Volume 8; Issue supp-S2

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Journal of Cystic Fibrosis
Volume 8; Issue supp-S2

Journal of Cystic Fibrosis

Volume 8; Issue supp-S2

1

New putative cis-acting regulatory variations in the CFTR gene

V. Viart, C. Bombieri, E. Lopez, C. René, M. Taulan, M. Claustres, M.C. Romey-Chatelain

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 65 KB

english, 2009

2

Editorial Board

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 43 KB

english, 2009

3

Foreword: Welcome to Brest to the 32nd European Cystic Fibrosis Conference

Claude Férec, Pierre Lehn

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 74 KB

english, 2009

4

Exonic sequence variations affecting splicing within exons 3, 4 and 5

A. Hinzpeter, A. Aissat, L. Golmard, A. de Becdelièvre, B. Costes, M. Goossens, E. Girodon, C. Costa, P. Fanen

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 65 KB

english, 2009

5

ETR-3 is a major regulator of CFTR pre-mRNA splicing

G. Dujardin, E. Buratti, N. Charlet-Berguerand, A. Mbopda, C. Le Jossic-Corcos, F. Pagani, C. Férec, L. Corcos

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 65 KB

english, 2009

6

Over-representation of NFκβ binding sites in CF human airway epithelial spheroid genes vs. nonCF

E.J. Solem, M. Hansen, P.S. Pedersen, J.T. Troelsen

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 65 KB

english, 2009

7

A new cryptic CFTR exon in mild CF

C. Costa, V. Prulière-Escabasse, L. Bassinet, L. Golmard, C. Gameiro, A. de Becdelièvre, M. Goossens, E. Girodon

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 58 KB

english, 2009

8

Validation of an interactive multimedia programme for informed decision-making in cystic fibrosis genetic testing

C. Castellani, S. Perobelli, V. Bianchi, P. Melotti, B.M. Assael, F. Lalatta

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 58 KB

english, 2009

9

The French CF Laboratory Network: seven years' experience

E. Girodon, M. des Georges, M.P. Audrézet, T. Bienvenu, E. Bieth, C. Costa, M. Delpech, M. Goossens, M. Claustres, C. Férec

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 58 KB

english, 2009

10

Complete sequencing of the CFTR gene using new generation GS-FLX sequencing technology

H. Cuppens, L. Vliegen, J.J. Cassiman

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 58 KB

english, 2009

11

Powerful strategy permits to rapidly characterise breakpoint junctions: essential for a better understanding of the molecular mechanism involving large rearrangements

C. Guittard, C. Thèze, M. des Georges, M. Claustres, M. Taulan

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 59 KB

english, 2009

12

MALDI-TOF mass spectrometry-based assay for CFTR gene mutation analysis in cystic fibrosis newborn screening programs

P. Raña-Díez, C. Colón, J.R. Alonso-Fernández, J.M. Fraga, A. Carracedo, F. Barros

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 59 KB

english, 2009

13

Sequence and MLPA analyses found CFTR mutations in all patients with classic CF

I. de Monestrol, V. Adermark, H. Cuppens, L. Hjelte

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 59 KB

english, 2009

14

Identification of large deletions and duplications in the CFTR gene using Multiple Ligation-dependent Probe Assay (MLPA), including one novel duplication and two novel deletions

M. Bulman, J. Brock, E. Brownsell, M.J. Schwarz

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 59 KB

english, 2009

15

Search for population-specific CFTR mutations: How to avoid the identification of unclassified variants

J.P. Altieri, C. Templin, C. Guittard, M. Claustres, M. des Georges

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 62 KB

english, 2009

16

Comprehensive analysis of the French NBS cohort: Excellent mutation detection rate despite high allelic heterogeneity

M. des Georges, E. Girodon, M.P. Audrézet, T. Bienvenu, E. Bieth, D. Cheillan, A. Iron, A. Kitzis, G. Lalau, M.C. Malinge, E. Houssin, M. Roussey, A. Munck

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 62 KB

english, 2009

17

In vivo and in vitro effect of E831X mutation

A. Hinzpeter, C. Costa, Y. Alembik, L. Weiss, M. Goossens, E. Girodon, P. Fanen

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 62 KB

english, 2009

18

Impact of the polymorphic variant 5 FR/G-260C in the Multidrug Resistance-associate Protein-1 gene on severity of cystic fibrosis

A. Mafficini, M. Ortombina, I. Sermet-Gaudelus, P. Lebecque, T. Leal, A. Leonard, G. Reychler, K. Dahan, X. Papermans, G. Lenoir, C. Sorio, P. Iansa, B.M. Assael, P. Melotti

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 62 KB

english, 2009

19

Nonclassic Cystic Fibrosis in subjects with D1152H CFTR mutation

P.R. Burgel, I. Fajac, D. Hubert, G. Bellis, T. Bienvenu, D.J. Dusser

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 60 KB

english, 2009

20

Cystic Fibrosis and mitochondrial gene mutation MT-RNRI

A.E. Hollsing, M.L. Bondesson

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 60 KB

english, 2009

21

Occurrence of complex CFTR alleles, revealed by extensive mutational analysis, can account for high sweat test variability

M. Lucarelli, L. Narzi, S.M. Bruno, A. Stamato, S. Pierandrei, F. Narzi, G. Ferraguti, A. Amato, S. Quattrucci, R. Strom

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 60 KB

english, 2009

22

Analysis of eNOS, TNFA, LTA, GSTM1, MBL2, ADRB2, HFE genes as modifier genes in Russian Cystic Fibrosis patients

E.E. Timkovskaya, N.V. Petrova, N.J. Kashirskaya, Z.A. Kusova, R.A. Zinchenko

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 60 KB

english, 2009

23

An appropriate diagnostic approach can improve detection of CFTR mutations: the experience in Patients with Classical Form of Cystic Fibrosis coming from an Italian Region with high genetic heterogeneity

A. Ravani, A. Venturoli, S. Carturan, S. Brioschi, M. Taddei Masieri, S. Fini, C. Trabanelli, B. Dolcini, P. Rimessi, F. Battistini, M. Ambroni, G.L. Grzincich, E. Calzolari, A. Ferlini

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 57 KB

english, 2009

24

Clinical phenotype for the G551D mutation

D.M. Comer, J.C. Rendall, V. Hall, M. Ennis, J.S. Elborn

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 56 KB

english, 2009

25

CFTR gene analysis in the Western-Ukrainian population: an unusually high frequency of the 2184insA mutation

P. Krenkova, H. Makukh, M. Hancarova, L. Dvorakova, A. Stambergova, M. Macek Jr.

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 57 KB

english, 2009

26

Identification of a novel frameshift mutation in CFTR gene: description, and clinical data

R. Gaillyová, I. Valášková, S. Tavandzis, A. Holčíková

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 57 KB

english, 2009

27

Spectrum of CFTR mutations in northern Portugal patients with CF and related phenotypes

A. Grangeia, F. Carvalho, M. Sousa, A. Barros

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 66 KB

english, 2009

28

The variety of Cystic Fibrosis genotypes of patients from Western Ukraine: ethnographical and population impact

H. Makukh, M. Tyrkus, D. Zastavna, H. Akopyan, L. Bober, O. Hnateyko

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 66 KB

english, 2009

29

The spectrum of CFTR mutations in populations from Romania

L. Tamas, Z.L. Popa, L. Pop, I. Popa, A. Anghel, Z. Popa, C. Samoila, I.M. Ciuca

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 66 KB

english, 2009

30

Molecular basis of cystic fibrosis in Republic of Macedonia: An update

S. Fustik, T. Jakovska, S. Koceva, G. Efremov

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 66 KB

english, 2009

31

Mutation analysis of CFTR gene in Slovak CF patients

A. Soltysova, A. Ficek, M. Baldovic, P. Kolesar, G. Minarik, L. Kadasi, H. Polakova, H. Kayserova

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 45 KB

english, 2009

32

Quality improvement in newborn screening for cystic fibrosis by process failure mode effects analysis (PFMEA)

P.M. Farrell, M.K. Kloosterboer, R.C. Reynolds, Z. Li

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 63 KB

english, 2009

33

Cystic fibrosis Heelprick among a newbOrn Population in the Netherlands: the CHOPIN-study

A.M. Vernooij-van Langen, J.G. Loeber, L.H. Elvers, R.H. Triepels, J.J. Gille, C.P. van der Ploeg, S. Reijntjens, E. Dompeling, J.E. Dankert-Roelse

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 63 KB

english, 2009

34

Cystic Fibrosis (CF) Newborn Screening (NBS) – Comparison of an IRT-PAP with an IRT-DNA based protocol in a German population

O. Sommerburg, M. Lindner, M. Muckenthaler, M.A. Mall, A. Kulozik, G.F. Hoffmann

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 63 KB

english, 2009

35

Revealing potential plasma lipid biomarkers of cystic fibrosis by mass spectrometry

C. Guerrera, J. Colas, D. Sands, D.L. Vieu, I. Sermet-Gaudelus, G. Astarita, D. Piomelli, A. Edelman, M. Ollero

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 63 KB

english, 2009

36

Evaluation of European protocols for measuring nasal potential differences

I. Bronsveld, M. Sinaasappel, K.W. Southern, I. Sermet-Gaudelus, T. Leal, P. Melotti, M. Ballmann, L. Hjelte, P.G. Middleton, K. De Boeck, M. Wilschanski

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 67 KB

english, 2009

37

Comparison of nasal potential difference measurements done on the nasal floor and under the inferior turbinate: repeatability

F. Vermeulen, F. Vermeulen, N. Feyaerts, M. Proesmans, K. De Boeck

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 67 KB

english, 2009

38

Comparison of nasal potential difference measurements done on the nasal floor and under the inferior turbinate: success rate and mean values

F. Vermeulen, F. Vermeulen, N. Feyaerts, M. Proesmans, K. De Boeck

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 67 KB

english, 2009

39

Evaluation of a new tool for measurement of sweat chloride concentration

D. Hubert, D.J. Dusser, A. Bry, I. Fajac

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 67 KB

english, 2009

40

Implementation of the UK Newborn Screening Programme

K.W. Southern, D. Sinclair, B. Judge, R.J. Pollitt, I.J. Doull, D.M. Bradley, J.F. Price

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 62 KB

english, 2009

41

Proficiency Testing for CF Newborn Screening

M.C. Earley, L. Li, R. Driscoll-Dunn, J. Mei, W.H. Hannon

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 62 KB

english, 2009

42

Survival analysis of CF patients diagnosed in a 35-year neonatal screening program in North-eastern Italy

N. Tacchella, P. Iansa, C. Castellani, B.M. Assael

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 62 KB

english, 2009

43

Towards a consensus on the early management of infants identified with cystic fibrosis following newborn screening (NBS)

I. Sermet-Gaudelus, S. Mayell, K.W. Southern

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 62 KB

english, 2009

44

Clinical characteristics of infants diagnosed through cystic fibrosis newborn screening (CF NBS)

D. Sands, K. Zybert, M. Oltarzewski, A. Sobczynska-Tomaszewska, A. Nowakowska, K. Walicka, K. Wertheim, R. Piotrowski

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 59 KB

english, 2009

45

Risk factors for poor outcomes in Cystic Fibrosis – 10 years of challenging experience in Eastern Europe

L.L. Dracea, L. Pop

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 59 KB

english, 2009

46

Comprehensive cost comparison of newborn screening strategies with novel inclusion of costs related to genetic counseling and collection of second specimens

J.M. Wells, M.A. Rosenberg, G. Hoffman, M.I. Anstead, P.M. Farrell

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 59 KB

english, 2009

47

Incidence of the CFTR exon 9 and its flanking sequence duplication on the mutation diagnosis in CF patients

A. EL-Seedy, T. Dudognon, F. Bilan, M.C. Pasquet, A. Iron, A. Kitzis, V. Ladeveze

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 59 KB

english, 2009

48

Inconclusive CF diagnosis in Neonatal Screening

C. Colón, P. Raña-Díez, A. Solar, C. Soler, L. García, R. Reparaz, A. Ruiz, J. Ramos, M. Tabarés, P. Pavón, R. Cabanas, J.R. Alonso-Fernández, A. Carracedo, F. Barros, J.M. Fraga

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 66 KB

english, 2009

49

CF Diagnosis Announcement Practices following a neonatal screening in France

L.J. Guéganton, G. Minguet, C. Langeard, C. Faquet, P. Cam, P. Lombrail, G. Rault

