Are changes in Modified Shuttle Walk Test performance related to changes in clinical status in CF children and adolescents?

Zanini, A., Cazzarolli, C., Tartali, C., Bellini, R., Longhini, B., Meschi, A., Assael, B.M.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 57 KB

english, 2014

360

175 Exercise intensity during interactive video game

Karapanagiotis, S., Gambazza, S., Brivio, A., Colombo, C.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 57 KB

english, 2014

361

176 Assessment of exercise capacity in patients with cystic fibrosis

Sovtic, A., Minic, P.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 57 KB

english, 2014

362

177 Physical activity, lung function and lung clearance index in children with cystic fibrosis

Sahlberg, M., Redfors, S., Lindblad, A.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 60 KB

english, 2014

363

178 Quantifying weight bearing activity in children and adolescents with cystic fibrosis

Karapanagiotis, S., Gambazza, S., Bisogno, A., Brivio, A., Colombo, C.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 60 KB

english, 2014

364

179 Assessing for ambulatory hypoxia in adult CF patients

Morris, A.R., Greenwood, J., Ledson, M., Walshaw, M.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 60 KB

english, 2014

365

180 Development of a musculoskeletal screening tool for adults with CF identifies common causes of pain and problems that potentially decrease physical activity: a tool for use in annual reviews

Button, B.M., Wilson, L.M., Gufler, A., Wilson, J.W.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 60 KB

english, 2014

366

181 Spinal deformities (SD) in young CF patients: two years experience of screening and follow up

Mamprin, G., Lucca, F., Gaiotto, S., Barbisan, M., Toffolo, M.G., Da Dalt, L., Ros, M.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 62 KB

english, 2014

367

183 Mycobacterium abscessus: stand alone hospital admission for agressive physiotherapy and nutritional review can extend periods between toxic IV antibiotic treatments

Tame, J., Turnbull, A., Forton, J.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 62 KB

english, 2014

368

184 Evaluation of the impact of SERPINA gene mutation on the occurrence of liver damage and cholestasis in patients diagnosed with cystic fibrosis

Więcek, S., Wos, H., Kordys-Darmolinska, B., Grzybowska-Chlebowczyk, U.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 59 KB

english, 2014

369

185 Transient elastography measurements in adults with cystic fibrosis liver disease

Jones, G.H., Richardson, P., Ledson, M., Walshaw, M., Greenwood, J.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 59 KB

english, 2014

370

186 Transient elastography can be used to guide monitoring of cystic fibrosis related liver disease in adult patients

Jones, G.H., Richardson, P., Ledson, M., Walshaw, M., Greenwood, J.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 59 KB

english, 2014

371

187 Evaluation of cystic fibrosis liver disease and the relation with risk factors in a Romanian centre

Ciuca, I., Pop, L., Popa, Z., Tamas, L., Guta, B. Almajan, Matusz, P.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 59 KB

english, 2014

372

188 Elongation of the small intestine (without histological changes) in young pigs with experimentally induced exocrine pancreatic insufficiency (EPI) – used as a model for children with EPI

Mößeler, A., Schwarzmaier, T., Gregory, P.C., Kamphues, J.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 61 KB

english, 2014

373

189 The variability of carbohydrate antigen 19-9 (CA 19-9) levels in cystic fibrosis patients

Leichsenring, M., Rueckel, B., Meissner, P., Kratzer, W.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 61 KB

english, 2014

374

190 Pancreatitis in patients with CF

Aguirre, A. Sojo, Ezquerra, N. Martinez, Bousoño García, C., Quiros, M.D. Acuña, Manzanares, J. Manzanares Lopez, Gonzalez, S. Heredia, Garcia, F. Baranda, Cordero, C. Vazquez

