D'Azzo, J.: search on Z-Library

The world's largest scientific articles store. 70,000,000+ articles for free.

Don't use scam websites

51

Three-dimensional structure of the human protective protein: structure of the precursor form suggests a complex activation mechanism

Gabby Rudenko, Erik Bonten, Alessandra d'Azzo, Wim GJ Hol

Journal:

Year:

1995

Language:

english

File:

PDF, 1.47 MB

english, 1995

52

Linear Control System Analysis and Design

D'Azzo, J., Houpis, C., Brunson, Richard L.

Journal:

IEEE Transactions on Systems Man and Cybernetics

Year:

1976

Language:

english

File:

PDF, 395 KB

english, 1976

53

GLB1 new polymorphism interferes with the residual enzymatic activity of mutated β-galactosidase

A Caciotti, T Bardelli, A D'azzo, E Zammarchi, A Morrone

Journal:

Acta Paediatrica

Year:

2002

Language:

english

File:

PDF, 171 KB

english, 2002

54

A rapid and simple microfractionation method for the analysis of hexosaminidase A and B activities in small numbers of cultured (amniotic fluid) cells

A. D'azzo, A. Hoogeveen, H.A. De Wit-Verbeek

Journal:

Clinica Chimica Acta

Year:

1978

Language:

english

File:

PDF, 501 KB

english, 1978

55

Vacuolization and alterations of lysosomal membrane proteins in cochlear marginal cells contribute to hearing loss in neuraminidase 1-deficient mice

Xudong Wu, Katherine A. Steigelman, Erik Bonten, Huimin Hu, Wenxuan He, Tianying Ren, Jian Zuo, Alessandra d’Azzo

Journal:

Biochimica et Biophysica Acta (BBA) - Molecular Basis of Disease

Year:

2010

Language:

english

File:

PDF, 3.63 MB

english, 2010

56

Muscle degeneration in neuraminidase 1-deficient mice results from infiltration of the muscle fibers by expanded connective tissue

Edmar Zanoteli, Diantha van de Vlekkert, Erik J. Bonten, Huimin Hu, Linda Mann, Elida M. Gomero, A. John Harris, Giulio Ghersi, Alessandra d'Azzo

Journal:

Biochimica et Biophysica Acta (BBA) - Molecular Basis of Disease

Year:

2010

Language:

english

File:

PDF, 9.52 MB

english, 2010

57

Protective protein/cathepsin A rescues N-glycosylation defects in neuraminidase-1

Dongning Wang, Slava Zaitsev, Garry Taylor, Alessandra d'Azzo, Erik Bonten

Journal:

Biochimica et Biophysica Acta (BBA) - General Subjects

Year:

2009

Language:

english

File:

PDF, 1.17 MB

english, 2009

58

GM1-ganglioside degradation and biosynthesis in human and murine GM1-gangliosidosis

Renata Sano, Vera M.T. Trindade, Alessandra Tessitore, Alessandra d'Azzo, Matheus B. Vieira, Roberto Giugliani, Janice C. Coelho

Journal:

Clinica Chimica Acta

Year:

2005

Language:

english

File:

PDF, 164 KB

english, 2005

59

Neuraminidase 1 Is a Negative Regulator of Lysosomal Exocytosis

Gouri Yogalingam, Erik J. Bonten, Diantha van de Vlekkert, Huimin Hu, Simon Moshiach, Samuel A. Connell, Alessandra d'Azzo

Journal:

Developmental Cell

Year:

2008

Language:

english

File:

PDF, 1.80 MB

english, 2008

60

GM1-Ganglioside-Mediated Activation of the Unfolded Protein Response Causes Neuronal Death in a Neurodegenerative Gangliosidosis

Alessandra Tessitore, Maria del P. Martin, Renata Sano, Yanjun Ma, Linda Mann, Angela Ingrassia, Eric D. Laywell, Dennis A. Steindler, Linda M. Hendershot, Alessandra d'Azzo

Journal:

Year:

2004

Language:

english

File:

PDF, 801 KB

english, 2004

61

GM1-Ganglioside Accumulation at the Mitochondria-Associated ER Membranes Links ER Stress to Ca2+-Dependent Mitochondrial Apoptosis

Renata Sano, Ida Annunziata, Annette Patterson, Simon Moshiach, Elida Gomero, Joseph Opferman, Michael Forte, Alessandra d'Azzo

Journal:

Year:

2009

Language:

english

File:

PDF, 1.84 MB

english, 2009

62

G.P.5 05 Skeletal muscle involvement in neuraminidase deficient mice

E. Zanoteli, G. Yogalingam, H. Hu, E. Bonten, A. d’Azzo

Journal:

Neuromuscular Disorders

Year:

2006

Language:

english

File:

PDF, 47 KB

english, 2006

63

G.P.19.10 Ozz-E3 ligase expression during muscle regeneration

E. Zanoteli, Y. Campos, N. Vergani, X. Qiu, K. Oberoi, H. Hu, L. Mann, A. d’Azzo

Journal:

Neuromuscular Disorders

Year:

2007

Language:

english

File:

PDF, 62 KB

english, 2007

64

G.P.19.09 The role of neuraminidase 1 in muscle atrophy

E. Zanoteli, E. Bonten, D. van de Vlekkert, L. Mann, A. d’Azzo

Journal:

Neuromuscular Disorders

Year:

2007

Language:

english

File:

PDF, 46 KB

english, 2007

65

P5.66 The role of Neuraminidase 1 on skeletal muscle regeneration

J.C. Neves, V.R. Rizzato, A. Fappi, T.S. Godoy, G.O. Xavier, G. Chadi, E. Bonten, D. van de Vlekkert, A. d‘Azzo, E. Zanoteli

Journal:

Neuromuscular Disorders

Year:

2011

Language:

english

File:

PDF, 48 KB

english, 2011

66

New mutations in the PPBG gene lead to loss of PPCA protein which affects the level of the β-galactosidase/neuraminidase complex and the EBP-receptor

Sabrina Malvagia, Amelia Morrone, Anna Caciotti, Tiziana Bardelli, Alessandra d’Azzo, Gina Ancora, Enrico Zammarchi, Maria Alice Donati

Journal:

Molecular Genetics and Metabolism

Year:

2004

Language:

english

File:

PDF, 752 KB

english, 2004

67

Short-term, high dose enzyme replacement therapy in sialidosis mice

Dongning Wang, Erik J. Bonten, Gouri Yogalingam, Linda Mann, Alessandra d’Azzo

Journal:

Molecular Genetics and Metabolism

Year:

2005

Language:

english

File:

PDF, 1.96 MB

english, 2005

68

Beneficial effects of substrate reduction therapy in a mouse model of GM1 gangliosidosis

Elena Elliot-Smith, Anneliese O. Speak, Emyr Lloyd-Evans, David A. Smith, Aarnoud C. van der Spoel, Mylvaganam Jeyakumar, Terry D. Butters, Raymond A. Dwek, Alessandra d’Azzo, Frances M. Platt

Journal:

Molecular Genetics and Metabolism

Year:

2008

Language:

english

File:

PDF, 835 KB

english, 2008

69

35. NEU1 is a negative regulator of lysosomal exocytosis

Alessandra d’Azzo, Erik Bonten, Diantha Van de Vlekkert, Gouri Yogalingam

Journal:

Molecular Genetics and Metabolism

Year:

2009

Language:

english

File:

PDF, 42 KB

english, 2009

70

6. Accumulation of GM1-ganglioside in ER-mitochondrion microdomains elicits mitochondrial Ca2+ overload and neuronal apoptosis

Ida Annunziata, Renata Sano, Annette Patterson, Alessandra d’Azzo

Journal:

Molecular Genetics and Metabolism

Year:

2009

Language:

english

File:

PDF, 44 KB

english, 2009

71

Emphysema in an adult with galactosialidosis linked to a defect in primary elastic fiber assembly

Anna Lehman, Andre Mattman, Don Sin, Peter Pare, Zheyuan Zong, Alessandra d'Azzo, Yvan Campos, Sandra Sirrs, Aleksander Hinek

Journal:

Molecular Genetics and Metabolism

Year:

2012

Language:

english

File:

PDF, 668 KB

english, 2012

72

Primary and Secondary Elastin-Binding Protein Defect Leads to Impaired Elastogenesis in Fibroblasts from GM1-Gangliosidosis Patients

Anna Caciotti, Maria Alice Donati, Tiziana Bardelli, Alessandra d'Azzo, Graziella Massai, Luciana Luciani, Enrico Zammarchi, Amelia Morrone

Journal:

The American Journal of Pathology

Year:

2005

Language:

english

File:

PDF, 772 KB

english, 2005

73

New mutations in two Dutch patients with early infantile galactosialidosis

J Groener, P Maaswinkel-Mooy, V Smit, M.v.d Hoeven, J Bakker, Y Campos, A d’Azzo

Journal:

Molecular Genetics and Metabolism

Year:

2003

Language:

english

File:

PDF, 347 KB

english, 2003

74

Ozz-E3, A Muscle-Specific Ubiquitin Ligase, Regulates β-Catenin Degradation during Myogenesis

Tommaso Nastasi, Antonella Bongiovanni, Yvan Campos, Linda Mann, James N Toy, Jake Bostrom, Robbert Rottier, Christopher Hahn, Joan Weliky Conaway, A.John Harris, Alessandra d'Azzo

Journal:

Developmental Cell

Year:

2004

Language:

english

File:

PDF, 1.02 MB

english, 2004

75

A low complexity partial transmit sequence scheme by use of dummy signals for PAPR reduction in OFDM systems

Varahram, P., Al-Azzo, W.F., Ali, B.M.