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 66 KB

english, 2009

50

Comparing six countries experience of newborn screening for CF

J. Cowlard, S.B. Carr, C.S. Pao

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 66 KB

english, 2009

51

Neonatal CF screening (2003–2008) in the Aquitaine region in France: high probability of a second CFTR gene mutation in heterozygotes with subnormal sweat tests

A. Iron, S. Bui, M.P. Reboul, P. Fergelot, D. Lacombe, M. Fayon

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 66 KB

english, 2009

52

Newborn screening for cystic fibrosis in Sicily (Italy): more benefits than harms

G. Vieni, F. Pardo, M. Lombardo, L. Termini, M.C. Lucanto, G. Traverso, M. Collura, M.L. Furnari, S. Faraci, G. Magazzù

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 60 KB

english, 2009

53

Cystic Fibrosis incidence in Lombardy over a seven year period

V. Paracchini, M. Seia, S. Raimondi, L. Porcaro, L. Costantino, P. Capasso, D. Degiorgio, D. Coviello, C. Colombo, T. Mariani, C. Corbetta

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 60 KB

english, 2009

54

Genetic aspect of two-year experience in cystic fibrosis newborn screening program in Poland

A. Norek, A. Sobczynska-Tomaszewska, M. Oltarzewski, K. Wertheim, K. Czerska, D. Sands, K. Zybert, J. Bal

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 60 KB

english, 2009

55

Patients homozygous for F508del are not different at the beginning

L. Homola, A. Holčíková, M. Kyr, I. Valášková

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 60 KB

english, 2009

56

Complete screening of the CFTR gene in idiopathic chronic pancreatitis

E. Masson, M.P. Audrézet, C. Le Maréchal, J.M. Chen, C. Férec

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 62 KB

english, 2009

57

Identification of CFTR rearrangements by a CGH locus specific array

S. Quéméner, C. Bénech, C. Le Maréchal, K. Giteau, M.P. Audrézet, J.M. Chen, C. Férec

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 62 KB

english, 2009

58

A two-days full-scanning of the CFTR gene for simultaneous detection of point mutations and large rearrangements using High Resolution Melting analysis (HRM) in combination with quantitative real-time PCR

C. Thèze, V. Gaston, G. Carriere, M. Claustres, M. des Georges, E. Bieth

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 63 KB

english, 2009

59

Strategy for prenatal diagnosis of cystic fibrosis in Russia

N.V. Petrova, E.E. Timkovskaya, T.A. Vasilyeva, R.A. Zinchenko

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 62 KB

english, 2009

60

Ability of ultrasonography to detect cystic fibrosis in utero

V. Scotet, I. Duguépéroux, M.P. Audrézet, M. Blayau, C. Férec

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 59 KB

english, 2009

61

First results of preimplantation genetic diagnosis of cystic fibrosis in Russia

P.A. Basanov, P.A. Gogolevsky, I.K. Gogolevsky, M.A. Ivanov, N.J. Kashirskaya, N.I. Kapranov, M.A. Kurtser

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 59 KB

english, 2009

62

Preimplantation genetic diagnosis for cystic fibrosis

C. Fernandez, C. Guittard, M. des Georges, J.P. Altieri, C. Templin, M. Claustres, A. Girardet

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 59 KB

english, 2009

63

Trisomy 21 – possible cause for false positive sweat test?

L. Pop, Z. Popa, C. Nicolicea, I.M. Ciuca, A. Lacatusu, E. Zborovszky, C. Gug, L. Tamas, I. Popa

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 59 KB

english, 2009

64

Modeling of the whole CFTR 3D structure and its conformational transitions

J.P. Mornon, P. Lehn, I. Callebaut

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 56 KB

english, 2009

65

Refinement of CFTR transmembrane segments by a novel prediction tool

D. Paulet, M. Claustres, C. Béroud

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 56 KB

english, 2009

66

Rescue of CF airway epithelial cell function in vitro by a CFTR potentiator, VX-770

F. Van Goor, B. Burton, S. Hadida, P. Grootenhuis, E.R. Olson, J. Wine, R. Frizzell, M.A. Ashlock, P. Negulescu

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 56 KB

english, 2009

67

Rescue of A455E CFTR by temperature, small molecule correctors and transcomplementation

L. Cebotaru, W. Guggino

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 56 KB

english, 2009

68

Molecular dissection of the MPB interacting site of CFTR

A. Billet, P. Melin, H. Cuppens, F. Becq

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 59 KB

english, 2009

69

Correction of the F508del-CFTR function by the Gonadotropin-Releasing hormone (GnRH) in polarized and non-polarized epithelial cells

N. Benz, P. Trouvé, C. Férec

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 59 KB

english, 2009

70

COMMD1 promotes CFTR trafficking through inhibition of ubiquitination

L. Drévillon, G. Tanguy, B. Saubamea, A. de Becdelièvre, A. Hinzpeter, N. Arous, P. Fanen

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 59 KB

english, 2009

71

Estrogen and phytoestrogens increase the CFTR and F508del CFTR expression and function

N. Hamdaoui, D.L. Vieu, M. Baudouin-Legros, A. Edelman, G. Planelles

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 59 KB

english, 2009

72

SiRNA calnexin promotes endogenous F508del-CFTR trafficking

D. Raveau, A. Cantereau, F. Becq, C. Norez

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 57 KB

english, 2009

73

Agonists of peroxisome proliferator activated receptor gamma (PPARγ) modulate transepithelial anion secretion in human bronchial epithelial cells

N. Madsen, M. Duszyk

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 57 KB

english, 2009

74

Connexin 26 is implied in the regulation of airway epithelium repair

S. Crespin, M. Bacchetta, I. Scerri, T. Dudez, M. Chanson

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 57 KB

english, 2009

75

Connexin channels mediate PGE2-dependent regulation of CFTR activity in Calu-3 cells

D. Losa, L. Scheckenbach, T. Dudez, M. Chanson

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 57 KB

english, 2009

76

CFTR and tight junctions in cultured bronchial epithelial cells

H.E. Nilsson, A. Dragomir, L. Lazorova, M. Johannesson, G.M. Roomans

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 55 KB

english, 2009

77

PDZ protein interaction: the missing link between CFTR and mucins

T. Pelaseyed, G.C. Hansson

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 55 KB

english, 2009

78

Regulation of mucin 5AC expression by arachidonic acid metabolites

I. Garcia-Verdugo, S. Tattermusch, D. Leduc, F. Dif, Y. Wu, L. Touqui

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 55 KB

english, 2009

79

Proteomic analysis of G551D and R117H-CFTR associated proteins

L. Teng, P. Trouvé, C. Férec

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 55 KB

english, 2009

80

Requirement of endosomal SNARE protein complex in CFTR activity/trafficking regulation

R. Clément, F. Fresquet, P. Melin, F. Becq, A. Kitzis, V. Thoreau

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 53 KB

english, 2009

81

Increased interaction of F508del-CFTR with K8/K18 cytokeratin network by direct binding of K8 to NBD1

J. Colas, G. Faure, S. Trudel, J. Fritsch, C. Guerrera, N. Davezac, F. Brouillard, H. Herrmann, M. Ollero, A. Edelman

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 53 KB

english, 2009

82

The calpain-caspase 12-caspase 3 cascade leading to apoptosis is altered in F508del-CFTR expressing cells

M. Kerbiriou, N. Benz, P. Trouvé, C. Férec

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 53 KB

english, 2009

83

Pharmacological inhibition of CFTR modifies cyclooxygenase-1 and -2 expression and PGD2 production in Calu-3 cells

M. Baudouin-Legros, M. Kelly, M. Ollero, A. Edelman

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 53 KB

english, 2009

84

Expression of Unfolded Protein Response (UPR) protein markers are increased in primary and cystic fibrosis (CF) nasal polyposis (NP)

L. Jeanson, C. Guerrera, M. Baudouin-Legros, S. Amselem, A. Coste, E. Escudier, A. Edelman

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 64 KB

english, 2009

85

Functional Evaluation of Cystic Fibrosis Transmembrane Conductance Regulator (CFTR) in human monocytes

C. Sorio, M. Buffelli, M. Ettorre, M. Vezzalini, M. Ricciardi, C. Angiari, J. Johansson, B.M. Assael, P. Melotti

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 64 KB

english, 2009

86

The antimicrobial peptide LL-37 modulates the inflammatory and host defense response of human neutrophils

S. Alalwani, J. Sierigk, C. Herr, O. Pinkenburg, R. Bals

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 64 KB

english, 2009

87

Airway epithelial responses to hypertonic solutions: different in vivo responses in CF and non-CF human subjects

P.G. Middleton, H.H. House

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 64 KB

english, 2009

88

Long acting β2-agonist and corticosteroid restore airway glandular cell functionality altered by Staphylococcus aureus virulence factors

J.M. Zahm, F. Delavoie, F. Toumi, C. Kileztky, J. Michel, G. Balossier, C. Coraux, P. Birembaut

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 63 KB

english, 2009

89

Are basal cells progenitors of the human bronchiolar epithelium?

T. Jolly, R. Le Naour, S. Collet, P. Birembaut, C. Coraux

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 63 KB

english, 2009

90

Epithelial factors produced during the remodelling of the human airway epithelium

J. Roux, T. Jolly, S. Collet, P. Birembaut, C. Coraux

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 63 KB

english, 2009

91

Mitochondrial glutathione and decreased complex I activity in cystic fibrosis models

M. Kelly, S. Trudel, T. Nguyen-Khoa, J. Fritsch, F. Djouadi, A. Edelman, F. Brouillard

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 63 KB

english, 2009

92

Activity of lysosomal carboxypeptidase A, neuraminidase and glucuronidase in saliva of cystic fibrosis patients

A. Minarowska, L. Minarowski, D. Sands, M. Knas, S. Szajda, A. Karwowska, M. Gacko

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 52 KB

english, 2009

93

Randomised, double blind, placebo-controlled Phase III Study of Bronchitol (inhaled dry powder mannitol) in Cystic Fibrosis (CF)

D. Bilton, P. Robinson, P. Cooper, B. Charlton

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 68 KB

english, 2009

94

Safety/Efficacy of Inhaled Human Alpha-1 Antitrypsin (AAT) in CF: A Phase II Clinical Study

E. Kerem, S. Bauer, P. Strauss, N. Jaffe, S. Armoni, T. Pugatsch, D. Shoseyov, N. Tov

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 68 KB

english, 2009

95

Final results of a 14- and 28-day study of VX-770 in subjects with CF

F.J. Accurso, S.M. Rowe, P.R. Durie, M.W. Konstan, J. Dunitz, D.B. Hornick, S.D. Sagel, M.P. Boyle, A.Z. Uluer, R.B. Moss, B.W. Ramsey, S.D. Freedman, Q. Dong, J. Zha, A.J. Stone, E.R. Olson, C.L. Ord

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 69 KB

english, 2009

96

Pharmacological characterization of a novel water-soluble activator of F508del-CFTR

J. Bertrand, B. Boucherle, L. Dannhoffer, P. Melin, C. Routaboul, J.L. Décout, F. Becq, C. Norez

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 68 KB

english, 2009

97

Roscovitine: a novel corrector for the functional rescue of F508del-CFTR protein

C. Norez, C. Vandebrouck, L. Meijer, F. Becq

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 57 KB

english, 2009

98

Effects of denufosol on sinusitis-related complaints in a phase 3 trial in cystic fibrosis patients

A.R. Mospan, T.A. Durham, A.E. Schaberg, F.J. Accurso

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 57 KB

english, 2009

99

Relationship between pulmonary exacerbations and lung function decline in a six month trial of denufosol

F.J. Accurso, T.A. Durham, A.E. Schaberg

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 57 KB

english, 2009

100

The novel long acting ENaC blocker P643 has therapeutic effects in chronic cystic fibrosis-like lung disease in mice

Z. Zhou, M. Harm, D.A. Treis, S.C. Schubert, J. Schatterny, S. Hirtz, J. Duerr, A.J. Hirsh, M. Ross Johnson, R.C. Boucher, M.A. Mall

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 58 KB

english, 2009

101

Effect of N-butyldeoxynojirimycin on chloride efflux from CF airway epithelial cells

I. Oliynyk, G.M. Roomans

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 71 KB

english, 2009

102

Flavonoides increase chloride conductance at the apical membrane of the respiratory epithelium in some CF-patients

C. Geidel, C. Rueckes-Nilges, S. Klahr, J. Burmeister, K. Weber, D. Schueler, R. Schulz, H. Lindemann, K.P. Zimmer

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 72 KB

english, 2009

103

Effective treatment of chronic Pseudomonas aeruginosa (Pa) infection with tobramycin inhalation powder in CF patients