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 61 KB

english, 2014

375

191 Prospective multinational DIOS survey: concomitant risk factors and treatment alternatives

Munck, A., Colombo, C., Kashirskaya, N., Ellemuter, H., Fotoulaki, M., Houwen, R.H., Wilschanski, M.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 61 KB

english, 2014

376

192 Clinical practice in Oslo University Hospital on diagnosis and management of distal intestinal obstructive syndrome

Dypvik, J., Storrøsten, O.-T.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 57 KB

english, 2014

377

193 Concentration of calprotectin in the stool of children with cystic fibrosis

Więcek, S., Wos, H., Kordys-Darmolinska, B., Sankiewicz-Szkołka, M., Grzybowska-Chlebowczyk, U.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 57 KB

english, 2014

378

194 A French survey on gastro-oesophageal reflux in CF: need for guidance

Languepin, J., Munck, A., Gros, G., Mas, E.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 57 KB

english, 2014

379

195 Use of CGMS (Continuous Glucose Monitoring System) in CF children with impaired or indeterminant glucose tolerance

Kavaliunaite, E., Drew, S., Peters, C., Margetts, R., Suri, R.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 57 KB

english, 2014

380

196 Prevalence of undiagnosed pre-diabetes and diabetes in a UK cohort of young people with cystic fibrosis

Selby, L., Rootsey, T., Williams, R.M., Ong, K.K., McShane, D.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 64 KB

english, 2014

381

197 Comparison of FRAX/NOGG with UK Cystic Fibrosis Trust guidance for low bone mineral density in cystic fibrosis

Greenhalgh, K., Addy, C., Bell, N.J., Bateman, K.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 64 KB

english, 2014

382

198 The prevalence of ΔF508 in cystic fibrosis patients with low bone mineral density in Republic of Macedonia

Jakovska-Maretti, T., Fustik, S.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 64 KB

english, 2014

383

200 Prevalence of dyslipidaemia in an Irish adult cystic fibrosis cohort

Blair, M., Harrison, M.J., Shortt, C., Fleming, C., Mccarthy, M., Murphy, D.M., Plant, B.J.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 63 KB

english, 2014

384

201 Vitamin A deficiency: prevalence and clinical implications for adult cystic fibrosis

Power, B.D., Harrison, M.J., Shortt, C., Fleming, C., Mccarthy, M., Murphy, D.M., Plant, B.J.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 63 KB

english, 2014

385

202 Vitamin A intake and serum retinol levels in children and adolescents with cystic fibrosis

Woestenenk, J.W., Broos, N., Stellato, R.K., Arets, H.G.M., van der Ent, C.K., Houwen, R.H.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 63 KB

english, 2014

386

203 Vitamin D3 deficiency as a predisposing factor for nasal polyposis in patients with cystic fibrosis

Fotoulaki, M., Iakovou, I., Karanika, P., Sotiriadou, F., Tenzidou, K., Konstantinidis, I.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 63 KB

english, 2014

387

204 Decreasing fat-soluble vitamin deficiencies by increased awareness and change of vitamin preparation

Olesen, A.M., Olesen, H.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 64 KB

english, 2014

388

205 Folate deficiency in adult patients at a regional cystic fibrosis (CF) centre

Cassidy, L., Morton, A., Etherington, C., Peckham, D.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 64 KB

english, 2014

389

206 Serum zinc concentration in cystic fibrosis patients with CFTR I1234V mutation associated with pancreatic sufficiency

Wahab, A. Abdul, Abu-Shahin, A., Allangawi, M., Rahman, M.O.A., Chandra, P.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 64 KB

english, 2014

390

207 Cow's milk allergy in cystic fibrosis children

Pop, L., Ciuca, I., Popa, Z., Guta, B. Almajan, Popescu, I.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 64 KB

english, 2014

391

208 Nutritional intervention among children with CF

Katseni, V., Hatziagorou, E., Lamboudis, D., Kampouras, A., Karagiozoglou-Lampoudi, T., Tsanakas, J.N.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 60 KB

english, 2014

392

209 Changes in nutritional status associated with chest exacerbations in children with cystic fibrosis

Smith, C., English, J., Chetty, K., Seddon, P.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 60 KB

english, 2014

393

210 Changes in the nutritional status and dietary intake of adults with cystic fibrosis since 1997

King, S.J., Sekuloska, Z., Gallo, R., Swan, I., Al-Helou, Z., Wilson, J.W., Tierney, A.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 60 KB

english, 2014

394

211 Overweight and obesity in the cystic fibrosis Israeli national center

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 60 KB

english, 2014

395

213 Dietary management of pregnant women with cystic fibrosis

Grunewald, D., Lahoreau, D., Burgel, P.-R., Chapron, J., Honoré, I., Kanaan, R., Dusser, D., Hubert, D.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 61 KB

