Volume 7; Issue supp-S2

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Journal of Cystic Fibrosis
Volume 7; Issue supp-S2

Journal of Cystic Fibrosis

Volume 7; Issue supp-S2

1

Editorial Board

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 35 KB

english, 2008

2

Foreword

Petr Pohunek, Milan Macek

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 49 KB

english, 2008

3

ENaC mutations in patients with CF-like disease

A.K. Azad, R. Rauh, J. Korbmacher, F. Stanke, H. Nuytten, B. Tümmler, K. De Boeck, L. Dupont, Y. Fichou, C. Ferec, E. Girodon, P. Lebecque, V. Skalicka, M. des Georges, M. Claustres, L. Hjelte, I. de

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 57 KB

english, 2008

4

The β-defensin region affects CF lung disease severity

H. Nuytten, C. De Boeck, J. Van Eldere, M. Macek, M. Stuhrmann, M. Schwartz, C. Castellani, M. Schwarz, H. Cuppens

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 57 KB

english, 2008

5

Disease severity in cystic fibrosis is modified by variants of the syntaxin 1A gene

T. von Kanel, J. Racine, R. Kraemer, F. Stanke, M. Schneider, A. Schaller, S. Gallati

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 57 KB

english, 2008

6

COX2 as a protective modifier of CF pulmonary disease severity

K. Czerska, A. Sobczynska-Tomaszewska, D. Sands, A. Nowakowska, K. Wertheim, D. Bak, J. Zielenski, J. Bai

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 57 KB

english, 2008

7

Modifiers genes' influence in pulmonary disease in a group of Mexican patients with cystic fibrosis

M.D. Chavez, E. Yokoyama, V. Camilo, F. Cuevas, A. Carnevale, J. Lezana, M. Macias, L. Orozco

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 50 KB

english, 2008

8

The CFTR M470V gene variant as a potential modifier of COPD severity

M. Stankovic, A. Nikolic, A. Divac, A. Tomovic, N. Petrovic-Stanojevic, M. Andjelic, V. Dopudja-Pantic, M. Mitic-Milikic, D. Radoikovic

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 50 KB

english, 2008

9

Analysis of eNOS, TNFA, LTA, GSTM1, MBL2, HFE genes as modifier genes in Russian cystic fibrosis patients

E.E. Timkovskaya, N.V. Petrova, N.J. Kashirskaya, R.A. Zinchenko

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 50 KB

english, 2008

10

The role of TGFbetal as modifier gene in Italian cystic fibrosis patients

M.D. Bettin, C. Bombieri, G. Malerba, L. Xumerle, F. Belpinati, C. Castellani, B.M. Assael, P.F. Pignatti

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 50 KB

english, 2008

11

Single Nucleotide Polymorphisms (SNPs) in genes of the innate immunity in cystic fibrosis patients: correlation with lung function and Pseudomonas aeruginosa colonisation

F. Haerynck, R. Rossau, E. De Meester, S. Van daele, P. Schelstraete, F. De Baets

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 65 KB

english, 2008

12

Cytokine polymorphisms influence lung disease progression in cystic fibrosis

H. Corvol, P.Y. Boelle, J. Brouard, N. Knauer, A. Henrion-Caude, K. Chadelat, C. Flamant, C. Charlier, M. Boule, B. Fauroux, C. Vallet, J. Feingold, F. Ratjen, H. Grasemann, A. Clement

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 65 KB

english, 2008

13

Hypoglycosylation and disease modifying polymorphism in cystic fibrosis

E. Marklova, Z. Albahri, H. Vanicek, V. Vavrova, V. Sedlak, A.M. Ali

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 65 KB

english, 2008

14

Do in silico tools predict the clinical consequences of CFTR missense mutations?

R. Dorfman, T. Nalpathamkalam, C. Taylor, T. Gonska, X. Yuan, Q. Huang, F. Lin, B. Jiang, M. Corey, L. Tsui, P. Durie, J. Zielenski

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 65 KB

english, 2008

15

Mutation scanning of the CFTR gene by high-resolution melting analysis (HRM)

P. Krenkova, A. Stambergova, P. Norambuena, M. Macek Jr.

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 47 KB

english, 2008

16

An automated methodology for high-throughput mutational analysis of CFTR

M. Lucarelli, G. Ferraguti, S.M. Bruno, S. Pierandrei, L. Narzi, A. Di Gioia, F. Ceci, S. Quattrucci, R. Strom

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 47 KB

english, 2008

17

Rapid detection of mutations in the CFTR gene using high-resolution melting analysis

M.P. Audrezet, A. Dabricot, C. Le Marechal, C. Fére

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 47 KB

english, 2008

18

Detection of large intra-CFTR rearrangements by MLPA: utilization of a new web-based software “eMLPA” for the analysis of raw data

J. Camajova, J. Krhounek, M. Hancarova, J. Vejvalka, M. Macek Sr, M. Macek

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 47 KB

english, 2008

19

Method validation in cystic fibrosis DNA diagnostics: a basic tool for quality assurance

A. Stambergova, J. Camajova, M. Macek Jr.

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 55 KB

english, 2008

20

Validating assays for relative quantification of cDNA CFTR from nasal epithelial brushing

L. Masvidal, A. Alvarez, L. Ruano, X. de Gracia, T. Casals

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 55 KB

english, 2008

21

Does the R117H mutation cause cystic fibrosis or not?

A. Norek, A. Sobczynska-Tomaszewska, J.K. Wolski, D. Sands, M. Trawinska-Bartnicka, E. Sapiejko, K. Czerska, K. Wertheim, J. Bai

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 55 KB

english, 2008

22

The variable phenotype of (TGJ^Ts or L997F compound heterozygotes

L. Narzi, A. Stamato, R. Cresta, S.M. Bruno, F. Narzi, S. Pierandrei, S. Quattrucci, R. Strom, M. Lucarelli

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 55 KB

english, 2008

23

Genotypes and borderline sweat tests in Irish CF patients -an update

C.M. King, M. Rogers, T. McDevitt, D. Lambert, D.E. Barton, S.A. Lynch

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 54 KB

english, 2008

24

Genotype-phenotype correlation in Russian CF patients

N.V. Petrova, E.E. Timkovskaya, R.A. Zinchenko, N.J. Kashirskaya

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 54 KB

english, 2008

25

CF gene large deletions: possible genotype/phenotype association

T. Repetto, C. Centrone, E. Pelo, M. Cavicchi, F. Torricelli

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 54 KB

english, 2008

26

Extensive genetic analysis in non-classic CF patients

Y. Fichou, M.P. Audrézet, P. Trouvé, A. Chauvin, C. Le Maréchal, C. Ferec

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 58 KB

english, 2008

27

Molecular cellular and functional study of seven rare mutations of CFTR

F. Fresquet, A. Sterlin, P. Melin, M. Baudis, M.C. Pasquet, F. Becq, A. Kitzis, F. Bilan

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 58 KB

english, 2008

28

Identification and characterization of three CFTR gene partial duplications

M. Legendre, A. LeFloch, F. Niel, C. Gameiro, J. Martin, D. Grenet, J. Derelle, V. Izard, C. Costa, M. Goossens, E. Girodon

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 58 KB

english, 2008

29

Chronic sinusitis in CF child carrying two missense mutations S519G and G576A in the NBF1 domain of CFTR

M.N. Feuillet-Fieux, J.P. Bonnefont, M. Ferrec, I. Sermet, B. Lacour, G. Lenoir

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 58 KB

english, 2008

30

Results of molecular-genetic testing of the CFTR gene mutations in Western Ukraine

H. Makukh, A. Melnyk, M. Tyrkus, L. Bober, O. Hnateyko

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 60 KB

english, 2008

31

Limits of standard kits for CF genetic test in Romania

L. Pop, I. Popa, L. Tamas, A. Anghel, Z. Popa, I.M. Ciuca, S. Turcu

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 60 KB

english, 2008

32

DNA analysis of CFTR gene on Department of Medical Genetics, University Hospital Brno 1992-2007

R. Gaillyová, I. Valáškova, I. Bartejsová, P. Havlíčková

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 60 KB

english, 2008

33

CF incidence calculated from heterozygote frequencies in Brazil

L.V. Arruda, C.A. Correia, A.F. Ribeiro, J.D. Ribeiro, C.S. Bertuzzo

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 60 KB

english, 2008

34

CFTR gene mutations in IRT/DNA cystic fibrosis newborn screening in Poland

A. Sobczynska-Tomaszewska, M. Oltarzewski, K. Wertheim, A. Norek, K. Czerska, D. Sands, K. Zybert, J. Bal

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 44 KB

english, 2008

35

Establishing sweat salt levels in normal healthy adults

P. Senthamilarasu, R. Jayaraj, S. Jakka, C. Grime, N. Vadalamudi, P. Barton, D. Isherwood, K.W. Southern

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 60 KB

english, 2008

36

Report of a new and important cause of falsely positive sweat test

K.P. Foote, S. Struthers, H. Barbour

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 60 KB

english, 2008

37

Intestinal current measurement for difficult CF diagnosis: reference values and reproducibility

N. Derichs, C. Stolpe, B. Tümmler, M. Ballmann

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 60 KB

english, 2008

38

Nasal potential difference in non classic cystic fibrosis – long term follow up

Y. Yaakov, R. Jaron, J. Rivlin, H. Blau, L. Bentur, Y. Yahav, E. Kerem, H. Bibi, E. Picard, M. Wilschanski

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 60 KB

english, 2008

39

“Adult onset CF”: previous misdiagnoses

M. Asim, A. Navi, N. Sinnott, S. Baird, M.J. Walshaw, M.J. Ledson

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 57 KB

english, 2008

40

Prognosis and clinical features of adult diagnosis CF

M. Asim, A. Navi, S. Baird, N. Sinnott, M.J. Walshaw, M.J. Ledson

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 57 KB

english, 2008

41

Dehydration: a common clinical feature suggesting the diagnosis of CF in Greece

T. Zervou, A. Katelari, D. Beri, I. Inglezos, S. Doudounakis

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 57 KB

english, 2008

42

Reproductive attitudes of parents of CF child: pregnancy termination vs choice to maintain an affected pregnancy

I. Duguépéroux, V. Scotet, M.P. Audrézet, M. Blayau, H. Journel, P. Parent, C. Férec

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 57 KB

english, 2008

43

Cascade carrier testing for cystic fibrosis: an Australian experience

B.J. McClaren, M.A. Aitken, R.J. Massie, S.A. Metcalfe, D.J. Amor

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 58 KB

english, 2008

44

A French collaborative study indicative of a very low classical-CF penetrance of R117H; implications for genetic counselling

C. Thauvin-Robinet, A. Munck, F. Huet, G. Bellis, E. Gautier, C. Férec, M. Audrézet, M. Claustres, M. DesGeorges, G. Lalau, T. Bienvenu, E. Bieth, B. Gerard, I. Sermet, G. Rault, J. Flori, J. Lafitte,

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 58 KB

english, 2008

45

Prenatal genetic diagnosis in cystic fibrosis by ARMS-PCR method and STR genotyping

L.A. Tamas, I. Popa, L. Pop, A. Anghel, Z. Popa, C. Samoila, I.M. Ciuca, A. Neghina, F. Lenghel, C. Gug

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 58 KB

english, 2008

46

Molecular strategy in hyperechogenic fetal bowel

V. Paracchini, D. Coviello, L. Costantino, L. Porcaro, P. Capasso, D. Degiorgio, M.C. Russo, C. Colombo, M. Seia

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 58 KB

english, 2008

47

Newborn screening for cystic fibrosis in the eastern part of Saxon ia

J. Hammermann, M. Stopsack, A. Rösen-Wolff, M. Gahr

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 57 KB

english, 2008

48

First year of Polish National CF Newborn Screening

D.A. Sands, K. Zybert, M. Oltarzewski, A. Sobczynska-Tomaszewska, K. Czerska, A. Norek, R. Piotrowski, A. Milanowski

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 57 KB

english, 2008

49

First results of newborn screening program for CF in Russia

V.D. Tolstova, N.Y. Kashirskaya, N.I. Kapranov, A.A. Khodunova, E.V. Denisenkova, E.V. Smazhil

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 57 KB

english, 2008

50

CF diagnosis in older siblings after a CF diagnosis via newborn screening: an additional benefit for NBS?