M.W. Konstan, D.E. Geller, P. Minic, F. Brockhaus, J. Zhang, G. Angyalosi

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 71 KB

english, 2009

104

Pharmacokinetics of tobramycin (TOBI™) after 4 and 8 weeks of continuous once daily or twice daily inhalation

E. Rietschel, H.G. Posselt, H.E. Heuer, N. Merkel, D. Staab

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 71 KB

english, 2009

105

Effect of multiple courses of Aztreonam Lysine for Inhalation (AZLI) on FEV1 and weight in patients with cystic fibrosis (CF) and Pseudomonas aeruginosa (PA): Analysis of 18 month data from CP-AI-006

C.M. Oermann, K.S. McCoy, G.Z. Retsch-Bogart, R.L. Gibson, A.B. Montgomery

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 69 KB

english, 2009

106

Efficacy of Aztreonam Lysine for Inhalation (AZLI) in patients with cystic fibrosis and drug resistant P. aeruginosa (DRPA)

K.S. McCoy, G.Z. Retsch-Bogart, R.L. Gibson, C.M. Oermann, M. McKevitt, A.B. Montgomery

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 69 KB

english, 2009

107

Adherence over multiple courses of Aztreonam Lysine for Inhalation (AZLI): effect on disease-related endpoints in patients with cystic fibrosis (CF) and Pseudomonas aeruginosa (PA)

C.M. Oermann, K.S. McCoy, G.Z. Retsch-Bogart, R.L. Gibson, A.L. Quittner, A.B. Montgomery

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 69 KB

english, 2009

108

Chronic toxicity study of lancovutide in beagle dogs

C. Wachter, R. Widmann

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 69 KB

english, 2009

109

Characterization of bacterial strains isolated from the CF patients in Georgia and evaluation of the efficacy of phage treatment

M.I. Kutateladze, E.S. Tevdoradze, N.S. Balarjishvili, N.R. Skhirtladze, R.S. Adamia, T.I. Tophuria

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 58 KB

english, 2009

110

A gift of Nature for the treatment of Pseudomonas aeruginosa

C. Sandre-Ballester

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 58 KB

english, 2009

111

Orphan drug designation to Anti-pseudomonas IgY

E. Nilsson, A.E. Hollsing, A. Larsson, H. Kollberg

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 58 KB

english, 2009

112

Activity of liposomal formulations on sputum isolated from CF Patients

M. Halwani, S. Hebert, Z.E. Suntres, M. Alipour, A. Omri

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 58 KB

english, 2009

113

New targeting method for nucleic acid transfer into the lung

F. Beilvert, E. Letrou-Bonneval, R. Chèvre, R. Labas, B. Pitard

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 68 KB

english, 2009

114

Variations on hydrophobic domains in Lipophosphoramidates results in lung transfection's improvement and lower toxicity

T. Montier, T. Le Gall, N. Carmoy, M. Lindberg, E. Létocart, A. Fraix, C. Lorilleux, J.J. Yaouanc, P. Delépine, D. Gillet, P.A. Jaffrès, P. Lehn

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 68 KB

english, 2009

115

Histidinylated linear PEIs as new DNA carriers for in vitro and in vivo gene transfer with low toxicity

P. Guégan, E. Bertrand, T. Le Gall, C. Pichon, T. Montier, P. Lehn, H. Cheradame, P. Midoux

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 68 KB

english, 2009

116

The Adenovirus chimeric vector Ad5F35/GFP-CFTR efficiently restores the CFTR deficiency in human airway epithelia via apical surface transduction

G. Gonzalez, O. Granio, K.J. Ashbourne-Excoffon, P. Henning, P. Melin, C. Norez, P.H. Karp, L. Lindholm, F. Becq, P. Boulanger, J. Zabner, S.S. Hong

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 68 KB

english, 2009

117

Cell targeting for CF gene therapy: Identification of a new specific cell ligand and selection of infectious papillomavirus mutants

A. Carpentier, E. Alvarez, L. Bousarghin, A. Delannoy, A. Touzé, P. Coursaget

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 63 KB

english, 2009

118

Click chemistry: a promising approach to improve targeting ability of non-viral pulmonary gene transfer

R. Labas, E. Letrou-Bonneval, R. Chèvre, F. Beilvert, B. Pitard

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 63 KB

english, 2009

119

Impact of polymers on lipid cationic mediated gene transfer

R. Chèvre, E. Letrou-Bonneval, R. Labas, F. Beilvert, B. Pitard

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 62 KB

english, 2009

120

Synthesis and transfection properties of a series of lipidic neamine derivatives

T. Le Gall, T. Montier, I. Baussanne, S. Halder, N. Carmoy, P. Lehn, J.L. Décout

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 63 KB

english, 2009

121

Intestinal Current Measurement (ICM) in Europe: towards a harmonised protocol for clinical trials in cystic fibrosis

N. Derichs, I. Bronsveld, M. Sousa, M.J. Hug, Y. Yaakov, M. Ballmann, M. Amaral, M. Wilschanski, H. de Jonge

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 60 KB

english, 2009

122

Target Inhalation Mode, a new Adaptive Aerosol Delivery mode for the reduction of treatment time when using the I-neb AAD System

A. Black, C. Smart, K. Nikander, T. Dyche, J. Denyer

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 59 KB

english, 2009

123

Nuclear delivery of DNA/histidine-polymer complexes: confocal microscopy real time investigation of the nuclear import of a plasmid DNA containing an optimized DNA κB sequence

G. Breuzard, C. Gonçalves, T. Thibault, H. Cheradame, P. Guégan, B. Hartmann, C. Pichon, P. Midoux

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 60 KB

english, 2009

124

Optimizing aerosol administration in Cystic Fibrosis and Asthma treatment with improved Smart Card technology

P. Kroneberg, B. Muellinger, A. Fischer, G. Scheuch

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 59 KB

english, 2009

125

Change in composition and structure of bacteria in the CF airway over one year

F.A. Stressmann, G.B. Rogers, T. Daniels, A.K. Lilley, M.P. Carroll, G. Jones, B. Forbes, N. Patel, K.D. Bruce

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 65 KB

english, 2009

126

Are Cough Swabs a Valid Tool in the Adult Cystic Fibrosis Population?

E. Lloyd, M.J. Ledson, M.J. Walshaw

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 65 KB

english, 2009

127

EuroCareCF European Microbiology Quality Assurance Trials

M. Hogardt, J. Ulrich, H. Riehn-Kopp, B. Tümmler

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 65 KB

english, 2009

128

Distribution of Burkholderia cepacia complex genomovars from agricultural samples in French western Brittany and epidemiological significance

M.L. Abalain, V. Barrère, S. Gouriou, F. Deniel, L. Castrec, C. Segonds, G. Héry-Arnaud, G. Rault, C. Payan, G. Barbier

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 65 KB

english, 2009

129

Comparison of biofilm formation between Burkholderia multivorans Burkholderia cenocepacia Pseudomonas aeruginosa in the presence or absence of mucin

G.G. Einarsson, A. McDowell, J.S. Elborn, S.L. Martin

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 65 KB

english, 2009

130

Congo Red staining of CF-related pathogens grown as biofilms in the absence or presence of mucin

G.G. Einarsson, A. McDowell, J.S. Elborn, S.L. Martin

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 65 KB

english, 2009

131

Clonally identical Burkholderia cepacia complex (Bcc) sequence type strain ST32 isolated from cystic fibrosis (CF) patients in French western Brittany compared to epidemiology of Bcc strains in France using Multilocus sequence typing (MLST)

M.L. Abalain, G. Héry-Arnaud, S. Gouriou, J. Lintanf, V. Barrere, C. Segonds, G. Chabanon, G. Rault, G. Barbier, C. Payan

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 65 KB

english, 2009

132

Burkholderia cenocepacia: nearing the end?

E.M. Spencer, A. Ponnuswamy, M.J. Ledson, M.J. Walshaw

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 64 KB

english, 2009

133

Lung transplantation in Burkholderia and Ralstonia infected CF patients

C. Segonds, R. Souilamas, D. Grenet, C. Dromer, A. Haloun, M. Reynaud-Gaubert, G. Chabanon

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 65 KB

english, 2009

134

In vitro activity of tigecycline and other antibiotics against Burkholderia cepacia complex (Bcc) and other cystic fibrosis (CF)-associated Gram negative bacteria

J. Kenning, S.P. Conway, M. Denton

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 65 KB

english, 2009

135

Microbiological and epidemiological features of clinical respiratory isolates of Burkholderia gladioli

C. Segonds, M. Thouverez, D. Grenet, P. Plésiat, G. Chabanon

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 65 KB

english, 2009

136

Evaluation of a novel chromogenic medium for isolation and characterization of Pseudomonas aeruginosa from the sputa of cystic fibrosis (CF) patients

D. Fournier, C. Bailly, D. Hocquet, K. Jeannot, P. Plésiat

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 65 KB

english, 2009

137

Volatile organic compound analysis in the early detection of Pseudomonas aeruginosa in cystic fibrosis

S. Smith, C.S. Probert, M. Williams, D.G. Downey

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 68 KB

english, 2009

138

Comparison of the sensitivity of six PCR formats for the detection of P. aeruginosa

P. Deschaght, T. De Baere, L. Van Simaey, S. Roels, P. Schelstraete, S. Van Daele, F. De Baets, M. Vaneechoutte

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 68 KB

english, 2009

139

Early detection of Pseudomonas aeruginosa (PA) in patients with cystic fibrosis (CF) by real-time PCR (RT-PCR): original method developed for a preliminary study

G. Héry-Arnaud, R. LeBerre, M.L. Abalain, J. Hardy, S. Gouriou, C. Payan

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 68 KB

english, 2009

140

Paranasal sinuses are a focus for P. aeruginosa (PA) lung infection in CF

H.K. Johansen, K. Aanaes, T. Pressler, S.K. Hansen, M. Skov, K.G. Nielsen, S. Molin, N. Høiby, C. Buchwald

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 68 KB

english, 2009

141

Segregation of children 5 and under diagnosed via newborn screening does not prevent acquisition of P. aeruginosa

K. McKay, P. Cooper, P. van Asperen

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 68 KB

english, 2009

142

Prevention of initial P. aeruginosa infection in children with cystic fibrosis: a multi-centre double-blind randomised controlled trial

G. Tramper-Stranders, T.F.W. Wolfs, W. van Aalderen, J. Kouwenberg, A. Nagelkerke, C.K. van der Ent

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 68 KB

english, 2009

143

Monitoring of the Initial Pseudomonas aeruginosa Colonization in Cystic Fibrosis Patients Demonstrated High Clonal Diversity

A. Fernández-Olmos, R. del Campo, A. Lamas, P. Ruiz-Garbajosa, L. Maiz, F. Baquero, R. Canton

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 68 KB

english, 2009

144

Clinical impact of a highly prevalent P. aeruginosa clone in Dutch CF patients

A.M. de Vrankrijker, R. van Mansfeld, T.F.W. Wolfs, F. Teding van Berkhout, R.J. Willems, M.J. Bonten, C.K. van der Ent

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 68 KB

english, 2009

145

An aerosol decay model of Pseudomonas aeruginosa survival

I.J. Clifton, L.A. Fletcher, C.B. Beggs, M. Denton, D. Peckham

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 65 KB

english, 2009

146

Genotyping of Pseudomonas aeruginosa isolates from aquatic environment at a Swedish hospital and relation to infection of lung transplanted patients with Pseudomonas

E. Johansson, C. Welinder-Olsson, C. Börjesson, L. Peterson, L. Larsson, M. Gilljam

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 65 KB

english, 2009

147

Molecular typing of Ps. aeruginosa direct from clinical specimens

E. McCulloch, M. McMillan, C. Lucas, G. Ramage, E. Mowat, C. William

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 65 KB

english, 2009

148

Is quorum sensing related to strain type in Pseudomonas aeruginosa

C. Frerichs, S. Crusz, M. Fletcher, M. Cámara, P. Williams, D. Barrett, K. Towner, A.R. Smyth

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 65 KB

english, 2009

149

Development of a low dose nasal infection model with Pseudomonas aeruginosa in mice

F. Woelbeling, A. Munder, B. Tümmler, U. Baumann

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 69 KB

english, 2009

150

Genotype based evaluation of eradication treatment of new P. aeruginosa infections in CF patients