english, 2014

396

214 Cystic fibrosis and pregnancy, a single centre case–control study

Girault, A., Blanc, J., Goffinet, F., Hubert, D.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 60 KB

english, 2014

397

215 Hand grip strength is associated with disease severity in adults with CF

Mead, L., Watson, H., Cousins, C., Haworth, C., White, H., Floto, R.A.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 60 KB

english, 2014

398

216 Hand strength, is it time to get a grip?

Proud, D., Rezaie, M., Lau, D., Ketchell, R.I., Duckers, J.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 58 KB

english, 2014

399

217 A novel use of BrEaD (breathlessness, eating and drinking)

Rezaie, M., Proud, D., Lau, D., Ketchell, R.I., O'Leary, C., Duckers, J.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 58 KB

english, 2014

400

218 Analysis of an online cystic fibrosis forum; common nutritional concerns and quality of nutritional information shared

Pearson, L., White, H.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 58 KB

english, 2014

401

219 A review of hospital and hospital in the home (HiTH) services at a paediatric cystic fibrosis (CF) centre

Moran, F.C., Barr, C., Kerr, M., Tannenbaum, E.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 61 KB

english, 2014

402

220 Safety, tolerability and patient preference of intravenous colistimethate sodium delivered by bolus compared to infusion in adults with cystic fibrosis

Evans, C., Gilday, N., Davies, R., Ahitan, B., Rashid, R., Whitehouse, J.L., Nash, E.F.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 61 KB

english, 2014

403

221 Outpatient parenteral antimicrobial therapy (OPAT) in patients with cystic fibrosis

Pedersen, M.G., Jensen-Fangel, S., Olesen, H., Petersen, J.E.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 61 KB

english, 2014

404

222 Successful administration of continuous intravenous β-lactam therapy for allergic CF patients failing standard antibiotic desensitization

Breuer, O., Cohen-Cymberknoh, M., Armoni, S., Kerem, E., Shoseyov, D.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 61 KB

english, 2014

405

223 Analysis of “cost drivers” for health care services use in cystic fibrosis patients: the experience of the Milan Cystic Fibrosis Center

Colombo, C., Daccò, V., Loi, S., Anelli, M., Alicandro, G.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 60 KB

english, 2014

406

225 French CF Quality Improvement Program (QIP): the experience of Rennes adult CF Centre

Berhault, I., Bachelot, S., Batard, E., Hiard, L., Jousseaume, M.T., Brinchault, G., Desrues, B., Belleguic, C.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 60 KB

english, 2014

407

226 A work load study to determine the proportion of time spent on delivering rescue vs. prevention clinical care in adults with cystic fibrosis

Lowther, M., Curley, R., Harrison, S., Jennings, A., Wildman, M.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 60 KB

english, 2014

408

227 Detecting early markers of CF-related pulmonary exacerbations using home telemetry and sputum biomarkers

Ukor, E.F., Ryan, J., Brown, K., Haworth, C.S., Auton, K., Floto, R.A.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 59 KB

english, 2014

409

228 Telemedicine videoconferencing – breaking down the barriers for cystic fibrosis (CF) patients living in rural and remote areas

Mitchell, L., Schultz, K., Clark, D., Wilson, J.W.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 59 KB

english, 2014

410

229 Review of personal hand held record for cystic fibrosis children

Narayan, O., Davies, S., Bakewell, K., Lenney, W., Gilchrist, F.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 58 KB

english, 2014

411

230 The development of a new quick/easy CF wellness score (Alfred Wellness Score for CF, “AweScore-CF”) to improve delivery of clinical care in the outpatient and inpatient settings suggests patients acclimatise to low lung function