Journal:

IEEE Transactions on Consumer Electronics

Year:

2010

Language:

english

File:

PDF, 313 KB

english, 2010

76

Correction of combined β-galactosidase/neuraminidase deficiency in human fibroblasts

André Hoogeveen, Alessandra d'Azzo, Reinhard Brossmer, Hans Galjaard

Journal:

Biochemical and Biophysical Research Communications

Year:

1981

Language:

english

File:

PDF, 512 KB

english, 1981

77

Fusion with enucleated fibroblasts corrects “I-cell” defect

A. D'Azzo, A. Konings, A. Verkerk, J.F. Jongkind, H. Galjaard

Journal:

Experimental Cell Research

Year:

1980

Language:

english

File:

PDF, 1.07 MB

english, 1980

78

Intercellular exchange of lysosomal hydrolases between mutant human fibroblasts and other cell types

D.J.J. Halley, N. Sacchi, A. d'Azzo, A.J.J. Reuser, H. Galjaard

Journal:

Experimental Cell Research

Year:

1980

Language:

english

File:

PDF, 1.67 MB

english, 1980

79

Isolation and expression of full length cDNA clone of human airway smooth muscle mannose receptor (ASM-MR)

Zhao, Yuling, Bonten, Erik, D'Azzo, Alessandra, Lew, Betty

Journal:

Journal of Allergy and Clinical Immunology

Year:

2002

Language:

english

File:

PDF, 136 KB

english, 2002

80

The Gene for Human Peptidase A is on Band 18q23 and Shows Triplex and Uniplex Dosage Effect

C. Danesino, Alessandra D'Azzo, Paola Maraschio, M. Fraccaro

Journal:

Clinical Genetics

Year:

1978

Language:

english

File:

PDF, 75 KB

english, 1978

81

Non-progressive psychomotor retardation in a child with severe deficiency of arylsulphatase A activity

C. DANESINO, ALESSANDRA 'AZZO, M. ARICA, A. F. PODESTA, G. BELUFFI, ELENA BIANCHI

Journal:

Clinical Genetics

Year:

1984

Language:

english

File:

PDF, 686 KB

english, 1984

82

Structural Alterations of Epididymal Epithelial Cells in Cathepsin A Deficient Mice Affect the Blood-Epididymal Barrier and Lead to Altered Sperm Motility

Hermo, L., Korah, N., Gregory, M., Liu, L. Y., Cyr, D. G., D'Azzo, A., Smith, C. E.

Journal:

Journal of Andrology

Year:

2007

Language:

english

File:

PDF, 3.82 MB

english, 2007

83

A Reconfigurable Direct RF Receiver With Jitter Analysis and Applications

Fudge, Gerald L., Azzo, Hamid M., Boyle, Frank A.

Journal:

IEEE Transactions on Circuits and Systems I Fundamental Theory and Applications

Year:

2013

Language:

english

File:

PDF, 1.82 MB

english, 2013

84

Closed-loop eigenstructure assignment by state feedback in multivariable linear systems

PORTER, B., D'AZZO, J. J.

Journal:

International Journal of Control

Year:

1978

Language:

english

File:

PDF, 154 KB

english, 1978

85

Mitochondria-associated ER Membranes (MAMs) and Glycosphingolipid Enriched Microdomains (GEMs): Isolation from Mouse Brain

Annunziata, Ida, Patterson, Annette, d'Azzo, Alessandra

Journal:

Journal of Visualized Experiments

Year:

2013

Language:

english

File:

PDF, 154 KB

english, 2013

86

A common structure for the potexviruses

Kendall, Amy, Bian, Wen, Maris, Alexander, Azzo, Caitlin, Groom, Joseph, Williams, Dewight, Shi, Jian, Stewart, Phoebe L., Wall, Joseph S., Stubbs, Gerald

Journal:

Year:

2013

Language:

english

File:

PDF, 740 KB

english, 2013

87

Identification and characterization of the nano-sized vesicles released by muscle cells

Romancino, Daniele P., Paterniti, Gaetano, Campos, Yvan, De Luca, Angela, Di Felice, Valentina, d’Azzo, Alessandra, Bongiovanni, Antonella

Journal:

Year:

2013

Language:

english

File:

PDF, 824 KB

english, 2013

88

Proportional and integral control of nonlinear systems

PACHTER, M., D'AZZO, J. J., VETH, M.