P. Schelstraete, P. Deschaght, S. Van Daele, F. Haerynck, L. Van Simaey, M. Vaneechoutte, F. De Baets

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 69 KB

english, 2009

151

Interim outcomes of a Pseudomonas aeruginosa (Pa) eradication protocol in young children in the Australasian Cystic Fibrosis Bronchoalveolar Lavage (ACFBAL) Study

J. Cheney, S. Vidmar, K. Grimwood, J.B. Carlin, C. Wainwright

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 69 KB

english, 2009

152

Eradication of Pseudomonas aeruginosa in adults with CF

S. Kenny, V. Hall, C. Goldsmith, J. Moore, J.C. Rendall, J.S. Elborn

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 69 KB

english, 2009

153

Genotyping of Pseudomonas aeruginosa isolates can predict the transition to chronic colonization in CF patients

P. Schelstraete, P. Deschaght, S. Van Daele, F. Haerynck, L. Van Simaey, M. Vaneechoutte, F. De Baets

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 68 KB

english, 2009

154

Analysis of proteins released from Pseudomonas aeruginosa clinical and laboratory strains: effects of azithromycin

G. Bergamini, P. Mauri, C. Cigana, D. Di Silvestre, A. Di Palma, A. Bragonzi, B.M. Assael, C. Sorio, P. Melotti

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

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english, 2009

155

Lack of Differences in Mutant Prevention Concentration Rates Between Cystic Fibrosis Pseudomonas aeruginosa Isolates in Planktonic and Biofilm Type of Growth

M. Garcia-Castillo, M.C. Turrientes, M.I. Morosini, F. Baquero, R. Canton, R. del Campo

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

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english, 2009

156

Antibiotics sensitivity in mucoid and non mucoid Pseudomonas aeruginosa isolates from cystic fibrosis patients

L. Cariani, G. Defilippi, D. Costantini, C. Colombo, M.L. Garlaschi, E. Torresani, A. Biffi

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 68 KB

english, 2009

157

Colistin sulfate/tobramycin combination is superior for killing biofilm P. aeruginosa than monotherapy in vitro

G. Herrmann, L. Yang, S. Molin, M. Ulrich, M. Haug, G. Doering

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 73 KB

english, 2009

158

Resistance in cystic fibrosis Pseudomonas aeruginosa strains is not mediated by common acquired antibiotic resistance genes

J.P. Pirnay, F. Bilocq, J. Van Eldere, T.L. Pitt, P. De Schaght, M. Vaneechoutte, S. Jennes, D. De Vos

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 73 KB

english, 2009

159

Resistance mechanisms to β-lactams in cystic fibrosis (CF) Pseudomonas aeruginosa isolates: a French Multicentre Study

C. Llanes, A. Mérens, C. Pourcel, M. Roussel-Delvallez, G. Vergnaud, J. Cavallo, P. Plésiat

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

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english, 2009

160

MRSA and macrolide resistant Staphylococcus aureus colonization rates in a Turkish CF center

O. Dogan, B. Sener, E. Yalcin, D. Dogru, U. Ozcelik, N. Kiper

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

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english, 2009

161

Comparison of MRSA isolated from patients in two paediatric CF centres

D.F. Gilpin, J. McCaughan, M. Muhlebach, M. Macfarlane, A. Reid, J.S. Elborn, W. Ziebuhr, M.M. Tunney

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

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english, 2009

162

Characterization of SCC mec types involved in persistent MRSA infections in cystic fibrosis patients

P. Cocchi, N. Ravenni, V. Boni, G. Doering, C. Braggion, G. Taccetti, S. Campana

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

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english, 2009

163

Community-Acquired MRSA causes earlier infection than Hospital-Acquired MRSA in patients with cystic fibrosis

S. Campana, P. Cocchi, F. Trevisan, C. Costantini, V. Raia, V. Lucidi, A. Negri, L. Ratcliff, R. Gagliardini, E. Provenzano, G. Doering, G. Taccetti, C. Braggion

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

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english, 2009

164

Eradication of methicillin resistant Staphylococcus aureus in cystic fibrosis

M. Kappler, M. Feilcke, A. Schweiger-Kabesch, C. Schröter, J. Liese, J. Ripper, A. Hector, M. Griese

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

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english, 2009

165

Staphylococcus aureus with decreased susceptibility to glycopeptides in cystic fibrosis patients

A. Filleron, R. Chiron, H. Jean-Pierre, M. Reverdy, F. Counil, L. Aleyrangues, E. Jumas-Bilak, H. Marchandin

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 68 KB

english, 2009

166

Characteristics of Staphylococcus aureus small colony variants (SCV) in CF patients

S. Yagci, G. Hascelik, E. Yalcin, D. Dogru, B. Sener, U. Ozcelik, N. Kiper

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

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english, 2009

167

Staphylococcus aureus small colony variants (SASCVs) in CF pts treated at Children's Memorial Health Institute, Warsaw, Poland

H. Dmenska, K. Semczuk, K. Dzierzanowska-Fangrat, D. Dzierzanowska

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 68 KB

english, 2009

168

Diversity of Candida spp in adult CF patients

C. Baxter, A.M. Jones, A.K. Webb, J. Thornback, D. Ireland, D. Denning

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 67 KB

english, 2009

169

Evaluation and management of fungal risk in Cystic Fibrosis: first results of a national French study

S. Leroy, V. Conseil, B. Coltey, Y. Lemeille, S. Dominique, G. Gargala, P. Domblides, I. Accoceberry, G. Loeuille, I. Durand-Joly, A. Fanton, O. Vagnier, F. Dalle, A. Boldron, C. Llerena, C. Pinel, J.

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 67 KB

english, 2009

170

Itraconazole (ITZ) resistant Aspergillus fumigatus (Af) in CF patients

M. Reijers, F. van Herpen, E. Houthuijs, J.L. Yntema, P.E. Verheij

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 67 KB

english, 2009

171

Fungal allergy in adult cystic fibrosis

C. Baxter, A.M. Jones, A.K. Webb, D. Denning

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 66 KB

english, 2009

172

Comparative study of predominant fecal microbiota of cystic fibrosis patients and healthy siblings

G. Duytschaever, G. Huys, L. Boulanger, K. De Boeck, P. Vandamme

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 67 KB

english, 2009

173

Clinical Microbiology of Haemophilus influenzae in Cystic Fibrosis

M.G. Fenger, H.V. Olesen, N. Nørskov-Lauritsen

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 71 KB

english, 2009

174

Detection of anaerobic bacteria in bronchoalveolar lavage fluid from paediatric CF patients

M.M. Tunney, E. Klem, D.F. Gilpin, S.J. McGrath, M. Muhlebach, R.C. Boucher, J.S. Elborn, M.C. Wolfgang

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 71 KB

english, 2009

175

Impact of strict anaerobs on the pathogenesis of lung infection in patients with Cystic Fibrosis

M. Ulrich, M. Haug, G. Doering

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 71 KB

english, 2009

176

Microbiological characteristics of Achromobacter xylosoxidans isolated from patients with cystic fibrosis

C.E. Levy, C.Z. Esteves, P. Dentini, L.C. Bonadia, C.S. Bertuzzo, A.F. Ribeiro, J.D. Ribeiro

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

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english, 2009

177

Cytotoxic activity evidence of Achromobacter xylosoxidans for pulmonar tissue

C.E. Levy, R.P. Mantovani, C.Z. Esteves, P. Dentini, A.C. Souza, J.D. Ribeiro, A.F. Ribeiro, L.C. Bonadia, C.S. Bertuzzo, T. Yano

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 59 KB

english, 2009

178

Treatment of Non-Tuberculous Mycobacteria in Adults with Cystic Fibrosis

C.S. Haworth, A.R. Bowden, J. Elliot, H.C. Barker, D. Bilton, D. Wat, J. Foweraker, R.A. Floto

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

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english, 2009

179

Chronic bronchial infection (cbi) with Bordetella bronchiseptica (Bb) in CF

C. Vazquez, F. Baranda, J.A. Saez, E. Urra, M. Santiago, A. Gomez, A. Sojo, F. Barron

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

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english, 2009

180

Clinical follow-up of 13 French CF patients with Inquilinus limosus

R. Chiron, H. Marchandin, F. Counil, E. Jumas-Bilak, G. Bellon, R. Nove-Josserand, A.M. Freydiere, M. de Montclos, D. Turck, M.O. Husson, D. Hubert, I. Sermet-Gaudelus, A. Ferroni, P. Morand, M. Rayna

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

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english, 2009

181

Ochrobactrum and Agrobacterium spp.: emerging opportunistic pathogens in cystic fibrosis patients?

C. Teyssier, E. Jumas-Bilak, F. Counil, A. Masnou, L. Aleyrangues, R. Chiron, H. Marchandin

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 63 KB

english, 2009

182

Large antibacterial spectrum of aminosterols derivatives towards multidrug resistant Gram-negative and Gram-positive bacteria from patients with cystic fibrosis

K. Alhanout, J. Brunel, D. Raoult, J.M. Rolain

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 63 KB

english, 2009

183

Human Neutrophil Peptide-1 (HNP-1) and a truncated analogue display antimicrobial activity against respiratory pathogens

F.T. Lundy, M.M. Tunney, C.C. Taggart, J.S. Elborn

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 63 KB

english, 2009

184

Serum tobramycin levels following delivery of tobramycin (TOBI®) via eFlow advanced nebuliser in children with cystic fibrosis

E.L. Guy, T.W. Lee, M. Bosomworth, M. Denton, S.P. Conway, K.G. Brownlee

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 63 KB

english, 2009

185

Monitoring of Tobramycin Levels by Fingerprick Sampling

A.M. Jones, B. Keevil, J. Beisty, A.K. Webb, D. McKenna, D. Clough

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 66 KB

english, 2009

186

Evidence of aminoglycoside cochleotoxicity measured by standard & high frequency audiometry and Distortion-Product otoacoustic emissions in paediatric Cystic Fibrosis patients

G. Al-Malky, R. Suri, S. Dawson, T. Sirimanna, D. Kemp

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 66 KB

english, 2009

187

Ototoxicity in Adults with Cystic Fibrosis

N.K. Payne, A.K. Webb, A.M. Jones, A. Camilleri, R.J. Bright-Thomas

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 66 KB

english, 2009

188

Investigation into the potential of sub-lethal photodynamic antimicrobial chemotherapy (PACT) to reduce susceptibility of Pseudomonas aeruginosa to antibiotics

C.M. Cassidy, J.S. Elborn, R.F. Donnelly, M.M. Tunney

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 66 KB

english, 2009

189

Association between CYP3A enzyme activity and ciprofloxacin and clarithromycin pharmacokinetics in patients with cystic fibrosis

X. Nielsen, K. Dalhoff, A. Jensen, G. Jürgens, C.R. Hansen, U. Johansen, T. Pressler, N. Høiby

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 59 KB

english, 2009

190

Pharmacokinetics and antibacterial activity of inhaled liposomal ciprofloxacin hydrochloride in healthy volunteers and in cystic fibrosis (CF) patients

P. Bruinenberg, B. Otulana, J. Blanchard, D. Cipolla, J. Wilson, D. Serisier

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 59 KB

english, 2009

191

Prevalence and clinical significance of autoantibodies in 144 adult patients with cystic fibrosis

F. Lachenal, K. Nkana, R. Nove-Josserand, N. Fabien, I. Durieu

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 70 KB

english, 2009

192

CF an Immune Disease?

M.O. Henke, B.K. Rubin, D.C. Gruenert, G. John

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 70 KB

english, 2009

193

Role of COMMD1 and CSN5 in transcriptional regulation of the CFTR gene

A. de Becdelièvre, A. Aissat, L. Drévillon, A. Hinzpeter, N. Arous, P. Fanen

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 70 KB

english, 2009

194

Anoxia prolongs the life and functionality of polymorphonuclear leukocytes

P.Ø. Jensen, T. Bjarnsholt, C. Moser, N. Høiby

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 70 KB

english, 2009

195

Is 3-nitrotyrosine a marker of inflammation in airways of patients with cystic fibrosis?