Button, B.M., Gufler, A., Clark, D., Mitchell, L., Wilson, J.W.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 59 KB

english, 2014

412

231 A study of treatment activities and perceived treatment burden in adults with cystic fibrosis

Mahmood, M., Green, C., Male, C., Priestley, L., Chapman, S.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 60 KB

english, 2014

413

232 The paediatric cystic fibrosis service at the Leeds Children's Hospital – a patient and parent perspective

Hunjan, H.S., Lee, T., Guy, E.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 60 KB

english, 2014

414

233 Three-year experience of a new clinic dedicated to the care of screened infants with equivocal CF related diagnosis

Fall, A.J., Urquhart, D.S.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 59 KB

english, 2014

415

234 Cystic fibrosis: new trends in ophthalmological evaluation

Nebbioso, M., Plateroti, A.M., Leggieri, E., Rossi, P., Savi, D., Vingolo, E.M., Quattrucci, S.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 60 KB

english, 2014

416

235 The CF couch potato! Habitual physical activity in an adult CF population

Howard, S., Mills-Bennett, R., Lau, D., Ketchell, R.I., Duckers, J.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 60 KB

english, 2014

417

236 The once-daily tacrolimus extended-release formulation provides similar drug exposure in non-CF and CF lung transplant recipients when compared to the conventional twice-daily formulation

Etienne, I., Woillard, J.-B., Marquet, P., Estenne, M., Knoop, C., Monchaud, C.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 60 KB

english, 2014

418

237 Thrush – a lesser spotted resident in the CF service?

Lee, J., Speight, L., Lau, D., Ketchell, R.I., Duckers, J.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 60 KB

english, 2014

419

238 Medication reconciliation in Wales – a problem shared

Richards, B., Lea-Davies, M., Speight, L., Lau, D., Ketchell, R.I., Duckers, J.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 60 KB

english, 2014

420

239 Using collaborative design and 3D printing to co-produce devices for CF care

Dexter, M., Heller, B., Hoo, Z.H., Milne, A., Wildman, M.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 53 KB

english, 2014

421

240 “Like” our Facebook page? – The use of social media to improve communication

Reid, N., Cox, K.J., Horsley, A., Paxton, J.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 53 KB

english, 2014

422

241 Totally implantable venous access devices (TIVAD), a survey at the Gothenburg CF-centre

Haugen, G., Strandner, K., Hufnagl, M., Lindblad, A., Gilljam, M.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 57 KB

english, 2014

423

242 In-house provision of a PICC/Midline service by the CF nursing team

Williams, D., Robinson, J., Bateman, K., Bell, N.J.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 57 KB

english, 2014

424

243 Home visits of CF coordinating nurses – experience of Necker hospital

Clairicia, M., Lustre, A., Bailly, C., Chedevergne, F., de Blic, J., Bourgeois, M. Le, Sermet-Gaudelus, I.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 57 KB

english, 2014

425

244 Awareness of infection control within cystic fibrosis health care – a Scandinavian study

Hunstad, E.J., Bakkeheim, E., Gilljam, M.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 57 KB

english, 2014

426

245 Side effects of oral antibiotics in small children with cystic fibrosis

Jakobsen, K.R., Bregnballe, V.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 55 KB

english, 2014

427

246 What do parents know? The results of a questionnaire asking about the process of a CF admission

Marote, A., Pitfield, C., Bryan, M., Sheehan, D., Choudary, F., Prasad, A.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 56 KB

english, 2014

428

247 How often do we communicate with parents in the first year following diagnosis?

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 55 KB

english, 2014

429

248 Taking sputum samples from small children wiht cystic fibrosis: a matter of cooperation

Pehn, M., Bregnballe, V.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 55 KB

english, 2014

430

249 Living with cystic fibrosis – a lonely, lifelong work

Homme, J., Bakkeheim, E., Hunstad, E.J., Sæteren, B.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 49 KB

english, 2014

431

250 The role of understanding in living with cystic fibrosis

Counihan, S.U.E., Coughlan, B.J., Connellan, S., Linnane, B.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 60 KB

english, 2014

432

251 Living with cystic fibrosis today: beyond the “Burden of Care”

Counihan, S.U.E., Coughlan, B.J., Connellan, S., Linnane, B.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 60 KB

english, 2014

433

252 A comparative international study of health related quality of life in Eastern Europe

Borawska-Kowalczyk, U., Bodnar, R., Meszaros, A., Ołtarzewski, M., Dorota, S.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 60 KB

english, 2014

434

253 Looking beyond the here and now – an association of lung function, unemployment and deprivation scores in an adult CF population in Wales

Edwards, V., Speight, L., Lau, D., Ketchell, R.I., Duckers, J.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 60 KB

english, 2014

435

254 Evaluating the psychological impact of newly implemented infection control measures for the nontuberculous mycobacterium Mycobacterium abscessus