A. Munck, E. Houssin, M. Roussey, CF care centres

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 57 KB

english, 2008

51

Impact on physiotherapy workload at the Leeds Regional Paediatric CF Unit following the first full year of the UK National CF Screening Programme

R. Ball, K. Brownlee, T. Lee, S. Conway

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 61 KB

english, 2008

52

Clinical outcome and CF care costs justify the need of newborn screening

V. Skalicka, D. Zemkova, T. Fischerova, L. Pelikan, F. Votava, V. Vavrova

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 61 KB

english, 2008

53

Results of DNA-based cystic fibrosis newborn screening proficiency testing

A. Laxova, M. Earley, P. Farrell, P. Mogayzel, H. Hannon

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 61 KB

english, 2008

54

Hepatic enzyme changes in cystic fibrosis (CF) newborn screened babies: incidence, risk factors and evolution

R.S. Malheiros, F.C. Reis, L.A. Peret, A.S. Braga, F.F. Mattos, A.A. Vergara, S.O. Melo

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 61 KB

english, 2008

55

Impact of patient hematocrit on CF newborn screening results

H. Wilde, M. Montgomery, L. Baskin, D. Gray, M. Lyon

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 53 KB

english, 2008

56

Parental experience of the CF Service in the first year after diagnosis

M. Musgrave, R. lies, M. Polichroniadis, D. McShane

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 53 KB

english, 2008

57

Insights into the structural features of the full length CFTR protein

J.P. Mornon, P. Lehn, I. Callebaut

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 59 KB

english, 2008

58

Structural characterization of novel CBAVD-causing mutations located in CFTR NBDs

A. Grangeia, A.M. Damas, F. Carvalho, M. Sousa, A. Barras

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 59 KB

english, 2008

59

CFTR missing the first four transmembrane segments enhances wild type and ΔF508 CFTR processing

L. Cebotaru, N. Vij, I. Ciobanu, J. Wright, W. Guggino

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 59 KB

english, 2008

60

The revertant mutants G550E and 4RK alter the processing efficiency and gating behaviour of the CF mutant G551D

L.S. Pissarra, Z. Xu, C.M. Farinha, D.N. Sheppard, M.D. Amaral

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 59 KB

english, 2008

61

Pathways for transport of CFTR

A.A. Mironov, R. Parashuraman, G.V. Beznoussenko, A. Luini

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 52 KB

english, 2008

62

The role of butyrate in CFTR-ENaC interactions

C. Iordache, M. Duszyk

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 52 KB

english, 2008

63

Annexin A5 increases the cell surface expression and the chloride channel function of the ΔF508-cystic fibrosis transmembrane regulator

P. Trouve, M.A. Le Drévo, N. Benz, M. Kerbiriou, M.A. Giroux-Metges, J.P. Pennec, C. Férec

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 52 KB

english, 2008

64

SUMOylation is necessary for CFTR trafficking

C. Schulze, M. Illenyi, P. Pagel, J. Tausendfreund, A. Roseher, D. Reinhardt, J. Glöckner-Pagel

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 52 KB

english, 2008

65

Renal cyst formation as tool for CFTR research

H. Li, W. Yang, F. Mendes, M.D. Amaral, D.N. Sheppard

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 58 KB

english, 2008

66

Activation of chloride secretion in human airway epithelial cells by a new pyrrolo[2,3-b]pyrazine

L. Dannhoffer, P. Melin, C. Faveau, B. Boucherle, C. Jayle, P. Corbi, Y. Mettey, J.L. Décout, F. Becq

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 58 KB

english, 2008

67

G622 amino acid has a crucial role in pharmacological activation of CFTR chloride channel by benzo[c]quinolizinium compounds

A. Billet, P. Melin, C. Norez, F. Bilan, Y. Mettey, E. Becq

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 58 KB

english, 2008

68

Ezrin and cAMP/PKA have different compartmentalization in CFBE410- and 16HBE14o- cells

S. Monterisi, M. Favia, L. Guerra, T. Fanelli, S.J. Reshkin, M. Zaccolo, M. Conese, V. Casavola

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 58 KB

english, 2008

69

The CD73/adenosine pathway regulates gap junctional intercellular communication in the CFTR-expressing Calu-3 airway cell line

L.K. Scheckenbach, M. Chanson

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 63 KB

english, 2008

70

β-adrenoceptors remodelling in cystic fibrosis human bronchi

E. Silantieff, F. Bossard, E. Lavazais Blancou, C. Gauthier

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 63 KB

english, 2008

71

Activity of lysosomal carboxypeptidase A in mixed saliva of cystic fibrosis patients

L. Minarowski, A. Minarowska, A. Karwowska, D. Sands

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 63 KB

english, 2008

72

Nicotinic receptor a7 regulates CFTR-dependent ion transport in the airway epithelium

J.M. Tournier, K. Maouche, J.M. Zahm, F. Delavoie, C. Coraux, I. Cloez-Tayarani, P. Birembaut

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 63 KB

english, 2008

73

Incidence of cartilage abnormalities on tracheal function in CFTR-deficient mice

E. Bonvin, P. Le Rouzic, J.F. Bernaudin, C.H. Cottart, C. Vandebrouck, T. Leal, A. Clement, M. Bonora

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 61 KB

english, 2008

74

Regulation of the KCa3.1 channel by AMP-activated protein kinase in Cl− secreting cells

H. Klein, L. Garneau, F. Dionne, M.A. Rober, E. Goupil, D. Thuringer, L. Parent, E. Brochiero, R. Sauve

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 61 KB

english, 2008

75

Expression of cystic fibrosis transmembrane regulator (CFTR) in human bone cells

C.A. Beeton, A.M. Condliffe, E.F. Shead, C.S. Haworth, J.E. Compston

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 61 KB

english, 2008

76

Inflammation and abnormal tissue remodeling in F508del mutant mice

R.M. Buijs-Offerman, J. Aarbiou, H. Jorna, M. Wilke, B.J. Scholte

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 61 KB

english, 2008

77

Transcriptional profile of human airway cells during the epithelial regeneration

C. Coraux, B. Marcet, J. Roux, T. Jolly, P. Barbry, P. Birembaut

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 61 KB

english, 2008

78

Transepithelial ion transport: the relationship with long-term survivors of cystic fibrosis

N.J. Simmonds, L. D'Souza, M. Roughton, J.C. Davies, E.W. Alton, M.E. Hodson

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 61 KB

english, 2008

79

Nasal potential difference testing – the effect of different glucose and chloride concentrations

P.G. Middleton, H.H. House

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 61 KB

english, 2008

80

Lentiviral transduction of differentiated airway epithelial cells in culture is enhanced by lysophosphatidylcholine

J. Aarbiou, R.M. Buijs-Offerman, P. van der Wegen, H.J. Jorna, B.J. Scholte

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 61 KB

english, 2008

81

Facilitation of lentiviral-mediated transduction of airway epithelial cells by magnetofection

C. Orlando, E. Copreni, O. Mykhaylyk, S. Castellani, O. Zelphati, C. Plank, M. Conese

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 61 KB

english, 2008

82

Transient in utero expression of CFTR does not improve survival of CF knockout mice

D.R. Gill, A. Varathalingam, H. Painter, A.E. Lawton, S.G. Sumner-Jones, G.A. Nunez-Alonso, M. Chan, F. Munkonge, E.W. Alton, S.C. Hyde, L.A. Davies

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 61 KB

english, 2008

83

PTC124 induces CFTR full-length production and activity in children with nonsense-mutation-mediated CF

I. Sermet-Gaudelus, T. Leal, K. De Boeck, G. Casimir, L. Hanssens, P. Hage, D. Roussel, A. Mogenet, S. Hirawat, G.L. Elfring, S. Constantine, L.L. Miller

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 61 KB

english, 2008

84

PTC124 treatment over 3 months improves pharmacodynamic and clinical parameters in patients with nonsense-mutation-mediated CF

M. Wilschanski, S. Armoni, Y. Yaakov, H. Blau, D. Shoseyov, M. Cohen, S. Hirawat, G.L. Elfring, A. Reha, L.L. Miller, E. Kerem

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 61 KB

english, 2008

85

Moli1901 (duramycin) increases chloride transport in cystic fibrosis airway epithelial and pancreatic cell lines

I. Oliynyk, G. Varelo gianni, G.M. Roomans, M. Johannesson

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 55 KB

english, 2008

86

Safety tolerability and efficacy of multiple doses of aerosolised Moli1901 in adolescents and adults with cystic fibrosis

E. Eber, H. Grasemann, G.H. Thalhammer, R. Widmann, F. Ratjen

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 55 KB

english, 2008

87

Preventive but not late amiloride therapy reduces morbidity and mortality of cystic fibrosis-like lung disease in mice

D. Treis, Z. Zhou, S. Schubert, M. Harm, J. Schatterny, S. Hirtz, J. Duerr, R.C. Boucher, M.A. Mall

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 55 KB

english, 2008

88

Duration of decreasing the nasal potential difference by amiloride-mannitol dry powder

P. Schüler, S. Luigart, S. Prange-Schmidt, C. Geidel, K.P. Zimmer, J. Pabst, H. Lindemann

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 55 KB

english, 2008

89

Hypertonie saline: effect on mucus rheology and spirometry

N. De Cono, P. Schelstraete, F. Haerynck, S. Van daele, N. Sanders, F. De Baets

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 63 KB

english, 2008

90

β-adrenergic stimulation alters sweat gland potential difference in cystic fibrosis (CF) patients but not healthy controls

T. Gonska, W. Ip, C. Bear, P. Durie, P. Quintan

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 63 KB

english, 2008

91

The effect of N-acetylcysteine on chloride efflux from airway epithelial cells

G. Varelogianni, I. Oliynyk, G.M. Roomans, M. Johannesson

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 63 KB

english, 2008

92

Preliminary results of oxidative status change in cystic fibrosis (CF) and oral addition with cysteine

A. De Alessandri, S. Beschi, R. Casciaro, C. Zucchi, T. Mora, L. Minicucci

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 63 KB

english, 2008

93

Clinical improvement in CF patients with a reduced glutathione treatment: an open observational study

A.G. Visca, C.T. Bishop, S. Hilton, V.M. Hudson

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 60 KB

english, 2008

94

Use of azithromycin in cystic fibrosis patients not infected with Pseudomonas aeruginosa

B.S. O'Connor, A.L. Reid, H.J. Steen, M.D. Shields, J.S. Elborn

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 60 KB

english, 2008

95

Does azithromycin inhibit the DNA hydrolysing activity of dornase alpha?

E.B. Wilms, D.J. Touw, H.G. Heijerman, N.N. Sanders

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 60 KB

english, 2008

96

Effect of multiple aztreonam lysine for inhalation (AZLI) cycles on disease-related endpoints and safety in patients with cystic fibrosis (CF) and Pseudomonas aeruginosa (PA): Interim analysis of 12 month data

C. Oermann, K. McCoy, G. Retsch-Bogart, R. Gibson, A. Quittner, A.B. Montgomery

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 60 KB

english, 2008

97

Inhaled tobramycin nebulizer solution for treatment of early Pseudomonas aeruginosa infection: the ELITE study

F. Ratjen, S. Stenglein, A. Munck

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 61 KB

english, 2008

98

A randomized placebo-controlled study of nebulized liposomal amikacin (Arikace™) in the treatment of cystic fibrosis patients with chronic Pseudomonas aeruginosa lung infection

L. Dupont, P. Minic, S. Fustic, H. Mazurek, E. Solyom, A. Feketova, E. Csiszer, R. Gupta

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 61 KB

english, 2008

99

Pharmacokinetics of ciprofloxacin PulmoSphere® inhalational powder

H. Stass, S. Baumann-Noss, H. Delesen, J. Nagelschmitz, S. Willmann, A. Edginton, D. Staab

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 61 KB

english, 2008

100

Single-dose pharmacokinetics of aerosol MP-376 (levofloxacin solution for inhalation) in cystic fibrosis patients: PK-PD implications

P.C. Griffith, C. Hansen, T. Pressler, T. Baichen, T.J. Jensen, D.E. Geller, K. Kesser, J. Rock, M. Surber, K. Bostian, M.N. Dudley

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 61 KB

english, 2008

101

Omalizumab – a treatment option against incipient allergic bronchopulmonary aspergillosis when combined with severe allergic asthma and diabetes mellitus

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 54 KB

english, 2008

102

Direct dispensing of dornase alfa improves adherence and lung function in cystic fibrosis (CF)

M. Hagelberg, M.J. Dooley, S.G. Poole, D. Leung, M. Bailey, F. Finlayson, D. Clark, M. Braithwaite, T. Kotsimbos, J.W. Wilson

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 54 KB

english, 2008

103

Sinu-nasal inhalation of Dornase alfa in CF. Results of a double-blind placebo-controlled pilot trial

J. Mainz, H.J. Mentzel, G. Schneider, J. Riethmuller, I. Schiller, C. Ritschel, J.F. Beck, B. Wiedemann

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 54 KB

english, 2008

104

Colistin CF for aerosol therapy of the upper airways – An in-vitro deposition study with the PARI SINUS

U. Schuschnig, E. Klopfer, A. Kriiner, R. Schmid, M. Keller

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 54 KB

english, 2008

105

Aerosol characteristics of hypertonic saline (HS) nebulised by the eFlow® rapid

E. Bitterle, A. Luithlen, K. Reul, D. Mueller, M. Keller

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 61 KB

english, 2008

106

Aerosol characteristics of eFlow® using different control units

M. Tservistas, K. Hoyer, S. Seemann, M. Keller, K. Knoch

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 61 KB

english, 2008

107

Changing features of patients with cystic fibrosis (CF) referred for lung transplantation assessment

S.J. Doe, A.D. De Soyza, J.L. Lordan, A.J. Fisher, P.A. Corris

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 61 KB

english, 2008

108

Fenretinide corrects fatty acid imbalance in CF mice: a possible therapy for CF patients?