M. Ulrich, F. Ratjen, P. Schmid-Grendelmeier, G. Doering

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 65 KB

english, 2009

196

8-isoprostaglandinF-2-alfa in urine as a marker of oxidative stress in cystic fibrosis patients. A longitudinal study

P.O. Schiøtz, P.M. Frandsen, T.S. Mikkelsen, E. Petersen, H.V. Olesen

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 65 KB

english, 2009

197

Sputum eosinophils are elevated in CF patients with asthma

A. Decraene, A. Willems-Widyastuti, J. Ceuppens, K. De Boeck, D. Bullens, L. Dupont

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 65 KB

english, 2009

198

Neutrophil Extracellular Traps impair the inhibition of elastase, protease 3 and cathepsin G in neutrophil suspensions from CF patients

S. Attucci, A. Gauthier, D. Brea, A. Dubois, F. Gauthier

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

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english, 2009

199

Prostaglandin E2 in exhaled breath condensate in cystic fibrosis

L. Fila, J. Musil, M. Prucha

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

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english, 2009

200

Comparison of Inflammatory responses to Pseudomonas aeruginosa Lipopolysaccharide isolates compared to Staphylococcus aureus Peptidoglycan

P.J. Buchanan, R.K. Ernst, J.S. Elborn, B.C. Shock

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 64 KB

english, 2009

201

Lung defense against Pseudomonas aeruginosa: the recognition by host cells of either LPS or flagellin is necessary and sufficient

E. Raoust, V. Balloy, I. Garcia-Verdugo, L. Touqui, R. Ramphal, M. Chignard

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 64 KB

english, 2009

202

Role of cytosolic phospholipase A2 in Pseudomonas aeruginosa-induced inflammation

Y. Wu, D. Leduc, V. Balloy, I. Garcia-Verdugo, M. Chignard, L. Touqui

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 64 KB

english, 2009

203

Prevalence of preclinical AA-amyloidosis in CF patients with chronic P. aeruginosa infection

K. Kötz, K. Magdorf, D. Staab, R.P. Linke

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 69 KB

english, 2009

204

Airways surface liquid depletion causes MMP-12 dependent emphysema in βENaC-overexpressing mice

S.C. Schubert, J.B. Trojanek, S. Diemer, A. Cobos, Z. Zhou, D.A. Treis, L. Dai, J. Schatterny, S. Hirtz, C. Schultz, M.A. Mall

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

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english, 2009

205

Increased susceptibility to allergic airway inflammation in a murine model of cystic fibrosis lung disease

J. Duerr, L. Dai, J. Schatterny, S. Hirtz, Z. Zhou, S.C. Schubert, M.A. Mall

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 70 KB

english, 2009

206

Evaluation of oxidant and antioxidant status in CFTR-KO mice: role of Peroxiredoxin 6

S. Trudel, M. Kelly, P. Thérond, T. Nguyen-Khoa, M. Dadlez, M. Ollero, D. Roussel, J. Fritsch, A. Edelman, F. Brouillard

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

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english, 2009

207

Allergic inflammation produces a hypersecretory airway ion transport phenotype in mice

P. Anagnostopoulou, L. Dai, J. Duerr, J. Schatterny, S. Hirtz, M.A. Mall

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 66 KB

english, 2009

208

Accumulation of NKT cells in tissues of cystic fibrosis mice

N. Siegmann, U. Griesenbach, E. Gulbins, G. Doering

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 66 KB

english, 2009

209

Azithromycin is not able to decrease inflammatory process in cystic fibrosis human bronchial epithelial cells

V. Saint-Criq, J. Jacquot, A. Clement, O. Tabary

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 66 KB

english, 2009

210

Weak anti-inflammatory effects of glucocorticoids on CF bronchial epithelial cells

C. Rebeyrol, L. Guillot, V. Saint-Criq, D. Ray, A. Clement, O. Tabary, P. Le Rouzic

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 66 KB

english, 2009

211

IP-10 induction after LPS stimulation is compromised in cystic fibrosis bronchial epithelial cells

M.O. Henke, D.C. Gruenert, B.K. Rubin, G. John

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 56 KB

english, 2009

212

Drug specific T cells in patients with a history of non-immediate hypersensitivity reactions

P. Whitaker, S. Lavergne, D. Naisbitt, J. Gooi, D. Peckham, K. Park

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 56 KB

english, 2009

213

Cytokine production in the differentiating human airway epithelium

S. Crespin, T. Dudez, I. Scerri, M. Chanson

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 56 KB

english, 2009

214

Decreased IL-8 secretion and expression by fluvastatin in primary human macrophages and in the whole blood from adult patients with cystic fibrosis

S. Jouneau, C. Belleguic, M. Bonizec, J. Galaine, G. Brinchault, B. Desrue, J.P. Gangneux, C.A. Martin-Chouly

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 56 KB

english, 2009

215

Analysis of CFTR expression in immune cell subsets of peripheral blood

M.A. van Meegen, S.W. Terheggen-Lagro, H. Hoelen, I. Braakman, P.J. Coffer, C.K. van der Ent, J.M. Beekman

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 59 KB

english, 2009

216

Decreased expression of Nod2-receptors in cystic fibrosis airway epithelial cells

G. Varelogianni, I. Oliynyk, H. Strid, E. Särndahl, G.M. Roomans

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

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english, 2009

217

Influence of CFTR mutations on bactericidal activity of human macrophages

V. Socci, S. Guglietta, F. Spadaro, F. Venuta, S. Quattrucci, F. Ascenzioni, P. Del Porto

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

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english, 2009

218

Molecular mechanisms of the pro-inflammatory role of membrane-associated PR3 during neutrophil apoptosis in cystic fibrosis

J. Gabillet, C. Kantari, M. Pederzoli-Ribeil, S. Moriceau, V. Witko-Sarsat

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

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english, 2009

219

Inhibition of cathepsins B and L by kininogens: a molecular investigation

C. Naudin, F. Lecaille, S. Chowdhury, J. Krupa, J.S. Mort, G. Lalmanach

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 61 KB

english, 2009

220

Increased allergic bronchopulmonary aspergillosis (ABPA) in CF – a result of global warming?

A. Ponnuswamy, S. Shahid, B. Govin, K. Hatton, M.J. Ledson, M.J. Walshaw

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 61 KB

english, 2009

221

Voriconazole therapy in children with cystic fibrosis and steroid-dependant allergic bronchopulmonary aspergillosis: Efficacy and adverse effects

A. Katelari, J. Limbari, A. Kapi, K. Xenofonte, S. Doudounakis

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 61 KB

english, 2009

222

Mathematical modelling of FEV1% allows early recognition of patients at risk

F. Gatti, A. Pugliese, P. Iansa, B.M. Assael

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 64 KB

english, 2009

223

Accuracy of a self-administered questionnaire to estimated maximal exercise capacity in CF patients

S. Leroy, F. Denis, M. Garet, C. Fabre, T. Perez, F. Roche, B. Wallaert

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 64 KB

english, 2009

224

Assessment of respiratory compliance in infants with cystic fibrosis

N. Pillarisetti, B. Linnane, H. Sowerbutts, B. Skoric, G. Hall, S. Ranganathan

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 64 KB

english, 2009

225

Spirometry and Impulse Oscillation measurements in children with cystic fibrosis (CF)

P.D. Bridge, F. MacLean, K.P. Sylvester, R. Iles

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 64 KB

english, 2009

226

Factors influencing the worsening of lung function between 16 and 18 years of age in Czech patients

D. Zemkova, L. Smolikova, L. Fila, J. Bartosova, M. Macek Jr., V. Vavrova

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 63 KB

english, 2009

227

Listing patients to lung transplantation (LTx). Experience of 110 cases in the CF Center of Verona

B.M. Assael, M. Barao-Ocampo, U. Pradal, C. Tartali, S. Perobelli, C. D'Orazio, S. Volpi

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

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english, 2009

228

Should Cystic Fibrosis patients be transplanted using “suboptimal organs”: insights from decision analysis

A. Thomas, Y. Locke, T.J. Locke, M. Wildman

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 63 KB

english, 2009

229

Osteoporosis and vertebral fractures in CF patients after lung transplantation

B. Zweytick, S. Holzer, B. Ghanim, J. Patsch, P. Jaksch, F. Kainberger, W. Klepetko

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 63 KB

english, 2009

230

Heart assessment during exercise can predict pulmonary hypertension (PH) in CF?

S. Favilli, S. Bresci, R. Giuntini, M. Cavicchi, C. Braggion

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 60 KB

english, 2009

231

The autopsy reports: Cor pulmonale in CF patients with aging

J. Lee, Y.W. Lee, W.J. Warwick

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 60 KB

english, 2009

232

Improvement in aerobic fitness and quality of life does not depend on severity of pulmonary disease in CF patients

A. Jung, D. Mueller, T. Radtke, J. Wildhaber, B. Knoepfli

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 60 KB

english, 2009

233

Respiratory exacerbations in children aged 0–3 years in the Australasian Cystic Fibrosis Bronchoalveolar Lavage (ACFBAL) Study

C.A. Byrnes, S. Vidmar, C. Wainwright

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 60 KB

english, 2009

234

Pre-flight evaluation of adult patients with cystic fibrosis

E. Edvardsen, B. Skrede, J. Homme, O.H. Skjønsberg

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 68 KB

english, 2009

235

Lung function variability in cystic fibrosis

G. Jifon, E.M. Spencer, J. Greenwood, M.J. Ledson, M.J. Walshaw

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 68 KB

english, 2009

236

FEV1 rate of decline in CF patients: towards zero overa8years period

A. Leonard, G. Reychler, T. Leal, P. Lebecque

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 68 KB

english, 2009

237

Prevalence of bone mass density loss in cystic fibrosis patients with progressive lung disease

B. Zweytick, S. Holzer, B. Ghanim, J. Patsch, P. Jaksch, F. Kainberger, W. Klepetko

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 68 KB

english, 2009

238

Clinical value of cough swab samples, versus induced sputum samples in children with cystic fibrosis

C. Lilos, E. Hatziagorou, F. Kirvassilis, V. Avramidou, M. Ioannou, D. Sofianou, P. Savopoulou, J. Tsanakas

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 63 KB

english, 2009

239

Are exhaled and nasal NO measurements useful in CF adult patients?

A. Bocherens, D. Sistek, M. Hofer, A. Sauty

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 63 KB

english, 2009

240

Which quantitative measurement of lung function correlates best with clinical picture during treatment of pulmonary exacerbations in CF?

I. Sequeiros, K. Hester, A.H. Kendrick, N.A. Jarad

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 63 KB

english, 2009

241

Lactate as a non-invasive marker of CF lung inflammation

T. Bensel, M. Stotz, B. Wollschlaeger, G. Taccetti, S. Campana, V. de Rose, K.C. Meyer, M. Borneff-Lipp, G. Doering, D. Worlitzsch

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 63 KB

english, 2009

242

Neutrophil elastase: its activity and content, the levels of anti-elastase in children with bronchopulmonary diseases

Y.V. Gorinova, O.I. Simonova, E.M. Vasilyeva, M.I. Bakanov

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 68 KB

english, 2009

243

Cytokine pattern in broncho-alveolar lavage in children with Cystic Fibrosis and infection with Pseudomonas aeruginosa

T. Frischer, T. Eiwegger, S. Renner, E. Nachbaur, F. Horak, Z. Szepfalusi, S. Gruber, P. Fucik, M. Gona

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 68 KB

english, 2009

244

In-vitro inhibition of neutrophil elastase activity by inhaled antibiotics used in cystic fibrosis patients

A. Hector, M. Feilcke, J. Ripper, A. Schweiger-Kabesch, C. Schröter, M. Kappler, M. Griese

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 68 KB

english, 2009

245

Airway Ca2+-activated Cl− channel (CaCC) activity is normal in mClca3-deficient mice

B. Jóhannesson, M. Bothe, C. Schultz, A.D. Gruber, M.A. Mall

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 68 KB

english, 2009

246

Dynamics of upper and lower airway colonisation with P.aeruginosa and S.aureus in CF-patients within 3.5 years

J.G. Mainz, J. Lindig, M. Schien, B. Wiedemann, W. Pfister, B.C. Kahl, J.F. Beck, B. Tümmler

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 65 KB

english, 2009

247

Synchronisation of intravenous (IV) antibiotic and in vitro susceptibility of sputum Pseudomonas aeruginosa (PA) does not influence outcome of care of adult CF patients–aprospective study

I. Sequeiros, R. Westley, K. Levitt, N.A. Jarad

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 65 KB

english, 2009

248

Chronic infection with Achromobacter xylosoxidans leads to rapid decrease towards end-stage lung disease in cystic fibrosis patients

C.R. Hansen, T. Pressler, K.G. Nielsen, T. Bjarnsholt, N. Høiby

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 65 KB

english, 2009

249

Early colonization by Staphylococcus aureus and Pseudomonas aeruginosa in newborn screening children

N.S. Champs, D.L. Gomes, C.G. Alvim, M.B. Bedram, I. Assis, M.G. Oliveira, E.V. Guimarães, P.M. Camargos

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 65 KB

english, 2009

250

Can Burkholderia Cepacia complex (BCC) be eradicated with nebulised Amiloride and Tobi?