Shearing, V., Offord, E., Haworth, C., Floto, A.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 64 KB

english, 2014

436

255 Cystic fibrosis patients acting as carers for their older relatives – the ‘cared for’ becoming the carer

Nash, E.F., Cammidge, S., Dallow, Z., Rashid, R., Whitehouse, J.L., Regan, A.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 64 KB

english, 2014

437

256 Mothers with CF: psychosocial data about an almost unknown group

Ullrich, G., Bobis, I., Bewig, B.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 64 KB

english, 2014

438

257 Development of parenthood website and pathway to support people with CF considering pregnancy and parenthood

Bateman, K., Phillips, S., Bell, N.J.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 64 KB

english, 2014

439

258 A qualitative study exploring the needs of mothers and fathers with CF

Barker, H., O'Leary, C., Moses, J.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 57 KB

english, 2014

440

259 Parenting stress in mothers with cystic fibrosis

Ullrich, G., Bobis, I., Bewig, B.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 57 KB

english, 2014

441

260 A prospective cohort study examining the prevalence of emotional and behavioural difficulties in children of patients with cystic fibrosis (CF)

Regan, A., Lynch, S., Mason, E., Davies, R., Evans, C., Whitehouse, J.L., Rashid, R., Nash, E.F.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 57 KB

english, 2014

442

261 Planning for pre-implantation diagnosis: a qualitative study

Järvholm, S., Broberg, M., Thurin-Kjellberg, A.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 57 KB

english, 2014

443

262 Fear of Progression Questionnaire for caregivers of youth with cystic fibrosis (FoP-Q/C)

Fidika, A., Mai, S., Herle, M., Goldbeck, L.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 59 KB

english, 2014

444

263 Parents’ understanding of genetic mutation and the implications for their child's CF

Parmar, S., Latchford, G., Duff, A., Lee, T.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 59 KB

english, 2014

445

264 Grandparental knowledge of cystic fibrosis treatment

Vertommen, A., Havermans, T., Vreys, M., Claes, I., Ruelens, C., Proesmans, M.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 59 KB

english, 2014

446

265 Exploring the pre-hospitalisation needs of parents of children with cystic fibrosis

Hughes, V.C., Phillips, S.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 59 KB

english, 2014

447

266 ‘Arresting’ psychological issues for better health outcomes in parents of infants and young children with cystic fibrosis

Branch-Smith, C.A., Pooley, J.A., Shields, L., Stick, S., Douglas, T.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 57 KB

english, 2014

448

267 Bringing bad news: the diagnosis of cystic fibrosis in childhood

Tack, J., Vertommen, A., Proesmans, M., Havermans, T.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 57 KB

english, 2014

449

268 The experiences of young people and their parents in the move from paediatric to adult cystic fibrosis services in Bristol: recommendations for an improved transition pathway

Wood, H.M., Phillips, S.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 57 KB

english, 2014

450

269 When I am grown up – evaluating the effectiveness of a transition program for adolescents with CF transferring to the adult hospital system

Morgan, A.L., Culnane, E., Glazner, J., Reardon, N.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 57 KB

english, 2014

451

270 Evaluation of parents’ compliance in the treatment of cystic fibrosis children

Rohovyk, N., Bober, L., Makukh, H., Rohovyk, M.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 60 KB

english, 2014

452

271 Adherence to medications in cystic fibrosis patients: a five-year retrospective analysis

Nasr, S.Z., Shakkottai, A., Kidwell, K.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 60 KB

english, 2014

453

272 The impact of disease severity and clinical variation on self-reported adherence

Shaw, N., White, H., Denman, S., Peckham, D.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 60 KB

english, 2014

454

273 Relationship between self-reported adherence, medication collections and clinical variation in cystic fibrosis

White, H., Denman, S., Shaw, N., Wynn, S., Pollard, K., Peckham, D.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 60 KB

english, 2014

455

274 Do poor adherers enter behaviour change interventions of inhaled therapy? Exploration of the “healthy complier” effect