Journal:

International Journal of Control

Year:

1996

Language:

english

File:

PDF, 205 KB

english, 1996

89

Lysosomal multienzyme complex: pros and cons of working together

Bonten, Erik J., Annunziata, Ida, d’Azzo, Alessandra

Journal:

Cellular and Molecular Life Sciences

Year:

2014

Language:

english

File:

PDF, 759 KB

english, 2014

90

[IEEE IEEE National Aerospace and Electronics Conference - Dayton, OH, USA (22-26 May 1989)] Proceedings of the IEEE National Aerospace and Electronics Conference - Multivariable control design for the control reconfigurable combat aircraft (CRCA)

Hammond, D., D'Azzo, J.J.

Year:

1989

Language:

english

File:

PDF, 463 KB

english, 1989

91

Expression of cDNA encoding the human “protective protein≓ associated with lysosomal β-galactosidase and neuraminidase: Homology to yeast proteases

Galjart, Niels J., Gillemans, Nynke, Harris, Alan, van der Horst, Gijsbertus T.J., Verheijen, Frans W., Galjaard, Hans, d'Azzo, Alessandra

Journal:

Year:

1988

Language:

english

File:

PDF, 1.41 MB

english, 1988

92

The gene encoding human protective protein (PPGB) is on chromosome 20

Wiegant, Joop, Galjart, Niels J., Raap, Anton K., d'Azzo, Alessandra

Journal:

Year:

1991

Language:

english

File:

PDF, 12.21 MB

english, 1991

93

Chaperone-mediated gene therapy with recombinant AAV-PPCA in a new mouse model of type I sialidosis

Bonten, Erik J., Yogalingam, Gouri, Hu, Huimin, Gomero, Elida, van de Vlekkert, Diantha, d'Azzo, Alessandra

Journal:

Biochimica et Biophysica Acta (BBA) - Molecular Basis of Disease

Year:

2013

Language:

english

File:

PDF, 1.65 MB

english, 2013

94

[Part 1: Biological Sciences] || Molecular Defect in Combined β -galactosidase and Neuraminidase Deficiency in Man

A. D'Azzo, A. Hoogeveen, A. J. J. Reuser, D. Robinson and H. Galjaard

Journal:

Proceedings of the National Academy of Sciences

Year:

1982

Language:

english

File:

PDF, 1.58 MB

english, 1982

95

The Atomic Model of the Human Protective Protein/Cathepsin A Suggests a Structural Basis for Galactosialidosis

Gabby Rudenko, Erik Bonten, Wim G. J. Hol and Alessandra d'Azzo

Journal:

Proceedings of the National Academy of Sciences

Year:

1998

Language:

english

File:

PDF, 1.54 MB

english, 1998

96

Correction of Murine Galactosialidosis by Bone Marrow-Derived Macrophages Overexpressing Human Protective Protein/Cathepsin A under Control of the Colony-Stimulating Factor-1 Receptor Promoter

Christopher N. Hahn, Maria Del Pilar Martin, Xiao-Yan Zhou, Linda W. Mann and Alessandra d'Azzo

Journal:

Proceedings of the National Academy of Sciences

Year:

1998

Language:

english

File:

PDF, 2.20 MB

english, 1998

97

[American Institute of Aeronautics and Astronautics Guidance, Navigation, and Control Conference - Scottsdale,AZ,U.S.A. (01 August 1994 - 03 August 1994)] Guidance, Navigation, and Control Conference - Formation flight control automation

Reyna, V., Pachter, M., D'Azzo, J.

Year:

1994

Language:

english

File:

PDF, 2.87 MB

english, 1994

98

[IEEE 34th Midwest Symposium on Circuits and Systems - Monterey, CA, USA (14-17 May 1991)] [1991] Proceedings of the 34th Midwest Symposium on Circuits and Systems - Output feedback stabilization of uncertain linear systems

Azzo, A.H., Sawan, M.E.

Year:

1992

Language:

english

File:

PDF, 187 KB

english, 1992

99

An automatic root locus plotter using an analog computer

Liethen, F. E., Houpis, C. H., D'azzo, J. J.

Journal:

Transactions of the American Institute of Electrical Engineers, Part II: Applications and Industry

Year:

1961

Language:

english

File:

PDF, 1.54 MB

english, 1961

100

[IEEE 2007 Asia-Pacific Conference on Communications - Bangkok, Thailand (2007.10.18-2007.10.20)] 2007 Asia-Pacific Conference on Communications - Time domain statistical control for PAPR reduction in OFDM system

Al-Azzo, Wisam F., Borhanuddin Mohd. Ali,, Sabira Khatun,, Sayed Jamalullail,

Year:

2007

Language:

english

File:

PDF, 1.56 MB

english, 2007