R. Ball, K.G. Brownlee, A. Duff, T.W. Lee, S.P. Conway

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 64 KB

english, 2009

251

Efficacy of Bramitob® on eradication of Ps. aeruginosa (PA)

D.T. Drinković, D. Tješić-D, J. Kelečić, A. Votava-Raić, A. Gagro, J. Vraneš

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 64 KB

english, 2009

252

TOBI 300 in Bulgarian cystic fibrosis patients

I.O. Galeva, M.I. Iankova, R. Markova

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 64 KB

english, 2009

253

Long term impact of azithromycin in paediatric cystic fibrosis patients

J. Fermeiro, S. Castanhinha, L. Pereira, C. Barreto

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 64 KB

english, 2009

254

Azithromycin long term effects in children with cystic fibrosis

A. Tamalet, A. Lemaire, M. Mahloul, D. Michon, A. Blondel, J.F. Vibert, D. Feldmann, B. Fauroux, A. Clement, H. Corvol

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 66 KB

english, 2009

255

Lung delivery of a new tobramycin nebuliser solution (150 mg/1.5 ml) by an investigational eFlow® nebuliser is equivalent to TOBI® but in a fraction of time

O. Denk, A.L. Coates, M. Keller, K. Leung, M. Green, J. Chan, N. Ribeiro, M. Charron

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 66 KB

english, 2009

256

Preclinical study of a new antibiotic for nebulization

L. Vecellio, J.P. Salin, G. Chantrel, J. Bordenave, S. Gatier, N. Leturc

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 66 KB

english, 2009

257

Effect of Positive Expiratory Pressure combined with Nebulization on Inhaled Dose: an In Vitro Evaluation

G. Reychler, L. Pitance, A. Leonard, G. Liistro, T. Leal, P. Lebecque

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 66 KB

english, 2009

258

Bronchodilator responsiveness and IgE in pediatric cystic fibrosis patients

S. Castanhinha, L. Pereira, C. Barreto

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 66 KB

english, 2009

259

Rationale for a low dose liposomal Ciclosporin A for inhalation via a customised eFlow® electronic nebuliser to prevent and treat bronchiolitis obliterans (BO)

M. Keller, O. Denk, J. Behr, H. Leuchte

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 66 KB

english, 2009

260

The role of Magnetic Resonance Imaging (MRI) in predicting severity of disease using a dedicated scoring chest system in patients with cystic fibrosis (CF)

S. Quattrucci, F. Fraioli, M.L. Mennini, A. Menichella, F. Patriarchi, G. Serra

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 67 KB

english, 2009

261

HRCT and LFT in monitoring CF lung disease

M. Polakovič, M. Čik, H. Kayserova, H. Jobbagyová

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 66 KB

english, 2009

262

Superiority of ATG induction therapy in lung transplant recipients with cystic fibrosis

P. Jaksch, J. Ankersmit, B. Zweytick, C. Aigner, G. Lang, A. Hoda, M. Keplinger, W. Klepetko

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 61 KB

english, 2009

263

Bronchiectasis (BE) on CT is a strong predictor of respiratory tract exacerbations in children with CF

M. Loeve, K. Gerbrands, W.C. Hop, M. Rosenfeld, H.A. Tiddens

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 61 KB

english, 2009

264

CT-detected early structural lung disease is progressive in infants and preschool children

L. Mott, C. Murray, N. de Klerk, S. Stick, S. Ranganathan, P. Sly

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 61 KB

english, 2009

265

35-year-old patient with cystic fibrosis (CF) and bilateral pulmonary infiltrates

C. Schwarz, A. Jobst, M. Barker, U. Wahn, D. Staab

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 61 KB

english, 2009

266

Infection by Nocardia farcinica in CF

J. Beucher, C. Belleguic, G. Brinchault, E. Deneuville, P.Y. Donnio, M. Roussey

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 64 KB

english, 2009

267

First colonisation with P. aeruginosa – only detected in the upper airways – eradicated with sinonasal inhalation of Tobramycin

J.G. Mainz, J. Lindig, C. Dopfer, W. Pfister, J.F. Beck

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 65 KB

english, 2009

268

Lung transplantation in patients with cystic fibrosis and Mycobacterium abscessus infection

M. Gilljam, M. Silverborn, H. Schersten

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 65 KB

english, 2009

269

Sequential bronchoscopy in the management of patients with lobar atelectasis

P. Whitaker, K.G. Brownlee, T.W. Lee, S.P. Conway, D. Peckham

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 65 KB

english, 2009

270

Validation of the MST-25: an extension of the modified shuttle test (MST)

M.R. Elkins, R.L. Dentice, P.T. Bye

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 66 KB

english, 2009

271

Mathematical modelling of oxygen uptake during recovery from exercise

D. Stevens, P.J. Oades, N. Armstrong, C.A. Williams

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 66 KB

english, 2009

272

Desaturation on 3-minute step test is associated with impaired outcomes at 12 months in adults with cystic fibrosis

A.E. Holland, T. Rasekaba, J. Wilson, B.M. Button

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 67 KB

english, 2009

273

Reference values for maximal aerobic exercise capacity in children with cystic fibrosis

P. van Leeuwen, H. Arets, C.K. van der Ent, H. Hulzebos

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 66 KB

english, 2009

274

Physical activity scoring and exercise capacity in adult CF patients

A. Morris, M.J. Ledson, M.J. Walshaw

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 64 KB

english, 2009

275

The “1km challenge” – a novel method to measure changes in exercise tolerance in children with cystic fibrosis during hospital admissions

L. Lester, J. Cowlard, C.S. Pao, S.B. Carr

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 65 KB

english, 2009

276

Heart rate recovery in young adult patients with cystic fibrosis

M. Sahlberg, A. Lindblad, B. Strandvik

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 64 KB

english, 2009

277

Use of Nintendo Wii for exercise in adult CF patients

L. Boyle, K. Lavery, J.S. Elborn, J.C. Rendall

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 64 KB

english, 2009

278

Respiratory exacerbations and muscle strength in adult patients with cystic fibrosis

B. Vrijsen, C. Burtin, H. Van Remoortel, T. Troosters, L. Dupont

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 64 KB

english, 2009

279

Electromyographic evaluation of muscular function in adults with cystic fibrosis

M. Gruet, L. Mely, J. Vallier, J. Brisswalter

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 64 KB

english, 2009

280

Assessment of specific exercise for correction of postural disorders in CF patients

B. Almajan-Guta, Z. Popa, I. Popa, L. Pop, I.M. Ciuca

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 64 KB

english, 2009

281

Musculoskeletal problems in Cystic Fibrosis

M. Marent-Huber, T. Wermke, M. Daigl Cattaneo, L. Carlucci

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 64 KB

english, 2009

282

Better satisfaction of cystic fibrosis paediatric patients with autogenic drainage associated to exercise compared to conventional chest physiotherapy

P. Reix, F. Aubert, B. Kassai, V. Bige, G. Bellon

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 63 KB

english, 2009

283

Efficiency of High frequency chest wall oscillation with “The Vest® Airway Clearance System” as daily physiotherapy in outpatients with CF

A.Y. Scherbakova, N.J. Kashirskaya, E.L. Amelina

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 63 KB

english, 2009

284

Physiotherapy: understanding the cough and spit

N.S. Cox, R.D. McAleer

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 63 KB

english, 2009

285

Early chest physical therapy (CP) programme in children with cystic fibrosis (CF) diagnosed by newborn screening (NS)

A. Valiente, N. Lopez-Galbany, V. Rodriguez-Sales, M. Bosque

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 63 KB

english, 2009

286

The use of NIV within a regional adult Cystic Fibrosis Centre

J. Barrett, P. Agostini, L. Gumery, S. Cameron, E.F. Nash, J. Whitehouse, D. Honeybourne

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 63 KB

english, 2009

287

A randomised, cross-over trial of upright sitting versus alternate side lying during nebulised delivery of medication in cystic fibrosis

R.L. Dentice, M.R. Elkins, P.T. Bye

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 63 KB

english, 2009

288

Evaluation of two different timings of Pulmozyme nebulisation in relation to chest physiotherapy in children with Cystic Fibrosis

P. Anderson, J. Morton

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 63 KB

english, 2009

289

A rheological investigation of cystic fibrosis sputum

S. Britland, D. Peckham, D. Eagland, N.J. Crowther

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 63 KB

english, 2009

290

Expectoration of sputum – a simple concept becomes a troublesome issue?

D.W. Riley, S. Tierney, A. Orr, A.M. Jones, M.E. Dodd

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 60 KB

english, 2009

291

Associations between walking distance and quality of life in children with CF

J.G. Nomden, M.M. van den Briel, E. van Weert

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 59 KB

english, 2009

292

Singing and Cystic Fibrosis: A pilot experience at Centre de Perharidy (Roscoff, France)

A. Dirou, E. Cueff, C. Lejosne, L.J. Guéganton, K. Revert, G. Rault

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

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english, 2009

293

Complementary Therapy: Planning a service for adults with Cystic Fibrosis

J. Hildage, D.W. Riley, R.J. McVean, H. Oxley, A. Brennan, M.E. Dodd

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 60 KB

english, 2009

294

PTs' role in the caring of CF patients in France in 2009

C. Lejosne, Y. Catelain, N. Christoflour, V. Louet, G. Gardin, A. Kern-Paquier, M.C. Issartel, L. Branchu, V. Vion, S. Julienne, G. Bellon

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

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english, 2009

295

Subsidising exercise in the community: the benefits for adults with cystic fibrosis

V.J. Gettins, D.W. Riley, R.J. McVean, R.J. Bright-Thomas, A.K. Webb, M.E. Dodd

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 60 KB

english, 2009

296

Outcome in Cystic Fibrosis Liver Disease

M. Rowland, C. Gallagher, G. Canny, P. Greally, D. Slattery, R. Hayes, R. O'Laoide, L. Daly, P.R. Durie, B. Bourke

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 68 KB

english, 2009

297

Fibrosis blood tests to detect liver disease in patients with cystic fibrosis

A.C. Wagner, M. Beaumesnil, E. Chaillou, F. Troussier, E. Darviot, N. Dib, P. Calès, J.L. Giniès

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 68 KB

english, 2009

298

Hepatic tissue TGF-β and SMAD proteins as markers of the fibrosing process in cystic fibrosis: a pilot study

F. Sotiriadou, M. Fotoulaki, P. Chitiroglou, K. Vassilaki, I. Tsitouridis, S. Nousia-Arvanitakis

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 68 KB

english, 2009

299

Immunity in CF associated liver disease

I.M. Ciuca, I. Popa, L. Pop, Z. Popa, A. Rosca, F. Horhat, L. Tamas

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 68 KB

english, 2009

300

The size of the spleen by MRI in patients with CF with and without diabetes

I. Sequeiros, K. Hester, M. Callaway, A. Williams, Z. Sund, F.S. Wong, N.A. Jarad

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 66 KB

english, 2009

301

Gallbladder dysfunction contributes to impaired bile salt homeostasis in cystic fibrosis

D. Debray, D. Rainteau, S. Lerondel, C. Rey, L. Humbert, V. Barbu, C. Wolf, C.H. Cottart, C. Housset

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 66 KB

english, 2009

302

Detection of bile acids in sputum as a screening method for assessment of aspiration of duodenogastric contents in patients with cystic fibrosis

A. Pauwels, A. Decraene, K. Blondeau, V. Mertens, L. Dupont, D. Sifrim

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 66 KB

english, 2009

303

Gastro-oesophageal reflux and gastric emptying in children with cystic fibrosis

B. Hauser, K. Blondeau, A. Malfroot, I. De Schutter, E. De Wachter, D. Sifrim, T. Devreker, Y. Vandenplas

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 66 KB

english, 2009

304

Immuno-Reactive Trypsine and extern pancreatic status in cystic fibrosis children

E. Chaillou, A.C. Wagner, M. Beaumesnil, C. Bonnemains, E. Darviot, J.L. Giniès

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 66 KB

english, 2009

305

Pancreatic status in cystic fibrosis patients depending upon phenotype-genotype correlations

L. Bober, O. Munduk, O. Hnateyko, H. Makukh

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 66 KB

english, 2009

306

Clinical outcome in cystic fibrosis patients with or without meconium ileus

K. Venkatesh, C.J. Taylor

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 66 KB

english, 2009

307

Intestinal inflammation is present in young infants with cystic fibrosis

A. Lisowska, J. Walkowiak

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 66 KB

english, 2009

308

Efficacy and safety of a new formulation of CREON® in patients with exocrine pancreatic insufficiency due to CF

B.C. Trapnell, K. Maguiness, G.R. Graff, D. Boyd, S.D. Caras, K. Beckmann, D. Bennett

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 57 KB

english, 2009

309

CREON®: efficacy and safety in children less than 7 years old with exocrine pancreatic insufficiency due to cystic fibrosis

S. Sander-Struckmeier, D. Boyd, S.D. Caras

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 57 KB

english, 2009

310

Early detection of glucose derangement in children with Cystic Fibrosis

V. Raia, F. De Gregorio, A. Sepe, I. De Simone, E. Mozzillo, G. Valerio, A. Franzese

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 63 KB

english, 2009

311

Early diagnosis of glucose intolerance and/or diabetes in children with cystic fibrosis

K. Walicka, D. Sands, K. Zybert, R. Piotrowski

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 63 KB

english, 2009

312

Re-audit of Cystic Fibrosis inpatient blood glucose monitoring with the unit policy

L. Robb, M. Richardson, J.A. Innes

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 62 KB

english, 2009

313

Perks and pitfalls of interstitial glucose monitoring – early experience from an ongoing pilot study

J.M. Helm, A.M. Jones, R. Rowe, M.E. Dodd, A.K. Webb

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 63 KB

english, 2009

314

Reactive hypoglycemia in non-diabetic cystic fibrosis patients

J.M. van den Berg, H.G. Heijerman

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 63 KB

english, 2009

315

Proof of principle. Treatment of cystic fibrosis-related diabetes: a possible role for complementary metformin?