G. Wojewodka, C. Guilbault, Z. Saeed, M. Hajduch, E. Matouk, J.B. De Sanctis, D. Radzioch

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 61 KB

english, 2008

109

Phase II study in young CF adults with the recombinant acid lipase MERISPASE®

G. Lenoir, C. Dubray, D. Hubert, R. Chiron, P. Philippe, J. Sarles

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 46 KB

english, 2008

110

First European CF microbiology quality assurance trial

M. Hogardt, D. Claus, H. Riehn-Kopp, B. Tümmler

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 60 KB

english, 2008

111

Patient-to-patient transmission of a multiresistant Pseudomonas aeruginosa strain in a summer camp detected by prospective follow up

F. Karpati, P. Meyer, V. Adermark, E. Johansson, C. Welinder-Olsson

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 60 KB

english, 2008

112

Cross-infection of Pseudomonas aeruginosa during an open air meeting on the beach

G. Ruiter, A. Terlingen, A. Fleer, H.G. Arets

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 60 KB

english, 2008

113

Are transmissible strains of Pseudomonas aeruginosa associated with increased morbidity and mortality for patients with CF?

A.M. Jones, M.E. Dodd, J.R. Govan, C.J. Doherty, A.K. Webb

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 60 KB

english, 2008

114

Screening of new patient referrals for infection with transmissible strains of Pseudomonas aeruginosa

A.M. Jones, M. Dodd, J. Govan, C. Doherty, K. Webb

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 65 KB

english, 2008

115

The changing prevalence of clonal strains of Pseudomonas aeruginosa (Psa) at two Australian CF centres

M.W. France, S. Bialasiewicz, C. Wainwright, C. Coulter, T. Kidd, M. Syrmis, M. Nissen, T. Sloots, S.C. Bell

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 65 KB

english, 2008

116

Clonal Pseudomonas aeruginosa strains and lung transplantation (LT) outcomes in CF

M.W. France, J. Courtney, C. Coulter, J. Govan, C. Doherty, F. Kermeen, P. Hopkins, K. McNeil, M. Al-Aloul, A.K. Webb, A. Jones, S.C. Bell

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 65 KB

english, 2008

117

Treatment burden of infection with a common transmissible Pseudomonas aeruginosa strain in CF

E. Spencer-Clegg, K. Mohan, M.J. Ledson, M.J. Walshaw

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 65 KB

english, 2008

118

Characterization of Pseudomonas aeruginosa (PA) recovered from swimming pools and from Italian cystic fibrosis (CF) patients

P. Morelli, M. Mentasti, A. Sangiuolo, L. Arata, G. Manno

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 60 KB

english, 2008

119

Is the 1-meter distance enough to prevent cross-infection in cystic fibrosis? Preliminary results of a prospective study

F. Festini, V. Galici, S. Neri, C. Mannini, C. Braggion

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 60 KB

english, 2008

120

Are cough swabs a reliable indicator of Pseudomonas aeruginosa status in patients with cystic fibrosis?

P. Whitaker, F. Nasar, T. Lee, M. Denton, S. Conway, D. Peckham

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 60 KB

english, 2008

121

Concordance of bacterial strains cultivated from upper and lower airways from CF patients

J. Mainz, L. Naehrlich, M. Schien, M. Kaeding, S. Mayr, L. Wiehlmann, W. Pfister, B.C. Kahl, J.F. Beck, B. Tümmler

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 60 KB

english, 2008

122

Utility of viral immunofluorescence in pulmonary exacerbations in adults with cystic fibrosis

B. Datta, P. Whitaker, I. Clifton, C. Etherington, S. Conway, M. Denton, D. Peckham

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 63 KB

english, 2008

123

Recurrence of PSA after early treatment: a long-term follow-up study

K. Rebmann, S. Junge, L. Wiehlmann, M. Ballmann

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 63 KB

english, 2008

124

Early eradication therapy for Pseudomonas aeruginosa: impact of prior clinical status pseudomonas antibody level and antibiotic regimen on success rates

C. Etherington, D. Peckham, S. Conway

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 63 KB

english, 2008

125

Diagnostic value of antibody anti Pseudomonas aeruginosa in early lung infection in cystic fibrosis patients

A. Biffi, D. Costantini, C. Colombo, L. Zazzeron, M.L. Garlaschi, E. Torresani, L. Cariani

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 63 KB

english, 2008

126

Fluctutations in phenotypes and genotypes within populations of Pseudomonas aeruginosa during pulmonary exacerbations in cystic fibrosis

J.L. Fothergill, M.J. Walshaw, M.J. Ledson, T.L. Pitt, C. Winstanley

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 59 KB

english, 2008

127

Typing of anomalous isolates of the Pseudomonas aeruginosa Liverpool Epidemic Strain using the Clondiag tube array chip

J.L. Fothergill, J.E. Corkill, J.E. Foweraker, M.J. Walshaw, M.J. Ledson, T.L. Pitt, C. Winstanley

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 59 KB

english, 2008

128

Genome sequence of a cystic fibrosis epidemic strain of Pseudomonas aeruginosa

C. Winstanley, J.L. Fothergill, I. Kukavica-Ibrulj, M. Langille, C. Paradis-Bleau, F. Sanschagrin, A. Bragonzi, G. Winsor, N.R. Thomson, F.S. Brinkman, R.C. Levesque, R.E. Hancock

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 59 KB

english, 2008

129

Pseudomonas aeruginosa with a specific OprD type predominantly present in chronically infected CF patients

P. Deschaght, J.P. Pirnay, T. De Baere, L. Van Simaey, P. Schelstraete, S. Van daele, F. De Baets, M. Vaneechoutte

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 59 KB

english, 2008

130

Pseudomonas aeruginosa (PA) resistant to colistin (CL) in Italian cystic fibrosis (CF) patients

G. Manno, P. Morelli, M. Mentasti, R. Casciaro, N. Cirilli, R. Gagliardini, A. D'Aprile, F. Gioffrè, D. Scuteri, G. Melioli

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 62 KB

english, 2008

131

Evolution of antibiotic resistance in Pseudomonas aeruginosa isolates from cystic fibrosis patients: results from a longitudinal study

S. Campana, S. Tekle, N. Ravenni, C. Braggion, G. Taccetti

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 62 KB

english, 2008

132

The sensibility of Ps. aeruginosa isolates in children with cystic fibrosis

E. Chioroglo, S. Sciuca, O. Turcu

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 62 KB

english, 2008

133

The effect of incubation of sub-minimum inhibitory concentration of antibiotics on strains of Pseudomonas aeruginosa (PA) in a desiccation survival model

I. Clifton, M. Denton, F. M'Zali, D. Peckham

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 62 KB

english, 2008

134

Synergic effect of cotrimoxazole in patients with cystic fibrosis infected with multiresistant Pseudomonas aeruginosa (PA)

S. Wissard, L. Lémée, S. Dominique, S. Pramil, L. Couderc, C. Marguet

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 64 KB

english, 2008

135

Gram-negative multiresistant non-epidemic strain infection in CF patients

P. Cocchi, N. Ravenni, F. Favari, G. Taccetti, S. Campana, C. Braggion

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 64 KB

english, 2008

136

Cost analysis of treatment for Pseudomonas aeruginosa infection in cystic fibrosis patients

G. Taccetti, A. Neri, V. Galici, V. Boni, F. Fanti, C. Braggion, S. Campana, F. Festini

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 64 KB

english, 2008

137

Microbiologic resistance and clinical efficacy of aztreonam lysine for inhalation (AZLI) in cystic fibrosis (CF)

K. McCoy, G. Retsch-Bogart, R. Gibson, C. Oermann, M. Braff, A.B. Montgomery

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 64 KB

english, 2008

138

Experience of inhaled tobramycin: impact in microbiological and clinical parameters in patients with cystic fibrosis

S. Castanhinha, P. Reis, J. Fermeiro, L. Pereira, C. Barreto

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 61 KB

english, 2008

139

Single daily administration of tobramycin (TO) after repeated multiple-dose treatment: oto- and nephrotoxicity and drug serum levels

G. Braccini, I. Lori, A. Neri, F. Festini, S. Campana, R. Ciuti, G. Taccetti

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 61 KB

english, 2008

140

Ototoxicity following once daily aminoglycoside administration in adults with CF

C. Elston, C. Orchard, A. Wee, D. Geddes, M. Hodson

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 61 KB

english, 2008

141

The effect of long term use of rhDNAse on pulmonary colonisation in children with cystic fibrosis

H. Bonestroo, M. Slieker, H.G. Arets

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 61 KB

english, 2008

142

Azithromycin long-term therapy in CF patients: microbiological and clinical effects

R. Casciaro, S. Pessano, M. Caso, M. Serafino, G. Manno, M. Mentasti, A. Tacchella, L. Minicucci

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

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english, 2008

143

Virulence of mucoid Pseudomonas aeruginosa strains in cystic fibrosis: New sequential infection model

C. Moser, M. van Gennip, T. Bjarnsholt, H. Calum, P.Ø. Jensen, B. Lee, O. Ciofu, M. Givskov, S. Molin, N. Høiby

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 60 KB

english, 2008

144

Respiratory syncytial virus (RSV) enhances Pseudomonas aeruginosa lung infection in mice

A.M. de Vrankrijker, O. Ciofu, N. Høiby, T.F. Wolfs, C.K. Van der Ent, H.K. Johansen

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 60 KB

english, 2008

145

The paranasal sinuses are focus for colonisation and chronic biofilm lung infection in CF patients

H.K. Johansen, J. Fisker, K. Bloksted, T. Pressler, M. Skov, S. Hansen, S. Molin, N. Høiby, C. Buchwald

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 60 KB

english, 2008

146

Biofilm formation and antimicrobial susceptibility of P. aeruginosa isolates cultured before and after antibiotic treatment of an acute exacerbation of pulmonary infection

D.F. Gilpin, J. Graham, J.S. Elborn, M.M. Tunney

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 62 KB

english, 2008

147

Correlation of biofilm formation ability and genomic relatedness in Pseudomonas aeruginosa strains isolated from cystic fibrosis patient sputa

T. Spasenovski, M.P. Carrol, K.D. Bruce

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 62 KB

english, 2008

148

Mixed species biofilm formation by aerobic and anaerobic bacteria isolated from the sputum of patients with cystic fibrosis

M.M. Tunney, K.A. Nixon, J.S. Elborn

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 62 KB

english, 2008

149

Origin of lactate in CF sputum

D. Worlitzsch, T. Bensel, B. Wollschlaeger, M. Borneff-Lipp, G. Doering

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 62 KB

english, 2008

150

Proteins released from Pseudomonas aeruginosa (Pa) referent and clinical strains under microaerobiosis and their effects on cystic fibrosis airways

C. Cigana, P. Mauri, D. Di Silvestre, G. Bergamini, A. Bragonzi, B.M. Assael, C. Sorio, P. Melotti

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 54 KB

english, 2008

151

Detection of low Pseudomonas aeruginosa colonization by real time polymerase chain reaction

T. Billard, S. Herwegh, N. Wizla, D. Turck, M.O. Husson

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 54 KB

english, 2008

152

Detection of Ps. aeruginosa in paediatric cystic fibrosis patients is enhanced by modern molecular laboratory techniques

E. McCulloch, C. Lucas, C. Williams

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 54 KB

english, 2008

153

Rapid identification of Burkhoideria cepacia from paediatric cystic fibrosis patients using real-time PCR

E. McCulloch, C. Lucas, C. Williams

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 54 KB

english, 2008

154

Identification of Burkholderia cepacia complex species by SNuPE and LAMP analysis of histidine biosynthetic genes

M.C. Papaleo, E. Perrin, I. Maida, B. Tarabella, M. Fondi, R. Fani

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 62 KB

english, 2008

155

Comparison of culture and molecular methods for detection and quantitation of aerobic and anaerobic bacteria in sputum from cystic fibrosis patients

M.M. Tunney, E. Klem, T.F. Moriarty, D.F. Gilpin, R.C. Boucher, J.S. Elborn, G. Doring, M.C. Wolfgang

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

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english, 2008

156

Molecular detection of multiple emerging pathogens in sputa from cystic fibrosis patients

F. Bittar, H. Richet, J.C. Dubus, M. Reynaud-Gaubert, N. Stremler, J. Sarles, D. Raoult, J.M. Rolain

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

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english, 2008

157

Comparison of the lung bacterial communities sampled from stable cystic fibrosis patients over time

F.A. Stressmann, G.B. Rogers, T. Daniels, A.K. Lilley, M.P. Carroll, K.D. Bruce

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

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english, 2008

158

Microbiology of the lower respiratory tract of infants with cystic fibrosis using terminal restriction length polymorphism

M.S. Payne, K. Bruce, G.J. Connett, J.P. Legg

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

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english, 2008

159

Anaerobic bacteria detected in sputum of cystic fibrosis patients by its cellular fatty acid markers

