Volume 14

Journal of Cystic Fibrosis

Volume 14

1

What is hepcidin telling us about the natural history of cystic fibrosis?

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 100 KB

english, 2015

2

Outcome in patients with cystic fibrosis liver disease

Rowland, Marion, Gallagher, Cliona, Gallagher, Charles G., Laoide, Risteárd Ó., Canny, Gerard, Broderick, Anne Marie, Drummond, Jennifer, Greally, Peter, Slattery, Dubhfeasa, Daly, Leslie, McElvaney,

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 557 KB

english, 2015

3

Upper aero-digestive contamination by Pseudomonas aeruginosa and implications in Cystic Fibrosis

Rivas Caldas, R., Boisramé, S.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 393 KB

english, 2015

4

Function, pharmacological correction and maturation of new Indian CFTR gene mutations

Sharma, Himanshu, Jollivet Souchet, Mathilde, Callebaut, Isabelle, Prasad, Rajendra, Becq, Frédéric

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 1.53 MB

english, 2015

5

Open label study of inhaled aztreonam for Pseudomonas eradication in children with cystic fibrosis: The ALPINE study

Tiddens, H.A.W.M., De Boeck, K., Clancy, J.P., Fayon, M., H.G.M., Arets, Bresnik, M., Derchak, A., Lewis, S.A., Oermann, C.M.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 349 KB

english, 2015

6

Mannose-binding lectin gene as a modifier of the cystic fibrosis phenotype in Argentinean pediatric patients

Gravina, Luis Pablo, Crespo, Carolina, Giugno, Hilda, Sen, Luisa, Chertkoff, Lilien, Mangano, Andrea, Castaños, Claudio

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 444 KB

english, 2015

7

Molecular epidemiology of Aspergillus collected from cystic fibrosis patients

Sabino, Raquel, Ferreira, Jose A.G., Moss, Richard B., Valente, Joana, Veríssimo, Cristina, Carolino, Elisabete, Clemons, Karl V., Everson, Cassie, Banaei, Niaz, Penner, John, Stevens, David A.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 209 KB

english, 2015

8

Indicators of pulmonary exacerbation in cystic fibrosis: A Delphi survey of patients and health professionals

McCourt, Fiona, O'Neill, Brenda, Logan, Ian, Abbott, Janice, Plant, Barry, McCrum-Gardner, Evie, McKeown, Stephanie, Stuart Elborn, J., Bradley, Judy M.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 461 KB

english, 2015

9

Randomized controlled trial of biofilm antimicrobial susceptibility testing in cystic fibrosis patients

Yau, Yvonne C.W., Ratjen, Felix, Tullis, Elizabeth, Wilcox, Pearce, Freitag, Andreas, Chilvers, Mark, Grasemann, Hartmut, Zlosnik, James, Speert, David, Corey, Mary, Stanojevic, Sanja, Matukas, Lariss

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 332 KB

english, 2015

10

Retinal screening of patients with cystic fibrosis-related diabetes in Wales — A real eye opener

Roberts, R., Speight, L., Lee, J., George, L., Ketchell, R.I., Lau, D., Duckers, J.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 385 KB

english, 2015

11

Cost-effectiveness of newborn screening for cystic fibrosis determined with real-life data

van der Ploeg, C.P.B., van den Akker-van Marle, M.E., Vernooij-van Langen, A.M.M., Elvers, L.H., Gille, J.J.P., Verkerk, P.H., Dankert-Roelse, J.E.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 365 KB

english, 2015

12

Survival benefit of induction immunosuppression in cystic fibrosis lung transplant recipients

Kirkby, Stephen, Whitson, Bryan A., Wehr, Allison M., Lehman, Amy M., Higgins, Robert S., Hayes, Don

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 298 KB

english, 2015

13

Ibuprofen rescues mutant cystic fibrosis transmembrane conductance regulator trafficking

Carlile, Graeme W., Robert, Renaud, Goepp, Julie, Matthes, Elizabeth, Liao, Jie, Kus, Bart, Macknight, Sean D., Rotin, Daniela, Hanrahan, John W., Thomas, David Y.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 1.03 MB

english, 2015

14

Disposition index identifies defective beta-cell function in cystic fibrosis subjects with normal glucose tolerance

Merjaneh, L., He, Q., Long, Q., Phillips, L.S., Stecenko, A.A.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 386 KB

english, 2015

15

The growing threat of nontuberculous mycobacteria in CF

Floto, R. Andres, Haworth, Charles S.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 98 KB

english, 2015

16

Use of neutrophil gelatinase-associated lipocalin (NGAL) in CF

Munro, Courtney, Ranganathan, Sarath, Coulthard, Kingsley, Quinlan, Cathy

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 93 KB

english, 2015

17

Regarding the article entitled “Iron supplementation does not worsen respiratory health or alter the sputum microbiome in cystic fibrosis”

Hoo, Z.H., Wildman, M.J.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 109 KB

english, 2015

18

Anti-ETAR and anti-AT1R autoantibodies are elevated in patients with endstage cystic fibrosis

Budding, K., van de Graaf, E.A., Hoefnagel, T., Kwakkel-van Erp, J.M., van Kessel, D.A., Dragun, D., Hack, C.E., Otten, H.G.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 254 KB

english, 2015

19

Central venous thrombosis and thrombophilia in cystic fibrosis: A prospective study

Munck, Anne, Kheniche, Ahmed, Alberti, Corinne, Hubert, Dominique, Martine, Reynaud-Gaubert, Nove-Josserand, Raphaele, Pin, Isabelle, Bremont, Francois, Chiron, Raphael, Couderc, Laure, Dalphin, Marie

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 220 KB

english, 2015

20

Cystic fibrosis-related bone disease explored using a four step algorithm

Brookes, Denise S.K., Briody, Julie N., Munns, Craig F., Davies, Peter S.W., Hill, Rebecca J.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 369 KB

english, 2015

21

Comparing Mycobacterium massiliense and Mycobacterium abscessus lung infections in cystic fibrosis patients

Roux, Anne-Laure, Catherinot, Emilie, Soismier, Nathalie, Heym, Beate, Bellis, Gil, Lemonnier, Lydie, Chiron, Raphaël, Fauroux, Brigitte, Le Bourgeois, Muriel, Munck, Anne, Pin, Isabelle, Sermet, Isab

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 390 KB

english, 2015

22

Pancreatic enzymes and Fibrosing Colonopathy

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 89 KB

english, 2015

23

Stimulation of β2-adrenergic receptor increases CFTR function and decreases ATP levels in murine hematopoietic stem/progenitor cells

Trotta, Teresa, Guerra, Lorenzo, Piro, Donatella, d'Apolito, Maria, Piccoli, Claudia, Porro, Chiara, Giardino, Ida, Lepore, Silvia, Castellani, Stefano, Di Gioia, Sante, Petrella, Antonio, Maffione, A

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 848 KB

english, 2015

24

Computed tomography correlates with improvement with ivacaftor in cystic fibrosis patients with G551D mutation

Sheikh, Shahid I., Long, Frederick R., McCoy, Karen S., Johnson, Terri, Ryan-Wenger, Nancy A., Hayes, Don

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 811 KB

english, 2015

25

News

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 547 KB

english, 2015

26

Opportunities for cystic fibrosis care teams to support treatment adherence

Riekert, Kristin A., Eakin, Michelle N., Bilderback, Andrew, Ridge, Alana K., Marshall, Bruce C.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 238 KB

english, 2015

27

Book Review

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 66 KB

english, 2015

28

Impact of alginate-producing Pseudomonas aeruginosa on alveolar macrophage apoptotic cell clearance

McCaslin, Charles A., Petrusca, Daniela N., Poirier, Christophe, Serban, Karina A., Anderson, Gregory G., Petrache, Irina

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 585 KB

english, 2015

29

Raw meat contaminated with epidemic clones of Burkholderia multivorans found in cystic fibrosis patients

Lupo, Agnese, Isis, Enver, Perreten, Vincent, Endimiani, Andrea

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 287 KB

english, 2015

30

A bioassay using intestinal organoids to measure CFTR modulators in human plasma

Dekkers, R., Vijftigschild, L.A.W., Vonk, A.M., Kruisselbrink, E., de Winter-de Groot, K.M., Janssens, H.M., van der Ent, C.K., Beekman, J.M.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 514 KB

english, 2015

31

Alternative outcomes for the multiple breath washout in children with CF

Stanojevic, Sanja, Jensen, Renee, Sundaralingam, Dasiga, Salazar, Juliana Giraldo, Yammine, Sophie, Singer, Florian, Latzin, Philipp, Amin, Reshma, Subbarao, Padmaja, Gustafsson, Per, Ratjen, Felix

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 461 KB

english, 2015

32

Randomized, single blind, controlled trial of inhaled glutathione vs placebo in patients with cystic fibrosis

Calabrese, C., Tosco, A., Abete, P., Carnovale, V., Basile, C., Magliocca, A., Quattrucci, S., De Sanctis, S., Alatri, F., Mazzarella, G., De Pietro, L., Turino, C., Melillo, E., Buonpensiero, P., Di

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 846 KB

english, 2015

33

The effect of short-term, high-dose oral N-acetylcysteine treatment on oxidative stress markers in cystic fibrosis patients with chronic P. aeruginosa infection — A pilot study

Skov, Marianne, Pressler, Tacjana, Lykkesfeldt, Jens, Poulsen, Henrik Enghusen, Jensen, Peter Østrup, Johansen, Helle Krogh, Qvist, Tavs, Kræmer, Dorthe, Høiby, Niels, Ciofu, Oana

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 391 KB

english, 2015

34

The challenges of developing effective anti-inflammatory agents in cystic fibrosis

Sagel, Scott D.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 140 KB

english, 2015

35

Vitamin D deficiency is associated with pulmonary dysfunction in cystic fibrosis

Sexauer, William P., Hadeh, Anas, Ohman-Strickland, Pamela A., Zanni, Robert L., Varlotta, Laurie, Holsclaw, Douglas, Fiel, Stanley, Graff, Gavin R., Atlas, Arthur, Bisberg, Dorothy, Hadjiliadis, Deni

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 369 KB

english, 2015

36

Pseudomonas aeruginosa genotypes acquired by children with cystic fibrosis by age 5-years

Kidd, Timothy J., Ramsay, Kay A., Vidmar, Suzanna, Carlin, John B., Bell, Scott C., Wainwright, Claire E., Grimwood, Keith

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 1.80 MB

english, 2015

37

Costs and health-related quality of life of patients with cystic fibrosis and their carers in France

Chevreul, Karine, Berg Brigham, Karen, Michel, Morgane, Rault, Gilles

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 239 KB

english, 2015

38

A phase 3, open-label, randomized trial to evaluate the safety and efficacy of levofloxacin inhalation solution (APT-1026) versus tobramycin inhalation solution in stable cystic fibrosis patients

Stuart Elborn, J., Geller, David E., Conrad, Douglas, Aaron, Shawn D., Smyth, Alan R., Fischer, Rainald, Kerem, Eitan, Bell, Scott C., Loutit, Jeffery S., Dudley, Michael N., Morgan, Elizabeth E., Van

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 462 KB

english, 2015

39

Epidemiology of nontuberculous mycobacteria among patients with cystic fibrosis in Scandinavia

Qvist, Tavs, Gilljam, Marita, Jönsson, Bodil, Taylor-Robinson, David, Jensen-Fangel, Søren, Wang, Mikala, Svahn, Anita, Kötz, Karsten, Hansson, Lennart, Hollsing, Annika, Hansen, Christine R., Finstad

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 337 KB

english, 2015

40

Editorial Board

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 86 KB

english, 2015

41

Corrigendum to “Prescribing practices for intravenous aminoglycosides in UK Cystic Fibrosis clinics: A questionnaire survey” [J Cyst Fibros (2013) 424-427]

Smyth, Alan R., Campbell, Emma L.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 88 KB

english, 2015

42

Nasal potential difference: Best or average result for CFTR function as diagnostic criteria for cystic fibrosis?

Keenan, Katherine, Avolio, Julie, Rueckes-Nilges, Claudia, Tullis, Elizabeth, Gonska, Tanja, Naehrlich, Lutz

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 489 KB

english, 2015

43

Is infection with hypermutable Pseudomonas aeruginosa clinically significant?

Auerbach, Adi, Kerem, Eitan, Assous, Marc Victor, Picard, Elie, Bar-Meir, Maskit

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 267 KB

english, 2015

44

Clinical relevance of Pseudomonas aeruginosa hypermutation in cystic fibrosis chronic respiratory infection

Oliver, Antonio

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 113 KB

english, 2015

45

Pharmacokinetics and tolerability of oral sildenafil in adults with cystic fibrosis lung disease

Taylor-Cousar, J.L., Wiley, C., Felton, L.A., St. Clair, C., Jones, M., Curran-Everett, D., Poch, K., Nichols, D.P., Solomon, G.M., Saavedra, M.T., Accurso, F.J., Nick, J.A.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 343 KB

english, 2015

46

Cystic fibrosis and the role of gastrointestinal outcome measures in the new era of therapeutic CFTR modulation

Bodewes, Frank A.J.A., Verkade, Henkjan J., Taminiau, Jan A.J.M., Borowitz, Drucy, Wilschanski, Michael

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 276 KB

english, 2015

47

Inflammation in cystic fibrosis lung disease: Pathogenesis and therapy

Cantin, André M., Hartl, Dominik, Konstan, Michael W., Chmiel, James F.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 732 KB

english, 2015

48

Aggregates of mutant CFTR fragments in airway epithelial cells of CF lungs: New pathologic observations

Du, Kai, Karp, Philip H., Ackerley, Cameron, Zabner, Joseph, Keshavjee, Shaf, Cutz, Ernest, Yeger, Herman

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 1.39 MB

english, 2015

49

Host-pathogen interplay in the respiratory environment of cystic fibrosis

Yonker, Lael M., Cigana, Cristina, Hurley, Bryan P., Bragonzi, Alessandra

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 839 KB

english, 2015

50

Cystic fibrosis mortality trend in Italy from 1970 to 2011

Alicandro, Gianfranco, Frova, Luisa, Di Fraia, Gennaro, Colombo, Carla

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 424 KB

english, 2015

51

Emerging bacterial pathogens and changing concepts of bacterial pathogenesis in cystic fibrosis

Parkins, Michael D., Floto, R. Andres

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 646 KB

english, 2015

52

Improved repeatability of nasal potential difference with a larger surface catheter

Vermeulen, François, Proesmans, Marijke, Boon, Mieke, De Boeck, Kris

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 728 KB

english, 2015

53

Microbiology review series: CF microbiology — Towards 2020 and beyond

Rogers, Geraint B., Tunney, Michael M.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 92 KB

english, 2015

54

Ivacaftor as salvage therapy in a patient with cystic fibrosis genotype F508del/R117H/IVS8-5T

Carter, S., Kelly, S., Caples, E., Grogan, B., Doyle, J., Gallagher, C.G., McKone, E.F.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 186 KB

english, 2015

55

The Lung Clearance Index as a probe for the effectiveness of short-term therapies in cystic fibrosis lung disease

Vanderhelst, Eef, De Meirleir, Liesbeth, Schuermans, Daniel, Malfroot, Anne, Vincken, Walter, Verbanck, Sylvia

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 128 KB

english, 2015

56

Cystic fibrosis (cf) and ovarian reserve: A cross-sectional study examining serum anti-mullerian hormone (amh) in young women

Schram, C.A., Stephenson, A.L., Hannam, T.G., Tullis, E.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 170 KB

english, 2015

57

Pulmonary function outcomes for assessing cystic fibrosis care

Wagener, Jeffrey S., Elkin, Eric P., Pasta, David J., Schechter, Michael S., Konstan, Michael W., Morgan, Wayne J.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 271 KB

english, 2015

58

Ivacaftor and sinonasal pathology in a cystic fibrosis patient with genotype deltaF508/S1215N

Vreede, C.L., Berkhout, M.C., Sprij, A.J., Fokkens, W.J., Heijerman, H.G.M.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 243 KB

english, 2015

59

Acknowledgement to Reviewers 2014

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 128 KB

english, 2015

60

Authors' response

Welsh, Liam, Nesci, Christopher, Tran, Haily, Tomai, Marisol, Ranganathan, Sarath

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 102 KB

english, 2015

61

Genotyping of Pseudomonas aeruginosa reveals high diversity, stability over time and good outcome of eradication

Johansson, E., Welinder-Olsson, C., Gilljam, M., Pourcel, C., Lindblad, A.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 527 KB

english, 2015

62

Sputum club cell protein concentration is associated with pulmonary exacerbation in cystic fibrosis

Laguna, Theresa A., Williams, Cynthia B., Brandy, Kyle R., Welchlin-Bradford, Cole, Moen, Catherine E., Reilly, Cavan S., Wendt, Christine H.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 335 KB

english, 2015

63

Protease–antiprotease imbalances differ between Cystic Fibrosis patients' upper and lower airway secretions

Hentschel, Julia, Fischer, Nele, Janhsen, Wibke K., Markert, Udo R., Lehmann, Thomas, Sonnemann, Jürgen, Böer, Klas, Pfister, Wolfgang, Hipler, Uta-Christina, Mainz, Jochen G.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 572 KB

english, 2015

64

Long-term treatment with oral N-acetylcysteine: Affects lung function but not sputum inflammation in cystic fibrosis subjects. A phase II randomized placebo-controlled trial

Conrad, C., Lymp, J., Thompson, V., Dunn, C., Davies, Z., Chatfield, B., Nichols, D., Clancy, J., Vender, R., Egan, M.E., Quittell, L., Michelson, P., Antony, V., Spahr, J., Rubenstein, R.C., Moss, R.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 512 KB

english, 2015

65

The p.Gly622Asp (G622D) mutation, frequently found in Reunion Island and in black populations, is associated with a wide spectrum of CF and CFTR-RD phenotypes

Marion, Heller, Natacha, Gaitch, Brigitte, Martinez, François, Cartault, Michel, Renouil, Corinne, Theze, Emmanuelle, Girodon, Thierry, Bienvenu

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 154 KB

english, 2015

66

News

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 146 KB

english, 2015

67

Evaluation of mold exposure in cystic fibrosis patients' dwellings and allergic bronchopulmonary risk

Rocchi, Steffi, Richaud-Thiriez, Bénédicte, Barrera, Coralie, Grenouillet, Frédéric, Dalphin, Jean-Charles, Millon, Laurence, Reboux, Gabriel

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 358 KB

english, 2015

68

Managing central venous obstruction in cystic fibrosis recipients—lung transplant considerations

Otani, Shinji, Westall, Glen P., Levvey, Bronwyn J., Marasco, Silvana, Lyon, Stuart, Snell, Gregory I.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 315 KB

english, 2015

69

Clinical expression of patients with the D1152H CFTR mutation

Terlizzi, Vito, Carnovale, Vincenzo, Castaldo, Giuseppe, Castellani, Carlo, Cirilli, Natalia, Colombo, Carla, Corti, Fabiola, Cresta, Federico, D'Adda, Alice, Lucarelli, Marco, Lucidi, Vincenzina, Mac

Journal:

Journal of Cystic Fibrosis

Year:

2015

File:

PDF, 224 KB

2015

70

Serum retinol levels and pulmonary function in children and adolescents with cystic fibrosis

Woestenenk, J.W., Broos, N., Stellato, R.K., Arets, H.G.M., van der Ent, C.K., Houwen, R.H.J.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 296 KB

english, 2015

71

Clinical relevance of Pseudomonas aeruginosa hypermutation in cystic fibrosis chronic respiratory infection

Bar-Meir, Maskit

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 84 KB

english, 2015

72

Altered intestinal bile salt biotransformation in a cystic fibrosis (Cftr−/−) mouse model with hepato-biliary pathology

Bodewes, Frank A.J.A., van der Wulp, Mariëtte Y.M., Beharry, Satti, Doktorova, Marcela, Havinga, Rick, Boverhof, Renze, James Phillips, M., Durie, Peter R., Verkade, Henkjan J.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 710 KB

english, 2015

73

Safety and efficacy of Creon® Micro in children with exocrine pancreatic insufficiency due to cystic fibrosis