Curley, R., Wildman, M.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 59 KB

english, 2014

456

275 Understanding barriers to weight gain, nebuliser use and exercise in CF

Milne, A., Rose, C., Thornton, S., Curley, R., Hoo, Z.H., Wildman, M.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 59 KB

english, 2014

457

276 Adherence scale in an adult cystic fibrosis center

Baran, E., Granero, N., Hendriksen, B., Butti, F., D'Ascenzo, V., Ibarra, S., Pistorio, V., Volta, L., García, G.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 59 KB

english, 2014

458

277 Can imprisonment be good for patients with CF?

Frost, F.J., Jones, G.H., Lloyd, E.A., Hunt, N., Greenwood, J., Ledson, M., Walshaw, M.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 59 KB

english, 2014

459

278 Developing patient resources for lung transplantation

Phillips, S., Addy, C., Bateman, K., Bell, N.J.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 61 KB

english, 2014

460

280 VEMSE-CF: psychosocial characteristics of patients participating in a prospective controlled care research study

Goldbeck, L., Fidika, A., Reimann, A., Hebestreit, H., Heuer, H.-E., Junge, S., Sens, B., Smaczny, C., von der Schulenburg, J.-M.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 61 KB

english, 2014

461

281 Patient-centered outcomes in CF research

Cirilli, N., Buzzetti, R., Costa, S., Magazzù, G.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 61 KB

english, 2014

462

282 Patient priorities for research in cystic fibrosis: the IPaCOR experience

Cirilli, N., Buzzetti, R., Costa, S., Magazzù, G.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 50 KB

english, 2014

463

283 Can CF patient registries identify pulmonary exacerbations?

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 63 KB

english, 2014

464

284 Prevalence of Staphylococcus aureus (SA) infection in patients with cystic fibrosis in a reference unit

Chilet, M., Hernández-Cabezas, A., Sancho-Tello, S., Molina, J.M., Pastor, A., Ansótegui, E., Salavert, M., López-Hontangas, J.L., Solé, A.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 63 KB

english, 2014

465

285 Some cystic fibrosis patients do not tolerate tobramycin dry powder inhalation

Boerner, G., Prante, S., Borella, F.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 63 KB

english, 2014

466

286 Adult patients with cystic fibrosis exhibit an increasing prevalence of chronic kidney disease with increasing age, particularly those with cystic fibrosis-associated diabetes mellitus and/or an organ transplant

Moore, D., English, S., Eustace, J.A., Shortt, C., Plant, B.J., Plant, W.D.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 63 KB

english, 2014

467

287 Prevalence and importance of urinary incontinence in females with cystic fibrosis

Strandberg, M., Sahlberg, M., Strandner, K., Ericson, P., Gilljam, M.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 61 KB

english, 2014

468

288 Airway clearance techniques used by people with cystic fibrosis in the UK

Hoo, Z.H., Daniels, T., Wildman, M., Teare, M.D., Bradley, J.M.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 61 KB

english, 2014

469

289 Ageing in cystic fibrosis: a comparison of adult patients attending a tertiary referral centre

O'Halloran, K., Harrison, M.J., Shortt, C., Fleming, C., Mccarthy, M., Murphy, D.M., Plant, B.J.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 62 KB

english, 2014

470

290 Clinical characteristics of adolescents with cystic fibrosis in the Moscow region (Russia)

Kondrateva, E., Kapranov, N., Krasovskiy, S., Kashirskaya, N., Amelina, E., Nikonova, V., Sherman, V., Cherniak, A.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 62 KB

english, 2014

471

292 Specific causes of mortality in CF patients in France 2007-2010

Burgel, P.-R., Hamard, C., Carlier, N., Kanaan, R., Abely, M., Hubert, D., Munck, A., Boussaud, V., Grenet, D., Lemonnier, L., Sponga, M., Martin, C.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 60 KB

english, 2014

472

293 Spectrum of mutations and survival data for adult CF patients from Sofia CF center

Galeva, I., Savov, A., Mileva, S., Yankova, M., Kabakchieva, R.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 60 KB

english, 2014

473

294 The experience of adult cystic fibrosis centre in Lithuania in 2009–2013

Malakauskas, K., Kalinauskaite, V., Sakalauskas, R.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 60 KB

english, 2014

474

295 CF patients diagnosed in adulthood: spectrum of referral source

Hunt, N., Jones, G.H., Phitidis, E., Murthy, M., Greenwood, J., Ledson, M., Walshaw, M.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 70 KB