S.Y. Semykin, G.A. Osipov, S.S. Postnikov, N.Y. Kashirskaya

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

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english, 2008

160

Evaluation of the effectiveness of the modified Burkholderia cepacia selective agar (BCSA) for isolation of B. cepacia complex from respiratory secretion in CF patients

K. Fiolo, P. Dentini, A.F. Ribeiro, J.D. Ribeiro, C.E. Levy

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

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english, 2008

161

Unusual species distribution of Burkholderia isolates from Danish cystic fibrosis patients

N. Norskov-Lauritsen, H.K. Johansen, T. Pressler, H.V. Olesen, N. Hoiby

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

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english, 2008

162

Epidemic outbreak of Burkholderia cepacia in a reference center of cystic fibrosis in Buenos Aires Argentina

G. Diez, V. D'Alessandro, F. Rentería, C. Varas, E. Segal

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

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english, 2008

163

Invasion of Burkholderia cepacia complex isolates into lung epithelial cells involves glycolipid receptors

T. Mullen, M. Callaghan, S. McClean

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

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english, 2008

164

Degradation of host defence molecules by CF-related pathogens grown as biofilms

G.G. Einarsson, S.L. Martin, B. Walker, J.S. Elborn, A. McDowell

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

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english, 2008

165

Cross-infection by Staphyiococcus aureus among cystic fibrosis patients

L. Pereira, C. Silva-Costa, F. Pinto, C. Barreto, M. Ramirez, J. Melo-Cristino

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

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english, 2008

166

Classical criteria for chronic infection predict the maintenance of the same Staphylococcus aureus strain in cystic fibrosis patients

L. Pereira, C. Silva-Costa, F. Pinto, C. Barreto, M. Ramirez, J. Melo-Cristino

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

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english, 2008

167

Methicillin-resistant Staphylococcus aureus from airway secretions from patients with cystic fibrosis

E. Hatziagorou, F. Kirvassilis, D. Sofianou, C. Antachopoulos, E. Roilides, J. Tsanakas

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

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english, 2008

168

Eradication of first sputum isolates of MRSA in adults with cystic fibrosis (CF)

A.B. Palamarthy, R. Howe, C. Davies, R.I. Ketchell

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

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english, 2008

169

Methicillin-resistant Staphylococcus aureus in cystic fibrosis patients

S. Pekcan, M. Kose, D. Dogru, N. Cobanoglu, E. Yalcin, U. Ozcelik, N. Kiper

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

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english, 2008

170

Impact of long-term airway Staphylococcus aureus (SA) colonisation in children with cystic fibrosis (CF): strains evolution and clinical outcome correlations

D. Claeys, M.V. Guillot, C.C. El Hachem, N. Curcio, C. Paris, M. Ellaffi, R. Leclerc, E. Bingen, P. Mariani

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

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english, 2008

171

Methicillin-resistant Staphylococcus aureus infection – what impact in cystic fibrosis patients morbidity?

J. Fermeiro, P. Reis, S. Castanhinha, L. Pereira, C. Barreto

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

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english, 2008

172

Do prophylactic antibiotics reduce isolation of Staphylococcus aureus in adult CF patients?

A.L. Brennan, R. Aul, M.E. Dodd, A.K. Webb, A.M. Jones

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

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english, 2008

173

Dynamics of colonization with Stenotrophomonas maltophilia (Sm) in patients with cystic fibrosis (CF)

C. Casaulta, S. Stirnemann, S. Droz, R. Kraemer, M.H. Schoeni, C. Aebi

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

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english, 2008

174

Water filters can prevent Stenotrophomonas maltophilia contamination of nebulizer equipment used by people with cystic fibrosis (CF)

R. Woodhouse, D. Peckham, S. Conway, M. Denton

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 60 KB

english, 2008

175

Clinical relevance of Achromobacter xylosoxidans from patients with cystic fibrosis

P. Dentini, K. Fiolo, J.D. Ribeiro, A.F. Ribeiro, L.M. Hollanda, M. Brocchi, C.E. Levy

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

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english, 2008

176

In vitro activity of taurolin against multiple antibiotic resistant strains of Gram-negative non-fermenters including Stenotrophomonas maltophilia and Achromobacter xylosoxidans from lung transplant patients

A. Nicholson, J.D. Perry, G. Short, S. Peart, F.K. Gould

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

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english, 2008

177

Inhaled high-dose ceftazidime in CF patients with multi-resistant, Gram-negative infections

C.R. Hansen, T. Pressler, B. Lærum, N. Høiby

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

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english, 2008

178

Bloodstream infections in cystic fibrosis – ten years experience at the Leeds Paediatric and Adult CF Units

R. Metcalfe, S. Conway, M. Denton

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 54 KB

english, 2008

179

The use of bronchoscopy in the diagnosis of pulmonary exacerbations in non-expectorating children with cystic fibrosis

G.J. Connett, N. Liddle, J.P. Legg

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

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english, 2008

180

Epidemiological profile of bacteria isolated from the respiratory tract of cystic fibrosis patients

P. Reis, S. Castanhinha, J. Fermeiro, L. Pereira, C. Barreto

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 54 KB

english, 2008

181

Non-fermenting Gram-negative rods isolated from patients with cystic fibrosis

C.E. Levy, P. Dentini, K. Fiolo, J.D. Ribeiro, G. Hessel, A.F. Ribeiro

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

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english, 2008

182

Trends in pathogens colonising the respiratory tract of adult patients with cystic fibrosis 1985–2005

F.A. Millar, N.J. Simmonds, M.E. Hodson

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 65 KB

english, 2008

183

Bacteriology of sputum in cystic fibrosis – 2 years of systematic monitoring

I. Sad, T. Folescu, P. Schwan, S. Cabral, R. Farme Damoed, C. Aranha, B. Marques, L. Higa

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

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english, 2008

184

Nontuberculous Mycobacterium in cystic fibrosis

S. Mulrennan, K. Dhamija, M. Cullen, M. Dodd, A. Webb, A. Jones

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

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english, 2008

185

Occurrence of fungi in the respiratory tract of adults with cystic fibrosis

E. Sauteur, M. Baixench, D. Hubert, N. Desmazes-Dufeu, R. Kanaan, A. Paugam

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

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english, 2008

186

Clinical value of Aspergillus detection in sputum obtained from 84 patients with cystic fibrosis

M. Roussey, S. Chevrier, F. Giroux, B. Desrues, C. Belleguic, E. Deneuville, C. Guiguen, J.P. Gangneux

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

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english, 2008

187

Tolerability of voriconazole in children with cystic fibrosis and allergic bronchopulmonary aspergillosis (ABPA)

A. Katelari, M. Tzanoudaki, E. Xenou, D. Beri, T. Zervou, S. Doudounakis

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

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english, 2008

188

Analysis of fungal-bacterial community interactions in cystic fibrosis airway secretions

G. Rogers, F. Stressmann, M. Carroll, K. Bruce

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

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english, 2008

189

Emergence and spread of a phylogenetic cluster of Corynebacteria in cystic fibrosis patients

C. Cassagne, F. Bittar, A. Toro, N. Stremler, J.C. Dubus, J. Sarles, D. Raoult, J.M. Rolain

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

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english, 2008

190

Inquilinus limosus: an easily missed emerging resistant respiratory pathogen in cystic fibrosis patients

F. Bittar, A. Leydier, E. Bosdure, A. Toro, M. Reynaud-Gaubert, S. Boniface, N. Stremler, J.C. Dubus, J. Sarles, D. Raoult, J.M. Rolain

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

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english, 2008

191

Nocardia farcinica isolation in CF sputum: therapeutic considerations

A. Malfroot, E. De Wachter, I. De Schutter, A. De Bel, D. Pierard, S. Lauwers

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

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english, 2008

192

Geosmithia argillacea – a potential new pathogen in cystic fibrosis lung disease?

R.C. Barton, A.M. Borman, E.M. Johnson, R.P. Hobson, S.P. Conway, T. Lee, D. Peckham, K.G. Brownlee

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

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english, 2008

193

Gut microbiota composition in cystic fibrosis patients: molecular approach and classical culture

J.M. Sánchez-Calvo, M. García-Castillo, A. Lamas, M. Rodriguez-Baños, L. Máiz, L. Suárez, F. Baquero, R. Cantón, R. del Campo

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

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english, 2008

194

Development and characterization of IgY as oral treatment in CF care

E. Nilsson, H. Kollberg, A. Larsson

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 46 KB

english, 2008

195

Antimicrobial potential of marine psychrotrophic bacteria isolated from Antarctic sponges

A. Lo Giudice, L. Michaud, S. Mangano, C. Caruso, V. Masciale, M.C. Papaleo, V. Bruni, R. Fani

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

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english, 2008

196

A transcriptome analysis of the in vitro response of Pseudomonas aeruginosa to polymorphonuclear leukocyte exposure

M. Alhede, T. Bjarnsholt, P.O. Jensen, M. Parsek, N. Høiby, T.B. Rasmussen, M. Givskov

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 64 KB

english, 2008

197

Defective CFTR Cl− channel enhances proteasomal degradation and reduces NF-κB activity in lung epithelial cells exposed to oxidative stress

E. Boncoeur, T. Roque, E. Bonvin, V. Saint Criq, M. Bonora, A. Clement, O. Tabary, J. Jacquot

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

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english, 2008

198

Targeting Cx43 protects against lung inflammation

M.Z. Richani Sarieddine, I. Garcia, B. Foglia, B.R. Kwak, M. Chanson

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

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english, 2008

199

Immunomodulatory properties of vitamin D in Scandinavian cystic fibrosis patients

T. Pincikova, K. Nilsson, F. Karpati, L. Hjelte

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

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english, 2008

200

Is there a genetic susceptibility or an autoimmune component in the natural history of CF related diabetes (CFRD)?

I. Sequeiros, N.A. Jarad, K. Hester, A. Williams, F.S. Wong

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 58 KB

english, 2008

201

Skin testing in cystic fibrosis patients with a history of multiple beta-lactam hypersensitivity reactions

P. Whitaker, J. Gooi, S. Conway, D. Peckham

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

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english, 2008

202

LPS induces increased bronchial hyperactivity and mucus over-production in CFTR−/− mice

F. Dif, P. Burgel, M. Ollero, D. Leduc, C. Martin, S. Tattermusch, M. Abolhassani, M. Lagranderie, D. Israel-Biet, Y. Kita, N. Uozumi, T. Shimizu, L. Touqui

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

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english, 2008

203

Atopic background as a risk factor for allergic bronchopulmonary aspergillosis in cystic fibrosis (CF) patients

A. Katelari, M. Kanariou, D. Hatzis, I. Inglezos, S. Doudounakis

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

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english, 2008

204

Immunoglobulin levels in cystic fibrosis patients: influence of age, gender and disease severity

E. Hatziagorou, M. Trachana, F. Kirvassilis, J. Tsanakas

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 63 KB

english, 2008

205

Azithromycin is not able to decrease inflammatory process in cystic fibrosis cells

V. Saint-Criq, P. Le Rouzic, J. Jacquot, A. Clément, O. Tabary

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 63 KB

english, 2008

206

Lack of control of Pseudomonas aeruginosa pulmonary infection in the absence of recognition of both lipopolysaccharide and flagellin

R. Ramphal, V. Balloy, J. Jyot, A. Verma, M. Si-Tahar, M. Chignard

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

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english, 2008

207

The respiratory burst of PMNs accelerates anaerobiosis in sputum from CF patients with chronic Pseudomonas aeruginosa lung infection

M. Kolpen, T. Bjarnsholt, C. Moser, L.D. Christensen, M.V. Gennip, C.R. Hansen, O. Ciofu, L. Mandsberg, A. Kharazmi, G. Döring, M. Givskov, N. Høiby, P.Ø. Jensen

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

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english, 2008

208

Relationship between Pseudomonas antibody levels clinical wellbeing and the Leeds criteria for infection status

T. Lee, D. Peckham, S. Conway, C. Etherington

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

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english, 2008

209

Potential role of EPI-hNE4 treatment in CF patients

V. Pruliere-Escabasse, G. Vuagniaux, C. Clerici, A. Coste, C. Planès

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

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english, 2008

210

Reduced frequency of reactions in patients with cystic fibrosis and continuous treatment with oral cephalosporins?