Kashirskaya, Nataliya Y., Kapranov, Nikolay I., Sander-Struckmeier, Suntje, Kovalev, Vladimir

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 421 KB

english, 2015

74

High-frequency audiometry reveals high prevalence of aminoglycoside ototoxicity in children with cystic fibrosis

Al-Malky, Ghada, Dawson, Sally J., Sirimanna, Tony, Bagkeris, Emmanouil, Suri, Ranjan

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 409 KB

english, 2015

75

WS09.3 Professional quality of life among CF healthcare providers

Goldbeck, L., Fidika, A., Heuer, H.-E., Junge, S., Smaczny, C., Reimann, A.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 63 KB

english, 2015

76

Cystic Fibrosis Foundation and European Cystic Fibrosis Society Survey of cystic fibrosis mental health care delivery

Abbott, J., Elborn, J.S., Georgiopoulos, A.M., Goldbeck, L., Marshall, B.C., Sabadosa, K.A., Smith, B.A., Quittner, A.L.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 1.07 MB

english, 2015

77

Pseudomonas aeruginosa in CF and non-CF homes is found predominantly in drains

Purdy-Gibson, M.E., France, M., Hundley, T.C., Eid, N., Remold, S.K.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 233 KB

english, 2015

78

WS10.2 Hypoxic epithelial necrosis triggers neutrophilic inflammation via IL-1 receptor signaling in cystic fibrosis-like lung disease

Zhou-Suckow, Z., Fritzsching, B., Schubert, S.C., Schatterny, J., Hirtz, S., Muley, T., Kahn, N., Welte, T., Randell, S.H., Länger, F., Schnabel, P., Herth, F.J.F., Mall, M.A.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 72 KB

english, 2015

79

WS19.4 Molecular epidemiology of hot-spots of mutation in antimicrobial resistance loci of Pseudomonas aeruginosa isolates from cystic fibrosis airways

Greipel, L., Cramer, N., Klockgether, J., Dorda, M., Mielke, S., Chouvarine, P., Wiehlmann, L., Tümmler, B.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 68 KB

english, 2015

80

113 Inhalative meropenem–tobramycin–colistin combination improves lung function in chronic Pseudomonas aeruginosa colonization

Herrmann, G., Freitag, E., Deppisch, C., Heyder, S., Graepler-Mainka, U., Riethmüller, J.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 71 KB

english, 2015

81

141 An open label investigation of the tolerability and pharmacokinetics of oral cysteamine in adults with cystic fibrosis

Devereux, G., Steele, S., Griffiths, K.J., Cotton, S., Fraser-Pitt, D., Devlin, E., Chrystyn, H., Norrie, J., O'Neil, D.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 65 KB

english, 2015

82

207 Effect of high-dose cholecalciferol supplementation (HCDS) on serum vitamin D concentrations in adults with cystic fibrosis (CF)

Willcox, E., Powell, M.J., Roche, A., Kuitert, L.M., Watson, D.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 64 KB

english, 2015

83

31 Sphingosine 1-phosphate receptor 3 is highly upregulated on human neutrophils upon migration to the airways

Ingersoll, S.A., Forrest, O., Brown, M.R., Tirouvanziam, R.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 61 KB

english, 2015

84

WS06.1 Stabilization of CFTR at the membrane by EPAC1 activation occurs through interaction with NHERF-1

Lobo, M., Fernandes, J., Amaral, M., Zaccolo, M., Farinha, C.M.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 67 KB

english, 2015

85

159 Promoting physical exercise by stealth

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 62 KB

english, 2015

86

268 Short-term pulmonary rehabilitation program in children and adolescents with chronic respiratory disease

Van de Wijdeven, P., Govaerts, L., Spooren, K., Van Aerschot, K., Moens, M.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 64 KB

english, 2015

87

WS18.3 Accuracy of modelling future trends in cystic fibrosis demography using the French Cystic Fibrosis Registry

Burgel, P.-R., Bellis, G.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 60 KB

english, 2015

88

Initial evaluation of the Parent Cystic Fibrosis Questionnaire—Revised (CFQ-R) in infants and young children

Alpern, Adrianne N., Brumback, Lyndia C., Ratjen, Felix, Rosenfeld, Margaret, Davis, Stephanie D., Quittner, Alexandra L.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 342 KB

english, 2015

89

WS02.5 Pharmacodynamics of ceftazidime combined with β-lactamase inhibitors in biofilm Pseudomonas aeruginosa in vitro

Wang, H., Jørgensen, C., Ciofu, O., Christophersen, L., Kolpen, M., Jensen, P.Ø., Song, Z., Moser, C., Høiby, N.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 73 KB

english, 2015

90

92 Increasing virulence, acute phenotypic adaptations and evolving host–pathogen interactions during chronic Burkholderia cepacia complex infection of the cystic fibrosis lung

Senior, N.J., Gore, S., Johnson, S.C., Vaitkute, G., Moore, K.A., Paszkiewicz, K.H., Kadioglu, A., Brown, A.R.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 68 KB

english, 2015

91

255 Annual medication review by a clinical pharmacist in an adult cystic fibrosis care center

Challet, C., Koutsokera, A., Hofer, M., Schaad, N., Sauty, A.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 62 KB

english, 2015

92

106 Descriptive analysis of inhaled antibiotic combination therapy in a large Belgian referral center

Goeminne, P.C., Van De Kerkhove, C., Dupont, L.J.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 69 KB

english, 2015

93

70 Dry powder inhalation devices are a safe alternative to nebulizers regarding contamination with CF specific pathogenic germs

Opitz, P., Schwarz, C., Fischer, R., Hogardt, M.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 67 KB

english, 2015

94

79 Development of the upper respiratory tract microbiome was investigated longitudinally in cystic fibrosis infants and controls 0–6 months of age

Prevaes, S.M.P.J., de Winter-de Groot, K.M., Janssens, H.M., Wang, X., Tramper-Stranders, G.A., Hasrat, R., Tiddens, H.A.W.M., van Westreenen, M., van der Ent, C.K., Sanders, E.A.M., Bogaert, D.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 68 KB

english, 2015

95

WS01.3 Lumacaftor in combination with ivacaftor in patients with cystic fibrosis who are homozygous for the F508del-CFTR mutation

Elborn, J.S., Ramsey, B., Boyle, M.P., Wainwright, C., Konstan, M., Huang, X., Marigowda, G., Waltz, D.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 72 KB

english, 2015

96

143 Lumacaftor/ivacaftor combination therapy in CF patients homozygous for F508del-CFTR with severe lung dysfunction

Elborn, J.S., Ramsey, B., Boyle, M.P., Wainwright, C., Konstan, M., Huang, X., Marigowda, G., Waltz, D.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 62 KB

english, 2015

97

An unusual cause of growth failure in cystic fibrosis: A salutary reminder of the interaction between glucocorticoids and cytochrome P450 inhibiting medication

Albert, Benjamin B., Jaksic, Mirjana, Ramirez, Jessica, Bors, Jacqueline, Carter, Philippa, Cutfield, Wayne S., Hofman, Paul L.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 746 KB

english, 2015

98

Breaking bad news, the diagnosis of cystic fibrosis in childhood

Havermans, Trudy, Tack, Jessica, Vertommen, Anneke, Proesmans, Marijke, de Boeck, Kris

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 194 KB

english, 2015

99

75 A single clone of Achromobacter xylosoxidans colonizes Belgian cystic fibrosis patients from different centres

Cools, P., Ho, E., Schelstraete, P., Würth, B., Franckx, H., Van Simaey, L., Van Daele, S., Verhulst, S., De Baets, F., Vaneechoutte, M.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 68 KB

english, 2015

100

96 Effect of Prevotella spp. capsular polysaccharide on resistance to antimicrobial peptides and host innate immune factors

Matier, T.B., Mooney, D., Valvano, M.A., Brennan, G.P., Silipo, A., Molinaro, A., Elborn, J.S., Tunney, M.M.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 71 KB

english, 2015

101

WS02.8 Altered therapeutic susceptibility of mucoid Pseudomonas aeruginosa in artificial sputum medium

Pritchard, M.F., Powell, L.C., Onsøyen, E., Rye, P.D., Hill, K.E., Thomas, D.W.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 73 KB

english, 2015

102

Cystic fibrosis — From basic science to clinical benefit: A review series

Hartl, Dominik, Amaral, Margarida

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 110 KB

english, 2015

103

328 Use of an insulin pump combined with the FreeStyle Libre interstitial glucose monitor in a needle-phobic adolescent with cystic fibrosis-related diabetes

Campbell, J., Wilkinson, I., Thalange, N., Kavanagh, C.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 65 KB

english, 2015

104

62 Molecular diagnosis of Pseudomonas aeruginosa infection in culture-negative samples from cystic fibrosis patients

Amiri, M., Mangiaterra, G., Pasquaroli, S., Vignaroli, C., Cirilli, N., Manso, E., Biavasco, F.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 68 KB

english, 2015

105

220 Nutritional outcomes of enteral nutrition in children with cystic fibrosis

Fisher, K., Patchell, C., Jones, S., Hull, L., Cooper, S., Desai, M.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 63 KB

english, 2015

106

WS01.6 The rational design of nanomedicines for chronic pulmonary infection treatment: Does size really matter?

Forier, K., Messiaen, A.-S., Raemdonck, K., Nelis, H., De Smedt, S.C., Demeester, J., Coenye, T., Braeckmans, K.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 68 KB

english, 2015

107

196 Prevalence of cataracts in a population of cystic fibrosis patients homozygous for the F508del mutation

Seliger, V., Bai, Y., Volkova, N., Tian, S., Waltz, D.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 71 KB

english, 2015

108

WS03.2 Coping with stress of mothers of children and adolescents with cystic fibrosis

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 61 KB

english, 2015

109

123 Twenty years of clinical studies on anti-Pseudomonas IgY to cystic fibrosis patients

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 70 KB

english, 2015

110

253 Why do some patients regularly fail to attend CF clinic?

Derry, D., Lanario, J.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 62 KB

english, 2015

111

276 Parental preparation for first admission

James, K., Phillips, S., Fulford, B.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 61 KB

english, 2015

112

WS14.2 Short-term effect of different physical exercise–physiotherapy combinations on sputum production, oxygen saturation and lung function in young patients with cystic fibrosis

Radtke, T., Christen, G., Huber, M. Kerstan, Hebestreit, H., Kriemler, S.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 66 KB

english, 2015

113

WS17.5 Patients with cystic fibrosis and the R117H mutation: The European experience

Naehrlich, L., Zolin, A., Colombo, C., De Boeck, K., Kashirskaya, N., Olesen, H.V.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 57 KB

english, 2015

114

WS17.6 FEV1% predicted in patients with at least one nonsense mutation and patients homozygous for F508del

Zolin, A., De Boeck, K.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 57 KB

english, 2015

115

WS18.4 Five-year survivorship in cystic fibrosis: Outcomes improve but the disease remains the same

Liou, T.G., Adler, F.R.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 59 KB

english, 2015

116

WS18.5 Direct medical cost of CF care in the Irish public healthcare system

Jackson, A.D., McAdams, R., Fletcher, G., McKone, E., Kelleher, C.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 51 KB

english, 2015

117

WS19.1 Disease-causing CFTR mutation and carriage of airway infections

Block, T., Granchelli, A., Adler, F.R., Liou, T.G.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 68 KB

english, 2015

118

WS19.2 Staphylococcus aureus population from cystic fibrosis patients in Spain: Results from a point-prevalence multicentre study

Caballero, J.D.D., Vindel, A., Tato, M., Cobo, M., Cantón, R., Del Campo, R.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 68 KB

english, 2015

119

WS19.3 Prevalence of small colony variants of Staphylococcus aureus from lower respiratory tract specimens

Carzino, R., King, L., Hart, E., Ranganathan, S.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 68 KB

english, 2015

120

WS19.5 Alginate phenotypes of Pseudomonas aeruginosa from a Brazilian CF center compared to Scandinavian CF centers

Caçador, N.C., Darini, A.L.C., Torres, L.A.G.M.M., Ciofu, O., Høiby, N.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 66 KB

english, 2015

121

WS19.6 Diversity of Pseudomonas aeruginosa in cystic fibrosis airways

Sommer, L.M., Marvig, R.L., Luján, A., Koza, A., Pressler, T., Molin, S., Johansen, H.K.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 66 KB

english, 2015

122

WS19.8 Comparative proteomic profiling of two Swedish CF Pseudomonas aeruginosa isolates reveals possible factors associated with the transmissible cystic fibrosis strain J-2

Johansson, E.A., Welinder-Olsson, C., Hansson, S. Folkesson

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 66 KB

english, 2015

123

WS20.1 Structure–activity relationship for OligoG-induced normalization of the CF mucus phenotype

Ermund, A., Meiss, L.N., Recktenwald, C.V., Onsøyen, E., Rye, P.D., Dessen, A., Berg, Y.P., Myrset, A.H., Hansson, G.C.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 64 KB

english, 2015

124

WS20.3 Acquired CFTR dysfunction in patients with primary ciliary dyskinesia (PCD)?

Cohen-Cymberknoh, M., Bar, G., Yaakov, Y., Cohen, M., Shoseyov, D., Kerem, E., Wilschanski, M.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 64 KB

english, 2015

125

WS20.4 Clinical outcomes of Real-World Kalydeco (CORK) study – a prospective 12 month analysis addressing the impact of CFTR modulation on the cystic fibrosis lung

Ronan, N.J., O'Callaghan, G.P., Mooney, D., Einarsson, G., Elborn, J.S., Ni Chroinin, M., Mullane, D., Murphy, D.M., O'Connor, O.J., Shortt, C., Tunney, M.M., Twomey, M., Maher, M.M., Eustace, J.A., P

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 65 KB

english, 2015

126

WS20.5 Cystic fibrosis related structural lung disease on high resolution computed tomography before and after ivacaftor therapy

Sayers, I., Sharma, A., Ranganathan, S., Cain, T., Skoric, B.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 55 KB

english, 2015

127

WS21.1 Evaluation of the use of IPV for the treatment of atelectasis in cystic fibrosis

McIlwaine, M.P., Lee Son, N., Richmond, M., Chilvers, M.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 60 KB

english, 2015

128

WS21.2 Skeletal muscle strength measurements in adult CF patients compared to controls

Pyl, F., Thys, J., Vandervennet, C., Declercq, D., De Baets, F., Van Biervliet, S.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 60 KB

english, 2015

129

WS21.4 Multiple breath nitrogen washout: The Exhalyzer D (Ecomedics) is more sensitive than the EasyOne Pro (NDD) in detecting ventilation inhomogeneities in children with CF and normal FEV1

Poncin, W., Berardis, S., Aubriot, A.-S., Lebecque, P.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 60 KB

english, 2015

130

WS21.5 The use of serum creatinine to estimate skeletal muscle mass in cystic fibrosis

Hilton, N.P., Morris, A.R., Walshaw, M.J., Greenwood, J., Ledson, M.J.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 71 KB

english, 2015

131

WS21.6 Prognostic value of breathing reserve index at anaerobic threshold during cardiopulmonary exercise testing in children with cystic fibrosis

O'Connor, R., Rand, S., Grillo, L., Hebestreit, H., Prasad, S.A., Urquhart, D.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 71 KB

english, 2015

132

WS21.7 The relationship of maximum inspiratory pressures with inspiratory muscle weakness and FEV1 in patients with cystic fibrosis chronically infected with Pseudomonas aeruginosa

Lavery, K., Moran, F., Rendall, J.C., Downey, D.G.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 71 KB

english, 2015

133

WS21.8 Validity of the Oxygen Uptake Efficiency Slope (OUES) as a parameter of maximal and submaximal exercise testing in children with mild CF

Cornette, J., Keyzer, M., Pyl, F., Coomans, I., Van Daele, S., Vandekerckhove, K.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 71 KB

english, 2015

134

WS21.9 Lung clearance index as a clinical trial outcome measure: Establishing the CTN LCI core facility

Saunders, C., Bayfield, K.J., Davies, J., De Boeck, K., Lindblad, A.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 60 KB

english, 2015

135

WS21.10 Respiratory muscle endurance training with normocapnic hyperpnea in patients with cystic fibrosis. A randomized controlled study

Giacomodonato, B., Graziano, L., Curzi, M., Perelli, T., De Sanctis, S., Varchetta, M., Alatri, F.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 60 KB

english, 2015

136

ePS01.1 Asian patients with CF: Does ethnicity influence our diagnostic criteria?

Bosch, B., Bilton, D., Sosnay, P., Amaral, M., Ishiguro, T., Gulmans, V., Cuppens, H., De Boeck, K.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 66 KB

english, 2015

137

ePS01.2 First year evaluation of the Portuguese pilot neonatal screening for cystic fibrosis

Sousa, R., Pereira, L., Cavaco, J., Silva, T., Vaz, L.G., Rocha, H., Vilarinho, L., Barreto, C.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 66 KB

english, 2015

138

ePS01.5 Update of CFTR mutation spectrum in cystic fibrosis patients from Peru

Audrézet, M.-P., Diringer, B., Le Millier, K., Kervennic, M.N., Aquino Ordinola, R., Purizaga Izquierdo, N., Férec, C.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 57 KB

english, 2015

139

ePS01.6 Application of next-generation sequencing for the analysis of CFTR in Serbian CF patients

Kusic-Tisma, J., Divac Rankov, A., Ljujic, M., Pejanovic, N., Stanic, B., Radojkovic, D.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 57 KB

english, 2015

140

ePS01.7 Is confirmatory genetic testing of all CF screen positives in Ontario justified?

Chauhan, N., Fleischer, E., Ho, S., Price, A.K.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 56 KB

english, 2015

141

ePS02.1 Anti-Aspergillus fumigatus antibodies in cystic fibrosis (CF) patients: A comparison of three methods

Grancini, A., Daprai, L., Biffi, A., Pozzi, C., Guarneri, D., Del Corno, G., Zanardelli, M., Torresani, E., Colombo, C.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 65 KB

english, 2015

142

ePS02.2 Fungal colonization in a cystic fibrosis adult population

Freire, G., Lopes, C., Freitas, F., Azevedo, P.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 65 KB

english, 2015

143

ePS02.3 Pseudomonas aeruginosa and Aspergillus fumigatus co-infection reduced the pro-inflammatory response in CF epithelial cells

Reece, E., Renwick, J., McClean, S., Greally, P.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 65 KB

english, 2015

144

ePS02.4 Fungus-reactive T-cells as sensitive and specific sensors to diagnose fungal infections in cystic fibrosis patients

Schwarz, C., Bacher, P., Scheffold, A.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 65 KB

english, 2015

145

ePS02.7 Significance of fungal isolation in CF paediatric patients

Romanowska, E., Dmeńska, H., Kołodziejczyk, M., Pawińska, A., Dzierżanowska-Fangrat, K.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 60 KB

english, 2015

146

ePS02.8 Prevalence and clinical associations of fungal airway isolates in the UK adult cystic fibrosis population

Felton, I.C., Yazbeck, L., Gunn, E., Moffatt, M., Cookson, W.O., Loebinger, M.R., MacNeill, S.J., Bilton, D., Simmonds, N.J.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 60 KB

english, 2015

147

ePS03.1 What is the relationship between patients’ beliefs about medicine and treatment adherence in adults with cystic fibrosis?

Keyte, R., Egan, H., Nash, E., Regan, A.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 63 KB

english, 2015

148

ePS03.2 Are beliefs about inhaled medications related to actual adherence?