J.M. van den Berg, H.G. Heijerman

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 64 KB

english, 2009

316

Efficacy of slow release insulin in patients with Cystic Fibrosis and Glucide Intolerance

L. Minicucci, R. Casciaro, A. De Alessandri, M. Haupt, M. Caso, V. Lucidi, F. Bagnasco

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 64 KB

english, 2009

317

Carbohydrate counting and insulin adjustment in Cystic Fibrosis related Diabetes

L. Robb, M. Richardson, S. Johnston, J.A. Innes

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 64 KB

english, 2009

318

Characteristics of visual function in adults with cystic fibrosis

K.S. Evans, C. Purslow, R.V. North, R.I. Ketchell

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 66 KB

english, 2009

319

Autonomic neuropathy in cystic fibrosis

A.B. Palamarthy, E. Thorncroft, L. George, R.I. Ketchell

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 66 KB

english, 2009

320

Thyroid dysfunction in newly diagnosed cystic fibrosis patients with pancreatic insufficiency and restitution with enzyme therapy

A. Katelari, C. Kanaka-Gantenbein, C. Mengreli, G.P. Chrousos, S. Doudounakis

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 66 KB

english, 2009

321

Assessment of bone mineralisation in cystic fibrosis

S.A. Rolin, C.D. Sheldon, N.J. Withers

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 66 KB

english, 2009

322

Osteoporosis and osteopenia in adults with cystic fibrosis: prevalence, associated factors and biological markers interest

S. Leroy, C. Prudhomme, I. Legroux-Gerot, T. Perez, B. Wallaert, B. Cortet

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 45 KB

english, 2009

323

Mineral bone density in children and bone status of adults with cystic fibrosis

E. Colin, A.C. Wagner, E. Chaillou, E. Darviot, T. Urban, M. Audran, J.L. Giniès

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 64 KB

english, 2009

324

Assessment of bone mass density by quantitative ultrasonography in children with cystic fibrosis

O. Turcu, S. Sciuca, E. Chioroglo

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 64 KB

english, 2009

325

Bone loss in CF: a fragmented picture

J. Robertson, K. MacDonald, J.A. Innes

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 64 KB

english, 2009

326

Evaluation of a new nutritional score in patients with cystic fibrosis

G. Alicandro, S. Loi, C. Speziali, L. Valmarana, R. Valmarana, L. Claut, N. Faelli, C. Colombo

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 64 KB

english, 2009

327

IBW < 85% in the first year of life and pulmonary manifestations at 6 years old, in patients with cystic fibrosis

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 60 KB

english, 2009

328

The effects of lung transplantation on the nutritional status of patients with cystic fibrosis

M. Caraher, S.J. Doe, A. Anderson, K. Heslop, S. Johnston, K. Stavers, S.J. Bourke

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 61 KB

english, 2009

329

Supplement Snack-Bar: a new approach to improve compliance with oral supplements in children with CF

C. Smith, J. Lenton, C. Warde, P. Seddon

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 61 KB

english, 2009

330

The experience of using megestrol acetate (MA) in a large UK adult CF centre

J. Barrett, B. Ahitan, E.F. Nash, J. Whitehouse, D. Honeybourne

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 61 KB

english, 2009

331

Sodium depletion in infants diagnosed with CF

J. Crocker, A. Devenny

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 63 KB

english, 2009

332

Soluble transferrin receptor for evaluating iron status in cystic fibrosis

E. Karlge-Nilsson, A. Lindblad

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 63 KB

english, 2009

333

Vitamin K status and supplementation in children with cystic fibrosis (CF)

K. Jones, R. Iles, D. McShane, C. Saward

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 63 KB

english, 2009

334

Vitamin K deficiency in CF patients is frequent despite its regular supplementation

P. Krzyzanowska, A. Lisowska, W. Cichy, A. Popiel, A. Pogorzelski, W. Skorupa, B. Kaminska, J. Walkowiak

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 63 KB

english, 2009

335

Plasma amino acid levels in cystic fibrosis patients

H.P. Ioannou, M. Fotoulaki, K. Vasilaki, P. Augoustides-Savvopoulou

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 62 KB

english, 2009

336

Will my CF diet make me ill?

E. Lake, R. Barnes, A. Morton, S. Wolfe

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 62 KB

english, 2009

337

Is enough attention paid to diet, weight and digestion?

E. Lake, R. Barnes, A. Morton, S. Wolfe

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 62 KB

english, 2009

338

Is dietetics the cinderella of the CF multidisciplinary team?

E. Lake, R. Barnes, A. Morton, S. Wolfe

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 62 KB

english, 2009

339

Provision of dietetic care in CF centres in the UK

A. Morton, S. Wolfe, R. Barnes

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 55 KB

english, 2009

340

Improvement of intestinal comfort in cystic fibrosis patients after probiotics consumption

R. del Campo, M. Garriga, J. Agrimbau, A. Lamas, L. Maiz, R. Canton, L. Suarez

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 55 KB

english, 2009

341

TIDES-CF Study: Who participates in psychosocial trials?

H.J. Bartig, M. Ammon, R. Wünderich, S. Junge, M. Ballmann, G. Ullrich

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 60 KB

english, 2009

342

Psychopathology in Turkish children and adolescents with diagnosis of cystic fibrosis

G. Senses Dinc, F. Unal, U. Ozcelik, S.E. Cengel Kultur, D. Dogru Ersoz, S. Pekcan, N. Kiper, E. Yalcin

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 60 KB

english, 2009

343

“You exceeded the cut-off score” – Parental reactions to their HADS-assessments

H.J. Bartig, R. Wünderich, G. Ullrich

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 60 KB

english, 2009

344

The significance of Experiential Avoidance concerning anxiety and depression in parents of CF children

U. Smrekar, T. Gerster, T. Beck, H. Mitmansgruber, J. Eder, H. Ellemunter

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 60 KB

english, 2009

345

Pilot study: impact of Cystic Fibrosis on emotional and marital satisfaction

A. Parent, S. Leroy, V. Christophe, J. Vanneste, G. Delelis, T. Perez, P. Antoine, B. Wallaert

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 62 KB

english, 2009

346

Anxiety and depression in CF patients' fathers and mothers

P. Catastini, G. Bertini, M. Picchi, S. Alberti, C. Braggion

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 62 KB

english, 2009

347

Emotional condition of adult with cystic fibrosis (CF): implication of illness or structure of personality?

P. Catastini, S. Alberti, G. Bertini, M. Picchi, C. Braggion

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 62 KB

english, 2009

348

Self-care: a qualitative study of adults with CF

D.T. Greenop, S.M. Glenn, D.J. Clifford, M.J. Ledson, M.J. Walshaw

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 62 KB

english, 2009

349

Reconsidering self-care: a sociological response to CF research

D.T. Greenop, S.M. Glenn, D.J. Clifford, M.J. Ledson, M.J. Walshaw

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 59 KB

english, 2009

350

Variation in bias of self-reported adherence to nebulisers in adults with Cystic Fibrosis

T. Hughes, K. Pollard, L. Goodacre, C. Sutton, S.P. Conway, D. Peckham

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 60 KB

english, 2009

351

Exploration of personality, psychosocial factors and illness effect on adherence behaviour in CF

M. Braithwaite, M. Egevad, S. Poole, M. Dooley, F.A. Finlayson, J. Wilson

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 60 KB

english, 2009

352

Open monitoring of adherence; is it better in those patients who bring their device for download?

P. McCormack, A. McDonald, K.W. Southern, P.S. McNamara

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 60 KB

english, 2009

353

Non-adherence as coping strategy of young adult patients with CF. A qualitative study

G.R. Seitz, K. Mörtl, M. Leichsenring, J. von Wietersheim

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 60 KB

english, 2009

354

Improving self efficacy in adolescents and young adults with cystic fibrosis (CF)

C. Wainwright, H. Saddington, J. Busch, L. Blizzard, H. Cameron-Tucker, J. Cheney, M. Jessup, E. Cummings, L. Joseph, P. Turner, D.W. Reid

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 60 KB

english, 2009

355

The Use of Patient Held Drug Information Cards to improve adherence: a questionnaire survey

G. Brady, L.M. MacDougall, A.J. Marshall, A.J. Smith, H.C. Rodgers

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 60 KB

english, 2009

356

Totally implanted venous access devices (TIVADs) in children with cystic fibrosis: Pilot satisfaction survey

P. Panesar, R. Squire, K.G. Brownlee, S.P. Conway, T.W. Lee

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 60 KB

english, 2009

357

Is it safe and practical to give once daily IV tobramycin to young people with cystic fibrosis at home?

C.A. Lawrence, L.J. Heaf, E.F. Burrows, J.J. Cottrell, J. Pope, K.W. Southern

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 64 KB

english, 2009

358

Clinical status at start of IV treatment and effect on daily life

K. Strandner, K. Herlitz, A. Lindblad

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 64 KB

english, 2009

359

Peripherally Inserted Central Catheter (PICC) for home IV therapy: a Belgian CF center experience

F. Wustefeld, T. Pirotte, F. Veyckemans, G. Reychler, A. Leonard, V. Hubaux, P. Lebecque

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 64 KB

english, 2009

360

Developing a Portacath needle removal device

Y. Locke, F.P. Edenborough, T.J. Locke

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 64 KB

english, 2009

361

Totally Implantable Venous Access devices (TIVADs) in Cystic Fibrosis with particular reference to associated complications

H.L. Mills, L. Jenkins, A. Leavy, A. Reid

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 60 KB

english, 2009

362

Estimating risk associated with home-based intravenous antibiotic therapy (IVAT)

C. Glasscoe, K.W. Southern, G.A. Lancaster, A.L. Quittner, E.F. Burrows, L.J. Heaf, K. Dyer, S. Davies, D. Forster, A. Bryon, K.G. Brownlee, A.J. Nunn

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 61 KB

english, 2009

363

Multicenter prospective study about complications of totally implantable central venous access ports in Italian people with CF: preliminary results

A. Dal Molin, C. Braggion, S. Bisogni, E. Rizzi, N. Tacchella, V. Carnovale, S. Del Vecchio, M.L. Furnari, M. Calamia, G. Tuccio, V. Spadea, F. Festini

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 61 KB

english, 2009

364

Vascular stenosis in CF patients with totally implantable vascular access devices

J. Greenwood, A. Ponnuswamy, B. Govin, M.J. Ledson, M.J. Walshaw

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 60 KB

english, 2009

365

Providing inpatient education on a segregated ward

J. Steel, C. Cole, M. Sherlock

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 59 KB

english, 2009

366

Camille and the Dragon. A magic story to explain CF disease to 3–5 year old children