M. Griese, J. Nuebel, M. Kappler

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

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english, 2008

211

Mannose-bin ding lectin – polymorphisms and modifying effect on CF

J. Brazova, T. Freiberger, A. Sediva

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

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english, 2008

212

Elevated IL-17 and IL-23 mRNA levels in sputum of stable CF patients

A. Decraene, A. Widyastuti, E. Dilissen, J. Ceuppens, D. Bullens, K. De Boeck, L. Dupont

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 66 KB

english, 2008

213

Aspergillus fumigatus-induced IL-8 synthesis by bronchial epithelial cells: lack of involvement of the TLR-MyD88 pathway

V. Balloy, J.M. Sallenave, M. Si-Tahar, J.P. Latgé, M. Chignard

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 66 KB

english, 2008

214

A new candidate biomarker of inflammation in CF airway: Amphiregulin

M. Adib-Conquy, T. Pedron, A.E. Petit-Bertron, O. Tabary, H. Corvol, J. Jacquot, A. Clement, J.M. Cavaillon

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 66 KB

english, 2008

215

Serum surfactant protein D: a possible marker for lung disease in cystic fibrosis

H.V. Olesen, G.L. Sørensen, P.O. Schiøtz, U. Holmskov

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 66 KB

english, 2008

216

Exhaled leukotriene B4 and nitric oxide in cystic fibrosis

K. Bloemen, V. Nelen, G. Schoeters, K. Desager

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 46 KB

english, 2008

217

Neutrophil elastase in exhaled breath condensate in cystic fibrosis

L. Fila, J. Musil, M. Prucha

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

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english, 2008

218

Intravenous methylprednisolone pulse therapy vs. oral prednisone for allergic bronchopulmonary aspergillosis (ABPA) in CF

M. Cohen-Cymberknoh, H. Blau, D. Shoseyov, O. Efrati, S. Armoni, E. Kerem

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

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english, 2008

219

21% prevalence of ABPA in a regional paediatric Cystic Fibrosis (CF) clinic – how high is too high?

C.A. Byrnes, M. Jaksic, J.C. Tate

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 64 KB

english, 2008

220

Infection with Mycobacterium abscessus deteriorates lung function dramatically in CF patients

K. Kötz, M. Gilljam, A. Lindblad

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 64 KB

english, 2008

221

Clinical difference between cystic fibrosis patients colonized with different bacteria

P. Reis, J. Fermeiro, S. Castanhinha, T. Rodrigues, L. Pereira, C. Barreto

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 64 KB

english, 2008

222

Segregation practice of CF patients in UK pulmonary function departments

R. Peat, J. Coulson, D. Russell, M.J. Ledson, M.J. Walshaw

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 56 KB

english, 2008

223

Volumetric ultra low dose expiratory computed tomography scans could be sufficient to monitor CF lung disease

M. Loeve, M.H. Lequin, M. de Bruijne, I. Hartmann, W.C. Hop, H.A. Tiddens

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 56 KB

english, 2008

224

Quantitative cough assessment in cystic fibrosis (CF)

E. Kerem, M. Wilschanski, G.L. Elfring, S. Hirawat, T. Pugatsch, A. Reha, S. Constantine, S.W. Peltz, L.L. Miller

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

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english, 2008

225

Nocturnal O2 and CO2 status in adult CF patients during an acute admission

S.C. Johnson, R. Bright-Thomas, M.E. Dodd, A.M. Jones, A.K. Webb, A.M. Bentley

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 56 KB

english, 2008

226

Working capacity and oxygen uptake in CF

M. Gilljam, A. Lindblad, P. Gustafsson, T. Gilljam

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 61 KB

english, 2008

227

Clinical and polysomnographic profile in miscigenated patients with cystic fibrosis

R.T. Ramos, P.B. Gregorio, I.C. Salles, C.H. Daltro, A. Tunes, M.A. Santana, A.X. Acosta

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 61 KB

english, 2008

228

Wisconsin–Brittany CF Newborn Screening Study: Comparison of progression of lung disease using the Wisconsin Chest X-ray scoring system in two screened cohorts

G. Rault, A. Cunningham, Z. Li, A. Laxova, L. Guéganton, I. Duguépéroux, M. Roussey, C. Férec, V. Scotet, P. Farrell

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 61 KB

english, 2008

229

Walking distance as an outcome of antibiotic course in patients with cystic fibrosis

G.L. Grzincich, M.C. Tripodi, S. Faverzani, F. Longo, M. Corchia, C. Spaggiari, R. Minari, G. Pisi

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 61 KB

english, 2008

230

Consideration on relation between pulmonary status and MBL deficiency in CF patients

I. Popa, I.M. Ciuca, L. Pop, Z. Popa, A. Rosca, R. Cioaca, L. Tamas

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 54 KB

english, 2008

231

Sputum investigation in children with cystic fibrosis

G. Petrova, P. Perenovska, T. Strateva, I. Mitov

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

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english, 2008

232

Evaluation of an early warning score (EWS) in cystic fibrosis: a retrospective study

R. Mills, A. Richards, R.I. Ketchell

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

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english, 2008

233

An audit of the introduction of cough plates in a regional paediatric cystic fibrosis unit

N.M. Byrne, C. O' Brien, D.A. Spencer

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 54 KB

english, 2008

234

Long-term monitoring of lung clearance index (LCI) in children with CF

F. Aljassim, A. Lindblad, P.M. Gustafsson

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 56 KB

english, 2008

235

Lung clearance index vs. FEV1 in healthy adults and patients with cystic fibrosis

T. Pantalitschka, H. Rueckel, T. Walter, J. Riethmueller, M. Hofbeck, W. Baden

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 56 KB

english, 2008

236

Outcome of lung clearance index (LCI) in relation to i.v. antibiotic use in children with CF

F. Aljassim, A. Lindblad, P.M. Gustafsson

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 56 KB

english, 2008

237

Long-term assessment of lung function, nutritional status and bacterial colonisation in CF patients after liver transplantation

H. Dmenska, B. Oralewska

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 56 KB

english, 2008

238

Bronchodilator responsiveness in infants with cystic fibrosis in Argentina

V. D'Alessandro, F. Rentería, S. Prates, E. Segal

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 59 KB

english, 2008

239

Spirometry in CF patients

J. Coulson, R. Peat, D. Russell, M.J. Ledson, M.J. Walshaw

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 59 KB

english, 2008

240

Correlation between pulmonary function and nutritional status, age, and bacterial colonization in cystic fibrosis (CF) patients

S. Lubovich, V. Rodriguez, S. Zaragoza, C. Kofman, L. Galanternik, M. Tonietti, A. Teper

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 59 KB

english, 2008

241

Correlation between respiratory function tests, scintigraphy and high-resolution computed tomography findings in patients with cystic fibrosis

M. Asian, E. Yalcin, B. Oguz, M. Kose, D. Dogru, M. Tuncel, P.Ö. Kiratli, M. Haliloglu, N. Kiper, U. Özcelik

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 59 KB

english, 2008

242

Sample size estimation for CF clinical trials using rate of lung function decline (RLFD) as an efficacy endpoint

D.R. VanDevanter, M.W. Konstan

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 60 KB

english, 2008

243

Adherence to nebulised therapies for Pseudomonas eradication in a paediatric CF population

P. McCormack, A. McDonald, L. Heaf, K.W. Southern, P.S. McNamara

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 60 KB

english, 2008

244

Reported and objective adherence to nebulised therapy in adult patients with cystic fibrosis

T.E. Hughes, K. Pollard, A. Black, S.P. Conway, D.G. Peckham

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 60 KB

english, 2008

245

Eradication of recent Pseudomonas aeruginosa isolation: TOBI versus colistin/ciprofloxacin

M. Proesmans, L. Boulanger, F. Vermeulen, K. De Boeck

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 60 KB

english, 2008

246

Dose finding for the inhalational tobramycin therapy using the new diaphragm nebulizer I-neb® AAD® System CF

C. Geidel, K. Weber, J. Stegemann, A. Black, H. Lindemann, K.P. Zimmer, D. Schüler

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 58 KB

english, 2008

247

In vitro characterization of BRAMITOB (inhaled tobramycin 300 mg/4 ml) with next generation nebulisers

T.C.M. Topini, O. Pechtold, K. Sommerer, R. Garzia

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 58 KB

english, 2008

248

Increased efficiency from the I-neb® AAD® System compared with a conventional jet nebulizer

A.J. Hurren, K. Williams, R.W. Potter, R.H. Hatley

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 58 KB

english, 2008

249

Precise dosing of five drugs commonly used by patients with cystic fibrosis using the I-neb® AAD® System

P.W. Potter, K. Williams, R.H. Hatley

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 58 KB

english, 2008

250

Delivery of dornase alfa from the I-neb® AAD® System

R.W. Potter, K. Williams, T.J. Hurren, R.H. Hatley

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 61 KB

english, 2008

251

Effects of inhaled salmeterol-fluticasone propionate on lung and epithelial cell functions in cystic fibrosis children: a double blind crossover study

K. Bessaci, M. Milliot, J.M. Zahm, C. Coraux, P. Mauran, F. Vitry, F. Gauthier, M. Abély

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 61 KB

english, 2008

252

Long term effects of inhaled tobramycin (TOBI®) in cystic fibrosis patients

I. Stelmach, A. Korzeniewska-Eksterowicz, T. Ruszczyk-Bilecka, M. Olszowiec-Chlebna

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 61 KB

english, 2008

253

A Belgian survey of long-term TOBI® treatment in cystic fibrosis patients

B. Penninckx, A. Malfroot, C. Knoop, K. De Boeck, L. Dupont, F. De Baets, K. Desager, P. Lebecque, J. Leclercq-Foucart, G. Casimir

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 58 KB

english, 2008

254

e-Flow rapid®: improved lung function and patient satisfaction with more volume delivered to the lungs during inhalation therapy in cystic fibrosis

S. Militz, M. Feilcke, C. Schröter, A. Kraxner, C. Eismann, M. Griese, M. Kappler

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

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english, 2008

255

Quality of life in people with cystic fibrosis whilst clinical stable

S.C. Bell, K. Walmsley, S. Sennini, K. Patel, D. Serisier, C. Wainwright, S.D. Bowler, M. Harris, J. McCormack

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 58 KB

english, 2008

256

Effect on quality of life and treatment adherence of nebulizations duration in cystic fibrosis (CF)

C. Thuilliez, M. Laurans, R. Morello, J.F. Duhamel, J. Brouard

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 58 KB

english, 2008

257

Cystic fibrosis and gender: a complex relationship

P. Trouvé, C. Férec

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 62 KB

english, 2008

258

Invasive mechanical ventilation: risk factor for death in patients with cystic fibrosis admitted to intensive care unit – Outcome and prolonged follow up

O. Efrati, I. Bylin, E. Segal, D. Vilozni, T. Gilboa, K. Shalev, A. Barak, Y. Sofer, A. Szeinberg, Y. Yahav, G. Paret

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 62 KB

english, 2008

259

The effect of inhaled steroids on bronchial hyperreactivity, oxidative status clinical and inflammatory parameters in patients with cystic fibrosis

Z.S. Uyan, G. Unluguzel, G. Haklar, E. Cakir, S. Oktem, R. Ersu, B. Karadag, F. Karakoc, E. Dagli

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 62 KB

english, 2008

260

Effectiveness of early intensive antibiotic therapy in the first Pseudomonas aeruginosa colonisation

A. Holcikova, E. Zarosska, M. Hanslianova

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 63 KB

english, 2008

261

Effects of the intravenous antibiotic therapy (IAT) in clinical parameters and spirometric results of patients with cystic fibrosis (CF) infected with Pseudomonas aeruginosa

C.I.S. Santos, M.A.G. Ribeiro, G. Hessel, A.F. Ribeiro, J.D. Ribeiro, A.M. Morcillo

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 63 KB

english, 2008

262

Dramatic effect of bolus methylprednisolone (MPSS) in severe respiratory distress (SRD) in CF children

S. Ghdifan, L. Couderc, C. Leguillon, B. Masseline, C. Marguet

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 63 KB

english, 2008

263

Longer term outcome of laparascopic fundoplication in patients with CF with and without lung transplant

B.M. Button, P. Burton, S. Roberts, M. Lee, G. Snell, W. Brown, J. Wilson

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 63 KB

english, 2008

264

Treatment requirements and associated costs with lung transplantation in adults with cystic fibrosis

T. Tse, P. Hopkins, K. McNeil, L. Nissen, S.C. Bell

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 57 KB

english, 2008

265

Malignancies and lung transplant

G. Cimino, I. Halili, D. Russo, M. Rolla, C. Scacchi, S. Quattrucci

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 57 KB

english, 2008

266

CF pediatric lung transplantation single center experience

R. Souilamas, R. Guillemain, V. Boussaud, C. Amrein, P. Chevalier, I. Sermet, S. Vrielynck, S. Pelluau, C. Heilbroner, G. Lenoir

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 57 KB

english, 2008

267

Fifteen years of lung transplantation (LTx) in patients with cystic fibrosis (CF): the Zurich experience

M. Hofer, C. Schmid, S. Irani, R. Speich, E.W. Russi, W. Weder, A. Boehler

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

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english, 2008

268

Influence of inhaled hypertonic saline combined with airway clearance on SpO2 heart rate dyspnoea and wet sputum weight in hospitalised CF patients

S. Vanlaethem, F. Van Ginderdeuren, H. Eyns, A. Malfroot

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 54 KB

english, 2008

269

Use and perceived benefits of nebulised hypertonic saline (HS) treatment in adult patients with cystic fibrosis

H.B. Langman, V.J. Gettins, J. Redfern, R.J. Bright-Thomas, A.M. Jones, A.K. Webb, M.E. Dodd

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 54 KB

english, 2008

270

Audit of a physiotherapy led nebuliser concordance programme for cystic fibrosis adults

L. Gumery, S. Cameron, A. Kailey, J. Lee, J. Whitehouse

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 54 KB

english, 2008

271

Attitudes to recreational androgenic anabolic steroids among adult CF patients

A. Morris, H. Miller, M.J. Ledson, M.J. Walshaw

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 54 KB

english, 2008

272

Pelvic floor muscle training in adolescent females with cystic fibrosis

J. Depiazzi, K. Johnston, C. Anastas

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 57 KB

english, 2008

273

Developing a musculoskeletal service for adults with cystic fibrosis

M. Ruane, R. Taylor, R. McVean, J. Ashbrook, A. Jones, M.E. Dodd

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 57 KB

english, 2008

274

Only a few osteoporotic adult CF patients and no vertebral fractures

L. Lannefors, P. Neglen, K. Hellberg, U. Dennersten

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

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english, 2008

275

First results of five year follow-up of exercise capacity in Belgian CF children: what do they tell us for the future?