Maclean, L., Duff, A.J.A., Ball, R., Bowmer, G., Masterson, C.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 63 KB

english, 2015

149

ePS03.3 Longer term tolerance and likely adherence to TOBI Podhaler in CF adults

Brown, C.J., Cameron, S., Carrolan, V., Ahitan, B., Phull, S., Rashid, R., Whitehouse, J., Nash, E.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 63 KB

english, 2015

150

ePS03.4 Patient reported adherence to ivacaftor

Williams, E., Edgeworth, D., Fantidis, M., Finlayson, F., Button, B.M., Clark, D., Tierney, A.C., Keating, D., Kotsimbos, T., Wilson, J.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 63 KB

english, 2015

151

ePS03.5 Adherence monitoring in cystic fibrosis centres: Current practice and pharmacists’ perspectives

Mooney, K., Ryan, C., Downey, D.G.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 55 KB

english, 2015

152

ePS03.6 Medication adherence and treatment practice in Hungary with cystic fibrosis patients

Bodnar, R., Szegedi, M., Molnar, M.J., Meszaros, A., Horvath, I.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 55 KB

english, 2015

153

ePS04.1 Longitudinal changes in lung clearance index in children with CF

Vermeulen, F., Proesmans, M., De Boeck, K.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 64 KB

english, 2015

154

ePS04.2 Infant lung function: First report of a novel infant multiple breath washout apparatus

Shawcross, A., Murray, C.S., Horsley, A.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 64 KB

english, 2015

155

ePS04.3 Comparison of CF and non-CF LCI results using the Exhalyzer D and Innocor™ devices

Bayfield, K.J., Saunders, C., Alton, E., Davies, J.C.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 64 KB

english, 2015

156

ePS04.4 Assessment of oxidative stress in cystic fibrosis: Comparison of airway and systemic malondialdehyde levels

Antus, B., Drozdovszky, O., Kelemen, K., Barta, I.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 64 KB

english, 2015

157

ePS04.5 MR diagnosis and follow-up in young CF patients with endobronchial invasive aspergillosis

Borzani, I.M., Russo, M.C., Rosso, L., Cervellin, G., Zazzeron, L., Colombo, C.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 69 KB

english, 2015

158

ePS04.7 Tobramycin nebulization with I-neb® in children with cystic fibrosis (TONI study): Pharmacokinetics and safety

van Velzen, A.J., Uges, J.W.F., Arets, H.G.M., Nuijsink, M., van der Wiel-Kooij, E.C., Pullens, B., Heijerman, H.G.M., Touw, D.J., Janssens, H.M.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 69 KB

english, 2015

159

ePS04.8 Effect of early intervention with inhaled hypertonic saline on lung function in infants and toddlers with cystic fibrosis (CF) diagnosed by neonatal screening

Teper, A., Balinotti, J., Rodríguez, V., Zaragoza, S., Lubovich, S., Kofman, C., Bournissen, F. Garcia

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 69 KB

english, 2015

160

ePS05.1 Nutritional formula pre-hydrolyzed by novel point of care lipase device (EFIC™) leads to increased fat absorption in young pigs with exocrine pancreatic insufficiency (EPI)

Grujic, D., Fedkiv, O., Nikandrova, E., Mosiejchuk, N., Kirko, S., Osadchenko, I., Kovalenko, T., Drahanchuk, O., Parshykov, O., Goncharova, E., Freedman, S., Martin, C., Pierzynowski, S.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 67 KB

english, 2015

161

ePS05.2 Novel point of care immobilized lipase device (EFIC™) is compatible with a range of nutritional formulas and can simplify delivery of hydrolyzed fat during tube feeding

Maki, J., Neelagiri, M., Olshaw, B., Devarakonda, S., Loring, G.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 67 KB

english, 2015

162

ePS05.3 Ivacaftor and its effects on body composition in adults with G551D related cystic fibrosis

Tierney, A.C., Edgeworth, D., Williams, E., Finlayson, F., Keating, D., Clark, D., Button, B.M., Kotsimbos, T., Wilson, J.W.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 67 KB

english, 2015

163

ePS05.4 A multidisciplinary approach can improve a low BMI in adults with cystic fibrosis

Whitehead, S., Pearson, C., O'Driscoll, M., Daniels, T.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 67 KB

english, 2015

164

ePS05.5 Cystic fibrosis bone disease: Is the CFTR corrector C18 an option for therapy?

Velard, F., Delion, M., Lemaire, F., Tabary, O., Touqui, L., Le Pimpec-Barthes, F., Sermet-Gaudelus, I., Gangloff, S., Jacquot, J.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 65 KB

english, 2015

165

ePS05.6 Cessation of pancreatic enzyme replacement therapy (PERT) after initiation of therapy with ivacaftor – a case series

Cheah, E., Venuti, E., McKay, K., Gaskin, K.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 65 KB

english, 2015

166

ePS05.7 Individual caloric intake in cystic fibrosis (CF) – how to calculate?

Junge, S., Dopfer, C., Stein, L., Kueck, M., Schlüter, K., Stetefeld, A.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 65 KB

english, 2015

167

ePS05.9 Benefits of long-term supplementation with omega-3 polyunsaturated fatty acids in cystic fibrosis

Hanssens, L., Thiébault, I., Lefevre, N., Malfroot, A., Gaspar, V., Knoop, C., Duchateau, J., Casimir, G.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 54 KB

english, 2015

168

ePS06.1 Stenotrophomonas maltophilia is increased in patients with cystic fibrosis-related diabetes and displays enhanced growth under physiologically-relevant levels of glucose

Fothergill, J.L., Dyce, P., Jones, G.H., Hickey, G., D'Amore, L., Lenzi, L., Ledson, M.J., Greenwood, J., Winstanley, C., Walshaw, M.J.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 73 KB

english, 2015

169

ePS06.3 Neutrophil elastase activity on the surface of sputum neutrophils is associated with severity of cystic fibrosis lung disease

Dittrich, A.S., Heath, N., Wiebel, M., Herth, F.J.F., Schultz, C., Mall, M.A.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 72 KB

english, 2015

170

ePS06.4 Upper airway infection and inflammation in CF and healthy controls during exacerbation and stable phases

Hentschel, J., Schilling, T., Arnold, C., Jahnsen, W., Hünniger, K., Hipler, U.-C., Pfister, W., Sonnemann, J., Lehmann, T., Mainz, J.G.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 73 KB

english, 2015

171

ePS06.5 Burkholderia cepacia complex acquisition: A threat in all CF patients?

Willekens, J., Wanyama, S., Thomas, M., De Wachter, E., De Schutter, I., Malfroot, A.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 67 KB

english, 2015

172

ePS06.9 Lung disease progression and inflammatory parameters in children with cystic fibrosis chronically colonized with Burkholderia cepacia complex

Shmarina, G., Pukhalskaya, D., Avakian, L., Semykin, S., Alioshkin, V., Kashirskaya, N.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 59 KB

english, 2015

173

1 Why does cystic fibrosis (CF) show the prevalence and distribution observed in human populations? A literature review

Mowat, A.J., Werpachowska, A.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 62 KB

english, 2015

174

3 Connexin 37 and connexin 43 genotypes in correlation to cytokines in induced sputum and blood in cystic fibrosis (CF)

Ludwig, M., Eickmeier, O., Smaczny, C., Schreiner, F., Dubois, W., Gampolo, D.N., Schubert, R., Zielen, S., Ganschow, R., Schmitt-Grohé, S.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 62 KB

english, 2015

175

4 The contribution of genes immune response modifiers in the development of cystic fibrosis and its phenotypes

Yankina, G.N., Kondrateva, E.I., Loshkova, E.V., Sergienko, D.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 62 KB

english, 2015

176

5 Is there an association between Pseudomonas aeruginosa chronic infection and CFTR genotype in adult cystic fibrosis (CF) patients?

Athanazio, R., Rached, S., Pieri, P.D.C., Marie, S. Kazue Nagahashi, Lerario, A., Carvalho-Pinto, R.M., Cukier, A., Stelmach, R.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 70 KB

english, 2015

177

6 How should we manage incidental identification of carrier status in children?

Vears, D., Delany, C., Massie, J., Gillam, L.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 69 KB

english, 2015

178

8 Molecular diagnosis of cystic fibrosis in the population of the Republic of Moldova

Barbova, N., Egorov, V., Darii, M., Sciuca, S.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 69 KB

english, 2015

179

10 Mild cystic fibrosis phenotype in adult patients with novel 3272–16T>A mutation

Krasovskiy, S., Amelina, E., Usacheva, M., Stepanova, A., Poliakov, A., Audrézet, M.-P., Férec, C., Kashirskaya, N.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 63 KB

english, 2015

180

12 Reverse hybridization enables fast and reliable detection of 25 common CF mutations

Weidler, S., Hammermann, J., Binkenstein, P., Müller, C., Rottwinkel, G., Stopsack, M., Lee-Kirsch, M.A.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 63 KB

english, 2015

181

15 Normal values and failure rate of sweat conductivity using Nanoduct Sweat Analysis System in healthy infants aged 4 days and 4 weeks

Mazur, A., Kuehni, C.E., Loher, J., Malzacher, A., Hornung, R., Barben, J.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 64 KB

english, 2015

182

16 A qualitative study of parents’ recommendations for improving the notification process and communication between health professionals and families for new diagnosis of cystic fibrosis

Razai, M.S., Williams, J., Nestel, R., Dalton, D.D.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 64 KB

english, 2015

183

17 Infants diagnosed clinically after false negative cystic fibrosis newborn screening may present with Pseudo-Bartter's-syndrome

Gjerstad, A.C., Bakkeheim, E., Handeland, K., Lundman, E., Pettersen, R.D., Storrøsten, O.T.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 64 KB

english, 2015

184

18 Energy intake in infants with cystic fibrosis at diagnosis by newborn screening

Huggins, T., Buckley, J., West, N.S.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 55 KB

english, 2015

185

19 Does newborn screening improve health status in CF children?

Panickar, J., Lowdon, J., Edgar, J., David, T.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 55 KB

english, 2015

186

20 More impact of inflammation on growth and respiratory function in girls

Lefevre, N., Hanssens, L., Casimir, G.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 63 KB

english, 2015

187

21 Long term azithromycin therapy in patients with cystic fibrosis

Emiralioğlu, N., Öztürk, Z.A., Yalçin, E., Doğru Ersöz, D., Özçelik, U., Kiper, N.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 63 KB

english, 2015

188

22 Defining the cystic fibrosis arthropathy phenotype: A serological and imaging pilot study

Fitch, G., Williams, K., Freeston, J.E., Dass, S., Whitaker, P., Peckham, D.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 63 KB

english, 2015

189

23 Seasonal variation in Aspergillus specific antibody levels – does weather influence exposure?

Barber, K., Jones, G.H., Ledson, M.J., Greenwood, J., Walshaw, M.J.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 63 KB

english, 2015

190

24 Basophil Activation Test may facilitate ABPA diagnosis in CF patients

Katelari, A., Tzanoudaki, M., Noni, M., Kaditis, A., Polaki, V., Limioti, A., Doudounakis, S.-E., Kanariou, M.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 67 KB

english, 2015

191

26 sCD14 in macrophages from patients with cystic fibrosis: Origin and involvement in inflammatory functions

Lévêque, M., Simonin-Le Jeune, K., Le Trionnaire, S., Jouneau, S., Belleguic, C., Brinchault, G., Desrues, B., Dimanche-Boitrel, M.-T., Martin-Chouly, C.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 67 KB

english, 2015

192

27 Chitinase and cystic fibrosis: A study of its expression and role in CF pathophysiology

Bouvet, G.F., Maignan, M., Berthiaume, Y.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 67 KB

english, 2015

193

29 Airway epithelial cell IP-10 production is regulated by miR-31 via the transcription factor IRF-1

Kerrigan, L., Taggart, C., Weldon, S.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 61 KB

english, 2015

194

30 Oxidative stress diminishes the number of functional neutrophil granulocytes in lungs of cystic fibrosis (CF) patients, which is ameliorated by glutathione treatment

Schiotz, P.O., Tolbod, L., Bouchelouche, K., Holm, M., Noerskov-Lauritsen, N., Froekiaer, J.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 62 KB

english, 2015

195

32 Mediation of pro/anti-inflammatory balance by vardenafil in mouse CF macrophages is dependent on CFTR expression

Dhooghe, B., Noel, S., Huaux, F., Panin, N., Leal, T.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 67 KB

english, 2015

196

34 Phagocyte collaboration for the control of Pseudomonas aeruginosa

Muntaka, S., Asante, A., Cámara, M., Martínez-Pomares, L.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 67 KB

english, 2015

197

39 Inhibition of CFTR slows forskolin-stimulated mucociliary clearance in ferret trachea

Joo, N.S., Jeong, J.H., Wine, J.J.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 67 KB

english, 2015

198

40 Is oxidative stress responsible for plasma membrane integrity alteration in macrophages from patients with cystic fibrosis?

Le Trionnaire, S., Lévêque, M., Belleguic, C., Deneuville, E., Desrues, B., Brinchault, G., Dabadie, A., Roussey, M., Jouneau, S., Gangneux, J.-P., Dimanche-Boitrel, M.-T., Martin-Chouly, C.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 55 KB

english, 2015

199

42 Microbiologic bacterial agents in a young cystic fibrosis population

Freitas, A.C., Neves, J.O., Barbosa, T., Lopes, V., Ramos, H., Senra, V., Rocha, H.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 60 KB

english, 2015

200

46 Microbiological airway flora in children with cystic fibrosis in the first year of life (To treat or not to treat, that's the question!)

Hübsch, M., Ulbrich, K., Hammermann, J.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 63 KB

english, 2015

201

48 Altered gut microbiota in stable patients with cystic fibrosis (CF) compared to controls and its relationship with intravenous (IV) antibiotic usage and lung function

Burke, D.G., Fouhy, F., Rea, M.C., Harrison, M.J., Stanton, C., O'Sullivan, O., Murphy, D.M., O'Callaghan, G.P., Eustace, J.A., Shanahan, F., Fleming, C., McCarthy, M., Shortt, C., Ross, R.P., Plant,

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 64 KB

english, 2015

202

49 Propidium monoazide (PMA) sample pretreatment impacts the abundance of rare populations in high-throughput sequencing analysis of CF lung mycobiome and bacteriome

Nguyen, L.D.N., Deschaght, P., Merlin, S., Loywick, A., Audebert, C., Viscogliosi, E., Vaneechoutte, M., Delhaes, L.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 62 KB

english, 2015

203

54 Limited transmission of non-tuberculous mycobacteria among Danish cystic fibrosis patients

Wang, M., Handberg, K.J., Bento, C., Qvist, T., Jensen-Fangel, S., Olesen, H.V., Høiby, N., Nørskov-Lauritsen, N.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 67 KB

english, 2015

204

58 Achromobacter xylosoxidans/ruhlandii colonized CF patients have more hospitalisations and IV antibiotic days

De Baets, F., Schelstraete, P., Haerynck, F., Van Simaey, L., Vaneechoutte, M., Van Daele, S.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 65 KB

english, 2015

205

59 Ralstonia mannitolilytica – an emerging threat in cystic fibrosis and lung transplantation

Perry, A., Gould, F.K., Brodlie, M., Ni Chroinin, M., Mullane, D., Plant, B., McElvaney, G., Gunaratnam, C., Schaffer, K., Egan, J., Kenna, D., Perry, C., Turton, J.F., Mahenthiralingham, E., Hannan,

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 65 KB

english, 2015

206

60 Serratia marcescens: An emerging pathogen or innocent bystander?

Belkarty, B., Bilton, D., Jones, A.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 65 KB

english, 2015

207

61 Comparison of two chromogenic media for isolation of Staphylococcus aureus from respiratory samples from patients with cystic fibrosis

Preece, C., Perry, A., Jones, A.L., Cummings, S.P., Bourke, S.J., Perry, J.D.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 68 KB

english, 2015

208

63 Pseudomonas aeruginosa pulmonary infection in CF patients in a Brazilian reference center: Antibody response monitoring

Mauch, R.M., Rossi, C.L., Ribeiro, J.D., Ribeiro, A.F., Nolasco da Silva, M.T., Levy, C.E.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 68 KB

english, 2015

209

65 Clinical outcomes of chronic “Prairie Epidemic Strain” Pseudomonas aeruginosa infection in adults with cystic fibrosis

Somayaji, R., Lam, J., Surette, M., Waddell, B., Purighalla, S., Sibley, C., Rabin, H.R., Parkins, M.D.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 65 KB

english, 2015

210

66 Incidence of Burkholderia cepacia complex infection in a Cystic Fibrosis Centre in Buenos Aires City, Argentina, from 2004 to 2014

Ibarra, L., Degrossi, J., Vargas, L. Jordá, Barrero, P., Vazquez, M., Teper, A., Galanternik, L.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 65 KB

english, 2015

211

69 The Cystic Fibrosis Sputum Induction Trial (CF-SpIT). Induced sputum in young healthy non-productive children with cystic fibrosis

Tame, J., Ronchetti, K., Paisey, C., Doull, I., Mahenthiralingham, E., Howe, R., Forton, J.T.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 68 KB

english, 2015

212

74 Burkholderia cepacia complex infection in an adult cystic fibrosis centre over a ten year period

Keating, D., Schaffer, K.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 68 KB

english, 2015

213

80 The microbiome in early cystic fibrosis lung disease: A longitudinal analysis

Frayman, K.B., Armstrong, D., Carzino, R., Ferkol, T., Grimwood, K., Storch, G., Wylie, K., Ranganathan, S.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 68 KB

english, 2015

214

82 Contribution of early and repeated nasopharyngeal aspirate cultures in pediatric cystic fibrosis

Cakir, E., Gedik, A.H., Yuksel, M., Iraz, M.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 67 KB

english, 2015

215

86 Molecular typing of rapidly growing mycobacteria (RGM) in patients with cystic fibrosis (CF)

Cariani, L., Teri, A., Biffi, A., Girelli, D., Guarneri, D., D'Accico, M., Beltrami, B., Defilippi, G., Porcaro, L., Costantino, L., Colombo, C., Arghittu, M., Torresani, E.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 67 KB

english, 2015

216

88 Prevalence and characterization of unusual Staphylococcus aureus strains with a mucoid phenotype recovered from the airways of cystic fibrosis patients

Birtel, J., Schwartbeck, B., Treffon, J., Kale, D., Kahl, J., Hirschhausen, N., Neumann, C., Lee, J.C., Götz, F., Rohde, H., Henke, H., Küster, P., Dübbers, A., Peters, G., Kahl, B.C.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 67 KB

english, 2015

217

89 Molecular characterization of strains of methicillin-resistant Staphylococcus aureus (MRSA) in patients with cystic fibrosis (CF)

Cariani, L., Teri, A., Biffi, A., Girelli, D., Guarneri, D., D'Accico, M., Beltrami, B., Defilippi, G., Colombo, C., Arghittu, M., Torresani, E.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 68 KB

english, 2015

218

91 Retrospective chart review of cases of cepacia syndrome (CS) in adults with cystic fibrosis (CF)

Usacheva, M., Krasovskiy, S., Amelina, E.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 68 KB

english, 2015

219

101 An audit of the clinical effectiveness of ceftazidime at varying doses in the treatment of respiratory exacerbations in cystic fibrosis

Booth, J., Hutchison, S., O'Beirne, A., West, N.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 66 KB

english, 2015

220

103 Minimum inhibition concentration characteristic of antibiotics on Pseudomonas aeruginosa strains from patients with cystic fibrosis

Pronoza, M., Sciuca, S., Ceban, A., Balanetchi, L.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 66 KB

english, 2015

221

107 Sputum flora among teenage cystic fibrosis patients using inhaled TOBI therapy for 5 and more years from Sofia CF center

Galeva, I., Mileva, S., Yankova, M., Markova, R.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 70 KB

english, 2015

222

108 Analysis of dry powder inhaler (DPI) antibiotics in an adult cystic fibrosis (CF) centre

Henry, A., Forster, E., Bell, N.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 69 KB

english, 2015

223

109 Influence of nebulized antibiotics on ciliary activity in vitro

Boon, M., Jaspers, M., Vermeulen, F., Proesmans, M., Jorissen, M., De Boeck, K.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 69 KB

english, 2015

224

111 An overview of a desensitization protocol to inhaled aztreonam

Riolo, G., Gent, K., Cortes, D., Tullis, E.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 69 KB

english, 2015

225

112 Analysis of long-term use of liposomal amikacin for inhalation (LAI) in patients with cystic fibrosis (CF) who have chronic infection from Pseudomonas aeruginosa