S. Francon, M. Clairicia, D. Fezaa, M. Sallort, M. Longo, E. Knoe, I. Sermet-Gaudelus

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 59 KB

english, 2009

367

Experience of parents of CF pre-teenagers participating in a therapeutic education program

V. Varlet, P. Varlet, M. Clairicia, M. Brechu, I. Sermet-Gaudelus

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 59 KB

english, 2009

368

The introduction of a new patient ‘welcome pack'

L. Speight, J. McKay, S. Buckingham, R.I. Ketchell

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 59 KB

english, 2009

369

Mentoring people with cystic fibrosis: evaluation of the preparation and process

M. Jessup, H. Cameron-Tucker, E. Cummings, L. Joseph, C. Wainwright, D.W. Reid

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 59 KB

english, 2009

370

Education and CF: experiences of parents and schools

S. Degelin, T. Havermans

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 59 KB

english, 2009

371

A way in therapeutic education (TE) for the children with cystic fibrosis and their family

C. Berville, V. David

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 59 KB

english, 2009

372

Creating a CF community – ‘CF in the City’ – a CF Newsletter

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 59 KB

english, 2009

373

Conceptual approach of an educational evaluation system for patients

C. Berville, R. Gagnayre, J. Iguenane, P. Douaud, D. Chevalier, V. Dumas, M. Vanbrabant, P. Leger, V. David

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 60 KB

english, 2009

374

European survey on schooling of children, teenagers and young adults with cystic fibrosis

I. Sermet-Gaudelus, T. Havermans, S. Ravilly

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 60 KB

english, 2009

375

Pedagogic drivers in therapeutic education for patients with cystic fibrosis

C. Berville, V. David, J. Iguenane, S. Ravilly

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 60 KB

english, 2009

376

Experience of a 1 year therapeutic education program

M. Clairicia, D. Fezaa, M. Sallort, M. Barbosa, M. Kirszenbaum, F. Chedevergne, S. Vrielynck, M. Brechu, L. Gaudet, A. Lindgren, I. Sermet-Gaudelus

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 60 KB

english, 2009

377

Quality of Care and Quality of Life: Patient/Healthcare Perspectives

S. Armoni, R.Y. Rony, E. Kerem

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 60 KB

english, 2009

378

Patient satisfaction survey of the annual review service at a regional adult cystic fibrosis (CF) centre

C. Evans, R. Davies, E.F. Nash, J. Whitehouse, D. Honeybourne

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 60 KB

english, 2009

379

Cystic Fibrosis Questionnaire Reference Data in a healthy, Dutch population 6–20 yrs

J.C. Sintnicolaas, J.L. Yntema, J.H. Vercoulen, J.B. Peters

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 60 KB

english, 2009

380

To tell or not to tell – Young people's experiences of disclosure

J. Hogan, K.W. Southern, J.J. Cottrell, E.F. Burrows

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 60 KB

english, 2009

381

Patient satisfaction in CF clinics – results from focus groups

K. Stahl, U. Smrekar, G. Steinkamp

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 62 KB

english, 2009

382

Quality of life in children with CF and their parents

J.G. Nomden, M.M. van den Briel, E. van Weert

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 62 KB

english, 2009

383

The perceived quality of the cystic fibrosis service and the subjective dimension of the illness experience for patient's parents and caregivers: a survey method to improve the care relationship

R. Grossi, E. Iacinti, M.C. Tripodi, F. Longo, G.L. Grzincich

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 63 KB

english, 2009

384

Pain in CF: a national survey on 1104 patients

S. Ravilly, B. Tourniaire, P. Cimerman

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 62 KB

english, 2009

385

School visits should be an integral part of the CF CNS service

J. Cowlard, C. Lambert, S.B. Carr, C.S. Pao

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 59 KB

english, 2009

386

Telephone calls by CF nurses

R. Panzo, L. Agrario, C. Dupont, N. Desmazes-Dufeu, R. Kanaan, P.R. Burgel, M.J. Nadaud, D.J. Dusser, D. Hubert

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 59 KB

english, 2009

387

The extended role of the CF healthcare professional – is it time to re-evaluate our role?

L.M. MacDougall, G. Brady, A.J. Marshall, A.J. Smith, H.C. Rodgers

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 59 KB

english, 2009

388

Use of modified early warning score in adults with Cystic Fibrosis

T. Hughes, R. Metcalfe, S.P. Conway, D. Peckham

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 59 KB

english, 2009

389

How we managed to improve a professional attitude in the nursing team to deal with topics of sexuality, fertility and reproduction in relation to CF patients

M. van Hattem, M. de Man, F. Teding van Berkhout

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 59 KB

english, 2009

390

Pregnancy and CF: Differing perspectives of patients and caregivers

I. Eisenstadt, T. Cohen, E. Kerem

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 59 KB

english, 2009

391

A tool to facilitate transition to adult care for young people with cystic fibrosis

N.A. Renton, J.J. Cottrell, E.F. Burrows, L.J. Heaf, R. Lwin, K.W. Southern

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 59 KB

english, 2009

392

Transition from paediatric to adult: experience of a cystic fibrosis care center

A.C. Wagner, C. Beloncle, F. Troussier, M. Chiffoleau, C. Person, T. Urban, E. Darviot, J.L. Giniès

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 59 KB

english, 2009

393

International benchmarking for cystic fibrosis patient outcomes using registry data

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 62 KB

english, 2009

394

Changes in Cystic Fibrosis mortality and persisting gender inequalities in Australia: 1979–2005

D.W. Reid, L. Blizzard, D. Shugg, C. Flowers, C. Cash, H. Greville

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 63 KB

english, 2009

395

Mortality study in a cohort of patients born since 1970 in Brittany (France)

I. Duguépéroux, V. Scotet, M.P. Audrézet, C. Férec

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 63 KB

english, 2009

396

Audit of deaths in a single adult CF centre

A. Saffy, A. Ponnuswamy, H. Miller, P. Dyce, M.J. Ledson, M.J. Walshaw

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 63 KB

english, 2009

397

Criteria for diagnosis of CF in the French Registry

L. Lemonnier, S. Ravilly, A. Munck, M. Roussey

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 60 KB

english, 2009

398

Extensive carrier testing and CF birth prevalence: evidence for a negative correlation

C. Castellani, L. Picci, A. Tamanini, A. Capodaglio, P. Girardi, P. Rizzotti, B.M. Assael

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 60 KB

english, 2009

399

Rectal prolapse in CF: a population study

R. Scott-Jupp, H.E. Kay, K. Giles

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 60 KB

english, 2009

400

The CFTRdele2,3 (21 kb) mutation is present in cystic fibrosis patients from Eastern Hungary

I. Balogh, E. Dzsudzsak, B. Nagy, F. Gönczi, R. Ujhelyi, M. Macek Jr., E. Ajzner, J. Kappelmayer

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 60 KB

english, 2009

401

The genealogical contribution to the understanding of the diffusion processes of the CFTR mutations: the case study of 1717–1G → A in Brittany (France)

N. Pellen, G. Bellis, F. Lapeyre, L.J. Guéganton, C. Rollet, G. Rault

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 66 KB

english, 2009

402

UMD-CFTR: a database dedicated to CF and CFTR-related diseases

C. Bareil, C. Béroud, C. Thèze, D. Paulet, C. René, D. Hamroun, M. des Georges, M. Claustres

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 66 KB

english, 2009

403

Polish National CF Registry – preliminary report

S. Stezowska-Kubiak, R. Piotrowski, A. Pogorzelski, D. Sands, M. Bartnicka-Trawinska, A. Popiel, A. Korzeniewska, B. Oralewska, R. Staszak-Kowalska, W. Skorupa, M. Rachel, J. Walkowiak

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 67 KB

english, 2009

404

CF registry in Northern Greece

E. Hatziagorou, M. Fotoulaki, J. Kioumis, A. Keramidiotis, K. Vasilaki, V. Tsaousis, E. Kanavakis, J. Tsanakas

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 66 KB

english, 2009

405

Clinical and genetic profile of patients from Moldova diagnosed with cystic fibrosis

S. Sciuca, O. Turcu, E. Chioroglo

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 51 KB

english, 2009

406

Audit of hearing surveillance in UK paediatric cystic fibrosis units

J.D. Wilkinson, J. Mora

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 62 KB

english, 2009

407

Corneal opacity: rare complication of cystic fibrosis

S. Pekcan, M. Kose, D. Dogru, N. Cobanoglu, E. Yalcin, M. Irkec, U. Ozcelik, N. Kiper

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 63 KB

english, 2009

408

Cost saving potential in pharmaceutical treatment of adult patients with cystic fibrosis

C.T. Baltin, C. Smaczny, T.O. Wagner

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 63 KB

english, 2009

409

Creatinine clearance in cystic fibrosis patients: MDRD, Cockcroft-Gault and measured creatinine clearance

I. Bronsveld, L.H. Conemans, E.A. van de Graaf, J.W. Lammers, F. Teding van Berkhout

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 63 KB

english, 2009

410

Development of a secure, on-line clinical health record to improve care in cystic fibrosis (CF)

F.A. Finlayson, P. Robertson, B.Y. Soo, N. Soh, J. Hughes, J. Wilson

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 63 KB

english, 2009

411

Estimating renal function in paediatric cystic fibrosis patients

C.T. Edwards, N. West

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 63 KB

english, 2009

412

Health care costs in the management of pregnant CF women

A. Ponnuswamy, E. Stoyanova, E.M. Spencer, C. Cowperthwaite, M.J. Ledson, M.J. Walshaw

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 63 KB

english, 2009

413

Impact of allergic sensitization on CF-associated chronic rhinosinusitis – Results from a multicentre interdisciplinary study

C. Dopfer, M. Schien, I. Schiller, L. Naehrlich, M. Kaeding, G. Frey, K. Thoss, B. Wiedemann, J.F. Beck, J.G. Mainz

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 63 KB

english, 2009

414

Implementation, uptake and impact of a cystic fibrosis electronic patient record system

D. Peckham, H. White, A. Morton, K. Pollard, C. Etherington, P. Whitaker, S.P. Conway, K.G. Brownlee, T.W. Lee, J. Taylor

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 60 KB

english, 2009

415

Anatomopathological changes in dead children with cystic fibrosis

S. Sciuca, O. Turcu, V. Petrovici

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 60 KB

english, 2009

416

New method for charting pulmonary function history

Y.W. Lee, J. Lee, W.J. Warwick

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 60 KB

english, 2009

417

Outreach clinics for the provision of specialist cystic fibrosis (CF) care to remote areas

S.J. Doe, A. Anderson, K. Stavers, K. Heslop, S. Johnston, M. Caraher, S.J. Bourke

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 60 KB

english, 2009

418

Overview of autopsy for CF patients: The organs weight analysis

J. Lee, W.J. Warwick, Y.W. Lee

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 59 KB

english, 2009

419

Patient satisfaction in a District General Hospital cystic fibrosis service

A. Johnstone, J. Davis

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 59 KB

english, 2009

420

Patients perspective of our CF related diabetes (CFRD) service

N. Singaroyan, F.P. Edenborough, J. Boadle, M. Wildman

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 59 KB

english, 2009

421

Preparing practitioners to meet the challenges of a specialist service. A joint venture between Bristol regional CF centres and University West of England

J. Dyer, K. Badlan

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 59 KB

english, 2009

422

Prevalence of bone demineralisation in Russian adult CF patients and associated risk factors

S. Krasovskiy, I. Baranova, E.L. Amelina

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 64 KB

english, 2009

423

Prevalence of renal impairment in children with cystic fibrosis (CF)

A. Andrieux, B. Llanas, J. Harambat, S. Bui, F. Nacka, M. Fayon

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 64 KB

english, 2009

424

Proteinuria in patients with cystic fibrosis: is there an association with genotype?

F.I. Gamboa, J.M. Cemlyn-Jones

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 63 KB

english, 2009

425

The Cystic Fibrosis Knowledge Questionnaire (CFKQ) – assessing disease-specific knowledge in adults with CF

E.F. Nash, R. Whitmill, R. Rashid, J. Whitehouse, D. Honeybourne

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 64 KB

english, 2009

426

Zinc in treatment of children with cystic fibrosis

Y.V. Gorinova, O.I. Simonova, E.M. Vasilyeva

Journal:

Journal of Cystic Fibrosis

Year:

2009

Language:

english

File:

PDF, 51 KB

english, 2009

427

Author Index

Journal:

Journal of Cystic Fibrosis

Year:

2009

File:

PDF, 86 KB

2009

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