english, 2014

475

296 Adult CF diagnosis – missed childhood opportunities or forme fruste disease?

Hunt, N., Phitidis, E., Murthy, M., Jones, G.H., Greenwood, J., Ledson, M., Walshaw, M.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 70 KB

english, 2014

476

297 Arab cystic fibrosis patients in Israel

Lavie, M., Lifshitz, I., Vilozni, D., Shapira, I., Sarouk, I., Bar, B.-E., Dagan, A., Livnat, G., Cohen-Cymberknoh, M., Mei-Zahav, M., Rivlin, J., Efrati, O.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 70 KB

english, 2014

477

298 Establishment of a Russian cystic fibrosis patient registry

Krasovskiy, S., Kashirskaya, N., Kapranov, N., Cherniak, A., Amelina, E., Kondrateva, E., Asherova, I., Boitsova, E., Brisin, V., Chikunov, V., Golubtsova, O., Ilenkova, N., Khachiyan, M., Kondakova,

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 70 KB

english, 2014

478

299 Chiari type I malformation in two adult patients with cystic fibrosis

Narasimhaiah, D., Etherington, C., Fitch, G., Whitaker, P., Peckham, D.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 63 KB

english, 2014

479

300 Pseudomonas aeruginosa colonization in a CF child's upper and lower airways: a father's meticulous approach to successful eradication

Gerber, A., Ebener, T., Lorenz, M., Hentschel, J., Pfister, W., Beck, J.F., Mainz, J.G.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 63 KB

english, 2014

480

301 Aspergillus nodi in cystic fibrosis (CF) patients: a rare entity. Report of two pediatric cases

Schelstraete, P., Van Daele, S., Haerynck, F., De Baets, F.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 63 KB

english, 2014

481

302 Comparison of airway clearance techniques (ACT) in the cystic fibrosis (CF) population: a single case study report

Forster, E., Swingwood, E., Nicholas, B., Bateman, K.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 63 KB

english, 2014

482

304 Incretin-based treatment of diabetes related to cystic fibrosis: a case study

Hellman, J., Fischier, J., Hollsing, A.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 64 KB

english, 2014

483

305 Use of fidaxomicin for Clostridium difficile-associated diarrhoea (CDAD) in cystic fibrosis

Bell, J., Lea-Davies, M., Ketchell, R.I., Lau, D., Duckers, J.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 64 KB

english, 2014

484

Author Index

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 76 KB

english, 2014

485

117 Significance of oxygen depletion in chronic lung infections in cystic fibrosis patients

Kolpen, M., Kühl, M., Kragh, K.N., Hansen, C.R., Pressler, T., Bjarnsholt, T., Moser, C., Høiby, N., Jensen, P.Ø.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 66 KB

english, 2014

486

199 Arterial stiffness in an ageing cystic fibrosis (CF) population attending the All Wales Adult Cystic Fibrosis Centre (AWACFC)

Choudhury, M., Gale, N., Cockcroft, J., Morgan, P., Duckers, J., Wong, S., Ketchell, R.I.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 64 KB

english, 2014

487

279 Proposal of a questionnaire for cystic fibrosis patients who have just been transplanted to ensure their safety before the first return home after transplantation

David, V., Marchand, C., Danner-Boucher, I., Berville, C.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 61 KB

english, 2014

488

291 Cystic fibrosis mortality trend in Italy between 1970 and 2011

Alicandro, G., Frova, L., Di Fraia, G., Colombo, C.

Journal:

Journal of Cystic Fibrosis

Year:

2014

Language:

english

File:

PDF, 60 KB

english, 2014

To build up a library is to create a life. It’s never just a random collection of books.

— Carlos María Domínguez

Official channel

Z-Library Desktop Launcher

Tor version

Z-Library

Z-Library Since 2009 support@z-lib.do

EnglishРусскийEspañolItalianoελληνικάاللغة العربيةBahasa IndonesiaBahasa Malaysiaहिन्दीDeutschFrançaisPortuguêsУкраїнськаPolski中文繁體中文日本語Tiếng ViệtAzərbaycan DiliՀայոց լեզուภาษาไทยTürk Diliქართველიবাংলাپښتوతెలుగుاردو한국어SrpskiБългарски