Bilton, D., Pressler, T., Fajac, I., Clancy, J.P., Minic, P., Cipolli, M., Galeva, I., Solé, A., Dupont, L.J., Mayer-Hamblett, N., Torchio, S., McGinnis, J.P., Eagle, G., Konstan, M.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 70 KB

english, 2015

226

114 Investigating the activity of antibiotics at aerosolized concentrations against Burkholderia cepacia complex biofilms

Kennedy, S., Yau, Y., Caraher, E., Waters, V.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 70 KB

english, 2015

227

115 Intravenous antibiotics for pulmonary exacerbations in people with cystic fibrosis – Cochrane review

Hurley, M., Prayle, A., Flume, P.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 70 KB

english, 2015

228

117 Safety profile of levofloxacin inhalation solution from 3 controlled cystic fibrosis clinical trials

Flume, P., VanDevanter, D.R., Cohen, F., Fleming, R., Elborn, J.S.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 69 KB

english, 2015

229

121 Extended HLA analysis in a cohort of patients hypersensitive to beta-lactam antibiotics

Whitaker, P., Alfirevic, A., Etherington, C., Clifton, I., Fitch, G., Pirmohamed, M., Peckham, D.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 70 KB

english, 2015

230

125 Viral load is high despite preserved interferon-β response in rhinovirus-infected CF cells

Dauletbaev, N., Das, M., Cammisano, M., Kooi, C., Leigh, R., Beaudoin, T., Rousseau, S., Lands, L.C.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 56 KB

english, 2015

231

128 The metabolic consequences of CFTR modulation with ivacaftor in a single adult cystic fibrosis centre cohort

Ronan, G., Ronan, N.J., Shortt, C., Fleming, C., Cronin, K., McCarthy, M., Hickey, C., Murphy, D.M., Eustace, J.A., O'Halloran, D.J., Plant, B.J.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 60 KB

english, 2015

232

131 The experience of nebulised aztreonam lysine at the All Wales Adult CF Centre (AWACFC)

Rees, A., Ketchell, R.I., Bridges, C., Duckers, J.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 68 KB

english, 2015

233

142 Development of an S/MAR based episomal vector for the CFTR gene delivery

De Rocco, D., Pompili, B., Cifani, N., DiDomenico, E.G., Del Porto, P., Ascenzioni, F.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 62 KB

english, 2015

234

146 Sinonasal inhalation of isotonic vs. hypertonic saline (6.0%) in CF patients with chronic rhinosinusitis – results of a multicentre, double-blind, controlled prospective trial

Mainz, J.G., Schaedlich, K., Hentschel, J., Schumacher, U., Koitschev, C., Koitschev, A., Riethmüller, J., Prenzel, F., Sommerburg, O., Staab, D., Gleiber, W., Beck, J.F., Arnold, C.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 63 KB

english, 2015

235

148 Prevalence of chronic rhinosinusitis and upper airways colonisation in the Welsh adult cystic fibrosis population

Mills-Bennett, R., Angulatta, V., Thomas, S., Duckers, J.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 60 KB

english, 2015

236

149 Etiological structure of lung infections in patients with cystic fibrosis

Sciuca, S., Balanetchi, L., Pronoza, M., Ceban, A.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 60 KB

english, 2015

237

152 Influencing factors of skeletal muscle weakness in adults with cystic fibrosis

Pyl, F., Vandervennet, C., Thijs, J., Declercq, D., De Baets, F., Van Biervliet, S.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 63 KB

english, 2015

238

154 INSPIRE-CF: An interim review of participation of children with cystic fibrosis randomised to a weekly supervised exercise intervention

Douglas, H., Ledger, S., Main, E., Jaramillo, L. Sarria, Rayner, P., Goldman, A., Giardini, A., Aurora, P.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 63 KB

english, 2015

239

155 Physical activity levels of children and adolescents with cystic fibrosis in Wales

Mackintosh, K.A., Evans, R.E., Barry, M., Clarke, J., McNarry, M.A.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 62 KB

english, 2015

240

156 Exercise performance in children with mild cystic fibrosis (CF): Are there arguments to enhance physical activity?

Keyzer, M., Cornette, J., Pyl, F., Coomans, I., Van Daele, S., Vandekerckhove, K.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 62 KB

english, 2015

241

171 Variation in random capillary blood glucose and HbA1c as predictors of cystic fibrosis related diabetes (CFRD)

White, H., Hurley, P., Oliver, S., Peckham, D.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 65 KB

english, 2015

242

177 Evolution of glycemia, insulinemia and glycosylated hemoglobin in a CF pediatric population

Denis, M.-H., Paquette, A., Marcotte, J.-É., Mailhot, G.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 67 KB

english, 2015

243

178 Glucose tolerance in cystic fibrosis patients over a 3-year period (DIAMUCO study)

Bourdy, S., Rabilloud, M., Touzet, S., Roche, S., Drai, J., Martin, C., Nove-Josserand, R., Reix, P., Pin, I., Camara, B., Reynaud, Q., Laville, M., Durieu, I.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 68 KB

english, 2015

244

179 12 years too late? Rethinking CFRD screening

McLean, M., Lambert, C., Gevers, E., Cowlard, J., Chaudry, R., Nwokoro, C.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 62 KB

english, 2015

245

185 Use of the hemoglobin A1c test as a screening tool for cystic fibrosis related diabetes

Nicolo, M., Dorgan, D., Ferrin, M., Holsclaw, D., Smith, S., Hadjiliadis, D.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 60 KB

english, 2015

246

187 Risk factors for pulmonary exacerbations (PEx) in pediatric cystic fibrosis (CF) patients

Lubovich, S., Buendía, J., Rodríguez, V., Zaragoza, S., Camargo, B., Alchundia, J., Galanternik, L., Ratto, P., Teper, A.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 62 KB

english, 2015

247

192 ABPAs in Pseudomonas aeruginosa colonized CF patients

De Baets, F., De Keyzer, L., Schelstraete, P., Van Daele, S., Wanyama, S.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 69 KB

english, 2015

248

198 Electrolyte depletion with metabolic alkalosis in infants with cystic fibrosis

Fustik, S., Jakovska-Maretti, T., Spirevska, L.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 71 KB

english, 2015

249

199 Metabolic alkalosis in patients with cystic fibrosis: Are we missing something?

Fitch, G., Etherington, C., Whitaker, P., Clifton, I., Bosomworth, M., Peckham, D.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 56 KB

english, 2015

250

200 A novel entity of a CFTR-related respiratory disease

Schulz, A., Tümmler, B.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 56 KB

english, 2015

251

201 Tibial cortical bone is impaired in adults with CF

Gensburger, D., Boutroy, S., Chapurlat, R., Nove-Josserand, R., Rabilloud, M., Roche, S., Durieu, I.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 64 KB

english, 2015

252

205 Hand grip strength and DXA in adults with cystic fibrosis

Mead, L., Watson, H., Haworth, C.S., Floto, R.A.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 64 KB

english, 2015

253

209 Optimizing vitamin D levels through the winter months in children with cystic fibrosis

Abrol, E., Ranganathan, S.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 64 KB

english, 2015

254

211 Vitamin D insufficiency is associated with pulmonary exacerbations in children with cystic fibrosis

McPhail, G.L., Chini, B., Siracusa, C., Fenchel, M., Szczesniak, R., Clancy, J.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 60 KB

english, 2015

255

218 Body composition estimation by bioelectrical impedance: Validation of an equation adapted to children with cystic fibrosis

Charatsi, A.-M., Rossin, H., Maruani, G., Pires-Kutala, C., Le Bourgeois, M., Letourneur, A., Attlan, E., Lambe, C., De Blic, J., Casimir, G., Sermet-Gaudelus, I.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 66 KB

english, 2015

256

222 Prevalence of overweight & obesity in the Scottish paediatric CF population

Crocker, J., Smith, G.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 63 KB

english, 2015

257

223 Prevalence of overweight and obesity in Scottish adults with cystic fibrosis

Robb, L., Richardson, M., Peters, A., Rodgers, H.C.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 63 KB

english, 2015

258

224 Nutritional status of patients with cystic fibrosis in Russia

Krasovskiy, S., Amelina, E., Kondratyeva, E., Cherniak, A., Voronkova, A., Sherman, V., Kashirskaya, N., Kapranov, N., Shabalova, L., Nikonova, V., Asherova, I., Boitsova, E., Brisin, V., Khachiyan, M

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 66 KB

english, 2015

259

227 Differences in the nutritional status of adults with cystic fibrosis with and without the DF508 homozygous genotype

Hopkins, D., Daniels, T., Marinio, L., Parsons, E.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 65 KB

english, 2015

260

229 Pancreatic genotype–phenotype co-variations in cystic fibrosis

Engjom, T., Lærum, B.N., Nylund, K., Erchinger, F., Gilja, O.H., Dimcevski, G.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 67 KB

english, 2015

261

232 Changes in nutritional status prior to lung transplantation – single centre experience over 10 years

Snowball, J.E., Chapman, S.J., Flight, W.G.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 66 KB

english, 2015

262

234 Vegetable, fruit, dairy and discretionary food intake of cystic fibrosis (CF) patients and comparison with the general population: A cross-sectional study

Tierney, A.C., Fong-To, S.A., Clode, M., Casamento, J., Yuen, A. Tsee Woon, King, S.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 66 KB

english, 2015

263

235 Serum zinc in pediatric patients with cystic fibrosis

Nedkova, V., Kolarova, N., Koleva, R., Yanev, N., Angelova, M.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 66 KB

english, 2015

264

236 Vitamin status in infants with cystic fibrosis during the first year of life

Ajmal, F.Q., Patchell, C., Clarke, J.R.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 62 KB

english, 2015

265

239 Intake of pancreatic enzymes: Consistent with the guidelines?

Declercq, D., De Baets, F., Van Biervliet, S.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 62 KB

english, 2015

266

241 Changes in fatty acid pattern of depot fat tissue in young pancreatic duct ligated pigs – used as a model for humans with pancreatic exocrine insufficiency

Mößeler, A., Gregory, P.C., Kamphues, J.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 65 KB

english, 2015

267

244 Kim's Word Book helps the dialogue between parents and their 3 to 5 year-old child affected by cystic fibrosis

Pesle, A., Gerardin, M., Laugery, M., Munck, A.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 59 KB

english, 2015

268

247 CFRD education: What information do patients value and who do they ask?

Lamb, D.L., Dyce, P., Walshaw, M.J.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 59 KB

english, 2015

269

248 “muko.fit” – a comprehensive health-care approach for patients with CF with critical causes and/or psycho-social challenges. First results regarding the initial 12 months within the project

Moos-Thiele, C., Hoffmann, S., Klümpen, W., Knauf, L., Mainz, J.G., Schwarz, C.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 60 KB

english, 2015

270

252 Recognition of pulmonary exacerbation (PEX) in adult patients with CF: An educational process to overcome barriers

David, V., Pougheon-Bertrand, D., Vion, V., Scalbert, M., Dury, S., Jollivet, D.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 62 KB

english, 2015

271

254 The value of the routine annual review chest radiograph in adults with CF

Addy, C., Symes, M., Bell, N., Bateman, K., Nazareth, D.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 62 KB

english, 2015

272

260 Quality improvement program (QIP) for adolescents in Paris Robert Debré (RD) CF Centre

Gerardin, M., Foucher, A. Vital, Pesle, A., Gonsseaume, S., Catto, S., Munck, A.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 65 KB

english, 2015

273

261 Audit and improvement of the cystic fibrosis liver service in a regional adult CF unit

Turnbull, A., Daniels, T., Carroll, M.P., Nash, K.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 62 KB

english, 2015

274

262 Role of an adapted physical activities professional at a paediatric CF centre

Fuchs, D., Gerardin, M., Gonsseaume, S., Azaiz, W., Delaisi, B., Houdouin, V., Da Costa, E., Munck, A.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 62 KB

english, 2015

275

264 How well established are links with allied medical and surgical specialties in CF care?

Wotton, C., Symes, M., Nazareth, D.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 62 KB

english, 2015

276

267 Peripherally-inserted central catheters use and care in cystic fibrosis: A survey on the practice of free-lance home care nurses in France

Chapron, J., Patalas, V., Surget, S., Jaouani, B.-L., Cases, F., Jaumain, C., Courtiol, C., Panzo, R., Hubert, D., Burnet, E., Honoré, I., Kanaan, R., Burgel, P.-R., Dusser, D., Dupont, C.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 64 KB

english, 2015

277

272 A proposal for specific monitoring sheets for patients taking ivacaftor

Kerbrat, M., Fretay, R., Chevalier, D., You, F., Chiffoleau, M., Hubault, A., Matras, C., Berhault, I., Jousseaume, M.T., L'Abbé, M.C., Pingon, C., Quillevere, M.C., Paul, S., Sery, K., Idres, M.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 65 KB

english, 2015

278

273 Influenza vaccination in CF adults: Coverage level and adverse reactions

Fila, L., Grandcourtova, A., Bartakova, L. Valentova

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 61 KB

english, 2015

279

277 Transformational care at the All Wales Adult CF Centre (AWACFC) – is ivacaftor making us fat? The impact of ivacaftor (Kalydeco®) on body composition

Prosser, A., Proud, D., Guhaniyogi, L., Speight, L., Lau, D., Ketchell, R.I., Duckers, J.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 64 KB

english, 2015

280

280 Sleep in children with cystic fibrosis. A questionnaire-based case–control study

D'Hondt, K., Raman, A., Pyl, F., De Baets, F., Van Biervliet, S.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 64 KB

english, 2015

281

281 Impact of physical activity on illness perception, self-esteem and HRQoL in children with CF

Vandenoetelaer, A., Gaspar, V., Namane, S.A., Hanssens, L., Knoop, C., Lambotte, I., Casimir, G.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 62 KB

english, 2015

282

283 Psycho-social aspects in children with cystic fibrosis from a regional centre in north-eastern Romania

Anton-Paduraru, D.-T., Moscalu, M., Oltean, C., Trandafir, L.M.S., Ciubara, A.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 62 KB

english, 2015

283

285 The psychological impact of adverse drug reactions amongst adults with cystic fibrosis

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 65 KB

english, 2015

284

287 Perception of first infection with Pseudomonas aeruginosa by people with CF, their families and close friends

Palser, S.C., Leighton, P., Rayner, O.C., Smyth, A.R.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 65 KB

english, 2015

285

290 Dietary forcing and conflicts during meals for children suffering from cystic fibrosis: The psychologist's point of view

Leger, P., David, V., Le Rhun, A., Chevalier, D.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 59 KB

english, 2015

286

292 Cystic fibrosis and transition to adult care in Northern Ireland

McNeilly, J., Downey, D.G., Elborn, J.S., Jenkins, L., Reid, A., Rendall, J.C.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 59 KB

english, 2015

287

296 The French clinical trials network: The National Platform for Clinical Research (NPCR)

Ronayette-Preira, A., Creton, M., Delaup, V., Devautour, C., Gauthier, B., Pengam, J., Pires, C., Roche, D., Valentin, F., Abely, M., Chiron, R., Colomb-Jung, V., De Carli, P., Dufeu, N., Durieu, I.,

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 62 KB

english, 2015

288

298 Comparison of adults with cystic fibrosis (diagnosed in childhood vs adulthood)

Baran, E., D'Ascenzo, V., Butti, F., Granero, N., Hendriksen, B., Bossia, D., Calzona, M.C., García, G., Pistorio, V., Volta, L., Ibarra, S.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 64 KB

english, 2015

289

299 Cultural differences in illness perception and treatment adherence

Gur, M., Yaniv, L., Teleshov, A., Agabaria, I., Bentur, L.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 64 KB

english, 2015

290

300 Prevalence and characteristics of attention deficit hyperactivity disorder (ADHD) in patients with cystic fibrosis (CF)

Cohen-Cymberknoh, M., Tanny, T., Blau, H., Kadosh, D., Mussaffi, H., Nir, V., Bentur, L., Shoseyov, D., Kerem, E., Berger, I.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 64 KB

english, 2015

291

303 Smoking cessation help should be available at CF reference centres – a Belgian national survey of smoking in patients with cystic fibrosis

Godding, V., Stevens, L., Galanti, L., De Boeck, K., De Baets, F., Malfroot, A., Hanssens, L., Knoop, C., Sacré, J.-P., Pierart, F., Van Schil, L., Desager, K., Lebecque, P.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 67 KB

english, 2015

292

306 National Registry of patients with cystic fibrosis in the Republic of Moldova in 2009–2014

Sciuca, S., Barbova, N., Balanetchi, L., Eremciuc, R., Pronoza, M.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 62 KB

english, 2015

293

308 National Cystic Fibrosis Patients Registry of Russia (RCFPR) in 2012

Krasovskiy, S., Amelina, E., Kashirskaya, N., Asherova, I., Basilaya, A., Baykova, G., Boytsova, E., Brisin, V., Cherniak, A., Chikunov, V., Dyachkova, A., Dybovskaya, V., Gembitskaya, T., Golubtsova,

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 64 KB

english, 2015

294

309 Poor prognosis factors in CF children

Lefevre, N., Hanssens, L., Casimir, G.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 62 KB

english, 2015

295

310 Prevalence of CF and spectrum of CFTR mutations in the Portuguese population

Grangeia, A., Alves, S., Gonçalves, L., Santos, A., Barros, A., Moura, C., Carvalho, F.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 61 KB

english, 2015

296

311 Treatment and demographic factors affecting time to next pulmonary exacerbation in cystic fibrosis

VanDevanter, D.R., Pasta, D.J., Konstan, M.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 61 KB

english, 2015

297

312 Outcomes and factors associated with poor outcome of children with cystic fibrosis admitted to the intensive care unit

Bucher, J., Oualha, M., Dupic, L., Lebourgeois, M., Lesage, F., Renolleau, S., Boussaud, V., Le Pimpec, F., Hubert, P., Sermet-Gaudelus, I., de Saint Blanquat, L.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 61 KB

english, 2015

298

313 An international study of survival of children with cystic fibrosis after the first episode of invasive mechanical ventilation

Prayle, A., Parslow, R., Erikson, S., Alexander, J., Vyas, H., Fogarty, A., Smyth, A.R.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 61 KB

english, 2015

299

317 When Pseudomonas aeruginosa and orthodontic appliances go together!

Rivas Caldas, R., Diriou, A., Rault, G., Gouriou, S., Virmaux, M., Barbier, G., Boisrame, S.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 66 KB

english, 2015

300

319 Nebulised temocillin for prophylaxis against Burkholderia vietnamiensis in an adult with cystic fibrosis

Marquette, M., Barker, H.C., Shafi, N.S., Johnson, C.J., Haworth, C.S.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 71 KB

english, 2015

301

320 The use of ivacaftor in CF mutations with residual functioning protein

Guigui, S., Condon, B., Cohen, R.I.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 71 KB

english, 2015

302

323 Cytomegalovirus (CMV) primoinfection caused serious deterioration in 2 young CF fathers

Pirson, J., Etienne, I., Ruiz-Patino, M., Sokolow, Y., Knoop, C.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 62 KB

english, 2015

303

325 Isolated heart transplantation for left heart failure in a CF patient

Barth, S., Bagheri-Hanson, A., Mazhari, N., Naehrlich, L.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 62 KB

english, 2015

304

326 DRESS syndrome should be included in the differential diagnosis of life-threatening systemic symptoms in patients with cystic fibrosis

Gohy, S., Froidure, A., Lebecque, P.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 65 KB

english, 2015

305

Editorial Board

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 57 KB

english, 2015

306

Editorial Board

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 53 KB

english, 2015

307

WS01.1 rAAV2/5 encoding a truncated CFTR rescues the CF phenotype in intestinal organoids and a CF mouse model

Carlon, M.S., Vidovic, D., Dekkers, J.F., da Cunha, M. Faria, Hollenhorst, M.I., Bijvelds, M., Van den Haute, C., Baekelandt, V., de Jonge, H., De Boeck, K., Gijsbers, R., Sermet-Gaudelus, I., Edelman

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 72 KB

english, 2015

308

WS01.2 QR-010, an RNA therapy, restores CFTR function using in vitro and in vivo models of ΔF508 CFTR