M. Vreys, M. Moens, F. Vermeulen, K. De Boeck, M. Proesmans

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 57 KB

english, 2008

276

Two-year follow-up for lung function, muscle strength and functional capacity in cystic fibrosis

H. Arikan, S. Savci, D. Inal-Ince, M. Bosnak-Guclu, M. Saglam, E. Yalcin, D. Dogru-Ersoz

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

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english, 2008

277

Chronotropic response to exercise in cystic fibrosis

D. Inal-Ince, S. Savci, H. Arikan, M. Saglam, M. Bosnak-Guclu, U. Ozcelik

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 57 KB

english, 2008

278

High frequency chest wall oscillation in cystic fibrosis

L.P. Osman, M. Roughton, M.E. Hodson, J.A. Pryor

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 57 KB

english, 2008

279

Adaptation of intrapulmonary percussive ventilation for children with cystic fibrosis

T.A. Bogdanova, N.I. Kapranov, N.Y. Kashirskaya

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 57 KB

english, 2008

280

Immediate effect of the forced expiration technique (FET) in the pulmonary function of patients with cystic fibrosis (CF)

C.I.S. Santos, A.M. Morcillo, A.F. Ribeiro, M.A.G. Ribeiro, R.N. Nogueira, J.D. Ribeiro

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 57 KB

english, 2008

281

Efficiency of West Airway Clearance System in combination with autogenic drainage physiotherapy technique in adult CF patients during lung exacerbation

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 57 KB

english, 2008

282

Manual contact-stimulating physiotherapy: a very important part of chest physiotherapy in CF infants

L. Smolikova, I. Zounkova, V. Skalicka, J. Brazova, L. Pelikan, D. Zemkova, V. Vavrova

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 57 KB

english, 2008

283

Short term improvement of pulmonary function tests following airway clearance using the TRI-GYM™ breathing exercisers

G. Sokol, O. Yona, D. Vilozny, A. Barak, K. Shalev, Y. Sofer, A. Szeinberg, A. Augarten, Y. Yahav, O. Efrati

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 57 KB

english, 2008

284

Is it possible to obtain high adherence to positive expiratory pressure (PEP) in infants with cystic fibrosis (CF) between 0 and 2 years?

U. Jakobsen, A. Schmidt

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 57 KB

english, 2008

285

Efficiency and compliance of physiotherapy combined techniques in children with age between 3 and 6 years

B. Almăjan-Gută, Z. Popa, I. Popa, L. Pop, I.M. Ciuca

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 57 KB

english, 2008

286

When is a lung function test to be performed evaluating the effects of an airway clearance therapy session in CF?

C. Rodriguez, L. Hjelte

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 57 KB

english, 2008

287

Physiotherapy input to an intensive management programme to improve outcome of care for CF patients treated at home with intravenous antibiotics (IV Abx) during pulmonary exacerbations (PExs)

J.M. Bond-Kendall, A. Henry, I. Sequeiros, D. Downey, N.A. Jarad

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 57 KB

english, 2008

288

Current practice in the use of bi-inspiratory positive airway pressure (BIPAP) therapy in cystic fibrosis

H.M. Douglass, H. Potter, N.A. Jarad

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 55 KB

english, 2008

289

Does cough severity influence pelvic fascia displacement in adolescent females with cystic fibrosis?

J. Depiazzi, K. Johnston, C. Anastas

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 55 KB

english, 2008

290

Management of adults with CF: what assessments and interventions do physiotherapists value?

K. Stiller, D. White, M. Williams

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 55 KB

english, 2008

291

Delivery of physiotherapy to shared care cystic fibrosis patients by specialist CF centre physiotherapists at the local general hospital

J. Bond-Kendall, A. Henry, D. Downey, A. Alexander, A. Penketh, N.A. Jarad

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 55 KB

english, 2008

292

Delayed development in newly diagnosed infants with CF: the importance of a broad based physiotherapy program

I. Eisenstadt, T. Cohen, D. Shoseyov, E. Kerem

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 54 KB

english, 2008

293

A proactive approach pays off in screened infants with CF

K.M. Sharp, J.D. Wilkinson

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 54 KB

english, 2008

294

Current practice in prescription assessment and use of oxygen therapy in cystic fibrosis – a national UK survey

H.M. Douglass, H. Potter, N.A. Jarad

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 54 KB

english, 2008

295

An audit of the importance of nose clips for spirometry in CF

L. Boyle, F. Kerr, A. Dunn, J. Rendall, S. Elborn

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 54 KB

english, 2008

296

Factors associated with arthropathy in a cohort of adult CF patients

H.M. Douglass, N.A. Jarad, A. James

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 51 KB

english, 2008

297

Factors that predict full publication of physiotherapy abstracts from major CF conferences

M. Elkins, R. Dentice

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 51 KB

english, 2008

298

An analysis of physiotherapy research abstracts at major regional cystic fibrosis conferences

R. Dentice, M. Elkins

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 51 KB

english, 2008

299

Gastroesophageal reflux and aspiration in CF patients

K. Blondeau, L.J. Dupont, V. Mertens, G. Verleden, A. Malfroot, Y. Vandenplas, B. Hăuser, D. Sifrim

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 62 KB

english, 2008

300

Enteropathy – a new finding in cystic fibrosis

S. Werlin, I. Benuri-Silbiger, L. Cohen, E. Kerem, M. Aviram, L. Bentur, H. Mussaffi, I. Bjarnasson, M. Wilschanski

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 62 KB

english, 2008

301

Constipation in pediatric cystic fibrosis patients: an underestimated medical condition

H.P. van der Doer, J.W. Woestenenk, R.H. Houwen

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 62 KB

english, 2008

302

Defining DIOS and constipation in cystic fibrosis: a multicenter study on the incidence characteristics and treatment of DIOS

H. van der Doer, R. Houwen, I. Sermet, A. Munck, B. Hăuser, J. Walkowiak, E. Robberecht, C. Colombo, M. Sinaasappel, M. Wilschanski

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 62 KB

english, 2008

303

Small intestine bacterial overgrowth (SIBO) in CF patients

A. Lisowska, P. Sobkowiak, W. Cichy, A. Breborowicz, J. Walkowiak

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 60 KB

english, 2008

304

The effect of tegaserod in patients with distal intestinal obstruction syndrome

I.R. Gooding, K.M. Gyi, M.E. Hodson, D. Westaby

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 60 KB

english, 2008

305

Is intestinal inflammation present in CF patients?

H. Tomasova, D. Zemkova, J. Bartosova, M. Macek Jr, V. Vavrova

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 60 KB

english, 2008

306

Fatty acid status in patients with CF-related liver disease

S. Van Biervliet, R. De Bruyne, J.P. Van Biervliet, E. Robberecht, A. Christophe

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 60 KB

english, 2008

307

MBL serum levels in children with CF-associated liver disease

I.M. Ciuca, I. Popa, L. Pop, Z. Popa, A. Rosca, R. Cioaca, L. Tamas

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 61 KB

english, 2008

308

The pancreas is not visible as an entity by magnetic resonance imaging in the majority of cystic fibrosis patients

I. Sequeiros, K. Hester, M. Callaway, A. Williams, Z. Garland, F.S. Wong, N.A. Jarad

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 61 KB

english, 2008

309

Acid steatocrit is not helpful in cystic fibrosis patients with mild or no steatorrhea

A. Blask-Osipa, A. Lisowska, S. Drzymala-Czyz, M. Chabasinska, P. Sobkowiak, J. Walkowiak

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 61 KB

english, 2008

310

Adiponectin may reflect the degree of the inflammatory fibrosing process in the cystic fibrosis liver

M. Fotoulaki, P. Panagopoulou, P. Chitiroglou, I. Tsitouridis, F. Sotiriadou, S. Nousia-Arvanitakis

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 61 KB

english, 2008

311

Ultrasonographic (US) findings of digestive system in children with cystic fibrosis

O. Turcu, S. Sciuca, E. Chioroglo, V. Morosanu

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 53 KB

english, 2008

312

Transient elastography (FibroScan) in patients with cystic fibrosis

A. Leonard, R. Menten, P. Clapuyt, P. Lebecque

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 53 KB

english, 2008

313

Prevalence of cystic fibrosis-related diabetes (CFRD) and its microvascular complications in an adult CF population

M. Choudhury, J. Lee, A. Prosser, L. Speight, L. George, R.I. Ketchell

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 58 KB

english, 2008

314

Impaired glucose metabolism in patients with CF during acute exacerbations

N. Nezer, D. Shoseyov, E. Kerem, S. Armoni, D. Zangen

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 58 KB

english, 2008

315

Can patients at risk of cystic fibrosis-related diabetes be identified early?

R. Richmond, D. McKenna, S. Tierney, R. Rowe, M. Dodd, A. Jones, C. Deaton

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 58 KB

english, 2008

316

Investigating suspected CF-related diabetes mellitus utilising serial capillary blood glucose profiling

J.D. Wilkinson, I.P. Craigie, G. Allison, C. Gallacher, J. Crocker, S. Kent

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

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english, 2008

317

Cystic fibrosis-related diabetes (CFRD) in the Czech Republic

S. Kolouskova, D. Zemkova, V. Skalicka, J. Bartosova, V. Vavrova

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 60 KB

english, 2008

318

Glucose tolerance changes in cystic fibrosis (CF) patients during a 10 years period

G.L. Grzincich, C. Spaggiari, R. Minari, M.C. Tripodi, F. Longo, C. Terzi, G. Chiari, G. Pisi

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 60 KB

english, 2008

319

Demographics of glucose metabolism and gender differences in cystic fibrosis

J.M. van den Berg, J.M. Kouwenberg, H.G. Heijerman

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 60 KB

english, 2008

320

A review of CF-related diabetes (CFRD) management – a patients perspective

A. Marshall, H. Rogers

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 60 KB

english, 2008

321

Effect of impaired glucose tolerance on clinical status in adult CF patients

H. Miller, K. Mohan, P. Dyce, R. Grainger, M.J. Ledson, M.J. Walshaw

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 60 KB

english, 2008

322

Is presence of cystic fibrosis-related diabetes really associated with a faster decline in pulmonary functions?

J.M. van den Berg, H.W. de Valk, E.A. van de Graaf, H.G. Heijerman

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 60 KB

english, 2008

323

Evaluation of glucose intolerance in adolescent CF patients

I. Aldag, N. Wright, N. West, J. McGaw, C. Taylor

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 60 KB

english, 2008

324

Loss of lean tissue mass in adults with CF: an independent predictor of loss of bone mineral density (BMD)

S.J. King, D.J. Topliss, T. Kotsimbos, I.B. Nyulasi, J.W. Wilson

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 60 KB

english, 2008

325

Fore arm bone characteristics in CF adolescents and young adults

E. De Wachter, O. Louis, P. Clerinx, I. Gies, A. Malfroot, J. Vanbesien, J. De Schepper

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 59 KB

english, 2008

326

CF osteopenia and bone tissue metabolism

A.M. Ozhegov, T.V. Simanova

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 59 KB

english, 2008

327

Influence of oral and inhaled corticosteroids treatment on bone mineral density (BMD) in patients with cystic fibrosis

T. Kapustina, V. Fedorova, A. Voronkova, N.I. Kapranov

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 59 KB

english, 2008

328

Audit of renal dysfunction in cystic fibrosis (CF)

L. Edwards, I. Scott, L. Philpott, A. Prosser, R.I. Ketchell

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 59 KB

english, 2008

329

Management dilemmas of renal calculi in cystic fibrosis

F. Healy, M. Waldron, F. Quinn, G. Canny

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 58 KB

english, 2008

330

Renal impairment in the adult cystic fibrosis population

S.J. King, C. De Clercq, D.J. Topliss, N. Thomson, J.W. Wilson

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 58 KB

english, 2008

331

Testosterone deficiency in adult males with cystic fibrosis

M.F. Katz, C. Wheeler, S. Cumming

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 58 KB

english, 2008

332

Pilot study on the effects of lycopene on oxidation and fatty acids in CF patients

G. Wojewodka, F. Kopriva, I. Oborna, J.B. De Sanctis, M. Hadjuch, D. Radzioch

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 58 KB

english, 2008

333

Metabolic alkalosis – clinical study of frequency genotype-phenotype correlation and treatment on 60 patients from Romania

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 55 KB

english, 2008

334

An audit to identify the communication process of a diabetic oral glucose tolerance test (OGTT) result to the patient before and after the introduction of standards

R. Richmond, D. McKenna, M. Dodd, A. Jones

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 55 KB

english, 2008

335

Is it necessary for all adult cystic fibrosis patients to have an annual oral glucose tolerance test (OGTT)?

