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Pathogenic VCP/TER94 Alleles Are Dominant Actives and Contribute to Neurodegeneration by Altering Cellular ATP Level in a Drosophila IBMPFD Model
Chang, Ya-Chu, Hung, Wan-Tzu, Chang, Yun-Chin, Chang, Henry C., Wu, Chia-Lin, Chiang, Ann-Shyn, Jackson, George R., Sang, Tzu-Kang, Frankel, Wayne N.Volume:
7
Language:
english
Journal:
PLoS Genetics
DOI:
10.1371/journal.pgen.1001288
Date:
February, 2011
File:
PDF, 12.27 MB
english, 2011