Beumer, W., Swildens, J., Henig, N., Anthonijsz, H., Biasutto, P., Leal, T., Ritsema, T.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 72 KB

english, 2015

309

WS01.4 VX-661 in combination with ivacaftor in patients with cystic fibrosis and the F508del-CFTR mutation

Pilewski, J.M., Cooke, J., Lekstrom-Himes, J., Donaldson, S.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 72 KB

english, 2015

310

WS01.5 An open-label study of the safety, pharmacokinetics, and pharmacodynamics of ivacaftor in patients aged 2 to 5 years with cystic fibrosis and a CFTR gating mutation: The KIWI study

Rosenfeld, M., Robertson, S., Green, Y., Cooke, J., Lawal, A., Davies, J.C.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 68 KB

english, 2015

311

WS02.1 Efficacy of a protocol for eradication of newly acquired MRSA: Results of the STAR-too trial

Goss, C.H., Thompson, V., Popowitch, E., Howe, D.L., Baines, A., Mayer-Hamblett, N., Jill, V., Muhlebach, M.S.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 72 KB

english, 2015

312

WS02.2 Aztreonam for inhalation solution (AZLI) for eradication of new onset Pseudomonas aeruginosa (PA) infection in children with cystic fibrosis (CF): Results of facemask vs. nebulizer mouthpiece use

Tiddens, H.A.W.M., De Boeck, K., Clancy, J.P., Fayon, M., Arets, H.G.M., Bresnik, M., Derchak, P.A., Lewis, S.A., Oermann, C.M.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 72 KB

english, 2015

313

WS02.3 Randomized, double-blind (DB), placebo-controlled study and open-label (OL) extension of liposomal amikacin for inhalation (LAI) in patients with refractory nontuberculous mycobacterial (NTM) lung disease (LD)

Olivier, K.N., Eagle, G., McGinnis, J.P., Micioni, L., Daley, C.L., Winthrop, K.L., Ruoss, S., Addrizzo-Harris, D.J., Flume, P., Dorgan, D., Salathe, M., Brown-Elliott, B.A., Wallace, R., Griffith, D.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 72 KB

english, 2015

314

WS02.4 Short-term and long-term effects of ivacaftor treatment on sputum microbiota in people with the G551D CFTR mutation

Pope, C.E., Jorth, P., Hisert, K.B., Grogan, B., Gallagher, C., Cooke, G., Donnelly, S.C., Welsh, M., Singh, P.K., McKone, E., Hoffman, L.R.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 72 KB

english, 2015

315

WS02.6 Increased bactericidal activity of colistin on Pseudomonas aeruginosa biofilms in anaerobic conditions

Kolpen, M., Appeldorff, C.F., Brandt, S., Mousavi, N., Kragh, K.N., Bjarnsholt, T., Ciofu, O., Høiby, N., Jensen, P.Ø.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 73 KB

english, 2015

316

WS02.7 Initial and chronic MRSA infection in cystic fibrosis

Gilpin, D.F., Murdock, S., Hoffman, L.R., Vallières, E., McGrath, S., Tunney, M.M., Elborn, J.S., Muhlebach, M.S.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 73 KB

english, 2015

317

WS03.1 Positive effects of a coaching program for parents after the diagnosis of CF following newborn screening

Noordhoek, J., Kuijer, Y., Broekmans, M., Gulmans, V.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 61 KB

english, 2015

318

WS03.3 Preparing first school entry for a child with cystic fibrosis: Contribution of a group education session

Gonsseaume, S., Pesle, A., Gerardin, M., Azaiz, W., Munck, A.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 61 KB

english, 2015

319

WS03.4 Trust, transition and choosing your battles: An exploration of partnership between young expert patients with CF and the healthcare team

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 61 KB

english, 2015

320

WS03.5 Employment and work disability in adults with cystic fibrosis: A cohort study

Digonnet, M., Laborde-Castérot, H., Boussaud, V., Grenet, D., Burgel, P.-R., Kanaan, R., Choudat, D., Hubert, D.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 59 KB

english, 2015

321

WS03.6 Pregnancies after lung transplantation: A retrospective multicenter French study about 39 pregnancies

Bry, C., Hubert, D., Reynaud-Gaubert, M., Dromer, C., Mal, H., Grenet, D., Boussaud, V., Claustre, J., le Pavec, J., Murris-Espin, M., Danner-Boucher, I.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 59 KB

english, 2015

322

WS04.1 Hypersecretion of glucagon-like peptide 1 (GLP1) in cystic fibrosis

Jones, G.H., Dyce, P., Tidbury, N.M., Greenwood, J., Ledson, M.J., Walshaw, M.J.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 68 KB

english, 2015

323

WS04.2 Growth hormone deficiency (GHD) in adult patients (pts) with cystic fibrosis (CF)

Pascucci, C., De Biase, R.V., Savi, D., Cimino, G., D'Alù, V., Sbardella, E., Isidori, A.M., Quattrucci, S.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 68 KB

english, 2015

324

WS04.3 Deficiency of dehydroepiandrosterone sulfate in pediatric and adult patients with cystic fibrosis

Shmarina, G., Pukhalskaya, D., Semykin, S., Avakian, L., Amelina, E., Krasovskiy, S., Usacheva, M., Alioshkin, V., Kashirskaya, N.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 68 KB

english, 2015

325

WS04.4 Prevalence of vitamin D deficiency and effectiveness of two different high dose (stoss) oral vitamin D supplementation protocols in a paediatric cystic fibrosis clinic in Australia

VanderHaak, N., Day, A., Miller, J., Pena, A., Tai, A., Martin, J.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 68 KB

english, 2015

326

WS04.6 Children with cystic fibrosis: How compromised is bone?

Reix, P., Bacchetta, J., Mazur, S., Delaup, V., Perceval, M., Braillon, P., Dray, J., Chapurlat, R., Boutroy, S.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 59 KB

english, 2015

327

WS05.1 The development of a website to facilitate transition from paediatric to adult CF services

Henderson, K., Henman, S., Shearing, V., Allen, R., Blatch, J., Johnson, C.J.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 62 KB

english, 2015

328

WS05.3 Sleep architecture in CF patients as assessed by the Body Media's SenseWear® Armband (SWA)

Opdekamp, C., Gaspar, V., Van Hove, O., Van Muylem, A., Hanssens, L., Casimir, G., Knoop, C.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 62 KB

english, 2015

329

WS05.4 Video games for positive expiratory pressure (PEP) therapy in children with cystic fibrosis: A pilot study

Brochu, A., Marcotte, J.-É., Marquis, N., Laberge, S., Duguay, D., Nataf, P., Gervais, Y., Balli, F., Nguyen, T.T.D.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 62 KB

english, 2015

330

WS05.5 Developing an audio-visual intervention to support children's adherence to home chest physiotherapy for cystic fibrosis

France, E.F., Semple, K., Grindle, M., Rowland, C., Duncan, K., McGhee, J.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 55 KB

english, 2015

331

WS05.6 A pilot study of enhanced community support via internet videoconferencing and physiotherapist home visits

Clayton, A., Haynes, F., Cook, M.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 55 KB

english, 2015

332

WS06.2 R117H-CFTR has a defect in channel gating activity that can be potentiated by ivacaftor

Van Goor, F., Huang, T., Powe, A., Burton, B., Young, T., Negulescu, P.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 67 KB

english, 2015

333

WS06.3 Evaluation of novel corrector–potentiator combinations for treating cystic fibrosis in various assays

Balut, C., Musch, S., Vortherms, T., Singh, A., Vandevelde, A., Swensen, A., Nelles, L., Tse, C., Conrath, K.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 67 KB

english, 2015

334

WS06.4 miR-9 and ANO1: Therapeutic targets in cystic fibrosis?

Sonneville, F., Ruffin, M., Le Rouzic, P., Guillot, L., Corvol, H., Tabary, O.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 67 KB

english, 2015

335

WS06.5 SLC26A9 chloride channels: Generation and functional characterization of stably-overexpressing FRT epithelial cells

Salomon, J.J., Spahn, S., Wang, X., Füllekrug, J., Bertrand, C.A., Mall, M.A.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 61 KB

english, 2015

336

WS06.6 Mucociliary transport is impaired in cystic fibrosis pig airways

Ermund, A., Meiss, L.N., Bähr, A., Klymiuk, N., Hansson, G.C.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 61 KB

english, 2015

337

WS07.1 Standardized treatment of pulmonary exacerbations (STOP) study: Treatment goals for pulmonary exacerbations

West, N.E., Goss, C.H., VanDevanter, D.R., Heltshe, S., Thompson, V., Sanders, D.B., Flume, P.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 65 KB

english, 2015

338

WS07.2 Bronchoalveolar lavage in children with cystic fibrosis and increasing Lung Clearance Index

Svedberg, M., Kötz, K., Wilmar, P., Gustavsson, P., Lindblad, A.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 64 KB

english, 2015

339

WS07.3 FEF25–75 does not contribute to the interpretation of spirometry in patients with cystic fibrosis

Vermeulen, F., De Boeck, K.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 64 KB

english, 2015

340

WS07.4 MBW and MRI as sensitive markers of stable CF lung disease and at exacerbation in children and adolescents

Stahl, M., Wielpütz, M.O., Gräber, S.Y., Hämmerling, S., Sommerburg, O., Eichinger, M., Mall, M.A.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 65 KB

english, 2015

341

WS07.5 Rhinovirus associated pulmonary exacerbations show a lack of FEV1 improvement in children with cystic fibrosis

Cousin, M., Molinari, N., Foulongne, V., Caimmi, D., Vachier, I., Abely, M., Chiron, R.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 55 KB

english, 2015

342

WS07.6 Is dental hygiene associated with survival? A 12 year cohort pilot study

Daniels, T., Khattiak, S., Narang, A., Dimitrov, B., Bush, A.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 55 KB

english, 2015

343

WS08.1 Aerosol delivery practice in Italian cystic fibrosis centres – a national survey

Carta, F., Gambazza, S., Brivio, A.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 60 KB

english, 2015

344

WS08.2/1 Use of the AKITA JET for inhalation treatment in cystic fibrosis – Part I: Clinical outcomes

Eyns, H., Willekens, J., Gaspar, V., Opdekamp, C., Van Hove, O., Galasso, C., Vanderhelst, E., Hanssens, L., Knoop, C., Malfroot, A.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 61 KB

english, 2015

345

WS08.2/2 Use of the AKITA JET for inhalation treatment in cystic fibrosis – Part II: Patients’ satisfaction

Eyns, H., Willekens, J., Opdekamp, C., Van Hove, O., Gaspar, V., Galasso, C., Vanderhelst, E., Hanssens, L., Knoop, C., Malfroot, A.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 61 KB

english, 2015

346

WS08.3 “Real world” experience of introduction of Colobreathe™ (Colo) in adults with cystic fibrosis

Langman, H.B., Brennan, A.L., Bright-Thomas, R.J., Jones, A.M., Riley, D.W., Johnson, S.C.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 60 KB

english, 2015

347

WS08.4/1 Inhaled mannitol (IM) in adults with cystic fibrosis – Part I: Clinical effects

Shaw, F., Parrott, H., Jones, A., Simmonds, N.J., Bilton, D.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 57 KB

english, 2015

348

WS08.4/2 Inhaled mannitol (IM) in adults with cystic fibrosis – Part II: Tolerability

Shaw, F., Parrott, H., Jones, A., Simmonds, N.J., Bilton, D.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 57 KB

english, 2015

349

WS08.5 Cayston® in clinical practice – one year follow-up

Lloyd, E.A., Jackson, M., Sapino-Vivo, R., Walshaw, M.J.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 57 KB

english, 2015

350

WS09.1 Should we advocate a structured venous access policy in adults with CF?

Colpaert, K., Ruelens, C., Lorent, N., Van Bleyenbergh, P., Dupont, L.J.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 63 KB

english, 2015

351

WS09.2 Radiation exposure in adults with CF attending Bristol Adult CF Centre

Addy, C., Symes, M., Bell, N., Bateman, K., Nazareth, D.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 63 KB

english, 2015

352

WS09.4 The role of resilience in quality of life of adult patients with cystic fibrosis (CF)

Rabanser, B., Mitmansgruber, H., Smrekar, U., Beck, T., Niedermayr, K., Eder, J., Ellemunter, H.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 63 KB

english, 2015

353

WS09.5 Effect of ivacaftor on wellness, quality of life and cognitive function in adults with cystic fibrosis and G551D mutation

Button, B.M., Edgeworth, D., Finlayson, F., Fantidis, M., Wilson, L., Talbot, A., Keating, D., Williams, E., Clark, D., Tierney, A.C., Kotsimbos, T., Wilson, J.W.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 64 KB

english, 2015

354

WS09.6 The effect of a 12-month adherence intervention, “CF My Way“, on medication possession, clinical outcomes and quality of life in CF adolescents and young adults

Landau, E., Kalamaro, V., Taizi, T., Kadosh, D., Mantin, H., Mussaffi, H., Blau, H.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 64 KB

english, 2015

355

WS09.7 The CF CARE programme for adherence training in the CF multidisciplinary team

Downey, D.G., Goldbeck, L., Havermans, T., Latchford, G., McCormick, J., Robinson, P.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 63 KB

english, 2015

356

WS09.8 End-of-life care in CF patients: France, 2007–2010

Burgel, P.-R., Martin, C., Kanaan, R., Bousseau, V., Grenet, D., Abely, M., Hubert, D., Munck, A., Lemonnier, L., Hamard, C.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 64 KB

english, 2015

357

WS09.9 Learning from patient deaths in CF: An audit of team debrief sessions at a UK adult CF centre

Reid, N., Oxley, H., Dowdall, F., Brennan, A.L.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 55 KB

english, 2015

358

WS09.10 “Writing for the future”, addressing the challenges of family communication at the end of life in cystic fibrosis

Downey, D.G., Calvert, A., McCafferty, M., Eves, H., Smith, R., McNeilly, J., Elborn, J.S., Rendall, J.C.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 55 KB

english, 2015

359

WS10.1 Investigating exogenous CFTR dysfunction in healthy human neutrophils

Mooney, D., Tunney, M.M., McGrath, S., McIlreavey, L., Johnston, E., Elborn, J.S.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 72 KB

english, 2015

360

WS10.3 Monitoring the pro-inflammatory effect of Pseudomonas aeruginosa culture supernatants and the inhibitory effect of azithromycin by in vivo imaging in IL-8 transiently transgenized mice

Bergamini, G., Stellari, F., Sandri, A., Ruscitti, F., Villetti, G., Sorio, C., Assael, B., Melotti, P., Lleo, M.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 72 KB

english, 2015

361

WS10.4 Transcriptomic analysis of normal and cystic fibrosis human bronchial epithelial cells infected with Pseudomonas aeruginosa reveals distinct gene activation

Balloy, V., Boudaya, S., Coppee, J.Y., Dillies, M.A., Varet, H., Proux, C., Corvol, H., Chignard, M., Guillot, L.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 72 KB

english, 2015

362

WS10.5 Pseudomonas aeruginosa adaptation as a potential risk factor to the progression of cystic fibrosis airway disease in mice and humans

Cigana, C., Lorè, N.I., Riva, C., De Fino, I., Cariani, L., Spagnuolo, L., Sipione, B., Rossi, G., Colombo, C., Bragonzi, A.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 63 KB

english, 2015

363

WS10.6 How does airway infection with chronic Gram-negative and nontuberculous mycobacteria affect lung function? A longitudinal study

Taylor-Robinson, D., Qvist, T., Waldmann, E., Olesen, H.V., Hansen, C.R., Mathiesen, I.H., Høiby, N., Katzenstein, T.L., Smyth, R., Diggle, P., Pressler, T.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 63 KB

english, 2015

364

WS10.7 The role of C-type lectins in the recognition of Pseudomonas aeruginosa

Rahman, T., Alshahrani, M., Irie, Y., Cámara, M., Martínez-Pomares, L.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 63 KB

english, 2015

365

WS11.1 Highlighting the importance of carrier testing in CF families

Duguépéroux, I., L'Hostis, C., Audrézet, M.-P., Rault, G., Parent, P., Blayau, M., Schmitt, S., Férec, C., Scotet, V.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 64 KB

english, 2015

366

WS11.2 The benefits of newborn screening for cystic fibrosis: The Canadian experience

Mak, D.Y., Stephenson, A.L., Lands, L.C.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 64 KB

english, 2015

367

WS11.3 Newborn screening for cystic fibrosis in Switzerland – performance after 4 years

Jurca, M., Kuehni, C.E., Rueegg, C.S., Fingerhut, R., Gallati, S., Torresani, T., Baumgartner, M., Barben, J.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 64 KB

english, 2015

368

WS11.4 The significance of a neonatal screening program in the early diagnosis of cystic fibrosis

Sherman, V., Kashirskaya, N., Kapranov, N., Kondrateva, E., Petrova, N., Voronkova, A., Shabalova, L., Nikonova, V., Krasovskiy, S., Cherniak, A., Amelina, E.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 64 KB

english, 2015

369

WS11.5 The consequences of no newborn cystic fibrosis screening in a well-developed country

Graham-Pedersen, M., Højte, C., Olesen, H.V., Pressler, T., Skov, M.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 65 KB

english, 2015

370

WS11.6 Newborn screening for cystic fibrosis: Rationale for p.Arg117His (R117H) removal from the CFTR mutation panel in France

Munck, A., Audrézet, M.-P., Thauvin-Robinet, C., Cheillan, D., Delmas, D., Girodon, E., Roussey, M.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 65 KB

english, 2015

371

WS11.7 Feeding, growth and nutritional status of infants with CF diagnosed through newborn screening (NBS): Findings from a new multi-center study in the USA

Lai, H.J., Zhang, Z., Chin, L.H., Dumas, S.N., Farrell, P.M.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 65 KB

english, 2015

372

WS11.8 Early diagnosis through newborn screening (NBS) improved long-term growth and adult height at age 18 years in CF patients with pancreatic insufficiency

Zhang, Z., Lindstrom, M.J., Farrell, P.M., Lai, H.J.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 65 KB

english, 2015

373

WS11.9 Parental perspectives of the experience of receiving a positive newborn screening result for cystic fibrosis

Chudleigh, J., Dignan, J., Buckingham, S., Wyatt, H., Metcalfe, A.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 55 KB

english, 2015

374

WS11.10 What words do we use when telephoning a parent to inform we suspect their baby has cystic fibrosis? The development of a phone-call script as a result of a quality improvement project

Bryon, M., Prasad, S.A., Suri, R., Ralph, A.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 55 KB

english, 2015

375

WS13.1 Microevolution of Pseudomonas aeruginosa in cystic fibrosis lungs

Cramer, N., Klockgether, J., Davenport, C.F., Tümmler, B.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 72 KB

english, 2015

376

WS13.2 The role of PGE2 in cystic fibrosis (CF) lung inflammation and the potential association with ivacaftor therapy and treatment response

O'Callaghan, G.P., Ronan, N.J., Foley, N., Lyons, C., O'Driscoll, A., Ni Chroinin, M., Mullane, D., Murphy, D., Shanahan, F., Eustace, J.A., Houston, A., Plant, B.J.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 72 KB

english, 2015

377

WS13.3 Impact of implementation of enhanced infection control and early eradication regimen for Mycobacterium abscessus infection in children with cystic fibrosis

Parikh, S., Lee, T., Guy, E., Edwards, C., Adams, A., Denton, M.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 72 KB

english, 2015

378

WS13.4 Prolongation of antibiotic treatment for cystic fibrosis pulmonary exacerbations

Waters, V., Stanojevic, S., Klingel, M., Chiang, J., Sonneveld, N., Kukkar, R., Tullis, E., Ratjen, F.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 72 KB

english, 2015

379

WS13.5 Pharmacokinetics and safety of once daily double dose inhaled tobramycin administered with the controlled-inhalation AKITA® and conventional PARI-LC® Plus nebulizer in cystic fibrosis

van Velzen, A.J., Bos, A.C., Touw, D.J., Tiddens, H.A.W.M., Heijerman, H.G.M., Janssens, H.M.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 54 KB

english, 2015

380

WS14.1 Ivacaftor improves exercise capacity in patients with G551D CF gene mutations

Edgeworth, D., Keating, D., Williams, E., Clark, D., Button, B.M., Tierney, A.C., Kotsimbos, T., Wilson, J.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 66 KB

english, 2015

381

WS14.3 Exercise testing as diagnostic marker for the outcome after intravenous antibiotic therapy for patients with cystic fibrosis

Hatzler, L., Brandt, C., Thronicke, A., Richter, H., Rohmel, J., Staab, D., Schwarz, C.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 66 KB

english, 2015

382

WS14.4 Does exercise participation affect FEV1 and the number of IV antibiotic days over 5 years in adults with CF?