J.C. Burgess, S.A. Srivastava, M.E. Hodson

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 55 KB

english, 2008

336

Communication processes and outcome following an impaired glucose tolerance test: findings from a clinical audit

D. McKenna, R. Richmond, R. Rowe, M. Dodd, A. Jones

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 55 KB

english, 2008

337

Screening tests for peripheral neuropathy in cystic fibrosis-related diabetes

S. Goodwin, D. McKenna, M. Dodd, A. Jones, A.K. Webb, R.E. Rowe

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 46 KB

english, 2008

338

Nutritional status body composition and exercise capacity in children with cystic fibrosis

K. Rylance, C.J. Taylor, A.S. Rigby

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 57 KB

english, 2008

339

Do Danish children with and without CF share nutritional habits?

J. Sundstrup, S. Fagt, C. Molgard, L. Onsgaard, T. Pressler

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 57 KB

english, 2008

340

Meconium ileus nutritional values and lung function

A.M. Olesen, J. Sundstrup, K. Nilsson, I.E. Moen

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 57 KB

english, 2008

341

Bone mineral density in cystic fibrosis patients – a 3-years follow-up and intervention

E. Ocenaskova, H. Vanicek, O. Pozler, A. Jebava

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 57 KB

english, 2008

342

Creation of CF growth charts: a multi-centric Italian study

B. Russo, A. Coruzzo, L. Valmarana, R. Valmarana, M.L. Guidotti, M. Maglieri, M. Pesola, E. Ravaioli, S. Beschi, S. Dester, D. Rinaldi, F. Alghisi, C. Colombo, V. Raia, T. Repetto, R. Padoan, A. De Al

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 58 KB

english, 2008

343

Body mass index and dairy intake in children with cystic fibrosis

F.M. Bartlett, K.L. Tavener, A.J. McKee, R.G. Ruiz

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 58 KB

english, 2008

344

Nutritional status in Turkish cystic fibrosis patients

O. Kelebek, G. Köksal, H. Gokmen Ozel, F. Tamer, O. Cavusoglu, M. Kose, S. Pekcan, D. Dogru, E. Yalcin, N. Kiper, U. Ozcelik

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 58 KB

english, 2008

345

Comparison of nutritional status and lung function in CF patients in R.Macedonia

L. Spirevska, S. Fustik, T. Jakovska

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 58 KB

english, 2008

346

Failure of vitamin D therapy to achieve adequate serum levels in children with cystic fibrosis

H. Midwinter, D. Hopkins, N.D. Archer, C.P. Burren, T.N. Hilliard

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 57 KB

english, 2008

347

The effect of vitamin D supplementation on vitamin D level in children with cystic fibrosis (CF)

M.F. Roddy, B. Elnazir, P. Greally

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 57 KB

english, 2008

348

Bone mineral density and serum vitamin D levels in children with cystic fibrosis (CF)

K. Jones, R. Ilies, D. McShane, J. Watson

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 57 KB

english, 2008

349

Seasonal variation of vitamin D and its relationship with vitamin D supplementation in children with cystic fibrosis

M.F. Roddy, B. Elnazir, P. Greally

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 57 KB

english, 2008

350

Routine vitamin supplementation provides normal serum vitamin A but not vitamin E concentrations in CF patients

S. Stezowska, S. Drzymala-Czyz, A. Lisowska, A. Popiel, W. Cichy, J. Walkowiak

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 60 KB

english, 2008

351

Vitamin D insufficiency in cystic fibrosis patients of central region of Russia

I.K. Asherova, O.B. Ershova

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 60 KB

english, 2008

352

Linoleic acid but not EPA and DHA correlates to prognostic markers in Scandinavian CF patients

L. Hielte, K. Nilsson, I.E. Moen, A. Lindblad, L. Mared, T. Pressler, G. Fluge, for the Scandinavian CF Study Consortium

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 60 KB

english, 2008

353

Clinical effect of long term oral DHA supplementation in cystic fibrosis patients

S. Van Biervliet, M. Devos, T. Delhaye, J.P. Van Biervliet, A. Christophe, E. Robberecht

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 60 KB

english, 2008

354

Influence of food and supplemental intake of linoleic acid on body weight of CF children

G. Sabolova, H. Kayserova, M. Certik, A. Helclova

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 61 KB

english, 2008

355

Influence of eating habits on body mass in adult CF patients

N. Sinnott, S. Baird, M. Asim, M.J. Walshaw, M.J. Ledson

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 61 KB

english, 2008

356

Home tube feeding in adults with cystic fibrosis: do patients really do it?

R.S. Chinuck, J.C. Dewar

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 61 KB

english, 2008

357

Dietary treatment with probiotics in patients with cystic fibrosis

F.M. Hollander, N.M. de Roos, G.T. Rijkers, F. Teding van Berkhout

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 61 KB

english, 2008

358

The effect of early and late stoma closure on nutritional outcome at 12 months of age in children with meconium ileus secondary to cystic fibrosis

D.M. Chong, L. Heaf, S.E. Kenny, K.W. Southern

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 57 KB

english, 2008

359

Oral protein calorie supplementation effectiveness on nutritional status of children with cystic fibrosis

C.C. Passos, A. Jardim Botelho, F.C. Reis

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 57 KB

english, 2008

360

Impact of aggressive nutritional intervention on early and late acquisition of CFRD in an adult population?

H. White, K. Pollard, C. Etherington, A. Morton, I. Clifton, S. Conway, D. Peckham

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 57 KB

english, 2008

361

Chocolate – thats no way to treat a hypoglycaemic attack!

S. Williams, J. Barrett, J. Whitehouse

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 57 KB

english, 2008

362

Comparison of cystic fibrosis inpatient blood glucose monitoring with the unit policy

L. Robb, M. Richardson

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 54 KB

english, 2008

363

Pilot testing of an interactive web-based meeting to replace group workshops in a nutrition education programme “Eat Well with CF” for adults with cystic fibrosis (CF)

H.M. Watson, C.S. Haworth

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 54 KB

english, 2008

364

Audit of present practice – the assessment and treatment of CF bone health in Scotland

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 54 KB

english, 2008

365

Taste and smell function in children with cystic fibrosis

J.E. Armstrong, D.G. Laing, F. Wilkes, A. Carroll, M. Aitken, A. Jaffe

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 54 KB

english, 2008

366

Hypoproteinemia and anemia in infants with cystic fibrosis

S. Fustik, T. Jakovska, L. Spirevska

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 50 KB

english, 2008

367

Perception of stools and bowel habits in adult CF patients

S. Pandya, A. Sobanska, M.J. Ledson, M.J. Walshaw

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 50 KB

english, 2008

368

Improving clinic attendance

J.K. Walker, F. Edenborough, M. Wildman, Z. Perveen, Y. Locke

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 57 KB

english, 2008

369

Concordance and perceived benefits in patients with cystic fibrosis using dossett boxes

M.E. Williams-Gunn, J. Keane, M. Butler, L.M. Kuitert

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 57 KB

english, 2008

370

An experiential approach to understanding adherence in CF

B. Ashby, J. Pagan, K. Lamballe, D. Beeforth, P. Cole, S. Earnshaw, F. Hampton, J. Higgins, F. Lindsay, S. Robson, P. Singleton, R. Weatherall

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 57 KB

english, 2008

371

Adherence to nebulised antibiotics in cystic fibrosis

G. Latchford, A. Duff, J. Quinn, S. Conway, M. Conner

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 57 KB

english, 2008

372

How a team adherence challenge led to increased communication between teenage patients and the CF team

P. Cole, F. Lindsay, P. Singleton, J. Pagan, B. Ashby

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 54 KB

english, 2008

373

Newborn screening in the northern region difficulties and dilemmas

A. Sewell, C. Sharpe, J. Bloomer, D. Spencer

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 54 KB

english, 2008

374

Influence of segregation policy on daily functioning of adult cystic fibrosis patients

E.A. Boerhof, W. Doeleman, G. Kempen

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 54 KB

english, 2008

375

Evaluation of “patient readiness” to graduate from pediatric to adult health care

A.M. Gravelle, A.G. Davidson

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 54 KB

english, 2008

376

Cystic fibrosis and tobacco smoke exposure

D. Cloquet, P. Hage, L. Hanssens, G. Casimir

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 60 KB

english, 2008

377

Progress in cystic fibrosis transition care in Canada

A.M. Gravelle, A.G. Davidson

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 60 KB

english, 2008

378

Quality of life in women with cystic fibrosis and urinary incontinence

S. Madge, P. Agent

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 60 KB

english, 2008

379

Optimal delivery of end of life care for CF patients families and staff

M. Braithwaite, J. Philip, H. Tranberg, F. Finlayson, M. Gold, T. Kotsimbos, J. Harris, J. Wilson

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 60 KB

english, 2008

380

Correlates of readiness to transfer to adult cystic fibrosis clinics

K.K. Marciel, K. Driscoll, J.S. Rogers, J.A. Marciel, D.M. Janicke

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 60 KB

english, 2008

381

Prevalence of passive exposure to cigarette and active smoking in a large pediatric CF centre in Montreal (Québec, Canada)

N. Yasbeck, J. Marcotte, S. Laporte, M. McKinney, S. Laberge

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 60 KB

english, 2008

382

Striving for glycaemic control in cystic fibrosis-related diabetes: a qualitative study

S. Tierney, C. Deaton, K. Webb, A. Jones, M. Dodd, D. McKenna, R. Rowe

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 60 KB

english, 2008

383

Segregated hospitalisation – the carer perspective

K. Russo, M. Donnelly, A.J. Reid

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 60 KB

english, 2008

384

Sleep problems in patients of an Adult Cystic Fibrosis Centre

I. Sharma, A.K. Webb, H. Oxley

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 56 KB

english, 2008

385

Introducing a programme of education for health care professionals working with adolescents

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 56 KB

english, 2008

386

Cystic fibrosis: what do teenagers really know?

J.C. Tate, N.M. Glubb, K. Tamihere, J.R. Mortimer, C.A. Byrnes

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 56 KB

english, 2008

387

Patient held drug information cards

L. MacDougall, A. Shaw, M. Pogson

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 56 KB

english, 2008

388

Patient and community education about cystic fibrosis (CF) in the North AI Bathina region of Oman: translation of a parent/patient manual

F. AI Hinai, M. Al Naqbi, S. Al Dhouwayani, M. Nasar, N. Al Balushi, M. Al Balushi, M. Al Oraimi, G. Shivalingam, U. Fass, T. Fleming

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 57 KB

english, 2008

389

Educational support for CF patients

W. Kamin, M. Amini, R. Schulz-Schaeffer, T.C. Topini

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 57 KB

english, 2008

390

Pathways Home Project: a pilot study of chronic disease self management in cystic fibrosis (CF)

M. Jessup, J. Busch, P. Turner, E. Cummings, H. Cameron-Tucker, P. Fitzpatrick, L. Joseph, E.H. Walters, D. Reid

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 57 KB

english, 2008

391

A DVD presentation – an adult cystic fibrosis couples support group: reducing isolation

D. Wilson, S. Osmond

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 57 KB

english, 2008

392

Integrating therapeutic education into healthcare: taking up all the opportunities to educate

H. Joachim, M. Bonnard

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 54 KB

english, 2008

393

Amplification of the challenges facing families with multiple siblings newly diagnosed with CF

S. Armoni, S. Kurtz, D. Shoseyov, A. Avital, S. Wexler, E. Kerem

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 54 KB

english, 2008

394

The impact of CF on siblings

T. Havermans, J. DeBoel, L. Wuytack, A. Tijtgat, A. Malfroot, M. Proesmans

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 54 KB

english, 2008

395

Siblings knowledge of CF and treatment

T. Havermans, J. DeBoel, L. Wuytack, A. Tijtgat, A. Malfroot

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 54 KB

english, 2008

396

Home visits: what is their purpose?

H. Miller, P. Dyce, C. Cowperthwaite, B. Govin, M.J. Ledson, M.J. Walshaw

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 54 KB

english, 2008

397

Getting children to wash their hands. What will work?