McAuley, K., Green, S., Major, E., Daniels, T.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 66 KB

english, 2015

383

WS14.5 Exercise testing as a supplementary measure to assess the benefit of intravenous antibiotic courses

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 58 KB

english, 2015

384

WS14.6 Gender differences and exercise performance in adults with cystic fibrosis

Savi, D., Quattrucci, S., Di Paolo, M., Leggieri, E., D'Alù, V., De Biase, R.V., Cucchiara, S., Palange, P., Simmonds, N.J.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 58 KB

english, 2015

385

WS16.1 Clinical Outcomes of Real-World Kalydeco (CORK) study – Investigating the impact of CFTR potentiation on the intestinal microbiota, exocrine pancreatic function and intestinal inflammation prospectively over 12 months

Deane, J., Ronan, N.J., O'Callaghan, G.P., Fouhy, F., Rea, M.C., O'Sullivan, O., Hill, C.J., Shanahan, F., Ross, R.P., McCarthy, M., Murphy, D.M., Eustace, J.A., Stanton, C., Plant, B.J.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 61 KB

english, 2015

386

WS16.2 The prevalence of gastroesophageal reflux disease in infants with cystic fibrosis diagnosed by newborn screening and the relationship with lung infection

Thursfield, R., Ravindran, R., Bush, A., Davies, J.C., Carr, S.B.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 61 KB

english, 2015

387

WS16.3 Consecutive transient elastography measurements to detect cystic fibrosis liver disease

Van Biervliet, S., De Bruyne, R., Velde, S. Vande, Van Winckel, M., Verdievel, H., De Looze, D., De Baets, F., Van Vlierberghe, H.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 61 KB

english, 2015

388

WS16.4 Non invasive liver elastography (LSM) and computed tomography (CT) for evaluation of liver disease in 57 cystic fibrosis adult patients

Hillaire, S., Regnard, N., Cazals-Hatem, D., De Miranda, S., Roux, A., Guth, A., Mellot, F., Grenet, D.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 61 KB

english, 2015

389

WS16.5 Pathological analysis of native liver in cystic fibrosis (CF) with severe portal hypertension reveals a vascular liver disease without cirrhosis

Hillaire, S., Cassiman, D., Cazals-Hatem, D., Grenet, D., De Miranda, S., Soubrane, O., Dupont, L.J., De Boeck, K., Libbrecht, L., Roskams, T., Paradis, V., Witters, P.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 68 KB

english, 2015

390

WS16.6 Is primary sclerosing cholangitis (PSC) a cystic fibrosis-related disorder? Electrophysiological testing and full sequencing of the CFTR gene

Wilschanski, M., Werlin, S., Konikoff, F., Saieg-Spielberg, S., Yaakov, Y., Cohen, M., Lalazar, G., Shibolet, O., Safadi, R., Galun, E., Mizrahi, M., Ilan, Y., Oren, R., Shouval, D., Audrézet, M.-P.,

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 68 KB

english, 2015

391

WS16.7 A cross-sectional and longitudinal metaproteomics approach reveals intestinal dysbiosis, and the presence of markers of chronic inflammation and mucus-related proteins in faecal samples of patients with cystic fibrosis

Debyser, G., Mesuere, B., Van de Weygaert, J., Clement, L., Aerts, M., Duytschaever, G., Dawyndt, P., De Boeck, K., Vandamme, P., Devreese, B.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 68 KB

english, 2015

392

WS17.1 The ancient origin of F508del-CF: When and where the mutation arose

Farrell, P.M., Génin, E., Férec, C., Giteau, K., Frischer, T., Renner, S., Riss, K., Barton, D.E., Repetto, T., Tzetis, M., Macek, M., Dunø, M., Rogers, M., Sahbatou, M., Rouault, K., Fichou, Y., Le M

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 67 KB

english, 2015

393

WS17.2 Identification of CF mutations in deep intronic regions: Design of antisense oligonucleotides for a targeted therapeutic approach

Varilh, J., Bonini, J., Thèze, C., Beyne, E., Altieri, J.-P., Verneau, F., Audrézet, M.-P., Férec, C., Bienvenu, T., Girodon, E., Tuffery-Giraud, S., Des Georges, M., Claustres, M., Raynal, C., Taulan

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 67 KB

english, 2015

394

WS17.3 Errors in documentation of genotype results in a large adult CF centre

Hartley, C.L., Barry, P.J., Green, H., Henchliffe, J., Brock, J., Tobi, S.E., Ramsden, S.C., Horsley, A.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 66 KB

english, 2015

395

WS17.4 Unexpected findings in the broadly used Elucigene CF-EU2 CFTR genotyping assay

Holubová, A., Libik, M., Dvoľáková, L., Paděrová, J., Ptákova, N., Macek, M.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 66 KB

english, 2015

396

WS18.1 Towards a better understanding of survival data in CF

Scotet, V., Duguépéroux, I., L'Hostis, C., Audrézet, M.-P., Rault, G., Lemonnier, L., Bellis, G., Férec, C.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 60 KB

english, 2015

397

WS18.2 Using funnel plots to make meaningful centre comparisons

Pierotti, L., Mohammed, M.A., Wildman, M., Bilton, D., Boote, J., Carr, S.B., Cullinan, P., Elston, C., Harrison, S., Allen, J., Norman, P., MacNeill, S.J.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 60 KB

english, 2015

398

WS19.7 Pseudomonas aeruginosa genotyping: Predicting transition to chronic colonization in cystic fibrosis patients

Jonckheere, L., Vaneechoutte, M., De Baets, F., Van Daele, S., Haerynck, F., Van Simaey, L., Schelstraete, P.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 66 KB

english, 2015

399

WS20.2 Intra-patient variability of sweat chloride concentrations in patients with cystic fibrosis (CF)

Vermeulen, F., Milenkovic, D., Davies, J., Bilton, D., Le Camus, C., De Boeck, K.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 64 KB

english, 2015

400

WS21.3 Acute changes in the lung clearance index after physiotherapy in children with cystic fibrosis

Lin, B., Yabsley, P., Middleton, A., Robinson, P., Jaffe, A., Selvadurai, H.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 60 KB

english, 2015

401

ePS01.3 Genotype–phenotype correlation in Russian cystic fibrosis patients with S466X–R1070Q complex allele

Petrova, N., Kashirskaya, N., Zinchenko, R., Timkovskaya, E., Voronkova, A., Krasovskiy, S., Shabalova, L., Kondrateva, E., Amelina, E., Sherman, V., Cherniak, A., Kapranov, N.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 67 KB

english, 2015

402

ePS01.4 Cystic fibrosis neonatal screening in Castilla-León (Spain), a fifteen years experience

Alonso-Ramos, M.-J., Tellería, J.J., Izquierdo, I., Samaniego, R., Fernández, I.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 66 KB

english, 2015

403

ePS02.5 A new risk factor predicts ABPA in patients with cystic fibrosis

Thronicke, A., Heger, N., Antweiler, E., Krannich, A., Röhmel, J., Brandt, C., Staab, D., Tintelnot, K., Schwarz, C.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 60 KB

english, 2015

404

ePS02.6 Rising prevalence of allergic bronchopulmonary aspergillosis (ABPA) in CF – an unforeseen result of climate change?

Barber, K., Jones, G.H., Ledson, M.J., Greenwood, J., Walshaw, M.J.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 60 KB

english, 2015

405

ePS04.6 Aspergillus fumigatus chronic colonization and lung function decline in CF may have a two-way relationship

Noni, M., Katelari, A., Kaditis, A., Spoulou, V., Dimopoulos, G., Bakoula, C., Doudounakis, S.-E.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 69 KB

english, 2015

406

ePS05.8 Vitamin K status and supplementation in children with cystic fibrosis (CF)

Jones, K., McShane, D., Ross-Russell, R., Lee, J., Saward, C., Lally, E.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 65 KB

english, 2015

407

ePS06.2 Immune cell localization in different compartments of human end-stage CF lungs

Lammertyn, E.J., Vandermeulen, E., Bellon, H., Goeminne, P.C., Vanaudenaerde, B.M., Dupont, L.J.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 72 KB

english, 2015

408

ePS06.6 Full reversibility of lung function decline following clearance of Mycobacterium abscessus complex infection

Qvist, T., Taylor-Robinson, D., Waldmann, E., Olesen, H.V., Hansen, C.R., Mathiesen, I.H., Høiby, N., Katzenstein, T.L., Smyth, R., Diggle, P., Pressler, T.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 67 KB

english, 2015

409

ePS06.7 Factors associated with failure to eradicate first or newly acquired Pseudomonas aeruginosa in patients with CF

Cohen-Cymberknoh, M., Gilead, N., Gartner, S., Simanovski, N., Canino, E., Carreño, J.C., Blau, H., Mussaffi, H., Gur, M., Rivlin, J., Bentur, L., Aviram, M., Picard, E., Hiller, N., Armoni, S., Breue

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 68 KB

english, 2015

410

ePS06.8 Cigarette smoke-induced changes in phenotype and virulence in Pseudomonas aeruginosa

McGown, K.-A., McGrath, S., Tunney, M.M., Elborn, J.S., Gilpin, D.F.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 67 KB

english, 2015

411

2 Genetic markers of low bone mineral density in patients with cystic fibrosis

Jakovska-Maretti, T., Petlickovski, A., Fustik, S.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 62 KB

english, 2015

412

7 Frequency of five CFTR gene mutations in miscegenated cystic fibrosis population of the Brazilian Northeast

Souza, E., Mota, L.R., Bittencourt, P.H., Pimentel, C.S.S., Lima, R.L.F.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 70 KB

english, 2015

413

9 Analysis of cystic fibrosis gene mutations in children with cystic fibrosis in a regional center in Eastern Romania

Trandafir, L.M.S., Tudose, A.A.M., Anton, D.T. Paduraru

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 63 KB

english, 2015

414

11 The risk of incorrect reporting or misinterpretation of genotype results

Wilson, J., Williams, E., Kotsimbos, T.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 63 KB

english, 2015

415

13 Final stage of hemostasis and FGB gene polymorphism in patients with cystic fibrosis

Gordeeva, O., Gorinova, Y., Simonova, O., Botvinyeva, V., Pushkov, A.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 51 KB

english, 2015

416

14 Standardized protocol for ratiometric measurement of b-adrenergic/cholinergic sweating in human sweat glands

Bergamini, G., Peserico, D., Leal, T., Tagliasacchi, M., Sorio, E., Ceri, S., Sorio, C., Assael, B., Wine, J.J., Melotti, P.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 64 KB

english, 2015

417

25 Interactions between cystic fibrosis (CF) and non-CF isolates of Aspergillus fumigatus and Pseudomonas aeruginosa in the development of a co-culture infection model for testing novel therapeutics

Devlin, E., Fraser-Pitt, D., Munro, C.A., O'Neil, D.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 67 KB

english, 2015

418

28 ER stress and TLR activation inter-regulate through p65, p38, STAT3, and XBP1s to modulate inflammation in cystic fibrosis

Tang, A., Turvey, S.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 61 KB

english, 2015

419

33 Procalcitonin and C reactive protein levels in hospitalised patients receiving intravenous antibiotics

Fitch, G., Etherington, C., Whitaker, P., Bosomworth, M., Peckham, D.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 67 KB

english, 2015

420

35 Deficiency of the Planar Cell Polarity protein CELSR3 in CF bronchial epithelial cells increases susceptibility to epithelial–mesenchymal transition

Noel, S., Dhooghe, B., Dykmans, A., Delbart, W., Leal, T.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 67 KB

english, 2015

421

36 Airway epithelial cell integrity protects from cytotoxicity of Pseudomonas aeruginosa quorum-sensing signals

Losa, D., Köhler, T., Saab, J. Bou, Bacchetta, M., Frieden, M., van Delden, C., Chanson, M.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 67 KB

english, 2015

422

37 The microbial metagenome of cystic fibrosis lower airways

Losada, P.M., Chouvarine, P., Schulz, A., Hedtfeld, S., Mielke, S., Dorda, M., Wiehlmann, L., Tümmler, B.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 67 KB

english, 2015

423

38 Sphingoid long chain bases prevent lung infection by Pseudomonas aeruginosa

Pewzner-Jung, Y., Tabazavareh, S.T., Grassmé, H., Becker, K.A., Japtok, L., Steinmann, J., Joseph, T., Lang, S., Tümmler, B., Schuchman, E.H., Lentsch, A.B., Kleuser, B., Edwards, M.J., Futerman, A.H.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 67 KB

english, 2015

424

41 Taxonomic signatures of CF airway microbiota distinguish between patients with lower and higher pulmonary function decline

Bacci, G., Paganin, P., Lopez, L., Vanni, C., Dalmastri, C., Cantale, C., Daddiego, L., Perrotta, G., Campana, S., De Alessandri, A., Taccetti, G., Fiscarelli, E.V., Lucidi, V., Mengoni, A., Bevivino,

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 60 KB

english, 2015

425

43 Gram-negative emerging pathogens: Prevalence and strain typing results from a large UK adult CF centre

Green, H., Bright-Thomas, R.J., Kenna, D., Jones, A.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 60 KB

english, 2015

426

44 Prevalence of emerging pathogens in a large paediatric CF centre

Panickar, J., David, T.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 60 KB

english, 2015

427

45 Decision making by young adults with CF about risk of patient–patient and environmental acquisition of infection

Bowmer, G., Latchford, G., Duff, A.J.A., Dye, L., Lawton, C., Denton, M., Lee, T.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 63 KB

english, 2015

428

47 Diagnostic dilemmas for CF microbiology labs using MALDI-TOF

Lucas, C., Srivastava, S., Balfour, A., Gould, I., Milne, K., MacKay, W., Williams, C.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 63 KB

english, 2015

429

50 A prospective study on non-tuberculous mycobacteria (NTM) in patients with CF

Schwarz, C., Hatzler, L., Schäfer, H., Lewin, A.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 61 KB

english, 2015

430

51 Network infectivity analysis of NTM infection in children with cystic fibrosis (CF) in the North East of England

Silberberg, B.P., Shirley, M.D.F., O'Brien, C.J., Brodlie, M., Robb, A., Perry, A., Rushton, S.P., Thomas, M.F.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 61 KB

english, 2015

431

52 Clinical characteristics and diagnosis of NTM infection in children with cystic fibrosis (CF) in the North East of England

Silberberg, B.P., Beattie, A., Lamb, R., Perry, A., Robb, A., O'Brien, C.J., Spencer, D.A., Brodlie, M., Thomas, M.F.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 62 KB

english, 2015

432

53 Non-tuberculous mycobacteria in cystic fibrosis: A single centre study of prevalence, sampling and microbiological outcomes

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 67 KB

english, 2015

433

55 Is whole genome sequencing necessary to exclude cross infection with Mycobacterium abscessus ST26 in paediatric cystic fibrosis patients?

Lucas, C., Wilkinson, J.D., Mitchell, C., Kenna, D., Turton, J., Mustafa, N., Williams, C.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 67 KB

english, 2015

434

56 Colonization by Rasamsonia argillacea in cystic fibrosis patients: A two-year retrospective study

Cariani, L., Biffi, A., Guarneri, D., Girelli, D., Teri, A., D'Accico, M., Beltrami, B., Arghittu, M., Torresani, E., Colombo, C.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 67 KB

english, 2015

435

57 Does Pandoraea cause clinical deterioration in healthy CF children?

Panickar, J., David, T.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 65 KB

english, 2015

436

64 Infection control (IC) knowledge, beliefs and behaviours (KBB) amongst those with epidemic Pseudomonas aeruginosa (ePA)

Somayaji, R., Waddell, B., Workentine, M.L., Nyberg, L., Leong, J., Rabin, H.R., Brager, N.P., Parkins, M.D.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 68 KB

english, 2015

437

67 CF patients with a declining FEV1: At risk for acquisition of Burkholderia cepacia complex infection?

Willekens, J., Wanyama, S., Thomas, M., De Wachter, E., De Schutter, I., Malfroot, A.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 65 KB

english, 2015

438

68 Respiratory viral detection in children with cystic fibrosis (CF)

Tješić-Drinković, I., Ljubin-Sternak, S., Vraneš, J., Tješić-Drinković, D.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 65 KB

english, 2015

439

71 Pseudomonas aeruginosa in paranasal sinuses and in lower airways in cystic fibrosis patients

Dolce, D., Bresci, S., Masi, E., Campana, S., Braggion, C., Taccetti, G.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 67 KB

english, 2015

440

72 Potential for airborne bacterial contamination in an outpatient respiratory clinic

McElderry, J., O'Neill, K., Tunney, M.M., Downey, D.G., Rendall, J.C., Moore, J.E., Elborn, J.S., Gilpin, D.F.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 68 KB

english, 2015

441

73 Impact of community-acquired MRSA and hospital-acquired MRSA on pulmonary function of CF patients

Campana, S., Ravenni, N., Cariani, L., Colombo, C., Fiscarelli, E., Lucidi, V., Raia, V., Iula, D.V., Pensabene, T., Collura, M., Braggion, C., Taccetti, G.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 68 KB

english, 2015

442

76 Identification of Pseudomonas aeruginosa infection in a paediatric CF population

Willis, E.R., Panickar, J.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 68 KB

english, 2015

443

77 Whole genome sequencing of multiple isolates of the Pseudomonas aeruginosa Liverpool epidemic strain reveals transmission and geographical clustering

Moore, M., Williams, D., Paterson, S., Tucker, N., Kenna, D., Turton, J., Loman, N., Taylor-Robinson, D., Southern, K., Walshaw, M.J., Fothergill, J.L., Winstanley, C.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 68 KB

english, 2015

444

78 Differences in infection, inflammation and structural abnormalities between the right and left lung

Carzino, R., King, L., Ranganathan, S.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 68 KB

english, 2015

445

81 The concordance between the microbiome of the upper and lower respiratory tract is investigated in infants with cystic fibrosis

Prevaes, S.M.P.J., de Steenhuijsen Piters, W.A.A., de Winter-de Groot, K.M., Janssens, H.M., Tramper-Stranders, G.A., Chu, M.L.J.N., Tiddens, H.A.W.M., van Westreenen, M., van der Ent, C.K., Sanders,

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 67 KB

english, 2015

446

82 Routine use of laryngeal aspiration reveals high prevalence of Haemophilus influenzae in respiratory secretions from young patients with cystic fibrosis

Vesterby, L., Holm, M., Nørskov-Lauritsen, N.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 67 KB

english, 2015

447

84 An optimized in vitro antibiotic susceptibility testing method for Staphylococcus aureus small colony variants

Precit, M.R., Wolter, D.J., Griffith, A., Burns, J.L., Hoffman, L.R.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 67 KB

english, 2015

448

85 Epidemiology of methicillin-resistant Staphylococcus aureus (MRSA) isolated from the respiratory tract of cystic fibrosis patients

Pena Amaya, P., Haim, S., Fernández, S., Di Gregorio, S., Teper, A., Vazquez, M., Lubovich, S., Galanternik, L., Mollerach, M.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 66 KB

english, 2015

449

87 Detection of enterotoxins (A–E) from Staphylococcus aureus isolated from CF sputum: Clinical significance of enterotoxigenic (ET+) strains of S. aureus in paediatric and adult CF patients

Wen, H., McCaughan, J., Schock, B., Reid, A., Rendall, J.C., Elborn, J.S., Downey, D.G., Ennis, M., Moore, J.E.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 67 KB

english, 2015

450

90 Phenotypic and genotypic characteristics of the epidemic clones of Burkholderia cenocepacia strains in patients with cystic fibrosis (CF) in Russian Federation

Shaginyan, I.A., Chernukha, M., Avetisyan, L., Alekseeva, G., Avakian, L., Kashirskaya, N., Kapranov, N.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 68 KB

english, 2015

451

93 Production of virulence factors by Prevotella isolates belonging to the cystic fibrosis (CF) respiratory microbiota

Sherrard, L.J., Matier, T.B., Nixon, K.A., McGrath, S., McIlreavey, L., Hatch, J., Wolfgang, M.C., Muhlebach, M.S., Gilpin, D.F., Elborn, J.S., Tunney, M.M.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 71 KB

english, 2015

452

94 Isolation and characterisation of bacteriophage infecting Prevotella spp. recovered from the cystic fibrosis (CF) airways

Mooney, D., Tunney, M.M., McGrath, S., McIlreavey, L., Einarsson, G., Pattison, S., Johnston, E., Elborn, J.S.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 71 KB

english, 2015

453

95 Susceptibility of CF Prevotella isolates to neutrophil and complement mediated immune clearance

Mooney, D., Tunney, M.M., McGrath, S., McIlreavey, L., Johnston, E., Elborn, J.S.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 71 KB

english, 2015

454

97 A review of inpatient antibiotic prescribing after 7 years – scratching below the surface

Spencer-Clegg, E., Sapino-Vivo, R., Jones, G.H., Walshaw, M.J.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 67 KB

english, 2015

455

98 Antibiotic prescription patterns for the treatment of Spanish cystic fibrosis patients: Results from a national multicentre survey study

Caballero, J.D.D., Del Campo, R., Tato, M., de la Pedrosa, E. Gómez G., Cobo, M., Cantón, R.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 67 KB

english, 2015

456

99 Active surveillance and containment of carbapenemase producing Enterobacteriaceae (CPE) in cystic fibrosis (CF) patients attending an Italian care centre

Morelli, P., Pescetto, L., Casciaro, R., De Alessandri, A., Delfino, E., Bandettini, R.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 67 KB

english, 2015

457

100 Macrolide resistance is common among members of the CF airway microbiota

Sherrard, L.J., Alawsi, F., McGrath, S., McIlreavey, L., Elborn, J.S., Tunney, M.M.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 67 KB

english, 2015

458

102 MRSA eradication in CF patients with lower respiratory tract infection

Vallières, E., Rendall, J.C., Moore, J.E., McCaughan, J., Tunney, M.M., Elborn, J.S., Downey, D.G.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 66 KB

english, 2015

459

104 Antimicrobial susceptibility of Pseudomonas aeruginosa (PA) and Staphylococcus aureus (SA) isolated from CF patients over 13 years

Semczuk, K., Dmeńska, H., Dzierżanowska-Fangrat, K., Dzierżanowska, D., Fronc, B., Szyszkiewicz, A.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 66 KB

english, 2015

460

105 The success of the early eradication therapy regimens for Pseudomonas aeruginosa in cystic fibrosis

Emiraliogˇlu, N., Yalçin, E., Meral, A., Şener, B., Doĝru Ersöz, D., Özçelik, U., Kiper, N.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 70 KB

english, 2015

461

110 Aztreonam for inhalation solution (AZLI) for eradication of new onset Pseudomonas aeruginosa (PA) infection in children with cystic fibrosis (CF): Evaluation of treatment failures

Tiddens, H.A.W.M., De Boeck, K., Clancy, J.P., Fayon, M., Arets, H.G.M., Bresnik, M., Derchak, P.A., Lewis, S.A., Oermann, C.M.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 70 KB

english, 2015

462

116 Pharmacokinetic variability of ciprofloxacin in cystic fibrosis – is CYP3A4 involved?

Schultz, A.N.Ø., Høiby, N., Nielsen, X.C., Pressler, T., Dalhoff, K., Duno, M., Buchard, A., Johansen, H.K., Dalbøge, C.S.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 71 KB

english, 2015

463

118 Efficacy and safety of colistimethate sodium in a paediatric population: Results from the FREEDOM trial

Schuster, A., Pressler, T., Zhu, H., Haberman, R.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 69 KB

english, 2015

464

119 Cellular allergy tests for antibiotic drug hypersensitivity in cystic fibrosis

Röhmel, J., Schwarz, C., Staab, D., Stock, P.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 69 KB

english, 2015

465

120 The prevalence of ticarcillin hypersusceptible Pseudomonas aeruginosa isolates from cystic fibrosis patients compared to non-cystic fibrosis patients

Hettiarachchi, I., Dhillon, R.P., Wootton, M.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 69 KB

english, 2015

466

122 Successful Burkholderia spp. eradication with hypothiocyanite/lactoferrin. In vitro study evidence over a worldwide collection of clinical strains

Sonmez, Y., Bechetoille, C., Perrotto, S., Payet-Burin, A., Juarez-Perez, V.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 70 KB

english, 2015

467

124 Lack of antimicrobial activity of ivacaftor against clinical CF respiratory isolates

Payne, J., McIlreavey, L., McGrath, S., Tunney, M.M., Elborn, J.S.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 70 KB

english, 2015

468

126 A phase 1 clinical study of CTX-4430 in cystic fibrosis patients

Springman, E., Grosswald, R., Philpot, E., MacGregor, G., Horsley, A., Bilton, D., Stewart, J., Elborn, J.S.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 59 KB

english, 2015

469

127 Pharmacokinetic and pharmacodynamic profile of CTX-4430 in two phase 1 studies

Springman, E., Bhatt, L., Grosswald, R., Philpot, E.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 59 KB

english, 2015

470

129 A phase 1 drug-drug interaction study of CTX-4430 assessing CYP3A4 induction

Ahuja, S., Grosswald, R., Christ, D., Bhatt, L., Springman, E.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 59 KB

english, 2015

471

130 Antimicrobial activity of liposomal β-glycan against Pseudomonas aeruginosa isolated from cystic fibrosis patients

Halwani, M., Balkhy, H.H., Khiyami, M.A., Omri, A.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 68 KB

english, 2015

472

132 Respirability assessment of amikacin from a novel dry powder inhaler versus nebulized solution

Balducci, A.G., Borella, F., Bettini, R., Colombo, P., Buttini, F.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 68 KB

english, 2015

473

133 Cost-effectiveness of dry-powder mannitol for inhalation as an add-on to best supportive care (BSC) in the treatment of adult cystic fibrosis (CF) patients in Ireland

Schwenkglenks, M., Toward, T.J., Dooley, B., Burns, R.M., Adams, E.J., Van Stiphout, J.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 68 KB

english, 2015

474

134 Rationale for evaluating (R)-roscovitine (Seliciclib) in patients with cystic fibrosis

Meijer, L., Nelson, D., Riazanski, V., Gabdulkhakova, A.G., Hery-Arnaud, G., Le Berre, R., Loaëc, N., Oumata, N., Galons, H., Nowak, E., Guéganton, L., Dorothée, G., Gray, R.D., Rossi, A.G., Witko-Sar

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 67 KB

english, 2015

475

135 Transformational care at the All Wales Adult CF Centre (AWACFC) – the impact of ivacaftor (Kalydeco®) one year on

Guhaniyogi, L., Speight, L., Lea-Davies, M., Prosser, A., Lau, D., Ketchell, R.I., Duckers, J.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 66 KB

english, 2015

476

136 Long-term tiotropium bromide therapy was retrospectively analyzed in adults with cystic fibrosis

Brandt, C., Thronicke, A., Schwarz, C.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 66 KB

english, 2015

477

137 Omalizumab therapy for allergic bronchopulmonary aspergillosis patients with cystic fibrosis

Emiraliogˇlu, N., Özçelik, U., Yalçın, E., Dogˇru Ersöz, D., Kiper, N.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 66 KB

english, 2015

478

138 Dysregulation of epithelial miR-148b contributes to goblet cell metaplasia, inflammation and alveolar damage in cystic fibrosis lung disease

Agrawal, R., Altamura, S., Stanke, F., Meister, M., Muley, T., Randell, S.H., Greene, C.M., Tümmler, B., Muckenthaler, M.U., Mall, M.A.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 65 KB

english, 2015

479

139 OligoG fluorescent conjugation for localisation in a mucoid pseudomonal biofilm

Pritchard, M.F., Ferguson, E.L., Powell, L.C., Onsøyen, E., Rye, P.D., Hill, K.E., Thomas, D.W.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 65 KB

english, 2015

480

140 Towards the clinical application of anti-pseudomonal bacteriophages: Activity is retained following nebulisation with a range of commercially available nebuliser systems

Pabary, R., Alegro, A., Alton, E., Bilton, D., Morales, S., Smrekar, F., Davies, J.C.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 65 KB

english, 2015

481

144 Effect of treatment with ivacaftor on exhaled nitric oxide

Grasemann, H., Gonska, T., Avolio, J., Tullis, E., Ratjen, F.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 63 KB

english, 2015

482

145 Lung ultrasound in CF children's exacerbation – one center experience

Ciuca, I.M., Pop, L.L.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 63 KB

english, 2015

483

147 Retained absorbable nasal packing after functional endoscopic sinus surgery (FESS) in paediatric cystic fibrosis patients with chronic rhinosinusitis

Aldag, I., West, N., Flemons, L., Mirza, S.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 63 KB

english, 2015

484

150 Influence of the F508del mutation on pulmonary function of patients with cystic fibrosis

Sciuca, S., Esanu, V., Balanetchi, L., Pronoza, M.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 60 KB

english, 2015

485

151 Prevalence of musculoskeletal pain in the Welsh adult cystic fibrosis population

Bridges, C., Rees, A., Caunter, S., Duckers, J.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 63 KB

english, 2015

486

153 The 15 m Shuttle Test is a valuable alternative to conventional shuttle tests in some CF patients

Van Hove, O., Gaspar, V., Opdekamp, C., Nguyen, T.-L., Van Muylem, A., Hanssens, L., Knoop, C., Casimir, G.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 63 KB

english, 2015

487

157 Pulmonary and extrapulmonary determinants of physical activity in adults with cystic fibrosis

Hubert, D., Cormier, C., Neveux, N., Aissat, F., Honoré, I., Chapron, J., Burgel, P.-R.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 62 KB

english, 2015

488

158 Exercise in non-exercising adult cystic fibrosis patients – a year long lottery funded project, Ninewells Hospital, Dundee

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 62 KB

english, 2015

489

160 The prevalence of chronic rhinosinusitis in paediatric cystic fibrosis

Harnett, N., Graham, S.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 62 KB

english, 2015

490

161 The effect of a short-stay revalidation program on lung function parameters and weight

Franckx, H., Verbruggen, T., Lessire, F., Dereeper, S., Chapelle, A.-C., De Guchtenaere, A., De Baets, F., Würth, B.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 63 KB

english, 2015

491

162 A review of non-medical prescribing in an adult CF centre

Forster, E., Henry, A., Bell, N.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 62 KB

english, 2015

492

163 Phoniatric voice rehabilitation in cystic fibrosis

Graziano, L., Tornaghi, M., Giacomodonato, B., Curzi, M., Perelli, T., De Sanctis, S., Varchetta, M., Alatri, F.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 59 KB

english, 2015

493

164 Autogenic drainage and assisted autogenic drainage in children with cystic fibrosis: A systematic review

Corten, L., Jelsma, J., Morrow, B.M.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 59 KB

english, 2015

494

165 “Real world” introduction of tobramycin inhalation powder TIP™ in adults with cystic fibrosis

Langman, H.B., Brennan, A.L., Bright-Thomas, R.J., Jones, A.M., Riley, D.W., Johnson, S.C.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 59 KB

english, 2015

495

166 Improvements in inhalational treatment amongst children using the Philips I-neb insight online software

Yonge, C., Keenan, V., Payne, S., Connett, G.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 59 KB

english, 2015

496

167 Evaluation of the oscillatory Cough Assist E70 in adults with cystic fibrosis (CF)

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 65 KB

english, 2015

497

168 Combining inhalation by a breath-actuated nebulizer (BAN) and exhalation with oscillating positive expiratory pressure device (OPEP) offers potential for simultaneous therapy: A laboratory study

Sharpe, R., Suggett, J., Avvakoumova, V., Schneider, H., Ali, R., Nagel, M.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 65 KB

english, 2015

498

169 The use of Airvo™ high flow humidification with cystic fibrosis patients – development of the service

Muggeridge, N., Lloyd, E.A., Walshaw, M.J., Greenwood, J.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 65 KB

english, 2015

499

170 Safety of nebulised hypertonic saline via Pari eFlow with Pari positive expiratory pressure (PEP) device in circuit for paediatric cystic fibrosis patients

Wilson, P., Lambert, C., Nwokoro, C.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 65 KB

english, 2015

500

172 Does the 60-minute OGTT value have clinical significance in CF adults?

Symes, M., Addy, C., Wotton, C., Bateman, K., Bell, N., Nazareth, D.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 65 KB

english, 2015

501

173 Validation of near patient testing blood capillary glucose for the oral glucose tolerance test in cystic fibrosis

Burgess, J.C., Donovan, J., Berry, H., Gyi, K.M., Bridges, N., Collins, S., Bilton, D., Simmonds, N.J.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 65 KB

english, 2015

502

174 Frequency of diabetic keto-acidosis in children with cystic fibrosis related diabetes

Kapur, A., Gravelle, A., Jenkins, S., Metzger, D., Chilvers, M.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 65 KB

english, 2015

503

175 Diabetes in patients with cystic fibrosis: An update from the DPV registry

Scheuing, N., Konrad, K., Thon, A., Bauer, M., Lilienthal, E., Schebek, M., Szczepanski, R., Holl, R.W.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 68 KB

english, 2015

504

176 Elevation of 90 minutes plasma glucose during oral glucose tolerance testing predicts development of cystic fibrosis related diabetes and lung function decline

Kotnik Pirs, A., Praprotnik, M., Krivec, U., Lepej, D., Bratina, N., Battelino, T., Bratanic, N.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 68 KB

english, 2015

505

180 Evaluation of leptin and ghrelin levels in the blood serum of patients diagnosed with cystic fibrosis

Wiecek, S., Wos, H., Kordys-Darmolinska, B., Sankiewicz-Szkolka, M., Grzybowska-Chlebowczyk, U.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 63 KB

english, 2015

506

181 Loss of the incretin effect in cystic fibrosis related diabetes (CFRD)

Jones, G.H., Dyce, P., Tidbury, N.M., Greenwood, J., Ledson, M.J., Walshaw, M.J.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 62 KB

english, 2015

507

182 Impact of ivacaftor on glycaemic health in patients carrying the G551D mutation

Barry, P.J., Banerjee, A., Horsley, A., Brennan, A.L.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 62 KB

english, 2015

508

183 Intermittent exogenous insulin may prevent progression of dysglycemia in pre-diabetic adults

Dyce, P., Jones, G.H., Walshaw, M.J., Nazareth, D.S., Malone, V.M., Sumner, C.L.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 60 KB

english, 2015

509

184 Utility of an ultra-long acting insulin to treat cystic fibrosis related diabetes

Dyce, P., Jones, G.H., Walshaw, M.J.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 60 KB

english, 2015

510

186 Manifestation and progression of illness in young children with cystic fibrosis: A targeted literature review

O'Sullivan, A.K., Kahle, J.S., VanDevanter, D.R., Sikirica, S., Hodgkins, P.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 60 KB

english, 2015

511

188 Standardized treatment of pulmonary exacerbations (STOP) study: Clinical presentations of pulmonary exacerbations

Sanders, D.B., Goss, C.H., VanDevanter, D.R., Heltse, S.L., Thompson, V., Flume, P.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 62 KB

english, 2015

512

189 Standardized treatment of pulmonary exacerbation (STOP) study: Symptomatic treatment response

Goss, C.H., Heltshe, S.L., Thompson, V., West, N.E., Sanders, D.B., VanDevanter, D.R., Flume, P.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 62 KB

english, 2015

513

190 Frequency and costs of pulmonary exacerbations and association with % predicted FEV1 in patients with cystic fibrosis

Rubin-Cahill, J.L., Thayer, S., Watkins, A., Wagener, J., Hodgkins, P., Schechter, M.S.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 62 KB

english, 2015

514

193 Isolated lung transplantation (LT) for cystic fibrosis patients with portal hypertension (PHT)

Cuquemelle, E., Hillaire, S., Grenet, D., De Miranda, S., Parquin, F.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 69 KB

english, 2015

515

194 Sensorineural hearing loss in patients with cystic fibrosis: A cross-sectional study

Van Hoorenbeeck, K., De Bruyne, N., Lequesne, M., Van de Heyning, P., Verhulst, S., Van Rompaey, V.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 69 KB

english, 2015

516

195 The effect of aminoglycoside antibiotics therapy on audiovestibular function in cystic fibrosis patients at the All Wales Adult Cystic Fibrosis Centre (AWACFC)

Williams, E., Speight, L., Lau, D., Ketchell, R.I., Duckers, J.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 71 KB

english, 2015

517

197 Right ventricular function in Ukrainian children with cystic fibrosis

Rohovyk, N., Ocheretna, O., Bober, L., Rohovyk, M., Zakharus, M., Makuh, H., Devinyak, O.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 71 KB

english, 2015

518

202 Bone mineral density and fractures at the All Wales Adult CF Centre (AWACFC)

Kealaher, E., Speight, L., Stone, M., Lau, D., Ketchell, R.I., Duckers, J.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 64 KB

english, 2015

519

203 Children's bone disease and its risk factors in our centre

Ciuca, I.M., Pop, L.L., Onet, D.I., Guta, B. Almajan, Ranetti, A., Popa, Z.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 64 KB

english, 2015

520

206 Bone quality at the time of lung transplant in cystic fibrosis patients

Mailhot, G., Dion, N., Bureau, N., Jomphe, V., Ferraro, P., Lands, L.C., Ste-Marie, L.-G.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 64 KB

english, 2015

521

208 Long-term and seasonal impact of a vitamin D3 (cholecalciferol) supplementation protocol on vitamin D [25(OH)D] serum levels among cystic fibrosis adults in a Montreal clinic

Mailhot, M., Labrèche, É., Coriati, A., Rabasa-Lhoret, R., Mircescu, H., Berthiaume, Y., Silviet-Carricart, M., Tremblay, F., Lavoie, A.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 65 KB

english, 2015

522

210 Response to vitamin D supplementation protocol in CF pediatric patients

Denis, M.-H., Caron, E., Marcotte, J.-É., Lebel, D.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 60 KB

english, 2015

523

212 Does our current diagnosis of cystic fibrosis related liver disease meet current diagnostic criteria?

Hughes, K., Evans, S., Speight, L., Ketchell, R.I., Lau, D., Duckers, J.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 60 KB

english, 2015

524

213 Diagnosis of liver disease in children with cystic fibrosis: Are we getting it right?

Cheruvalli, V., Lee, T.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 60 KB

english, 2015

525

214 Cystic fibrosis and cirrhosis in Russia

Kondratyeva, E., Kapranov, N., Kashirskaya, N., Sherman, V., Belmer, V.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 51 KB

english, 2015

526

215 Characterization of gastroesophageal reflux with combined multichannel intraluminal impedance–pH (MII-pH) in a group of children with CF

Brecelj, J., Orel, R.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 66 KB

english, 2015

527

216 Gastrostomy button primary placement using an endoscopically guided gastropexy technique in cystic fibrosis: A single centre's early experience

Hutchings, P., Lee, K., Watson, K., Hayee, B., Elston, C.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 66 KB

english, 2015

528

219 Nutritional intervention in paediatric cystic fibrosis patients leads to improvement of nutritional status – Preliminary results of a prospective study