C. Sharpe, J. Bloomer, A. Sewell

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 54 KB

english, 2008

398

Home visits by the coordinating nurse at an adult CF centre

L. Agrario, N. Desmazes-Dufeu, C. Dupont, R. Panzo, M.J. Nadaud, R. Kanaan, P.R. Burgel, D. Manach, D. Dusser, D. Hubert

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 54 KB

english, 2008

399

Evaluation of a home care service for adults with cystic fibrosis (CF) attending the West Midlands Regional CF Centre

J. Hussey, C. Evans, R. Davies, J. Whitehouse

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 54 KB

english, 2008

400

Independent nurse prescribing for CF in a UK adult unit

H. Miller, P. Dyce, C. Cowperthwaite, B. Govin, M.J. Ledson, M.J. Walshaw

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 54 KB

english, 2008

401

Use of the hospital anxiety and depression scale (HADS) in an adult cystic fibrosis (CF) centre

C. Evans, A. Regan, L. Grant, R. Davies, J. Whitehouse

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 54 KB

english, 2008

402

Anxiety and depression in CF patients after lung transplantation

A. Matossian, T. Havermans, N. Claes, C. Knoop, L. Dupont

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 54 KB

english, 2008

403

Anxiety and depression in adult patients with cystic fibrosis

K. Heslop Sr, S. Johnston, K. Stavers, K. Anderson, M. Wafer, K. Heslop, M. Caraher, A.D. Gascoigne, A. Anderson, S.J. Bourke

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 54 KB

english, 2008

404

A psychopathological overview of adolescents with cystic fibrosis

M. Kirszenbaum, P. Canoui, M.N. Rossillol, C. Elie, S. Vrielynck, I. Sermet-Gaudelus, B. Thouvenin

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 54 KB

english, 2008

405

Prediction of posttraumatic stress symptoms in the families of children with cystic fibrosis

I. Gökler, G. Erden, S. Pekcan, M. Köse, N. Cobanoglu, U. Özcelik, N. Kiper

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 54 KB

english, 2008

406

Symptoms of anxiety and depression pulmonary function and their association with life satisfaction in patients with cystic fibrosis

T. Besier, A.L. Quittner, L. Goldbeck

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 54 KB

english, 2008

407

Anxiety and depression in dyads of adolescents with CF and their caregivers

L. Goldbeck, A.L. Quittner, T. Besier

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 54 KB

english, 2008

408

Psychological particularities in children with cystic fibrosis

A. Tarnovschi, N. Bucun, S. Sciuca

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 55 KB

english, 2008

409

Impact on lung function and body mass index (BMI) when CF patients become parents

L.F. Lauritsen, T. Pressler

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 55 KB

english, 2008

410

The Italian Caregiver Quality of Life Cystic Fibrosis (CQOLCF) Scale: initial validation

F. Gobbi, F. Lupi, F. Battistini, M. Ambroni, W. Wiltshire

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 55 KB

english, 2008

411

Challenge of Living with Cystic Fibrosis (CLCF): psychometric validation

C. Glasscoe, K.W. Southern, H. Hope, E. Burrows, L. Heaf, K. Brownlee, J.A. Smith, J. Hill, G.A. Lancaster, M. Bryon, A.L. Quittner

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 55 KB

english, 2008

412

An audit of the employment experiences of cystic fibrosis patients

D. Langman, S.R. Brennan

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 54 KB

english, 2008

413

Sexuality in CF patients in Czech Republic

H. Chladova, T. Tesarova, P. Hodkova, P. Weiss, A. Klapetek, A. DeMartini, L. Fila, D. Zemkova, L. Smolikova, M. Lekes

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 54 KB

english, 2008

414

Attitudes and quality of life after transplantation: do CF patients differ from other transplanted patients?

T. Havermans, A. Matossian, N. Claes, O. Van den Bergh, C. Knoop, L. Dupont

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 54 KB

english, 2008

415

Coping and quality of life in young people with cystic fibrosis

S. Williams, I. Hobbis, K. Mastroyannopoulou, M. Polichroniadis, R. lies

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 54 KB

english, 2008

416

The expert CF patient; an untapped resource

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 55 KB

english, 2008

417

The psychosocial impact of a late CF diagnosis

C. Blunt, L. Steed, M. Clark, S. Scott, M.E. Hodson, S.L. Elkin

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 55 KB

english, 2008

418

Coping with cystic fibrosis – CF adults and parents of a child with CF in Czech Republic

P. Hodkova, J. Abbott, I. Mala, H. Chladova

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 55 KB

english, 2008

419

‘I am normal’: young peoples perspectives of CF and the influence this has on treatment adherence

J. Hogan, M. Horgan, S. Glenn, K.W. Southern, J. Cottrell, E. Burrows

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 55 KB

english, 2008

420

What do CF patients and their parents tell about infection control?

P. Catastini, S. Magni, S. Agliozzo, T. Repetto, C. Braggion

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 55 KB

english, 2008

421

The annual assessment in cystic fibrosis; writing directly to families

V. King, J. Finnegan, E.F. Burrows, L.J. Heaf, R. Lwin, K.W. Southern

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 55 KB

english, 2008

422

“Copying letters” to CF patients: patient perceptions of benefit

K. Treacy, J.S. Elborn, J. Rendall, J.M. Bradley

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 55 KB

english, 2008

423

What defines a pulmonary exacerbation? The perceptions of adults with cystic fibrosis

J. Abbott, A. Holt, H.C. Rodgers, A. Morton, A. Hart, L. MacDougall, M. Pogson, G. Milne, S.P. Conway

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 46 KB

english, 2008

424

Disadvantage for patients over 24 months at diagnosis of cystic fibrosis

I. de Monestrol, Å Klint, P. Sparen, L. Hjelte

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 59 KB

english, 2008

425

Effect of urban environment on pulmonary exacerbations and use of bronchodilators in patients with cystic fibrosis

P. Whitaker, C. Etherington, B. Datta, V. Harrison, S. Conway, D. Peckham

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 59 KB

english, 2008

426

Development of a patient-reported outcome measure in adult cystic fibrosis

M.S. Salek, L. Corke, R.I. Ketchell

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 59 KB

english, 2008

427

Clear illustration of improved survival in CF: the experience of Brittany (France)

V. Scotet, I. Dugueperoux, M. Audrezet, G. Rault, M. Roussey, V. Moisan-Petit, M. Dagorne, M. Munck, P. Vic, P. Vigneron, G. Bellis, C. Ferec

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 59 KB

english, 2008

428

Impact of French national guidelines on clinical management of cystic fibrosis (CF)

S. Touzet, S. Bourdy, G. Bellon, I. Pin, C. Cracowski, C. Colin, I. Durieu

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 57 KB

english, 2008

429

Forty years isolation from W. Europe and its influence on the course of CF: an unwanted experiment

D. Zemkova, V. Skalicka, J. Bartosova, M. Macek Jr, V. Vavrova

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 57 KB

english, 2008

430

Cystic fibrosis in the Czech Republic

V. Vavrova, on behalf of the Czech CF Working Group

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 57 KB

english, 2008

431

Epidemiology of cystic fibrosis of the Omani population in the North AI Bathina region in Oman

H. AlBadi, M. Al Rawahy, S. Al Maskary, S. Al Sarhani, L. Al Maamari, G. Shivalingam, U. Fass, T. Heming

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 57 KB

english, 2008

432

The prognosis of cystic fibrosis in the Western Cape province of South Africa: a 33 year study

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 60 KB

english, 2008

433

The characteristic of children with cystic fibrosis from Moldova according to European Registry criteria

S. Sciuca, E. Chioroglo, O. Turcu, A. Jivalcovschi, V. Egorov

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 60 KB

english, 2008

434

Data from the Croatian CF Registry

D. T-Drinkovic, D. Tjesic-D, J. Kelecic, A. Votava

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 60 KB

english, 2008

435

CF Registry in Slovakia

H. Kayserová, A. Feketeová, B. Takáč, I. Mikulasova, B. Remiš, D. Zlochová, M. Hájková, M. Brezina

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 60 KB

english, 2008

436

Evaluation of CF database in Republic of Macedonia

T. Jakovska-Maretti, S. Fustik, L. Spirevska

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 54 KB

english, 2008

437

The development of cystic fibrosis care in the South West including the development and impact of the South and West Cystic Fibrosis Database: a retrospective review

J. Tyrrell, S.J. Gooch, K. Giles

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 54 KB

english, 2008

438

The UK CF Registry – a successful transition to a web-based system

E. Gunn, M. Baker, A. Larsen

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 54 KB

english, 2008

439

The cost of paediatric cystic fibrosis to the NHS in the Eastern Region

J. Jarrett, R. lies, M. Mugford, J. Legh-Smith

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 54 KB

english, 2008

440

Cost development in pharmaceutical treatment of adult patients with cystic fibrosis

C.T. Baltin, C. Smaczny, T.O. Wagner

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 54 KB

english, 2008

441

Age specific guidelines developed for scheduled monitoring and investigations in a pediatric CF clinic

D.K. Houlden, L.K. Semple, M.D. Montgomery

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 54 KB

english, 2008

442

Obtaining ethics approval for a multi-centre cystic fibrosis (CF) study in Australia

T.J. Kidd, P.T. Bye, C. Harbour, B.R. Rose, G.B. Marks, P.J. Robinson, S.C. Bell

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 54 KB

english, 2008

443

The European Normative framework on the involvement of CF minors in clinical trials

W. Pinxten, H. Nys, K. Dierickx

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 54 KB

english, 2008

444

Client satisfaction within a paediatric District General Hospital (DGH) cystic fibrosis (CF) service

A.J. Hannam, A. Shenoy, U. O'Hea, L. Alker

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 54 KB

english, 2008

445

ECORN-CF project in the Czech Republic: first experiences

J. Brazova, V. Vavrova, A. Pickova, L. Smolikova, M. Macek Jr

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 54 KB

english, 2008

446

CF Education for respiratory trainees in one UK region

S. Baird, N. Sinnott, A. Mohammad, M.J. Ledson, M.J. Walshaw

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 54 KB

english, 2008

447

Views on medicines of adults with cystic fibrosis

A. Plummer, S. Thornton, B. Torry

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 55 KB

english, 2008

448

Doll-like face: is it an underestimated clinical presentation of cystic fibrosis?

M. Kose, S. Pekcan, N. Kiper, A. Tana Asian, N. Cobanoglu, E. Yalcin, D. Dogru, U. Ozcelik

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 55 KB

english, 2008

449

A solution for severe urinary incontinence in women with cystic fibrosis: a case series

J. Helm, H. Langman, M. Dodd, A. Ahluwalia, A. Jones, K. Webb

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 55 KB

english, 2008

450

Perceived adherence of adults with cystic fibrosis and the views of the multidisciplinary team

A. Plummer, S. Thornton, B. Torry

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 55 KB

english, 2008

451

An intensive home management as a potential method to improve outcome of care for cystic fibrosis patients treated at home with intravenous antibiotics during pulmonary exacerbations

I. Sequeiros, Z. Garland, N.A. Jarad

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 57 KB

english, 2008

452

Experience with totally implantable venous access devices in CF patients

G.H. Thalhammer, E. Eber, B. Oberwaldner, D. Dacar, M.S. Zach

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 57 KB

english, 2008

453

A 5-year retrospective study of totally implantable ports in CF patients

E. De Wachter, I. De Schutter, T. De Backer, A. Malfroot

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 57 KB

english, 2008

454

Growing up with TIVADs: effect on line position

S. Baird, N. Sinnott, A. Mohammad, M.J. Walshaw, M.J. Ledson

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 57 KB

english, 2008

455

How long can TIVADS be left unflushed?

B. Govin, H. Miller, C. Cowperthwaite, P. Dyce, M.J. Ledson, M.J. Walshaw

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 57 KB

english, 2008

456

Central vein obstruction due to TIVADs: treatment in one CF centre

N. Sinnott, S. Baird, M. Asim, M.J. Ledson, M.J. Walshaw

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 57 KB

english, 2008

457

Effects of pregnancy on the health of women with CF

S. Madge, P. Agent, G. Thorpe-Beeston

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 57 KB

english, 2008

458

The increasing range and complexity of surgery in patients with cystic fibrosis

E. Moisey, K. Heslop, A. Anderson, K. Stavers, M. Caraher, S. Johnston, A.D. Gascoigne, S.J. Bourke

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 57 KB

english, 2008

459

Serum cystatin C as a measure of renal function in patients with cystic fibrosis (CF)

N. Soulsby, H. Greville, J. Martin, G. Smith, D. Kennedy, K. Coulthard, C. Doecke

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 53 KB

english, 2008

460

Issues for cystic-fibrosis affected: recommendations for Asian resource-poor-nations to improve access-to-care

S. Pramod, R. Nirmalkumar

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 53 KB

english, 2008

461

Cystic fibrosis and Down's syndrome

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 52 KB

english, 2008

462

Diagnosis of cystic fibrosis in a four-months-old boy with acute liver failure

U. Graepler-Mainka, E. Sturm, U. Vogel, A. Knisley, C. Sokollik, M. Stern

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 52 KB

english, 2008

463

A rare presenting symptom of cystic fibrosis: acrodermatitis enteropathica-like skin eruptions

S. Pekcan, M. Kose, D. Dogru, B. Sekerel, U. Ozcelik, N. Cobanoglu, E. Yalcin, N. Kiper

Journal:

Journal of Cystic Fibrosis

Year:

2008

Language:

english

File:

PDF, 52 KB

english, 2008

464

Author Index

Journal:

Journal of Cystic Fibrosis

Year:

2008

File:

PDF, 79 KB

2008