Mexia, S., Asseiceira, I., Rodrigues, T., Pereira, L., Barreto, C.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 66 KB

english, 2015

529

221 Influence of nutritional status of children with cystic fibrosis on disease outcome

Yankov, I., Genkova, N., Bosheva, M.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 63 KB

english, 2015

530

225 Nutritional status of children with cystic fibrosis (CF) in Russia and neighboring territories

Sokolova, I., Roslavtseva, E., Zvonkova, N., Simonova, O., Borovik, T., Bushueva, T., Ignatova, A.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 65 KB

english, 2015

531

226 Ultrasound and adipometer body fat measurement of cystic fibrosis (CF) children and adolescents

Marostica, P., Souza, R., Baptista, R., Filho, J. Heinzmann, Pinto, L., Epifanio, M., Donadio, M.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 65 KB

english, 2015

532

228 The association between nutritional status, serum creatinine and lung function in adults with cystic fibrosis

Hopkins, D., Daniels, T., Marinio, L., Parsons, E.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 67 KB

english, 2015

533

230 History of meconium ileus is associated with low fat tissue mass in children and adolescents with cystic fibrosis

Kaditis, A., Doulgeraki, A., Petrocheilou, A., Katelari, A., Noni, M., Doudounakis, S.-E.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 67 KB

english, 2015

534

231 The effect of ivacaftor on exocrine pancreatic function in patients with cystic fibrosis and the G551D CFTR mutation who are naïve for ivacaftor

McKay, K., Cheah, E., Venuti, E., Gaskin, K.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 67 KB

english, 2015

535

233 Resting energy expenditure in patients with cystic fibrosis decreases after lung transplantation

Hollander, F., Woestenenk, W., Kok, A., de Roos, N., van de Graaf, E.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 66 KB

english, 2015

536

237 Meal and daily variation in enzyme to fat matching in CF patients across a 7 day period: A cross-sectional study

Tierney, A.C., Yuen, A. Tsee Woon, Casamento, J., Fong-To, S.A., Clode, M., King, S.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 62 KB

english, 2015

537

238 How are pancreatic enzymes distributed over mealtimes and meal types?

Declercq, D., De Baets, F., Van Biervliet, S.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 62 KB

english, 2015

538

240 A randomized, double-blind, multicentre, multinational crossover comparison of the pancreatic enzyme product (PEP) APT-1008 (ZENPEP®) to KREON® in the treatment of exocrine pancreatic insufficiency (EPI) associated with cystic fibrosis (CF) in patients ≥12 years of age

Taylor, C.J., Thieroff-Ekerdt, R., Shiff, S., Magnus, L., Fleming, R., Gommoll, C.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 65 KB

english, 2015

539

242 Effects of experimentally induced pancreatic exocrine insufficiency on digestibility of electrolytes (praecaecal/total tract), urinary electrolyte content and acid-base status in young pigs – used as a model for children

Mößeler, A., Höltershinken, M., Kamphues, J.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 65 KB

english, 2015

540

243 Effects of pancreatic exocrine insufficiency on growth, bone density and IGF 1 serum levels of young growing pigs – used as a model for children

Mößeler, A., Liesegang, A., Schwarzmaier, T., Piechotta, M., Kamphues, J.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 65 KB

english, 2015

541

245 Identifying needs in education for children aged 7–8 y and their parents

David, V., Leger, P., You, F., Chevalier, D., Loppinet, V.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 59 KB

english, 2015

542

246 Parental understanding of mutation class-specific treatments for CF and implications for their child's CF

Parmar, S., Latchford, G., Duff, A.J.A., Lee, T.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 59 KB

english, 2015

543

249 Diabetes in cystic fibrosis – education (DICE) – the impact of a structured education programme for the management of cystic fibrosis related diabetes (CFRD) on quality of life

Collins, S., Watson, K., Elston, C., Gyi, K.M.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 60 KB

english, 2015

544

250 Young patients with cystic fibrosis (CF) – a new approach for nutritional care? A dietitian and Youth Ambassador project

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 59 KB

english, 2015

545

251 A personalized education program allows self-management in adult CF patients for intravenous antibiotic therapy at home

Therouanne, S., Menu, R., Prévotat, A., Leroy, S., Wizla, N.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 59 KB

english, 2015

546

256 Understanding the psychological difficulties patients with cystic fibrosis share at annual review

James, K., Phillips, S.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 65 KB

english, 2015

547

257 Administering the PHQ8 and GAD7 in routine UK CF care in situ utilisation in a paediatric and an adult centre

Duff, A.J.A., Bowmer, G., Waldron, R., Cammidge, S., Peckham, D., Latchford, G.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 65 KB

english, 2015

548

259 Improving inpatient cystic fibrosis related diabetes (CFRD) care: The patients’ perspective

Pandya, S., Dyce, P., Walshaw, M.J.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 65 KB

english, 2015

549

263 The good, the bad and the future: Families’ views on the Royal Brompton Hospital (RBH) paediatric cystic fibrosis (CF) homecare service

Dixon, E., Murray, N., Collins, N., Carr, S.B.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 62 KB

english, 2015

550

265 Drug allergy documentation in the All Wales Adult CF Centre (AWACFC)

Basrai, S., Young, M., Lea-Davies, M., Speight, L., Lau, D., Ketchell, R.I., Duckers, J.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 64 KB

english, 2015

551

266 Experience of Mycobacterium abscessus eradication therapy at Aberdeen Royal Infirmary

Griffiths, K.J.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 64 KB

english, 2015

552

269 Living with cystic fibrosis in a remote or rural area

Jessup, M.M., Shields, L., Douglas, T., Smyth, W., Abernethy, G., Priddis, L.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 65 KB

english, 2015

553

270 Home antibiotic treatment in cystic fibrosis: An effective, cost saving and preferred choice among patients with CF

Hatziagorou, E., Chrysochoou, E., Kirvassilis, F., Tsanakas, J.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 65 KB

english, 2015

554

271 The development of a paediatric telephone triage tool in a cystic fibrosis unit in the UK

Bloomer, J., Sharpe, C.A., Sewell, A., Fagan, C.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 65 KB

english, 2015

555

274 Nurse prescribing for children with cystic fibrosis (CF). An initiative to improve service delivery

Sharpe, C.A., Bloomer, J., Sewell, A., Fagin, C.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 62 KB

english, 2015

556

275 A quality improvement program (QIP) aimed at improving nutritional status of cystic fibrosis (CF) patients aged 2–12 years at CF Centre Roscoff: Update at the end of the 3 year period

Revert, K., Pengam, J., Madec, M.-L., Audran, L., Maitrallin, L., Lesné, P.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 62 KB

english, 2015

557

278 Depression, anxiety and adherence to inhalation therapy in adolescents and adults with cystic fibrosis

Fidika, A., Goldbeck, L.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 64 KB

english, 2015

558

279 Prevalence of pain in adults with CF with and without lung transplantation

Van Wijngaerden, M., Colpaert, K., Dupont, L.J.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 64 KB

english, 2015

559

282 A preventative psychosocial care approach (PPCA) for promoting psychological wellbeing for people with CF (PWCF) and their caregivers

Oxley, H., Bryon, M., Brewin, P.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 62 KB

english, 2015

560

284 The Quality of Life (QoL) after lung transplantation (LT) between omnipotence, denial and reality principle

Catastini, P., Martellacci, A., Braggion, C.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 62 KB

english, 2015

561

286 Emotional distress, coping and quality of life in children with cystic fibrosis: A cross-cultural study

Touchèque, M., Duncan, C., Bee, C., Orenstein, D., Moffett, K., Casimir, G., Sacré, J.-P, Pierart, F., Malfroot, A., Etienne, A.-M.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 66 KB

english, 2015

562

288 Resilience, intolerance of uncertainty, and CF patients’ quality of life

Mitmansgruber, H., Rabanser, B., Smrekar, U., Beck, T., Niedermayr, K., Eder, J., Ellemunter, H.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 65 KB

english, 2015

563

289 How do men and women with cystic fibrosis think their illness and associated experiences affects their body image, sexuality, relationships and their ideas about parenthood?

Anderson, R., Pearce, A., Graham, C.A., Ingham, R.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 59 KB

english, 2015

564

291 The views of adolescents with CF on their transition and transfer to adult services

Bowmer, G., Duff, A.J.A., Sowerby, C.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 59 KB

english, 2015

565

293 Understanding young people's anxiety about transitioning from paediatric to adult services – a service improvement project

Massey-Chase, R.A., O'Dea, B., Reilly, C.C., Perrin, F., Macedo, P., Elston, C.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 61 KB

english, 2015

566

294 Aspiring to independence: The personal experiences of young people with cystic fibrosis, asthma and healthy controls

Gladwell, D.J., Owen, J., West, N.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 61 KB

english, 2015

567

295 Cognition in adult patients with cystic fibrosis (CF) with and without cystic fibrosis related diabetes (CFRD)

Chadwick, H.K., Morton, A.M., Driffill, A., Wood, A., Gillgrass, L., Dye, L., Lawton, C., Mansfield, M.W., Peckham, D.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 61 KB

english, 2015

568

297 Does socioeconomic status correlate with clinical outcomes in children with CF in Southwestern Ontario?

Chauhan, N., Cassidy, K., Cooper, A., Itterman, J., Price, A.K.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 64 KB

english, 2015

569

301 Contraceptive practices and gynecological survey in women with cystic fibrosis

Jablonski, C. Rousset, Nove-Josserand, R., Perceval, M., Reynaud, Q., Durupt, S., Lega, J.-C., Durieu, I.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 52 KB

english, 2015

570

302 MucoDoméos: An electronic medical record (SMR) dedicated to the CF patients

Bonomo, E., Lemonnier, L., Colomb-Jung, V., Vernhet, P., Brémont, F., Jan, G.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 66 KB

english, 2015

571

304 Children with typical CF have better spirometric data than children with non CF bronchiectasis (BE) – a Belgian multicentric study

Godding, V., De Baets, F., De Boeck, K., Malfroot, A., Lebecque, P.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 66 KB

english, 2015

572

305 CF registry in Northern Greece over a 7 year period

Hatziagorou, E., Manika, K., Kioumis, J., Vantsi, P., Karailidou, M., Tsourtsoulas, A., Sourla, E., Tzetis, M., Tsanakas, J.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 66 KB

english, 2015

573

307 Cystic Fibrosis Patient Registry of Moscow and Moscow Region (CFPRMMO) in 2010–2012

Amelina, E., Krasovsky, A., Voronkova, A., Cherniak, A., Gorinova, Y., Kashirskaya, N., Kondratieva, E., Nikonova, V., Shabalova, L., Shelepneva, N., Sherman, V., Simonova, O., Usacheva, M., Kapranov,

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 63 KB

english, 2015

574

314 Missed newborn screening for CF presenting to the haematologists

Kavaliunaite, E., Owen, E., Wallis, C.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 66 KB

english, 2015

575

315 Late diagnosis of CF in a family with R117H

McNeilly, J., Rendall, J.C., Elborn, J.S., Downey, D.G.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 66 KB

english, 2015

576

316 A longitudinal investigation of genomic and phenotypic factors leading to adaptation of Pseusomonas aeruginosa in a cystic fibrosis patient

D'Arcangelo, S., Bailey, K.E., Jousson, O.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 66 KB

english, 2015

577

318 Candida blankii: New agent in cystic fibrosis airways?

Zaragoza, S., Galanternik, L., Vazquez, M., Teper, A., Córdoba, S., Finquelievich, J.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 71 KB

english, 2015

578

321 Changes in lung function and airway microbiology following ivacaftor therapy in an adult G551D homozygote

Green, H., Barry, P.J., Paisey, C., Smith, A., Jones, A., Horsley, A., Marchesi, J., Mahenthiralingham, E.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 71 KB

english, 2015

579

322 A case of asymptomatic exercise and Wolff–Parkinson–White syndrome: Physio's be aware!

Douglas, H., Ledger, S., Main, E., Rand, S., Giardini, A., Aurora, P.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 62 KB

english, 2015

580

324 Thrombo-embolic disease in CF patients: Difficult to diagnose, difficult to treat

Pirson, J., Etienne, I., Ruiz-Patino, M., Sokolow, Y., Knoop, C.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 62 KB

english, 2015

581

327 Severe anemia in infancy may be the first sign of cystic fibrosis

Sismanlar, T., Aslan, A., Ezgu, F.S., Ciftci, B.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 65 KB

english, 2015

582

329 Partial recovery of exocrine pancreatic function and intestinal fat absorption after ivacaftor treatment

Zwolsman, M.G., Koppelman, G.H., Rottier, B.L., Bodewes, F.A.J.A.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 65 KB

english, 2015

583

330 Hepatopulmonary syndrome may mask cystic fibrosis

Aslan, A., Sismanlar, T., Sarı, S., Dalgic, B., Oguz, D., Ezgu, F.S.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 51 KB

english, 2015

584

Author Index

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 87 KB

english, 2015

585

Association between the introduction of a new cystic fibrosis inhaled antibiotic class and change in prevalence of patients receiving multiple inhaled antibiotic classes

Dasenbrook, Elliott C., Konstan, Michael W., VanDevanter, Donald R.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 325 KB

english, 2015

586

Prevalence of Scedosporium species and Lomentospora prolificans in patients with cystic fibrosis in a multicenter trial by use of a selective medium

Sedlacek, L., Graf, B., Schwarz, C., Albert, F., Peter, S., Würstl, B., Wagner, S., Klotz, M., Becker, A., Haase, G., Laniado, G., Kahl, B., Suerbaum, S., Seibold, M., Tintelnot, K.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 331 KB

english, 2015

587

News

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 164 KB

english, 2015

588

WS05.2 30 day challenge – using social media to support adult CF patients to exercise in the adult CF service Dundee

Smith, A., Gouick, L.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 62 KB

english, 2015

589

WS04.5 Vitamin D influence on respiratory exacerbations and hospitalizations in cystic fibrosis patients

Abu-Fraiha, Y., Elyashar-Earon, H., Shoseyov, D., Cohen-Cymberknoh, M., Armoni, S., Kerem, E., Wilschanski, M.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 59 KB

english, 2015

590

191 Lung function and health care resource utilization in patients with cystic fibrosis

Rubin-Cahill, J.L., Thayer, S., Watkins, A., Wagener, J., Hodgkins, P., Schechter, M.S.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 69 KB

english, 2015

591

Adherence to Ivacaftor is suboptimal

Abbott, Janice, Bilton, Diana

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 114 KB

english, 2015

592

Editorial Board

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 98 KB

english, 2015

593

News

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 147 KB

english, 2015

594

Equivalent substrates enable simultaneous study of gastrointestinal pH and CF-related diabetes

Borowitz, Drucy, Gelfond, Daniel

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 306 KB

english, 2015

595

Impact of storage conditions on metabolite profiles of sputum samples from persons with cystic fibrosis

Zhao, Jiangchao, Evans, Charles R., Carmody, Lisa A., LiPuma, John J.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 517 KB

english, 2015

596

Insulin secretion abnormalities in exocrine pancreatic sufficient cystic fibrosis patients

Wooldridge, Jamie L., Szczesniak, Rhonda D., Fenchel, Matthew C., Elder, Deborah A.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 281 KB

english, 2015

597

News

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 296 KB

english, 2015

598

The ideal and the real world of mental health care delivery

Ullrich, Gerald, Steinkamp, Gratiana, Stahl, Katja

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 104 KB

english, 2015

599

Effect of ivacaftor therapy on exhaled nitric oxide in patients with cystic fibrosis

Grasemann, Hartmut, Gonska, Tanja, Avolio, Julie, Klingel, Michelle, Tullis, Elizabeth, Ratjen, Felix

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 291 KB

english, 2015

600

Should we monitor exhaled NO to assess the restoration of CFTR function in CF patients

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 96 KB

english, 2015

601

Enhancement of Pulmozyme activity in purulent sputum by combination with poly-aspartic acid or gelsolin

Bucki, Robert, Cruz, Katrina, Pogoda, Katarzyna, Eggert, Ashley, Chin, LiKang, Ferrin, Marianne, Imbesi, Giovanna, Hadjiliadis, Denis, Janmey, Paul A.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 1.07 MB

english, 2015

602

Is the home environment an important factor in the occurrence of fungal events in cystic fibrosis?

Sapet, A., Normand, A.C., Oudyi, M., Le Bel, N. Stremler-, Piarroux, R., Dubus, J.C.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 278 KB

english, 2015

603

The epidemiology of poor outcomes after pulmonary exacerbations

Sanders, Don B.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 109 KB

english, 2015

604

Risk of hemoptysis in cystic fibrosis clinical trials: A retrospective cohort study

Thompson, V., Mayer-Hamblett, N., Kloster, M., Bilton, D., Flume, P.A.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 323 KB

english, 2015

605

Implications of multiple freeze-thawing on respiratory samples for culture-independent analyses

Cuthbertson, Leah, Rogers, Geraint B., Walker, Alan W., Oliver, Anna, Hoffman, Lucas R., Carroll, Mary P., Parkhill, Julian, Bruce, Kenneth D., van der Gast, Christopher J.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 308 KB

english, 2015

606

Acute effects of viral respiratory tract infections on sputum bacterial density during CF pulmonary exacerbations

Chin, Melanie, De Zoysa, Maya, Slinger, Robert, Gaudet, Ena, Vandemheen, Katherine L., Chan, Francis, Hyde, Lucie, Mah, Thien-Fah, Ferris, Wendy, Mallick, Ranjeeta, Aaron, Shawn D.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 580 KB

english, 2015

607

Osteopontin is increased in cystic fibrosis and can skew the functional balance between ELR-positive and ELR-negative CXC-chemokines

Jovic, Sandra, Shikhagaie, Medya, Mörgelin, Matthias, Erjefält, Jonas S., Kjellström, Sven, Egesten, Arne

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 2.14 MB

english, 2015

608

Experience of care from the perspective of individuals with cystic fibrosis and families: Results from 70 CF Foundation accredited programs in the USA

Homa, Karen, Sabadosa, Kathryn A., Marrow, Laura C., Marshall, Bruce C.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 230 KB

english, 2015

609

The influence of breathing mode on tobramycin serum levels using the I-neb AAD system in adults with cystic fibrosis

van Velzen, A.J., Uges, J.W.F., Le Brun, P.P.H., Shahbabai, P., Touw, D.J., Heijerman, H.G.M.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 311 KB

english, 2015

610

Strain rate echocardiography uncovers subclinical left ventricular dysfunction in cystic fibrosis

Sellers, Zachary M., McGlocklin, Lori, Brasch, Andrea

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 343 KB

english, 2015

611

Intraductal papillary mucinous neoplasm of the pancreas in an adult patient with cystic fibrosis after double-lung transplantation

Eigner, W., Mesteri, I., Tribl, B., Ba-Ssalamah, A., Friedl, J., Trauner, M., Kazemi-Shirazi, L.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 364 KB

english, 2015

612

Can biliary endoscopy play a role in liver disease associated to cystic fibrosis?

Cantù, P., Claut, L., Elvevi, A., Parzanese, I., Maggioni, M., Conte, D., Penagini, R., Colombo, C.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 789 KB

english, 2015

613

Sorting out the gray zone: Cystic fibrosis newborn screening

McColley, Susanna A.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 116 KB

english, 2015

614

Editorial Board

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 56 KB

english, 2015

615

Finding new drugs to enhance anion secretion in cystic fibrosis: Toward suitable systems for better drug screening. Report on the pre-conference meeting to the 12th ECFS Basic Science Conference, Albufeira, 25–28 March 2015

Verkman, Alan S., Edelman, Aleksander, Amaral, Margarida, Mall, Marcus A., Beekman, Jeffrey M., Meiners, Torsten, Galietta, Luis J.V., Bear, Christine E.

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 207 KB

english, 2015

616

Editorial Board

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 1.40 MB

english, 2015

617

News

Quittner, Alexandra, Abbott, Janice

Journal:

Journal of Cystic Fibrosis

Year:

2015

Language:

english

File:

PDF, 129 KB

english, 2015

To build up a library is to create a life. It’s never just a random collection of books.

— Carlos María Domínguez

Official channel

Z-Library Desktop Launcher

Tor version

Z-Library

Z-Library Since 2009 support@z-lib.do

EnglishРусскийEspañolItalianoελληνικάاللغة العربيةBahasa IndonesiaBahasa Malaysiaहिन्दीDeutschFrançaisPortuguêsУкраїнськаPolski中文繁體中文日本語Tiếng ViệtAzərbaycan DiliՀայոց լեզուภาษาไทยTürk Diliქართველიবাংলাپښتوతెలుగుاردو한국어SrpskiБългарски